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Embryonal extrahepatic bile duct rhabdomyosarcoma

MedGen UID:
234244
•Concept ID:
C1333505
•
Neoplastic Process
Synonyms: Embryonal Extrahepatic Bile Duct Rhabdomyosarcoma; embryonal extrahepatic bile duct rhabdomyosarcoma; embryonal rhabdomyosarcoma (disease) of extrahepatic bile duct; Embryonal Rhabdomyosarcoma of Extrahepatic Bile Duct; embryonal rhabdomyosarcoma of extrahepatic bile duct; Embryonal Rhabdomyosarcoma of the Extrahepatic Bile Duct; embryonal rhabdomyosarcoma of the extrahepatic bile duct; Extrahepatic Bile Duct Embryonal Rhabdomyosarcoma; extrahepatic bile duct embryonal rhabdomyosarcoma; extrahepatic bile duct embryonal rhabdomyosarcoma (disease)
 
Monarch Initiative: MONDO:0002576

Definition

An embryonal rhabdomyosarcoma that arises from the extrahepatic bile ducts. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVEmbryonal extrahepatic bile duct rhabdomyosarcoma

Recent clinical studies

Etiology

A child with unresectable biliary rhabdomyosarcoma: 48-month disease-free survival after liver transplantation.
Paganelli M, Beaunoyer M, Samson Y, Dal Soglio D, Dubois J, Lallier M, Alvarez F
Pediatr Transplant 2014 Aug;18(5):E146-51. Epub 2014 May 12 doi: 10.1111/petr.12279. PMID: 24815678

Diagnosis

Biliary Embryonal Rhabdomyosarcoma: A Case Report.
Chowdhury MM, Warid MM, Mohammed S, Sobhan SA, Haque MN, Quiyum MA, Rahman Z, Mahmud R, Tanjim SM, Rahman MM
Mymensingh Med J 2023 Jul;32(3):880-883. PMID: 37391989
A Rare Association With Obstructive Jaundice.
Borges VP, Alves R, Coimbra J
Gastroenterology 2020 Apr;158(5):e12-e13. Epub 2019 Nov 15 doi: 10.1053/j.gastro.2019.10.043. PMID: 31738922
A child with unresectable biliary rhabdomyosarcoma: 48-month disease-free survival after liver transplantation.
Paganelli M, Beaunoyer M, Samson Y, Dal Soglio D, Dubois J, Lallier M, Alvarez F
Pediatr Transplant 2014 Aug;18(5):E146-51. Epub 2014 May 12 doi: 10.1111/petr.12279. PMID: 24815678
Embryonal rhabdomyosarcoma of the ampulla of Vater in early childhood: report of a case and review of literature.
Perera MT, McKiernan PJ, Brundler MA, Hobin DA, Mayer DA, Mirza DF, Sharif K
J Pediatr Surg 2009 Feb;44(2):e9-e11. doi: 10.1016/j.jpedsurg.2008.10.113. PMID: 19231522
Embryonal rhabdomyosarcoma (sarcoma botryoides) of the common bile duct: a case report.
Majmudar B, Kumar VS
Hum Pathol 1976 Nov;7(6):705-8. doi: 10.1016/s0046-8177(76)80081-0. PMID: 992649

Therapy

A child with unresectable biliary rhabdomyosarcoma: 48-month disease-free survival after liver transplantation.
Paganelli M, Beaunoyer M, Samson Y, Dal Soglio D, Dubois J, Lallier M, Alvarez F
Pediatr Transplant 2014 Aug;18(5):E146-51. Epub 2014 May 12 doi: 10.1111/petr.12279. PMID: 24815678

Prognosis

Hepatobiliary rhabdomyosarcoma in children: diagnostic radiology.
Roebuck DJ, Yang WT, Lam WW, Stanley P
Pediatr Radiol 1998 Feb;28(2):101-8. doi: 10.1007/s002470050305. PMID: 9472056
Embryonal rhabdomyosarcoma of the ampulla of Vater with long-term survival following pancreaticoduodenectomy.
Caty MG, Oldham KT, Prochownik EV
J Pediatr Surg 1990 Dec;25(12):1256-8. doi: 10.1016/0022-3468(90)90523-c. PMID: 2286899
Sarcoma botryoides of the extrahepatic bile ducts. A light- and electron microscopic study of a case.
Kindblom LG, Dalberg K
Pathol Res Pract 1980 Dec;170(1-3):258-66. doi: 10.1016/S0344-0338(80)80172-5. PMID: 18788169
Embryonal rhabdomyosarcoma (sarcoma botryoides) of the common bile duct: a case report.
Majmudar B, Kumar VS
Hum Pathol 1976 Nov;7(6):705-8. doi: 10.1016/s0046-8177(76)80081-0. PMID: 992649

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