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Central nervous system mesenchymal non-meningothelial tumor

MedGen UID:
234104
Concept ID:
C1332893
Neoplastic Process
Synonyms: central nervous system mesenchymal non-meningothelial tumor; Central Nervous System Mesenchymal, Non-Meningothelial Neoplasm; central nervous system mesenchymal, non-meningothelial neoplasm; Central Nervous System Mesenchymal, Non-Meningothelial Tumor; central nervous system mesenchymal, non-meningothelial tumor; central nervous system mesenchymal, non-meningothelial tumour; Central Nervous System Soft Tissue Neoplasm; central nervous system soft tissue neoplasm; Central Nervous System Soft Tissue Tumor; central nervous system soft tissue tumor; central nervous system soft tissue tumour; CNS Soft Tissue Neoplasm; CNS soft tissue neoplasm; CNS Soft Tissue Tumor; CNS soft tissue tumor; CNS soft tissue tumour; Mesenchymal Non-Meningothelial Tumor of the Central Nervous System; mesenchymal non-meningothelial tumor of the central nervous system; mesenchymal non-meningothelial tumour of the central nervous system; Mesenchymal, Non-Meningothelial Tumor of Central Nervous System; mesenchymal, non-meningothelial tumor of central nervous system; Mesenchymal, Non-Meningothelial Tumor of CNS; mesenchymal, non-meningothelial tumor of CNS; Mesenchymal, Non-Meningothelial Tumor of the CNS; mesenchymal, non-meningothelial tumor of the CNS; mesenchymal, non-meningothelial tumour of central nervous system; mesenchymal, non-meningothelial tumour of CNS; mesenchymal, non-meningothelial tumour of the CNS; non-meningothelial mesenchymal tumor; non-meningothelial mesenchymal tumour; Soft Tissue Neoplasm of Central Nervous System; soft tissue neoplasm of central nervous system; Soft Tissue Neoplasm of CNS; soft tissue neoplasm of CNS; Soft Tissue Neoplasm of the Central Nervous System; soft tissue neoplasm of the central nervous system; Soft Tissue Neoplasm of the CNS; soft tissue neoplasm of the CNS; Soft Tissue Tumor of Central Nervous System; soft tissue tumor of central nervous system; Soft Tissue Tumor of CNS; soft tissue tumor of CNS; Soft Tissue Tumor of the Central Nervous System; soft tissue tumor of the central nervous system; Soft Tissue Tumor of the CNS; soft tissue tumor of the CNS; soft tissue tumour of central nervous system; soft tissue tumour of CNS; soft tissue tumour of the central nervous system; soft tissue tumour of the CNS
 
Monarch Initiative: MONDO:0003244

Definition

A benign or malignant mesenchymal neoplasm originating in the central nervous system or the meninges and showing fibrous, fibrohistiocytic, adipose, myoid, endothelial, chondroid or osseous, but not meningothelial differentiation. Depending on the histological features and clinical behavior of these neoplasms, their grade ranges from benign (WHO grade I) to highly malignant (WHO grade IV). (Adapted from WHO) [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVCentral nervous system mesenchymal non-meningothelial tumor

Recent clinical studies

Prognosis

Meredith DM, Alexandrescu S
Brain Pathol 2022 Jul;32(4):e13059. Epub 2022 Mar 9 doi: 10.1111/bpa.13059. PMID: 35266242Free PMC Article
Lopez-Nunez O, Cafferata B, Santi M, Ranganathan S, Pearce TM, Kulich SM, Bailey KM, Broniscer A, Rossi S, Zin A, Nasrallah MP, Li MM, Zhong Y, Miele E, Alaggio R, Surrey LF
Brain Pathol 2021 Jan;31(1):70-83. Epub 2020 Nov 6 doi: 10.1111/bpa.12900. PMID: 32997853Free PMC Article
Majumdar K, Mandal S, Thakkar R, Saran RK, Srivastava AK
Brain Tumor Pathol 2014 Jan;31(1):62-7. Epub 2013 Mar 2 doi: 10.1007/s10014-013-0138-0. PMID: 23456087
Alén JF, Lobato RD, Gómez PA, Boto GR, Lagares A, Ramos A, Ricoy JR
Acta Neurochir (Wien) 2001;143(6):575-86. doi: 10.1007/s007010170062. PMID: 11534674

Clinical prediction guides

d'Amati A, Gianno F, Scuccimarri L, Lastilla M, Messina R, Signorelli F, Zimatore DS, Barresi S, Miele E, Alaggio R, Rossi S, Maiorano E, Ingravallo G, Giangaspero F, Antonelli M
Acta Neuropathol Commun 2023 Jun 13;11(1):95. doi: 10.1186/s40478-023-01596-9. PMID: 37312212Free PMC Article
Tauziède-Espariat A, Hasty L, Métais A, Varlet P
Acta Neuropathol Commun 2023 Feb 3;11(1):22. doi: 10.1186/s40478-023-01522-z. PMID: 36737790Free PMC Article
Lopez-Nunez O, Cafferata B, Santi M, Ranganathan S, Pearce TM, Kulich SM, Bailey KM, Broniscer A, Rossi S, Zin A, Nasrallah MP, Li MM, Zhong Y, Miele E, Alaggio R, Surrey LF
Brain Pathol 2021 Jan;31(1):70-83. Epub 2020 Nov 6 doi: 10.1111/bpa.12900. PMID: 32997853Free PMC Article

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