U.S. flag

An official website of the United States government

Format

Send to:

Choose Destination

Childhood vagina botryoid rhabdomyosarcoma

MedGen UID:
232055
•Concept ID:
C1332945
•
Neoplastic Process
Synonyms: botryoid-type embryonal rhabdomyosarcoma of the vagina of childhood; Childhood Botryoid-Type Embryonal Rhabdomyosarcoma of the Vagina; childhood botryoid-type embryonal rhabdomyosarcoma of the vagina; Childhood Sarcoma Botryoides of the Vagina; childhood sarcoma Botryoides of the vagina; childhood vagina botryoid rhabdomyosarcoma; Childhood Vaginal Botryoid-Type Embryonal Rhabdomyosarcoma; Childhood Vaginal Embryonal Rhabdomyosarcoma; paediatric botryoid-type embryonal rhabdomyosarcoma of the vagina; pediatric botryoid-type embryonal rhabdomyosarcoma of the vagina; Vaginal Childhood Botryoid-Type Embryonal Rhabdomyosarcoma; vaginal childhood botryoid-type embryonal rhabdomyosarcoma; Vaginal Childhood Sarcoma Botryoides; vaginal childhood sarcoma Botryoides
 
Monarch Initiative: MONDO:0003993

Definition

A morphologic variant of embryonal rhabdomyosarcoma occurring in female children. The neoplasm arises from the vagina. It is characterized by the formation of a cambium layer in the affected tissue and polypoid nodules with an abundant myxoid stroma. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVChildhood vagina botryoid rhabdomyosarcoma

Professional guidelines

PubMed

Management of stage I cervical sarcoma botryoides in childhood and adolescence.
Gruessner SE, Omwandho CO, Dreyer T, Blütters-Sawatzki R, Reiter A, Tinneberg HR, Bohle RM
Eur J Pediatr 2004 Aug;163(8):452-6. Epub 2004 Jun 2 doi: 10.1007/s00431-004-1469-y. PMID: 15173941

Recent clinical studies

Etiology

Clinical Study on Female Genital Tract Rhabdomyosarcoma in Childhood: Changes During 20 Years in One Center.
Yang J, Yang J, Yu M, Yuan Z, Cao D, Keng S
Int J Gynecol Cancer 2017 Feb;27(2):311-314. doi: 10.1097/IGC.0000000000000872. PMID: 27870705
Rhabdomyosarcoma of the uterus in a postmenopausal patient.
Podczaski E, Sees J, Kaminski P, Sorosky J, Larson JE, DeGeest K, Zaino RJ, Mortel R
Gynecol Oncol 1990 Jun;37(3):439-42. doi: 10.1016/0090-8258(90)90384-w. PMID: 2190875

Diagnosis

Clinical Study on Female Genital Tract Rhabdomyosarcoma in Childhood: Changes During 20 Years in One Center.
Yang J, Yang J, Yu M, Yuan Z, Cao D, Keng S
Int J Gynecol Cancer 2017 Feb;27(2):311-314. doi: 10.1097/IGC.0000000000000872. PMID: 27870705
Sarcoma botryoides of the uterine cervix in a 46-year-old woman: case report and literature review.
Miyamoto T, Shiozawa T, Nakamura T, Konishi I
Int J Gynecol Pathol 2004 Jan;23(1):78-82. doi: 10.1097/01.pgp.0000101147.41312.54. PMID: 14668557
From the archives of the AFIP. Genitourinary rhabdomyosarcoma in children: radiologic-pathologic correlation.
Agrons GA, Wagner BJ, Lonergan GJ, Dickey GE, Kaufman MS
Radiographics 1997 Jul-Aug;17(4):919-37. doi: 10.1148/radiographics.17.4.9225391. PMID: 9225391
Embryonal rhabdomyosarcoma of the uterine corpus mistaken for small cell carcinoma: a case report.
Shu WH, Chang TC, Hsueh S, Kuo TT
Changgeng Yi Xue Za Zhi 1996 Jun;19(2):181-6. PMID: 8828263

Therapy

Management of stage I cervical sarcoma botryoides in childhood and adolescence.
Gruessner SE, Omwandho CO, Dreyer T, Blütters-Sawatzki R, Reiter A, Tinneberg HR, Bohle RM
Eur J Pediatr 2004 Aug;163(8):452-6. Epub 2004 Jun 2 doi: 10.1007/s00431-004-1469-y. PMID: 15173941

Prognosis

Clinical Study on Female Genital Tract Rhabdomyosarcoma in Childhood: Changes During 20 Years in One Center.
Yang J, Yang J, Yu M, Yuan Z, Cao D, Keng S
Int J Gynecol Cancer 2017 Feb;27(2):311-314. doi: 10.1097/IGC.0000000000000872. PMID: 27870705
From the archives of the AFIP. Genitourinary rhabdomyosarcoma in children: radiologic-pathologic correlation.
Agrons GA, Wagner BJ, Lonergan GJ, Dickey GE, Kaufman MS
Radiographics 1997 Jul-Aug;17(4):919-37. doi: 10.1148/radiographics.17.4.9225391. PMID: 9225391
Rhabdomyosarcoma of the uterus in a postmenopausal patient.
Podczaski E, Sees J, Kaminski P, Sorosky J, Larson JE, DeGeest K, Zaino RJ, Mortel R
Gynecol Oncol 1990 Jun;37(3):439-42. doi: 10.1016/0090-8258(90)90384-w. PMID: 2190875

Clinical prediction guides

Management of stage I cervical sarcoma botryoides in childhood and adolescence.
Gruessner SE, Omwandho CO, Dreyer T, Blütters-Sawatzki R, Reiter A, Tinneberg HR, Bohle RM
Eur J Pediatr 2004 Aug;163(8):452-6. Epub 2004 Jun 2 doi: 10.1007/s00431-004-1469-y. PMID: 15173941

Supplemental Content

Table of contents

    Clinical resources

    Practice guidelines

    • PubMed
      See practice and clinical guidelines in PubMed. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.
    • Bookshelf
      See practice and clinical guidelines in NCBI Bookshelf. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.

    Consumer resources

    Reviews

    Recent activity

    Clear Turn Off Turn On

    Your browsing activity is empty.

    Activity recording is turned off.

    Turn recording back on

    See more...