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Diencephalic cancer

MedGen UID:
233659
Concept ID:
C1334576
Neoplastic Process
Synonyms: cancer of diencephalon; diencephalic cancer; diencephalic neoplasm; diencephalon cancer; Malignant Diencephalic Neoplasm; malignant diencephalic neoplasm; Malignant Diencephalic Neoplasms; malignant diencephalic neoplasms; Malignant Diencephalic Tumor; malignant diencephalic tumor; malignant diencephalic tumour; malignant diencephalon neoplasm; malignant neoplasm of diencephalon; tumor of diencephalon; tumour of diencephalon
 
Monarch Initiative: MONDO:0002786

Definition

A malignant neoplasm that occurs in the diencephalon. [from NCI]

Professional guidelines

PubMed

Ertiaei A, Hanaei S, Habibi Z, Moradi E, Nejat F
Pediatr Neurosurg 2016;51(5):223-8. Epub 2016 Apr 16 doi: 10.1159/000445064. PMID: 27082859
Baizabal-Carvallo JF, Cardoso F, Jankovic J
Mov Disord 2015 Feb;30(2):171-9. Epub 2014 Dec 9 doi: 10.1002/mds.26093. PMID: 25487777
Allen JC
Pediatr Neurosurg 2000 Mar;32(3):154-62. doi: 10.1159/000028922. PMID: 10867564

Recent clinical studies

Etiology

Carta S, Le Duy D, Rogemond V, Derache N, Chaumont H, Fromont A, Cabasson S, Boudot de la Motte M, Honnorat J, Marignier R
J Neurol Neurosurg Psychiatry 2023 Sep;94(9):738-741. Epub 2023 Feb 21 doi: 10.1136/jnnp-2022-330707. PMID: 36810322
Gorelyshev S, Savateev AN, Mazerkina N, Medvedeva O, Konovalov AN
Adv Tech Stand Neurosurg 2022;45:97-137. doi: 10.1007/978-3-030-99166-1_3. PMID: 35976448
Ho CY, Bornhorst M, Almira-Suarez MI, Donev K, Grafe M, Gordish-Dressman H, Rodriguez FJ
J Neuropathol Exp Neurol 2020 Jan 1;79(1):67-73. doi: 10.1093/jnen/nlz115. PMID: 31793986Free PMC Article
Bizzarri C, Bottaro G
Horm Res Paediatr 2015;83(4):232-41. Epub 2015 Feb 5 doi: 10.1159/000369802. PMID: 25659607
Fleischman A, Brue C, Poussaint TY, Kieran M, Pomeroy SL, Goumnerova L, Scott RM, Cohen LE
Pediatrics 2005 Jun;115(6):e742-8. doi: 10.1542/peds.2004-2237. PMID: 15930202

Diagnosis

Carta S, Le Duy D, Rogemond V, Derache N, Chaumont H, Fromont A, Cabasson S, Boudot de la Motte M, Honnorat J, Marignier R
J Neurol Neurosurg Psychiatry 2023 Sep;94(9):738-741. Epub 2023 Feb 21 doi: 10.1136/jnnp-2022-330707. PMID: 36810322
Tavares LS, Pinho RS, Aragão MM, Cappellano AM, Dastoli PA, Cavalheiro S, da Silva NS
Childs Nerv Syst 2023 May;39(5):1115-1122. Epub 2023 Feb 8 doi: 10.1007/s00381-023-05869-5. PMID: 36752912
Ho CY, Bornhorst M, Almira-Suarez MI, Donev K, Grafe M, Gordish-Dressman H, Rodriguez FJ
J Neuropathol Exp Neurol 2020 Jan 1;79(1):67-73. doi: 10.1093/jnen/nlz115. PMID: 31793986Free PMC Article
Aihara Y, Chiba K, Eguchi S, Amano K, Kawamata T
Neurol Med Chir (Tokyo) 2018 Jan 15;58(1):1-9. Epub 2017 Nov 9 doi: 10.2176/nmc.ra.2017-0081. PMID: 29118304Free PMC Article
Baizabal-Carvallo JF, Cardoso F, Jankovic J
Mov Disord 2015 Feb;30(2):171-9. Epub 2014 Dec 9 doi: 10.1002/mds.26093. PMID: 25487777

Therapy

La Spina M, Caruso M, Gulizia C, Comella M, Soma R, Meli M, Samperi P, Bertuna G, Di Cataldo A, Russo G
Curr Oncol 2023 Sep 13;30(9):8401-8410. doi: 10.3390/curroncol30090610. PMID: 37754525Free PMC Article
Green K, Panagopoulou P, D'Arco F, O'Hare P, Bowman R, Walters B, Dahl C, Jorgensen M, Patel P, Slater O, Ahmed R, Bailey S, Carceller F, Collins R, Corley E, English M, Howells L, Kamal A, Kilday JJ, Lowis S, Lumb B, Pace E, Picton S, Pizer B, Shafiq A, Uzunova L, Wayman H, Wilson S, Hargrave D, Opocher E
Neuro Oncol 2023 Apr 6;25(4):774-785. doi: 10.1093/neuonc/noac223. PMID: 36239316Free PMC Article
Gupta M, Chan TM, Santiago-Dieppa DR, Yekula A, Sanchez CE, Elster JD, Crawford JR, Levy ML, Gonda DD
J Neurosurg Pediatr 2020 Dec 25;27(3):317-324. doi: 10.3171/2020.7.PEDS20373. PMID: 33361479
Wagner LM, Myseros JS, Lukins DE, Willen CM, Packer RJ
Pediatr Blood Cancer 2018 May;65(5):e26917. Epub 2018 Jan 25 doi: 10.1002/pbc.26917. PMID: 29369501
Mulholland PJ
Cerebellum 2006;5(1):55-63. doi: 10.1080/14734220600551707. PMID: 16527765

Prognosis

La Spina M, Caruso M, Gulizia C, Comella M, Soma R, Meli M, Samperi P, Bertuna G, Di Cataldo A, Russo G
Curr Oncol 2023 Sep 13;30(9):8401-8410. doi: 10.3390/curroncol30090610. PMID: 37754525Free PMC Article
Carta S, Le Duy D, Rogemond V, Derache N, Chaumont H, Fromont A, Cabasson S, Boudot de la Motte M, Honnorat J, Marignier R
J Neurol Neurosurg Psychiatry 2023 Sep;94(9):738-741. Epub 2023 Feb 21 doi: 10.1136/jnnp-2022-330707. PMID: 36810322
Trapani S, Bortone B, Bianconi M, Rubino C, Sardi I, Lionetti P, Indolfi G
Ital J Pediatr 2022 Aug 17;48(1):147. doi: 10.1186/s13052-022-01316-4. PMID: 35978327Free PMC Article
Ho CY, Bornhorst M, Almira-Suarez MI, Donev K, Grafe M, Gordish-Dressman H, Rodriguez FJ
J Neuropathol Exp Neurol 2020 Jan 1;79(1):67-73. doi: 10.1093/jnen/nlz115. PMID: 31793986Free PMC Article
Aihara Y, Chiba K, Eguchi S, Amano K, Kawamata T
Neurol Med Chir (Tokyo) 2018 Jan 15;58(1):1-9. Epub 2017 Nov 9 doi: 10.2176/nmc.ra.2017-0081. PMID: 29118304Free PMC Article

Clinical prediction guides

Carta S, Le Duy D, Rogemond V, Derache N, Chaumont H, Fromont A, Cabasson S, Boudot de la Motte M, Honnorat J, Marignier R
J Neurol Neurosurg Psychiatry 2023 Sep;94(9):738-741. Epub 2023 Feb 21 doi: 10.1136/jnnp-2022-330707. PMID: 36810322
Gorelyshev S, Savateev AN, Mazerkina N, Medvedeva O, Konovalov AN
Adv Tech Stand Neurosurg 2022;45:97-137. doi: 10.1007/978-3-030-99166-1_3. PMID: 35976448
Ho CY, Bornhorst M, Almira-Suarez MI, Donev K, Grafe M, Gordish-Dressman H, Rodriguez FJ
J Neuropathol Exp Neurol 2020 Jan 1;79(1):67-73. doi: 10.1093/jnen/nlz115. PMID: 31793986Free PMC Article
Bizzarri C, Bottaro G
Horm Res Paediatr 2015;83(4):232-41. Epub 2015 Feb 5 doi: 10.1159/000369802. PMID: 25659607
Burr IM, Slonim AE, Danish RK, Gadoth N, Butler IJ
J Pediatr 1976 Mar;88(3):439-44. doi: 10.1016/s0022-3476(76)80260-0. PMID: 1245953

Recent systematic reviews

Pascual JM, Prieto R, Carrasco R
Acta Neurochir (Wien) 2011 Dec;153(12):2403-25; discussion 2426. Epub 2011 Sep 15 doi: 10.1007/s00701-011-1149-4. PMID: 21918833

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