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Childhood Clear Cell Sarcoma of Soft Tissue

MedGen UID:
234126
Concept ID:
C1332964
Neoplastic Process
Synonyms: Childhood Clear Cell Sarcoma of Soft Parts; Pediatric Clear Cell Sarcoma of Soft Parts

Definition

A clear cell sarcoma of soft tissue occurring in children. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVChildhood Clear Cell Sarcoma of Soft Tissue

Professional guidelines

PubMed

Qureshi SS, Bhagat M, Verma K, Yadav S, Prasad M, Vora T, Chinnaswamy G, Amin N, Smriti V, Baheti A, Laskar S, Khanna N, Ramadwar M, Shah S
J Pediatr Urol 2020 Aug;16(4):475.e1-475.e9. Epub 2020 Jun 5 doi: 10.1016/j.jpurol.2020.05.168. PMID: 32620510
Gooskens SL, Graf N, Furtwängler R, Spreafico F, Bergeron C, Ramírez-Villar GL, Godzinski J, Rübe C, Janssens GO, Vujanic GM, Leuschner I, Coulomb-L'Hermine A, Smets AM, de Camargo B, Stoneham S, van Tinteren H, Pritchard-Jones K, van den Heuvel-Eibrink MM; International Society of Paediatric Oncology–Renal Tumour Study Group (SIOP–RTSG)
Nat Rev Urol 2018 May;15(5):309-319. Epub 2018 Feb 27 doi: 10.1038/nrurol.2018.14. PMID: 29485128
Ahmed HU, Arya M, Levitt G, Duffy PG, Sebire NJ, Mushtaq I
Lancet Oncol 2007 Sep;8(9):842-8. doi: 10.1016/S1470-2045(07)70276-0. PMID: 17765193

Recent clinical studies

Etiology

Pearson ADJ, Federico S, Gatz SA, Ortiz M, Lesa G, Scobie N, Gounaris I, Weiner SL, Weigel B, Unger TJ, Stewart E, Smith M, Slotkin EK, Reaman G, Pappo A, Nysom K, Norga K, McDonough J, Marshall LV, Ludwinski D, Ligas F, Karres D, Kool M, Horner TJ, Henssen A, Heenen D, Hawkins DS, Gore L, Bender JG, Galluzzo S, Fox E, de Rojas T, Davies BR, Chakrabarti J, Carmichael J, Bradford D, Blanc P, Bernardi R, Benchetrit S, Akindele K, Vassal G
Eur J Cancer 2023 Sep;190:112950. Epub 2023 Jun 21 doi: 10.1016/j.ejca.2023.112950. PMID: 37441939
Libes J, Hol J, Neto JCA, Vallance KL, Tinteren HV, Benedetti DJ, Villar GLR, Duncan C, Ehrlich PF
Pediatr Blood Cancer 2023 May;70 Suppl 2:e30343. doi: 10.1002/pbc.30343. PMID: 37096796
Libes J, Hol J, Neto JCA, Vallance KL, Tinteren HV, Benedetti DJ, Villar GLR, Duncan C, Ehrlich PF
Pediatr Blood Cancer 2023 Jan;70(1):e30006. Epub 2022 Nov 3 doi: 10.1002/pbc.30006. PMID: 36326750
Friesenbichler W, Lüftinger R, Kropshofer G, Henkel M, Amann G, Furtwängler R, Graf N, Kager L
Pediatr Blood Cancer 2021 May;68(5):e28860. Epub 2021 Jan 12 doi: 10.1002/pbc.28860. PMID: 33438324
Gooskens SL, Graf N, Furtwängler R, Spreafico F, Bergeron C, Ramírez-Villar GL, Godzinski J, Rübe C, Janssens GO, Vujanic GM, Leuschner I, Coulomb-L'Hermine A, Smets AM, de Camargo B, Stoneham S, van Tinteren H, Pritchard-Jones K, van den Heuvel-Eibrink MM; International Society of Paediatric Oncology–Renal Tumour Study Group (SIOP–RTSG)
Nat Rev Urol 2018 May;15(5):309-319. Epub 2018 Feb 27 doi: 10.1038/nrurol.2018.14. PMID: 29485128

Diagnosis

Frankel AO, Lathara M, Shaw CY, Wogmon O, Jackson JM, Clark MM, Eshraghi N, Keenen SE, Woods AD, Purohit R, Ishi Y, Moran N, Eguchi M, Ahmed FUA, Khan S, Ioannou M, Perivoliotis K, Li P, Zhou H, Alkhaledi A, Davis EJ, Galipeau D, Randall RL, Wozniak A, Schoffski P, Lee CJ, Huang PH, Jones RL, Rubin BP, Darrow M, Srinivasa G, Rudzinski ER, Chen S, Berlow NE, Keller C
Mod Pathol 2022 Sep;35(9):1193-1203. Epub 2022 Apr 21 doi: 10.1038/s41379-022-01075-x. PMID: 35449398
Friesenbichler W, Lüftinger R, Kropshofer G, Henkel M, Amann G, Furtwängler R, Graf N, Kager L
Pediatr Blood Cancer 2021 May;68(5):e28860. Epub 2021 Jan 12 doi: 10.1002/pbc.28860. PMID: 33438324
Chong WC, Cain JE
Anat Rec (Hoboken) 2020 Oct;303(10):2561-2577. Epub 2019 Nov 18 doi: 10.1002/ar.24315. PMID: 31738020
Aw SJ, Chang KTE
Arch Pathol Lab Med 2019 Aug;143(8):1022-1026. Epub 2019 Jan 10 doi: 10.5858/arpa.2018-0045-RS. PMID: 30628851
Gooskens SL, Furtwängler R, Vujanic GM, Dome JS, Graf N, van den Heuvel-Eibrink MM
Eur J Cancer 2012 Sep;48(14):2219-26. Epub 2012 May 12 doi: 10.1016/j.ejca.2012.04.009. PMID: 22579455

Therapy

Pearson ADJ, Federico S, Gatz SA, Ortiz M, Lesa G, Scobie N, Gounaris I, Weiner SL, Weigel B, Unger TJ, Stewart E, Smith M, Slotkin EK, Reaman G, Pappo A, Nysom K, Norga K, McDonough J, Marshall LV, Ludwinski D, Ligas F, Karres D, Kool M, Horner TJ, Henssen A, Heenen D, Hawkins DS, Gore L, Bender JG, Galluzzo S, Fox E, de Rojas T, Davies BR, Chakrabarti J, Carmichael J, Bradford D, Blanc P, Bernardi R, Benchetrit S, Akindele K, Vassal G
Eur J Cancer 2023 Sep;190:112950. Epub 2023 Jun 21 doi: 10.1016/j.ejca.2023.112950. PMID: 37441939
Bailey K, Cost C, Davis I, Glade-Bender J, Grohar P, Houghton P, Isakoff M, Stewart E, Laack N, Yustein J, Reed D, Janeway K, Gorlick R, Lessnick S, DuBois S, Hingorani P
F1000Res 2019;8 Epub 2019 Apr 15 doi: 10.12688/f1000research.18139.1. PMID: 31031965Free PMC Article
Gooskens SL, Graf N, Furtwängler R, Spreafico F, Bergeron C, Ramírez-Villar GL, Godzinski J, Rübe C, Janssens GO, Vujanic GM, Leuschner I, Coulomb-L'Hermine A, Smets AM, de Camargo B, Stoneham S, van Tinteren H, Pritchard-Jones K, van den Heuvel-Eibrink MM; International Society of Paediatric Oncology–Renal Tumour Study Group (SIOP–RTSG)
Nat Rev Urol 2018 May;15(5):309-319. Epub 2018 Feb 27 doi: 10.1038/nrurol.2018.14. PMID: 29485128
Zekri W, Yehia D, Elshafie MM, Zaghloul MS, El-Kinaai N, Taha H, Refaat A, Younes AA, Alfaar AS
J Egypt Natl Canc Inst 2015 Jun;27(2):97-100. Epub 2015 Apr 28 doi: 10.1016/j.jnci.2015.03.002. PMID: 25934445
Dall'Igna P, De Corti F, Alaggio R, Cecchetto G
Eur J Pediatr Surg 2014 Dec;24(6):482-7. Epub 2014 Dec 5 doi: 10.1055/s-0034-1396422. PMID: 25478665

Prognosis

Sloan EA, Gupta R, Koelsche C, Chiang J, Villanueva-Meyer JE, Alexandrescu S, Eschbacher JM, Wang W, Mafra M, Ud Din N, Carr-Boyd E, Watson M, Punsoni M, Oviedo A, Gilani A, Kleinschmidt-DeMasters BK, Coss DJ, Lopes MB, Reddy A, Mueller S, Cho SJ, Horvai AE, Lee JC, Pekmezci M, Tihan T, Bollen AW, Rodriguez FJ, Ellison DW, Perry A, von Deimling A, Chang SM, Berger MS, Solomon DA
Brain Pathol 2022 Jul;32(4):e13037. Epub 2021 Nov 25 doi: 10.1111/bpa.13037. PMID: 34821426Free PMC Article
Zekri W, Yehia D, Elshafie MM, Zaghloul MS, El-Kinaai N, Taha H, Refaat A, Younes AA, Alfaar AS
J Egypt Natl Canc Inst 2015 Jun;27(2):97-100. Epub 2015 Apr 28 doi: 10.1016/j.jnci.2015.03.002. PMID: 25934445
Gooskens SL, Furtwängler R, Vujanic GM, Dome JS, Graf N, van den Heuvel-Eibrink MM
Eur J Cancer 2012 Sep;48(14):2219-26. Epub 2012 May 12 doi: 10.1016/j.ejca.2012.04.009. PMID: 22579455
Ahmed HU, Arya M, Levitt G, Duffy PG, Sebire NJ, Mushtaq I
Lancet Oncol 2007 Sep;8(9):842-8. doi: 10.1016/S1470-2045(07)70276-0. PMID: 17765193
Broecker B
Urol Clin North Am 2000 Aug;27(3):463-9, ix. doi: 10.1016/s0094-0143(05)70094-x. PMID: 10985146

Clinical prediction guides

Doganis D, Karalexi MA; NARECHEM-ST collaborating group, Panagopoulou P, Bouka P, Bouka E, Markozannes G, Ntzani EE, Steliarova-Foucher E, Petridou ET
Cancer Epidemiol 2022 Jun;78:102153. Epub 2022 Apr 4 doi: 10.1016/j.canep.2022.102153. PMID: 35390585
Qureshi SS, Bhagat M, Verma K, Yadav S, Prasad M, Vora T, Chinnaswamy G, Amin N, Smriti V, Baheti A, Laskar S, Khanna N, Ramadwar M, Shah S
J Pediatr Urol 2020 Aug;16(4):475.e1-475.e9. Epub 2020 Jun 5 doi: 10.1016/j.jpurol.2020.05.168. PMID: 32620510
Gooskens SL, Kenny C, Lazaro A, O'Meara E, van Tinteren H, Spreafico F, Vujanic G, Leuschner I, Coulomb-L'Herminé A, Perotti D, de Camargo B, Bergeron C, Acha García T, Tanaka M, Pieters R, Pritchard-Jones K, Graf N, van den Heuvel-Eibrink MM, O'Sullivan MJ
Genes Chromosomes Cancer 2016 Feb;55(2):143-7. Epub 2015 Nov 6 doi: 10.1002/gcc.22320. PMID: 26542179
Royer-Pokora B
Pediatr Nephrol 2013 Jan;28(1):13-23. Epub 2012 Mar 30 doi: 10.1007/s00467-012-2146-4. PMID: 22461142
Gooskens SL, Furtwängler R, Vujanic GM, Dome JS, Graf N, van den Heuvel-Eibrink MM
Eur J Cancer 2012 Sep;48(14):2219-26. Epub 2012 May 12 doi: 10.1016/j.ejca.2012.04.009. PMID: 22579455

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