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Premalignant hematological system disease

MedGen UID:
233342
Concept ID:
C1335471
Disease or Syndrome
Synonyms: Premalignant Hematologic Condition; premalignant hematologic condition; premalignant hematological system disease
 
Monarch Initiative: MONDO:0060782

Definition

A hematologic disorder which does not display the morphologic and/or clinical characteristics of an overt malignancy. Representative examples include atypical lymphoproliferative disorders and myelodysplastic syndromes. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVPremalignant hematological system disease

Professional guidelines

PubMed

Musto P, Engelhardt M, Caers J, Bolli N, Kaiser M, Van de Donk N, Terpos E, Broijl A, De Larrea CF, Gay F, Goldschmidt H, Hajek R, Vangsted AJ, Zamagni E, Zweegman S, Cavo M, Dimopoulos M, Einsele H, Ludwig H, Barosi G, Boccadoro M, Mateos MV, Sonneveld P, Miguel JS
Haematologica 2021 Nov 1;106(11):2799-2812. doi: 10.3324/haematol.2021.278519. PMID: 34261295Free PMC Article
Mitsuyasu R
Clin Infect Dis 1999 Jul;29(1):35-43. doi: 10.1086/520177. PMID: 10433562
Fantasia JE
Dent Clin North Am 1997 Oct;41(4):877-90. PMID: 9344282

Recent clinical studies

Etiology

Kreiniz N, Gertz MA
Leuk Lymphoma 2023 Jul-Aug;64(8):1361-1372. Epub 2023 May 25 doi: 10.1080/10428194.2023.2216818. PMID: 37229535
Sklavenitis-Pistofidis R, Aranha MP, Redd RA, Baginska J, Haradhvala NJ, Hallisey M, Dutta AK, Savell A, Varmeh S, Heilpern-Mallory D, Ujwary S, Zavidij O, Aguet F, Su NK, Lightbody ED, Bustoros M, Tahri S, Mouhieddine TH, Wu T, Flechon L, Anand S, Rosenblatt JM, Zonder J, Vredenburgh JJ, Boruchov A, Bhutani M, Usmani SZ, Matous J, Yee AJ, Jakubowiak A, Laubach J, Manier S, Nadeem O, Richardson P, Badros AZ, Mateos MV, Trippa L, Getz G, Ghobrial IM
Cancer Cell 2022 Nov 14;40(11):1358-1373.e8. doi: 10.1016/j.ccell.2022.10.017. PMID: 36379208Free PMC Article
Chan LN, Aghania E, Leveille E, Müschen M
Biochem Soc Trans 2021 Jun 30;49(3):1467-1478. doi: 10.1042/BST20201316. PMID: 34196360
Fujino T, Kitamura T
Exp Hematol 2020 Mar;83:74-84. Epub 2020 Jan 13 doi: 10.1016/j.exphem.2020.01.002. PMID: 31945396
Kaner J, Desai P, Mencia-Trinchant N, Guzman ML, Roboz GJ, Hassane DC
Cold Spring Harb Perspect Med 2020 Apr 1;10(4) doi: 10.1101/cshperspect.a035675. PMID: 31615870Free PMC Article

Diagnosis

Kreiniz N, Gertz MA
Leuk Lymphoma 2023 Jul-Aug;64(8):1361-1372. Epub 2023 May 25 doi: 10.1080/10428194.2023.2216818. PMID: 37229535
Sklavenitis-Pistofidis R, Aranha MP, Redd RA, Baginska J, Haradhvala NJ, Hallisey M, Dutta AK, Savell A, Varmeh S, Heilpern-Mallory D, Ujwary S, Zavidij O, Aguet F, Su NK, Lightbody ED, Bustoros M, Tahri S, Mouhieddine TH, Wu T, Flechon L, Anand S, Rosenblatt JM, Zonder J, Vredenburgh JJ, Boruchov A, Bhutani M, Usmani SZ, Matous J, Yee AJ, Jakubowiak A, Laubach J, Manier S, Nadeem O, Richardson P, Badros AZ, Mateos MV, Trippa L, Getz G, Ghobrial IM
Cancer Cell 2022 Nov 14;40(11):1358-1373.e8. doi: 10.1016/j.ccell.2022.10.017. PMID: 36379208Free PMC Article
Johnson DE, Burtness B, Leemans CR, Lui VWY, Bauman JE, Grandis JR
Nat Rev Dis Primers 2020 Nov 26;6(1):92. doi: 10.1038/s41572-020-00224-3. PMID: 33243986Free PMC Article
Hartmann L, Metzeler KH
Genes Chromosomes Cancer 2019 Dec;58(12):828-838. Epub 2019 Apr 16 doi: 10.1002/gcc.22756. PMID: 30939217
Roschewski M, Wilson WH
Cancer J 2012 Sep-Oct;18(5):469-74. doi: 10.1097/PPO.0b013e31826c5e19. PMID: 23006954

Therapy

Kreiniz N, Gertz MA
Leuk Lymphoma 2023 Jul-Aug;64(8):1361-1372. Epub 2023 May 25 doi: 10.1080/10428194.2023.2216818. PMID: 37229535
Sklavenitis-Pistofidis R, Aranha MP, Redd RA, Baginska J, Haradhvala NJ, Hallisey M, Dutta AK, Savell A, Varmeh S, Heilpern-Mallory D, Ujwary S, Zavidij O, Aguet F, Su NK, Lightbody ED, Bustoros M, Tahri S, Mouhieddine TH, Wu T, Flechon L, Anand S, Rosenblatt JM, Zonder J, Vredenburgh JJ, Boruchov A, Bhutani M, Usmani SZ, Matous J, Yee AJ, Jakubowiak A, Laubach J, Manier S, Nadeem O, Richardson P, Badros AZ, Mateos MV, Trippa L, Getz G, Ghobrial IM
Cancer Cell 2022 Nov 14;40(11):1358-1373.e8. doi: 10.1016/j.ccell.2022.10.017. PMID: 36379208Free PMC Article
Johnson DE, Burtness B, Leemans CR, Lui VWY, Bauman JE, Grandis JR
Nat Rev Dis Primers 2020 Nov 26;6(1):92. doi: 10.1038/s41572-020-00224-3. PMID: 33243986Free PMC Article
Scarpignato C, Sloan JA, Wang DH, Hunt RH
Ann N Y Acad Sci 2020 Dec;1481(1):90-107. Epub 2020 Aug 21 doi: 10.1111/nyas.14447. PMID: 32822080
Roschewski M, Wilson WH
Cancer J 2012 Sep-Oct;18(5):469-74. doi: 10.1097/PPO.0b013e31826c5e19. PMID: 23006954

Prognosis

Kreiniz N, Gertz MA
Leuk Lymphoma 2023 Jul-Aug;64(8):1361-1372. Epub 2023 May 25 doi: 10.1080/10428194.2023.2216818. PMID: 37229535
Sklavenitis-Pistofidis R, Aranha MP, Redd RA, Baginska J, Haradhvala NJ, Hallisey M, Dutta AK, Savell A, Varmeh S, Heilpern-Mallory D, Ujwary S, Zavidij O, Aguet F, Su NK, Lightbody ED, Bustoros M, Tahri S, Mouhieddine TH, Wu T, Flechon L, Anand S, Rosenblatt JM, Zonder J, Vredenburgh JJ, Boruchov A, Bhutani M, Usmani SZ, Matous J, Yee AJ, Jakubowiak A, Laubach J, Manier S, Nadeem O, Richardson P, Badros AZ, Mateos MV, Trippa L, Getz G, Ghobrial IM
Cancer Cell 2022 Nov 14;40(11):1358-1373.e8. doi: 10.1016/j.ccell.2022.10.017. PMID: 36379208Free PMC Article
Bustoros M, Anand S, Sklavenitis-Pistofidis R, Redd R, Boyle EM, Zhitomirsky B, Dunford AJ, Tai YT, Chavda SJ, Boehner C, Neuse CJ, Rahmat M, Dutta A, Casneuf T, Verona R, Kastritis E, Trippa L, Stewart C, Walker BA, Davies FE, Dimopoulos MA, Bergsagel PL, Yong K, Morgan GJ, Aguet F, Getz G, Ghobrial IM
Nat Commun 2022 Jun 15;13(1):3449. doi: 10.1038/s41467-022-30694-w. PMID: 35705541Free PMC Article
Johnson DE, Burtness B, Leemans CR, Lui VWY, Bauman JE, Grandis JR
Nat Rev Dis Primers 2020 Nov 26;6(1):92. doi: 10.1038/s41572-020-00224-3. PMID: 33243986Free PMC Article
Maura F, Bolli N, Rustad EH, Hultcrantz M, Munshi N, Landgren O
JAMA Oncol 2020 Mar 1;6(3):425-432. doi: 10.1001/jamaoncol.2019.4659. PMID: 31830214Free PMC Article

Clinical prediction guides

Homan CC, Drazer MW, Yu K, Lawrence DM, Feng J, Arriola-Martinez L, Pozsgai MJ, McNeely KE, Ha T, Venugopal P, Arts P, King-Smith SL, Cheah J, Armstrong M, Wang P, Bödör C, Cantor AB, Cazzola M, Degelman E, DiNardo CD, Duployez N, Favier R, Fröhling S, Rio-Machin A, Klco JM, Krämer A, Kurokawa M, Lee J, Malcovati L, Morgan NV, Natsoulis G, Owen C, Patel KP, Preudhomme C, Raslova H, Rienhoff H, Ripperger T, Schulte R, Tawana K, Velloso E, Yan B, Kim E, Sood R, Hsu AP, Holland SM, Phillips K, Poplawski NK, Babic M, Wei AH, Forsyth C, Mar Fan H, Lewis ID, Cooney J, Susman R, Fox LC, Blombery P, Singhal D, Hiwase D, Phipson B, Schreiber AW, Hahn CN, Scott HS, Liu P, Godley LA, Brown AL; NISC Comparative Sequencing Program
Blood Adv 2023 Oct 24;7(20):6092-6107. doi: 10.1182/bloodadvances.2023010045. PMID: 37406166Free PMC Article
Kreiniz N, Gertz MA
Leuk Lymphoma 2023 Jul-Aug;64(8):1361-1372. Epub 2023 May 25 doi: 10.1080/10428194.2023.2216818. PMID: 37229535
Sklavenitis-Pistofidis R, Aranha MP, Redd RA, Baginska J, Haradhvala NJ, Hallisey M, Dutta AK, Savell A, Varmeh S, Heilpern-Mallory D, Ujwary S, Zavidij O, Aguet F, Su NK, Lightbody ED, Bustoros M, Tahri S, Mouhieddine TH, Wu T, Flechon L, Anand S, Rosenblatt JM, Zonder J, Vredenburgh JJ, Boruchov A, Bhutani M, Usmani SZ, Matous J, Yee AJ, Jakubowiak A, Laubach J, Manier S, Nadeem O, Richardson P, Badros AZ, Mateos MV, Trippa L, Getz G, Ghobrial IM
Cancer Cell 2022 Nov 14;40(11):1358-1373.e8. doi: 10.1016/j.ccell.2022.10.017. PMID: 36379208Free PMC Article
Johnson DE, Burtness B, Leemans CR, Lui VWY, Bauman JE, Grandis JR
Nat Rev Dis Primers 2020 Nov 26;6(1):92. doi: 10.1038/s41572-020-00224-3. PMID: 33243986Free PMC Article
Fujino T, Kitamura T
Exp Hematol 2020 Mar;83:74-84. Epub 2020 Jan 13 doi: 10.1016/j.exphem.2020.01.002. PMID: 31945396

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