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Conventional angiosarcoma

MedGen UID:
234174
•Concept ID:
C1333155
•
Neoplastic Process
Synonyms: Conventional Angiosarcoma; conventional angiosarcoma
 
Monarch Initiative: MONDO:0003025

Definition

An angiosarcoma characterized by the presence of malignant spindle endothelial cells. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVConventional angiosarcoma

Professional guidelines

PubMed

Cutaneous angiosarcoma of the head and face: a single-center analysis of treatment outcomes in 43 patients in Japan.
Ito T, Uchi H, Nakahara T, Tsuji G, Oda Y, Hagihara A, Furue M
J Cancer Res Clin Oncol 2016 Jun;142(6):1387-94. Epub 2016 Mar 25 doi: 10.1007/s00432-016-2151-2. PMID: 27015673
Tumor molecular profiling in the treatment of refractory cancers.
Birendra KC, Afzal MZ, Sochaki A, Wentland KA, Chang R, Singh S, O'Rourke T
J Exp Ther Oncol 2015;11(1):27-32. PMID: 26259387
Chemoradiotherapy with taxane is superior to conventional surgery and radiotherapy in the management of cutaneous angiosarcoma: a multicentre, retrospective study.
Fujisawa Y, Yoshino K, Kadono T, Miyagawa T, Nakamura Y, Fujimoto M
Br J Dermatol 2014 Dec;171(6):1493-500. Epub 2014 Nov 10 doi: 10.1111/bjd.13110. PMID: 24814962

Recent clinical studies

Etiology

Epithelioid hemangioendothelioma of skin and soft tissues: clinicopathologic and immunohistochemical study of 30 cases.
Mentzel T, Beham A, Calonje E, Katenkamp D, Fletcher CD
Am J Surg Pathol 1997 Apr;21(4):363-74. doi: 10.1097/00000478-199704000-00001. PMID: 9130982
Epithelioid hemangioendothelioma of the head and neck: a clinicopathologic report of twelve cases.
Ellis GL, Kratochvil FJ 3rd
Oral Surg Oral Med Oral Pathol 1986 Jan;61(1):61-8. doi: 10.1016/0030-4220(86)90204-5. PMID: 3456142

Diagnosis

Mediastinal Epithelioid Angiosarcoma, New Insights into an Uncommon Diagnosis: A Case Report and Literature Review.
Navarro Sanchez JM, Oommen T, Lum C, Halford Z, Vierkoetter K
Hawaii J Health Soc Welf 2023 Sep;82(9):208-212. PMID: 37694219Free PMC Article
The capillary lobule variant of radiation-associated angiosarcoma in the setting of breast cancer: A diagnostic pitfall.
Agrawal S, Fritchie KJ, Fernandez AP, Ko JS, Bergfeld W, Rubin BP, Billings SD
J Cutan Pathol 2023 Feb;50(2):140-146. Epub 2022 Oct 10 doi: 10.1111/cup.14328. PMID: 36107728Free PMC Article
Radiation-associated angiosarcoma in the setting of breast cancer mimicking radiation dermatitis: A diagnostic pitfall.
Daniels BH, Ko JS, Rowe JJ, Downs-Kelly E, Billings SD
J Cutan Pathol 2017 May;44(5):456-461. Epub 2017 Feb 21 doi: 10.1111/cup.12917. PMID: 28169467
Epithelioid hemangioendothelioma of the parotid salivary gland.
Pigadas N, Mohamid W, McDermott P
Oral Surg Oral Med Oral Pathol Oral Radiol Endod 2000 Jun;89(6):730-8. doi: 10.1067/moe.2000.106299. PMID: 10846129
Composite hemangioendothelioma: a complex, low-grade vascular lesion mimicking angiosarcoma.
Nayler SJ, Rubin BP, Calonje E, Chan JK, Fletcher CD
Am J Surg Pathol 2000 Mar;24(3):352-61. doi: 10.1097/00000478-200003000-00003. PMID: 10716148

Prognosis

Epithelioid hemangioendothelioma of the parotid salivary gland.
Pigadas N, Mohamid W, McDermott P
Oral Surg Oral Med Oral Pathol Oral Radiol Endod 2000 Jun;89(6):730-8. doi: 10.1067/moe.2000.106299. PMID: 10846129
Epithelioid hemangioendothelioma of skin and soft tissues: clinicopathologic and immunohistochemical study of 30 cases.
Mentzel T, Beham A, Calonje E, Katenkamp D, Fletcher CD
Am J Surg Pathol 1997 Apr;21(4):363-74. doi: 10.1097/00000478-199704000-00001. PMID: 9130982
Periosteal epithelioid hemangioendothelioma with leptomeric fibrils.
Hirose T, Sano T, Shinomiya S, Hizawa K, Endo H, Henmi T
Ultrastruct Pathol 1987;11(4):405-10. doi: 10.3109/01913128709048434. PMID: 3113022
Epithelioid hemangioendothelioma of the head and neck: a clinicopathologic report of twelve cases.
Ellis GL, Kratochvil FJ 3rd
Oral Surg Oral Med Oral Pathol 1986 Jan;61(1):61-8. doi: 10.1016/0030-4220(86)90204-5. PMID: 3456142

Clinical prediction guides

Retiform haemangioendothelioma.
Fukunaga M, Endo Y, Masui F, Yoshikawa T, Ishikawa E, Ushigome S
Virchows Arch 1996 Jul;428(4-5):301-4. doi: 10.1007/BF00196705. PMID: 8764941

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