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Cerebellopontine angle embryonal tumor

MedGen UID:
232045
Concept ID:
C1332904
Neoplastic Process
Synonyms: C-P angle PNET; C-P angle primitive neuroectodermal neoplasm; C-P angle primitive neuroectodermal tumor; C-P angle primitive neuroectodermal tumour; cerebellar Pontine angle PNET; cerebellar Pontine angle primitive neuroectodermal neoplasm; cerebellar Pontine angle primitive neuroectodermal tumor; cerebellar Pontine angle primitive neuroectodermal tumour; cerebellopontine angle embryonal tumor; Cerebellopontine Angle Embryonal Tumor, NOS; Cerebellopontine Angle Embryonal Tumor, Not Otherwise Specified; cerebellopontine angle PNET; cerebellopontine angle primitive neuroectodermal; cerebellopontine angle primitive neuroectodermal neoplasm; cerebellopontine angle primitive neuroectodermal tumor; cerebellopontine angle primitive neuroectodermal tumour; primitive neuroectodermal neoplasm of C-P angle; primitive neuroectodermal neoplasm of cerebellar Pontine angle; primitive neuroectodermal neoplasm of cerebellopontine angle; primitive neuroectodermal neoplasm of the C-P angle; primitive neuroectodermal neoplasm of the cerebellar Pontine angle; primitive neuroectodermal neoplasm of the cerebellopontine angle; primitive neuroectodermal tumor of C-P angle; primitive neuroectodermal tumor of cerebellar Pontine angle; primitive neuroectodermal tumor of cerebellopontine angle; primitive neuroectodermal tumor of the C-P angle; primitive neuroectodermal tumor of the cerebellar Pontine angle; primitive neuroectodermal tumor of the cerebellopontine angle; primitive neuroectodermal tumour of C-P angle; primitive neuroectodermal tumour of cerebellar Pontine angle; primitive neuroectodermal tumour of cerebellopontine angle; primitive neuroectodermal tumour of the C-P angle; primitive neuroectodermal tumour of the cerebellar Pontine angle; primitive neuroectodermal tumour of the cerebellopontine angle
 
Monarch Initiative: MONDO:0003141

Definition

A central nervous system embryonal tumor, not otherwise specified arising from the cerebellopontine angle of the infratentorial brain. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVCerebellopontine angle embryonal tumor

Professional guidelines

PubMed

Lassaletta L, Acle Cervera L, Altuna X, Amilibia Cabeza E, Arístegui Ruiz M, Batuecas Caletrio Á, Benítez Del Rosario J, Cabanillas Farpón R, Costales Marcos M, Escada P, Espinosa-Sánchez JM, García Leal R, Gavilán J, Gómez Martínez J, González-Aguado R, Martinez-Glez V, Guerra Jiménez G, Harguindey Antolí-Candela A, Hernández García BJ, Orús Dotú C, Polo López R, Manrique M, Martín Sanz E, Martínez Álvarez R, Martínez H, Martínez-Martínez M, Rey-Martinez J, Ropero Romero F, Santa Cruz Ruiz S, Vallejo LÁ, Soto Varela A, Varela-Nieto I, Morales Puebla JM
Acta Otorrinolaringol Esp (Engl Ed) 2024 Mar-Apr;75(2):108-128. Epub 2024 Feb 10 doi: 10.1016/j.otoeng.2023.10.005. PMID: 38346489
Halliday J, Rutherford SA, McCabe MG, Evans DG
Expert Rev Neurother 2018 Jan;18(1):29-39. Epub 2017 Nov 7 doi: 10.1080/14737175.2018.1399795. PMID: 29088993
Lin EP, Crane BT
AJNR Am J Neuroradiol 2017 Nov;38(11):2034-2043. Epub 2017 May 25 doi: 10.3174/ajnr.A5213. PMID: 28546250Free PMC Article

Recent clinical studies

Etiology

Dhayalan D, Tveiten ØV, Finnkirk M, Storstein A, Hufthammer KO, Goplen FK, Lund-Johansen M; V-REX Trial investigators
JAMA 2023 Aug 1;330(5):421-431. doi: 10.1001/jama.2023.12222. PMID: 37526718Free PMC Article
Nugroho SW, Anindya Y, Hafif M, Wicaksana BA, Desbassari F, Sadewo W, Perkasa SAH
Clin Neurol Neurosurg 2023 May;228:107683. Epub 2023 Mar 21 doi: 10.1016/j.clineuro.2023.107683. PMID: 37001475
Hobson CE, Saliba J, Vorasubin N, Lyles RH, Mastrodimos B, Cueva RA
Laryngoscope 2022 May;132(5):1093-1098. Epub 2021 Oct 27 doi: 10.1002/lary.29922. PMID: 34704617
Totten DJ, Manzoor NF, Perkins EL, Labadie RF, Bennett ML, Haynes DS
Laryngoscope 2021 Sep;131(9):2081-2087. Epub 2021 Feb 10 doi: 10.1002/lary.29434. PMID: 33567134
Toescu SM, Aquilina K
Curr Oncol Rep 2019 Jul 29;21(9):78. doi: 10.1007/s11912-019-0826-y. PMID: 31359299

Diagnosis

Jung T, Kim H, Jang M, Kim T, Lee DH, Shin JE, Kim CH
Acta Otolaryngol 2023 Nov-Dec;143(11-12):951-957. Epub 2024 Jan 26 doi: 10.1080/00016489.2023.2290202. PMID: 38108643
Dhayalan D, Tveiten ØV, Finnkirk M, Storstein A, Hufthammer KO, Goplen FK, Lund-Johansen M; V-REX Trial investigators
JAMA 2023 Aug 1;330(5):421-431. doi: 10.1001/jama.2023.12222. PMID: 37526718Free PMC Article
Chiaramonte C, Rabaste S, Jacquesson T, Meyronet D, Cotton F, Jouanneau E, Berhouma M
World Neurosurg 2018 Apr;112:18-24. Epub 2018 Jan 8 doi: 10.1016/j.wneu.2018.01.012. PMID: 29325939
Friedmann DR, Grobelny B, Golfinos JG, Roland JT Jr
Otolaryngol Clin North Am 2015 Jun;48(3):461-75. doi: 10.1016/j.otc.2015.02.006. PMID: 26043142
Carlson ML, Link MJ, Wanna GB, Driscoll CL
Otolaryngol Clin North Am 2015 Jun;48(3):407-22. Epub 2015 Apr 15 doi: 10.1016/j.otc.2015.02.003. PMID: 25886814

Therapy

Dhayalan D, Tveiten ØV, Finnkirk M, Storstein A, Hufthammer KO, Goplen FK, Lund-Johansen M; V-REX Trial investigators
JAMA 2023 Aug 1;330(5):421-431. doi: 10.1001/jama.2023.12222. PMID: 37526718Free PMC Article
Nugroho SW, Anindya Y, Hafif M, Wicaksana BA, Desbassari F, Sadewo W, Perkasa SAH
Clin Neurol Neurosurg 2023 May;228:107683. Epub 2023 Mar 21 doi: 10.1016/j.clineuro.2023.107683. PMID: 37001475
Ortiz García IM, Jorques Infante AM, Cordero Tous N, Almansa López J, Expósito Hernández J, Olivares Granados G
Neurocirugia (Astur : Engl Ed) 2023 Nov-Dec;34(6):283-291. Epub 2023 Feb 24 doi: 10.1016/j.neucie.2023.02.001. PMID: 36842609
Bin-Alamer O, Fogg D, Wei Z, Duehr J, Mallela AN, Niranjan A, Lunsford LD, Abou-Al-Shaar H
J Neurosurg 2023 Feb 1;138(2):413-419. Epub 2022 Jun 24 doi: 10.3171/2022.5.JNS22935. PMID: 35901754
Halliday J, Rutherford SA, McCabe MG, Evans DG
Expert Rev Neurother 2018 Jan;18(1):29-39. Epub 2017 Nov 7 doi: 10.1080/14737175.2018.1399795. PMID: 29088993

Prognosis

Nugroho SW, Anindya Y, Hafif M, Wicaksana BA, Desbassari F, Sadewo W, Perkasa SAH
Clin Neurol Neurosurg 2023 May;228:107683. Epub 2023 Mar 21 doi: 10.1016/j.clineuro.2023.107683. PMID: 37001475
Hobson CE, Saliba J, Vorasubin N, Lyles RH, Mastrodimos B, Cueva RA
Laryngoscope 2022 May;132(5):1093-1098. Epub 2021 Oct 27 doi: 10.1002/lary.29922. PMID: 34704617
Vinchon M, Leblond P
Neurochirurgie 2021 Feb;67(1):23-27. Epub 2019 Sep 5 doi: 10.1016/j.neuchi.2019.04.006. PMID: 31494131
Chiaramonte C, Rabaste S, Jacquesson T, Meyronet D, Cotton F, Jouanneau E, Berhouma M
World Neurosurg 2018 Apr;112:18-24. Epub 2018 Jan 8 doi: 10.1016/j.wneu.2018.01.012. PMID: 29325939
Chandler CL, Ramsden RT
Br J Hosp Med 1993 Mar 3-16;49(5):335-43. PMID: 8472085

Clinical prediction guides

Huo Z, Wang Z, Luo H, Maimaitiming D, Yang T, Liu H, Li H, Wu H, Zhang Z
Neuro Oncol 2024 Mar 4;26(3):444-457. doi: 10.1093/neuonc/noad201. PMID: 37862593Free PMC Article
Dhayalan D, Tveiten ØV, Finnkirk M, Storstein A, Hufthammer KO, Goplen FK, Lund-Johansen M; V-REX Trial investigators
JAMA 2023 Aug 1;330(5):421-431. doi: 10.1001/jama.2023.12222. PMID: 37526718Free PMC Article
Vinchon M, Leblond P
Neurochirurgie 2021 Feb;67(1):23-27. Epub 2019 Sep 5 doi: 10.1016/j.neuchi.2019.04.006. PMID: 31494131
Ramaswamy AT, Golub JS
Neuroimaging Clin N Am 2019 Feb;29(1):173-182. Epub 2018 Oct 31 doi: 10.1016/j.nic.2018.09.003. PMID: 30466639
Lin EP, Crane BT
AJNR Am J Neuroradiol 2017 Nov;38(11):2034-2043. Epub 2017 May 25 doi: 10.3174/ajnr.A5213. PMID: 28546250Free PMC Article

Recent systematic reviews

Nugroho SW, Anindya Y, Hafif M, Wicaksana BA, Desbassari F, Sadewo W, Perkasa SAH
Clin Neurol Neurosurg 2023 May;228:107683. Epub 2023 Mar 21 doi: 10.1016/j.clineuro.2023.107683. PMID: 37001475
Lasica N, Arnautovic K, Tadanori T, Vulekovic P, Kozic D
Sci Rep 2023 Mar 17;13(1):4442. doi: 10.1038/s41598-023-30677-x. PMID: 36932101Free PMC Article
Totten DJ, Manzoor NF, Perkins EL, Labadie RF, Bennett ML, Haynes DS
Laryngoscope 2021 Sep;131(9):2081-2087. Epub 2021 Feb 10 doi: 10.1002/lary.29434. PMID: 33567134
Pogoda L, Nijdam JS, Smeeing DPJ, Voormolen EHJ, Ziylan F, Thomeer HGXM
Eur Arch Otorhinolaryngol 2021 Oct;278(10):3643-3651. Epub 2021 Feb 1 doi: 10.1007/s00405-021-06627-6. PMID: 33523284Free PMC Article
Muzevic D, Legcevic J, Splavski B, Cayé-Thomasen P
Cochrane Database Syst Rev 2014 Dec 16;(12):CD009897. doi: 10.1002/14651858.CD009897.pub2. PMID: 25511415

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