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Paranasal sinus adenoid cystic carcinoma

MedGen UID:
233840
Concept ID:
C1335337
Neoplastic Process
Synonyms: Accessory Sinus Adenoid Cystic Carcinoma; accessory sinus adenoid cystic carcinoma; Adenoid Cystic Carcinoma of Accessory Sinus; adenoid cystic carcinoma of accessory sinus; Adenoid Cystic Carcinoma of Paranasal Sinus; adenoid cystic carcinoma of paranasal sinus; Adenoid Cystic Carcinoma of the Accessory Sinus; adenoid cystic carcinoma of the accessory sinus; Adenoid Cystic Carcinoma of the Paranasal Sinus; adenoid cystic carcinoma of the paranasal sinus; Paranasal Sinus Adenoid Cystic Carcinoma; paranasal sinus adenoid cystic carcinoma
 
Monarch Initiative: MONDO:0006352

Definition

A rare adenoid cystic carcinoma that arises from the paranasal sinuses. It usually has an aggressive clinical course characterized by high recurrence rates and distant metastases. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVParanasal sinus adenoid cystic carcinoma

Professional guidelines

PubMed

Fang Y, Peng Z, Wang Y, Gao K, Liu Y, Fan R, Zhang H, Xie Z, Jiang W
Oral Oncol 2022 Jul;130:105945. Epub 2022 Jun 2 doi: 10.1016/j.oraloncology.2022.105945. PMID: 35662026
Larnaudie A, Delaby N, Marcy PY, Leleu T, Costes-Martineau V, Vergez S, de Gabory L, Quintyn JC, Doré M, Pointreau Y, Thariat J
Cancer Radiother 2022 Feb-Apr;26(1-2):156-167. Epub 2021 Dec 22 doi: 10.1016/j.canrad.2021.10.007. PMID: 34953697
Husain Q, Kanumuri VV, Svider PF, Radvansky BM, Boghani Z, Liu JK, Eloy JA
Otolaryngol Head Neck Surg 2013 Jan;148(1):29-39. Epub 2012 Oct 12 doi: 10.1177/0194599812464020. PMID: 23064210

Recent clinical studies

Diagnosis

McDonald HR, Char DH
Ann Ophthalmol 1985 Dec;17(12):757-9. PMID: 3004304

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