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Central Nervous System Paraganglioma

MedGen UID:
232042
Concept ID:
C1332890
Neoplastic Process
Synonyms: CNS Paraganglioma; Paraganglioma of Central Nervous System; Paraganglioma of CNS; Paraganglioma of the Central Nervous System; Paraganglioma of the CNS

Definition

An extra-adrenal paraganglioma arising from the central nervous system. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVCentral Nervous System Paraganglioma

Professional guidelines

PubMed

Laks S, van Leeuwaarde R, Patel D, Keutgen XM, Hammel P, Nilubol N, Links TP, Halfdanarson TR, Daniels AB, Tirosh A; Pancreatic Manifestations Recommendations Development Subcommittee of the VHL Alliance
Cancer 2022 Feb 1;128(3):435-446. Epub 2021 Nov 4 doi: 10.1002/cncr.33978. PMID: 34735022
Jindal G, Miller T, Raghavan P, Gandhi D
Radiol Clin North Am 2017 Jan;55(1):151-166. Epub 2016 Oct 25 doi: 10.1016/j.rcl.2016.08.003. PMID: 27890183
Kamoun M, Mnif MF, Charfi N, Kacem FH, Naceur BB, Mnif F, Dammak M, Rekik N, Abid M
Am J Med Sci 2014 Jan;347(1):64-73. doi: 10.1097/MAJ.0b013e31828aaeee. PMID: 23514671

Recent clinical studies

Etiology

Laks S, van Leeuwaarde R, Patel D, Keutgen XM, Hammel P, Nilubol N, Links TP, Halfdanarson TR, Daniels AB, Tirosh A; Pancreatic Manifestations Recommendations Development Subcommittee of the VHL Alliance
Cancer 2022 Feb 1;128(3):435-446. Epub 2021 Nov 4 doi: 10.1002/cncr.33978. PMID: 34735022
Dénes J, Korbonits M
Endocrine 2021 Mar;71(3):663-674. Epub 2021 Feb 4 doi: 10.1007/s12020-021-02633-0. PMID: 33543431Free PMC Article
Rednam SP, Erez A, Druker H, Janeway KA, Kamihara J, Kohlmann WK, Nathanson KL, States LJ, Tomlinson GE, Villani A, Voss SD, Schiffman JD, Wasserman JD
Clin Cancer Res 2017 Jun 15;23(12):e68-e75. doi: 10.1158/1078-0432.CCR-17-0547. PMID: 28620007
Barontini M, Dahia PL
Best Pract Res Clin Endocrinol Metab 2010 Jun;24(3):401-13. doi: 10.1016/j.beem.2010.01.002. PMID: 20833332
Erlic Z, Neumann HP
Hormones (Athens) 2009 Jan-Mar;8(1):29-38. doi: 10.14310/horm.2002.1219. PMID: 19269919

Diagnosis

Toledo RA, Jimenez C, Armaiz-Pena G, Arenillas C, Capdevila J, Dahia PLM
Endocr Rev 2023 Mar 4;44(2):312-322. doi: 10.1210/endrev/bnac025. PMID: 36301191Free PMC Article
Laks S, van Leeuwaarde R, Patel D, Keutgen XM, Hammel P, Nilubol N, Links TP, Halfdanarson TR, Daniels AB, Tirosh A; Pancreatic Manifestations Recommendations Development Subcommittee of the VHL Alliance
Cancer 2022 Feb 1;128(3):435-446. Epub 2021 Nov 4 doi: 10.1002/cncr.33978. PMID: 34735022
Erlic Z, Neumann HP
Hormones (Athens) 2009 Jan-Mar;8(1):29-38. doi: 10.14310/horm.2002.1219. PMID: 19269919
Mann SJ
Curr Hypertens Rep 2008 Feb;10(1):12-8. doi: 10.1007/s11906-008-0005-2. PMID: 18367021
Maher ER, Kaelin WG Jr
Medicine (Baltimore) 1997 Nov;76(6):381-91. doi: 10.1097/00005792-199711000-00001. PMID: 9413424

Therapy

Deeks ED
Drugs 2021 Nov;81(16):1921-1927. doi: 10.1007/s40265-021-01606-x. PMID: 34613603
Salama Y, Albanyan S, Szybowska M, Bullivant G, Gallinger B, Giles RH, Asa S, Badduke C, Chiorean A, Druker H, Ezzat S, Hannah-Shmouni F, Hernandez KG, Inglese C, Jani P, Kaur Y, Krema H, Krimus L, Laperriere N, Lichner Z, Mete O, Sit M, Zadeh G, Jewett MAS, Malkin D, Stockley T, Wasserman JD, Xu W, Schachter NF, Kim RH
Clin Genet 2019 Nov;96(5):461-467. Epub 2019 Aug 6 doi: 10.1111/cge.13613. PMID: 31368132
Chondrogiannis S, Marzola MC, Rubello D
PET Clin 2014 Jul;9(3):307-21. Epub 2014 Apr 29 doi: 10.1016/j.cpet.2014.03.007. PMID: 25030394
van Hulsteijn LT, Corssmit EP, Coremans IE, Smit JW, Jansen JC, Dekkers OM
Radiother Oncol 2013 Feb;106(2):161-8. Epub 2013 Jan 16 doi: 10.1016/j.radonc.2012.11.002. PMID: 23332889
Mann SJ
Curr Hypertens Rep 2008 Feb;10(1):12-8. doi: 10.1007/s11906-008-0005-2. PMID: 18367021

Prognosis

Reich M, Jaegle S, Neumann-Haefelin E, Klingler JH, Evers C, Daniel M, Bucher F, Ludwig F, Nuessle S, Kopp J, Boehringer D, Reinhard T, Lagrèze WA, Lange C, Agostini H, Lang SJ
Acta Ophthalmol 2021 Dec;99(8):e1492-e1500. Epub 2021 Mar 15 doi: 10.1111/aos.14843. PMID: 33720516
Popp I, Weber WA, Combs SE, Yuh WTC, Grosu AL
Top Magn Reson Imaging 2019 Apr;28(2):63-71. doi: 10.1097/RMR.0000000000000198. PMID: 31022049
Gossage L, Eisen T
Nat Rev Clin Oncol 2010 May;7(5):277-88. Epub 2010 Apr 6 doi: 10.1038/nrclinonc.2010.42. PMID: 20368728
Suárez C, Sevilla MA, Llorente JL
Eur Arch Otorhinolaryngol 2007 Jul;264(7):719-31. Epub 2007 Mar 2 doi: 10.1007/s00405-007-0267-3. PMID: 17333230
Antonelli NM, Dotters DJ, Katz VL, Kuller JA
Obstet Gynecol Surv 1996 Feb;51(2):125-34. doi: 10.1097/00006254-199602000-00022. PMID: 8622836

Clinical prediction guides

Vetrano IG, Gioppo A, Faragò G, Pinzi V, Pollo B, Broggi M, Schiariti M, Ferroli P, Acerbi F
Adv Exp Med Biol 2023;1405:377-403. doi: 10.1007/978-3-031-23705-8_14. PMID: 37452946
Toledo RA, Jimenez C, Armaiz-Pena G, Arenillas C, Capdevila J, Dahia PLM
Endocr Rev 2023 Mar 4;44(2):312-322. doi: 10.1210/endrev/bnac025. PMID: 36301191Free PMC Article
Szalat A, Oleinikov K, Nahmias A, Meiner V, Ben-Haim S, Atlan K, Lev-Cohain N, Appelbaum L, Gomori M, Mazeh H, Khalaileh A, Pe'er J, Lossos A, Shoshan Y, Grozinsky-Glasberg S, Gross DJ
Endocr Pract 2020 Oct;26(10):1131-1142. doi: 10.4158/EP-2020-0220. PMID: 33471715
Salama Y, Albanyan S, Szybowska M, Bullivant G, Gallinger B, Giles RH, Asa S, Badduke C, Chiorean A, Druker H, Ezzat S, Hannah-Shmouni F, Hernandez KG, Inglese C, Jani P, Kaur Y, Krema H, Krimus L, Laperriere N, Lichner Z, Mete O, Sit M, Zadeh G, Jewett MAS, Malkin D, Stockley T, Wasserman JD, Xu W, Schachter NF, Kim RH
Clin Genet 2019 Nov;96(5):461-467. Epub 2019 Aug 6 doi: 10.1111/cge.13613. PMID: 31368132
Gossage L, Eisen T
Nat Rev Clin Oncol 2010 May;7(5):277-88. Epub 2010 Apr 6 doi: 10.1038/nrclinonc.2010.42. PMID: 20368728

Recent systematic reviews

Kakodkar P, Houlihan LM, Preul M, Bermingham N, Lim C
Br J Neurosurg 2023 Oct;37(5):967-975. Epub 2021 Mar 19 doi: 10.1080/02688697.2021.1902477. PMID: 33739182
Bessis D, Bigorre M, Malissen N, Captier G, Chiaverini C, Abasq C, Barbarot S, Boccara O, Bourrat E, El Fertit H, Eschard C, Hubiche T, Lacour JP, Leboucq N, Mahé E, Mallet S, Marque M, Martin L, Mazereeuw-Hautier J, Milla N, Phan A, Plantin P, Picot MC, Puzenat E, Rigau V, Vabres P, Fraitag S, Boralevi F; Groupe de Recherche Clinique en Dermatologie Pédiatrique
J Am Acad Dermatol 2017 Mar;76(3):478-487. Epub 2016 Oct 11 doi: 10.1016/j.jaad.2016.08.046. PMID: 27742172
van Hulsteijn LT, Corssmit EP, Coremans IE, Smit JW, Jansen JC, Dekkers OM
Radiother Oncol 2013 Feb;106(2):161-8. Epub 2013 Jan 16 doi: 10.1016/j.radonc.2012.11.002. PMID: 23332889

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