U.S. flag

An official website of the United States government

Format

Send to:

Choose Destination

Spindle cell rhabdomyosarcoma

MedGen UID:
224766
Concept ID:
C1266134
Neoplastic Process
Synonyms: SCRMS; Spindle Cell Rhabdomyosarcoma; spindle cell rhabdomyosarcoma; spindle cell rhabdomyosarcoma (morphologic abnormality)
SNOMED CT: Spindle cell rhabdomyosarcoma (404055006); Spindle cell rhabdomyosarcoma (128749008)
 
Monarch Initiative: MONDO:0002581

Definition

An uncommon variant of rhabdomyosarcoma characterized by the presence of whorls of spindle cells forming a storiform pattern. In children it usually arises in the paratesticular region. In adults it usually arises from the deep soft tissues in the head and neck. [from NCI]

Professional guidelines

PubMed

Ahmeti H, Jüttner E, Röcken C, Jansen O, Laudes M, Synowitz M
J Neurol Surg A Cent Eur Neurosurg 2023 May;84(3):295-299. Epub 2021 Nov 15 doi: 10.1055/s-0041-1735857. PMID: 34781400
Parham DM
F1000Res 2018;7 Epub 2018 Dec 20 doi: 10.12688/f1000research.16236.1. PMID: 30613391Free PMC Article
Carroll SJ, Nodit L
Arch Pathol Lab Med 2013 Aug;137(8):1155-8. doi: 10.5858/arpa.2012-0465-RS. PMID: 23899074

Recent clinical studies

Etiology

Han R, Dermawan JK, Demicco EG, Ferguson PC, Griffin AM, Swanson D, Antonescu CR, Dickson BC
Genes Chromosomes Cancer 2022 Nov;61(11):645-652. Epub 2022 May 20 doi: 10.1002/gcc.23052. PMID: 35521817Free PMC Article
Agaram NP, LaQuaglia MP, Alaggio R, Zhang L, Fujisawa Y, Ladanyi M, Wexler LH, Antonescu CR
Mod Pathol 2019 Jan;32(1):27-36. Epub 2018 Sep 4 doi: 10.1038/s41379-018-0120-9. PMID: 30181563Free PMC Article
Zhao Z, Yin Y, Zhang J, Qi J, Zhang D, Ma Y, Wang Y, Li S, Zhou J
Int J Clin Exp Pathol 2015;8(11):13814-20. Epub 2015 Nov 1 PMID: 26823695Free PMC Article
Yasui N, Yoshida A, Kawamoto H, Yonemori K, Hosono A, Kawai A
Pediatr Blood Cancer 2015 Jun;62(6):1011-6. Epub 2014 Dec 31 doi: 10.1002/pbc.25367. PMID: 25557260
Parham DM, Ellison DA
Arch Pathol Lab Med 2006 Oct;130(10):1454-65. doi: 10.5858/2006-130-1454-RIAACA. PMID: 17090187

Diagnosis

Han R, Dermawan JK, Demicco EG, Ferguson PC, Griffin AM, Swanson D, Antonescu CR, Dickson BC
Genes Chromosomes Cancer 2022 Nov;61(11):645-652. Epub 2022 May 20 doi: 10.1002/gcc.23052. PMID: 35521817Free PMC Article
Whittle S, Venkatramani R, Schönstein A, Pack SD, Alaggio R, Vokuhl C, Rudzinski ER, Wulf AL, Zin A, Gruver JR, Arnold MA, Merks JHM, Hettmer S, Koscielniak E, Barr FG, Hawkins DS, Bisogno G, Sparber-Sauer M
Eur J Cancer 2022 Jun;168:56-64. Epub 2022 Apr 19 doi: 10.1016/j.ejca.2022.03.022. PMID: 35452896Free PMC Article
Chrisinger JSA, Wehrli B, Dickson BC, Fasih S, Hirbe AC, Shultz DB, Zadeh G, Gupta AA, Demicco EG
Virchows Arch 2020 Nov;477(5):725-732. Epub 2020 Jun 19 doi: 10.1007/s00428-020-02870-0. PMID: 32556562
Carroll SJ, Nodit L
Arch Pathol Lab Med 2013 Aug;137(8):1155-8. doi: 10.5858/arpa.2012-0465-RS. PMID: 23899074
Mentrikoski MJ, Golden W, Bourne TD, Legallo R
Pediatr Dev Pathol 2013 Jan-Feb;16(1):35-8. Epub 2012 Oct 31 doi: 10.2350/12-04-1180-CR.1. PMID: 23113671

Therapy

Whittle SB, Hicks MJ, Roy A, Vasudevan SA, Reddy K, Venkatramani R
Pediatr Blood Cancer 2019 Nov;66(11):e27935. Epub 2019 Jul 24 doi: 10.1002/pbc.27935. PMID: 31339226
Gui H, Lhospital E, Staddon AP, Nagda SN, Zager EL, Zhang PJL, Brooks JS
Int J Surg Pathol 2019 May;27(3):328-335. Epub 2018 Oct 1 doi: 10.1177/1066896918802030. PMID: 30270691
Wu TT, Wang QY, Zhou SH, Zheng ZJ
Int J Clin Exp Pathol 2014;7(8):5254-8. Epub 2014 Jul 15 PMID: 25197406Free PMC Article
Latz S, Ellinger J, Goltz D, Marx C, Leuschner I, Müller SC, Fechner G
Int J Urol 2013 Sep;20(9):935-7. Epub 2013 Jan 16 doi: 10.1111/iju.12082. PMID: 23320845
Goosens V, Van den Berghe I, De Clercq C, Casselman J
Int J Oral Maxillofac Surg 2008 Apr;37(4):395-7. Epub 2007 Nov 26 doi: 10.1016/j.ijom.2007.09.173. PMID: 18023143

Prognosis

Whittle S, Venkatramani R, Schönstein A, Pack SD, Alaggio R, Vokuhl C, Rudzinski ER, Wulf AL, Zin A, Gruver JR, Arnold MA, Merks JHM, Hettmer S, Koscielniak E, Barr FG, Hawkins DS, Bisogno G, Sparber-Sauer M
Eur J Cancer 2022 Jun;168:56-64. Epub 2022 Apr 19 doi: 10.1016/j.ejca.2022.03.022. PMID: 35452896Free PMC Article
Chrisinger JSA, Wehrli B, Dickson BC, Fasih S, Hirbe AC, Shultz DB, Zadeh G, Gupta AA, Demicco EG
Virchows Arch 2020 Nov;477(5):725-732. Epub 2020 Jun 19 doi: 10.1007/s00428-020-02870-0. PMID: 32556562
Whittle SB, Hicks MJ, Roy A, Vasudevan SA, Reddy K, Venkatramani R
Pediatr Blood Cancer 2019 Nov;66(11):e27935. Epub 2019 Jul 24 doi: 10.1002/pbc.27935. PMID: 31339226
Yasui N, Yoshida A, Kawamoto H, Yonemori K, Hosono A, Kawai A
Pediatr Blood Cancer 2015 Jun;62(6):1011-6. Epub 2014 Dec 31 doi: 10.1002/pbc.25367. PMID: 25557260
Carroll SJ, Nodit L
Arch Pathol Lab Med 2013 Aug;137(8):1155-8. doi: 10.5858/arpa.2012-0465-RS. PMID: 23899074

Clinical prediction guides

Hornick JL, Nielsen GP
Am J Surg Pathol 2019 Oct;43(10):1323-1330. doi: 10.1097/PAS.0000000000001290. PMID: 31107719
Jo VY, Mariño-Enríquez A, Fletcher CDM, Hornick JL
Am J Surg Pathol 2018 Oct;42(10):1275-1285. doi: 10.1097/PAS.0000000000001092. PMID: 29863547
Hung YP, Fletcher CD, Hornick JL
Am J Surg Pathol 2017 May;41(5):596-606. doi: 10.1097/PAS.0000000000000795. PMID: 28009608
Zhao Z, Yin Y, Zhang J, Qi J, Zhang D, Ma Y, Wang Y, Li S, Zhou J
Int J Clin Exp Pathol 2015;8(11):13814-20. Epub 2015 Nov 1 PMID: 26823695Free PMC Article
Fernando Val-Bernal J, Fernández N, Gómez-Román JJ
Pathol Res Pract 2000;196(1):67-72. doi: 10.1016/s0344-0338(00)80024-2. PMID: 10674275

Supplemental Content

Table of contents

    Clinical resources

    Practice guidelines

    • PubMed
      See practice and clinical guidelines in PubMed. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.
    • Bookshelf
      See practice and clinical guidelines in NCBI Bookshelf. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.

    Consumer resources

    Recent activity

    Your browsing activity is empty.

    Activity recording is turned off.

    Turn recording back on

    See more...