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Non-Neoplastic Endocrine Disorder

MedGen UID:: 233771
•Concept ID:: C1335007
•: Disease or Syndrome

Definition

A non-neoplastic disorder that affects the endocrine system. Representative examples include diabetes mellitus, hyperthyroidism, and adrenal gland insufficiency. [from NCI]

Term Hierarchy

GTR
MeSH

CClinical test, RResearch test, OOMIM, GGeneReviews, VClinVar

CROGVNon-Neoplastic Endocrine Disorder

Pathological Conditions, Signs and Symptoms
- Pathological process
  - Disease
    - Disorder by Site
      - Disorder of endocrine system
        Non-Neoplastic Endocrine Disorder
        11-Beta-Hydroxylase Deficiency
        17-Alpha-Hydroxylase/17,20 Lyase Deficiency
        21-Hydroxylase Deficiency
        Salt-Wasting 21-Hydroxylase Deficiency
        Simple Virilizing 21-Hydroxylase Deficiency
        3 beta-Hydroxysteroid dehydrogenase deficiency
        Adrenal cortical hypofunction
        Central adrenal insufficiency
        Adrenocorticotropin deficient adrenal insufficiency
        Adrenocorticotropin receptor defect
        Corticotropin-releasing hormone deficient adrenal insufficiency
        Corticotropin-releasing hormone receptor defect
        Primary adrenal insufficiency
        Acute adrenal insufficiency
        Primary adrenocortical insufficiency
        Atrophy of thyroid
        Autoimmune polyendocrinopathy
        Autoimmune polyendocrinopathy type 3
        Autoimmune polyendocrinopathy type 4
        Polyglandular autoimmune syndrome, type 1
        Polyglandular autoimmune syndrome, type 2
        Congenital Adrenal Gland Disorder
        Congenital adrenal hyperplasia
        Adrenal Gland Hyperplasia II
        Antley-Bixler syndrome with genital anomalies and disordered steroidogenesis
        Classic congenital adrenal hyperplasia
        Classic congenital adrenal hyperplasia due to 21-hydroxylase deficiency
        Congenital adrenal hyperplasia due to cytochrome P450 oxidoreductase deficiency
        Congenital lipoid adrenal hyperplasia due to STAR deficency
        Deficiency of steroid 11-beta-monooxygenase
        Deficiency of steroid 17-alpha-monooxygenase
        Macronodular adrenal hyperplasia
        Micronodular adrenal hyperplasia
        Multinodular Adrenal Hyperplasia
        Non-classic congenital adrenal hyperplasia
        Congenital adrenal hypoplasia
        Congenital adrenal hypoplasia, X-linked
        Miniature Adult Form of AHC
        Congenital Thyroid Gland Disorder
        Congenital hypothyroidism
        Congenital hypothyroidism with ectopic thyroid
        Congenital iodine deficiency syndrome
        Deficiency of iodide peroxidase
        Dual Oxidase 2 Deficiency
        Genetic transient congenital hypothyroidism
        Hypothyroidism due to iodide transport defect
        Hypothyroidism due to TSH receptor mutations
        Hypothyroidism, congenital, nongoitrous, 2
        Iodotyrosine deiodination defect
        Isolated thyroid-stimulating hormone deficiency
        Pendred syndrome
        Thyroglobulin Deficiency
        Thyroid dyshormonogenesis
        Thyroid dyshormonogenesis 6
        Congenital thyroid hypoplasia
        Ectopic thyroid
        Accessory ectopic thyroid tissue
        Lingual thyroid
        Thyroid agenesis
        Cortisol 11-beta-ketoreductase deficiency
        Diabetes insipidus
        Adipsic Diabetes Insipidus
        Central diabetes insipidus
        Autosomal Dominant Neurohypophyseal Diabetes Insipidus
        Neurohypophyseal diabetes insipidus
        Dipsogenic diabetes insipidus
        Nephrogenic diabetes insipidus
        Diabetes insipidus, nephrogenic, autosomal
        Diabetes insipidus, nephrogenic, X-linked
        Wolfram syndrome
        Wolfram syndrome 1
        Wolfram syndrome 2
        Wolfram syndrome, mitochondrial form
        Disorder of AMH
        Disorder of AMH Receptor
        Disorder of Androgen Synthesis
        Endocrine Disorder Arising from Mental Factor
        Glucose metabolism disease
        Diabetes mellitus
        Childhood Diabetes Mellitus
        Complication due to diabetes mellitus
        Diabetes mellitus type 1
        Diabetes mellitus without complication
        Gestational diabetes
        Latent autoimmune diabetes in adults
        Leprechaunism syndrome
        Lipoatrophic diabetes
        Maturity onset diabetes mellitus in young
        Mitochondrial Diabetes
        Monogenic diabetes
        New Onset Diabetes After Transplant
        Pre-Gestational Diabetes
        Prediabetes syndrome
        Type II diabetes mellitus
        Glucose intolerance
        Impaired glucose tolerance
        Glycosuria
        Familial renal glucosuria
        Hyperglycemia
        Neonatal hyperglycemia
        Postprandial hyperglycemia
        Hyperinsulinemia
        Familial hyperinsulinism
        Fasting hyperinsulinemia
        Hyperinsulinemic hypoglycemia
        Insulin resistance
        Hypoglycemia
        Fasting hypoglycemia
        Hypoketotic hypoglycemia
        Insulin coma
        Ketotic hypoglycemia
        Neonatal hypoglycemia
        Nonketotic hypoglycemia
        Reactive hypoglycemia
        Recurrent hypoglycemia
        Goiter
        Congenital goiter
        Diffuse goiter
        Endemic goiter
        Euthyroid goiter
        Euthyroid multinodular goiter
        Graves disease
        Neonatal Graves disease
        Thyroid eye disease
        Hypothyroid Goiter
        Lingual goiter
        Nodular goiter
        Multinodular goiter
        Uninodular goiter
        Nontoxic goiter
        Non-toxic nodular goiter
        Plummer disease
        Substernal goiter
        Gonadal agenesis
        Hyperandrogenism due to cortisone reductase deficiency
        Hyperthyroidism
        Acquired Hyperthyroidism
        Central Hyperthyroidism
        Congenital Hyperthyroidism
        Hyperthyroxinemia, familial dysalbuminemic
        Iodine-induced hyperthyroidism
        Primary Hyperthyroidism
        Transient Primary Hypothyroidism
        Thyroid crisis
        Thyrotoxicosis
        Hyperthyroidism with Hashimoto disease
        Neonatal thyrotoxicosis
        Thyrotoxicosis from ectopic thyroid tissue
        Thyrotoxicosis with diffuse goiter
        Thyrotoxicosis with toxic multinodular goiter
        Thyrotoxicosis with toxic single thyroid nodule
        Hypogonadism
        Eunuchism
        Hypergonadotropic hypogonadism
        Congenital Hypergonadotropic Hypogonadism
        Follicle Stimulating Hormone Receptor Deficiency
        Hypogonadism with anosmia
        Hypogonadotropic hypogonadism 1 with or without anosmia
        Hypogonadotropic hypogonadism 2 with or without anosmia
        Hypogonadotropic hypogonadism 3 with or without anosmia
        Hypogonadotropic hypogonadism 4 with or without anosmia
        Hypogonadotropic hypogonadism 5 with or without anosmia
        Hypogonadotropic hypogonadism 6 with or without anosmia
        Hypogonadotropic hypogonadism
        Acquired Hypogonadotropic Hypogonadism
        Congenital hypogonadotropic hypogonadism
        Hypogonadotropic Hypogonadism with Adrenal Hypoplasia Congenita
        Isolated Hypogonadotropic Hypogonadism
        Infantilism, Sexual
        Klinefelter syndrome
        Male hypogonadism
        Acquired testicular failure
        Congenital Testicular Failure
        Primary testicular failure
        Hypoparathyroidism
        22q11 Deletion Syndrome
        DiGeorge syndrome
        Acquired Hypoparathyroidism
        Autoimmune hypoparathyroidism
        Autosomal dominant hypocalcemia 1
        Congenital hypoparathyroidism
        Hypoparathyroidism - X-linked
        Hypoparathyroidism, autosomal recessive
        Iatrogenic Hypoparathyroidism
        Primary Hypoparathyroidism
        Transient Neonatal Hypoparathyroidism
        Hypopituitarism
        Anterior hypopituitarism
        Abnormal prolactin level
        Congenital isolated adrenocorticotropic hormone deficiency
        Gonadotropin deficiency
        Panhypopituitarism
        Pituitary dwarfism
        Hypothyroidism
        Acquired hypothyroidism
        Central hypothyroidism
        Acquired central hypothyroidism
        Hypothalamic hypothyroidism
        Iatrogenic Central Hypothyroidism
        Pituitary hypothyroidism
        Compensated hypothyroidism
        Iodine Deficiency Hypothyroidism
        Myxedema
        Primary hypothyroidism
        Iatrogenic Primary Hypothyroidism
        Transient hypothyroxinemia
        Wolff-Chaikoff Phenomenon
        Mullerian aplasia and hyperandrogenism
        Pituitary gland hypoplasia
        Pseudohypoparathyroidism
        Pseudohypoparathyroidism type 1B
        Pseudohypoparathyroidism type 1C
        Pseudohypoparathyroidism type I A
        Pseudopseudohypoparathyroidism
        Pseudohypoparathyroidism type II
        Pyknodysostosis
        Testosterone 17-beta-dehydrogenase deficiency
        Thyroiditis
        Autoimmune thyroiditis
        Hashimoto thyroiditis
        Postpartum thyroiditis
        Subacute lymphocytic thyroiditis
        IgG4-related thyroid disease
        Subacute thyroiditis
        Suppurative thyroiditis
        Turner syndrome
        Monosomy X
        Mosaic Turner syndrome
        Turner syndrome due to structural X chromosome anomalies

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Non-Neoplastic Endocrine Disorder

Definition

Term Hierarchy

Professional guidelines

PubMed

Recent clinical studies

Etiology

Diagnosis

Therapy

Prognosis

Clinical prediction guides

Recent systematic reviews

Supplemental Content

Table of contents

Practice guidelines

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