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Thyroid lymphoma

MedGen UID:
234947
Concept ID:
C1336753
Neoplastic Process
Synonyms: Lymphoma of the Thyroid; lymphoma of the thyroid; Lymphoma of the Thyroid Gland; lymphoma of the thyroid gland; Lymphoma of Thyroid; lymphoma of thyroid; Lymphoma of Thyroid Gland; lymphoma of thyroid gland; Malignant lymphoma of thyroid gland; Primary Thyroid Gland Lymphoma; primary thyroid gland lymphoma; Thyroid Gland Lymphoma; thyroid gland lymphoma; Thyroid Lymphoma; thyroid lymphoma
SNOMED CT: Malignant lymphoma of thyroid gland (278051002)
 
Monarch Initiative: MONDO:0019962
Orphanet: ORPHA97285

Definition

A rare primary organ-specific lymphoma characterized by primary origin in the thyroid gland, sometimes involving cervical lymph nodes, and infrequently more distant sites. Diffuse large B-cell lymphoma is most common, followed by MALT lymphoma, and follicular lymphoma. More rare types include T-cell lymphomas, Burkitt lymphoma, or classic Hodgkin lymphoma. The condition is usually associated with Hashimoto thyroiditis. Patients typically present with a mass in the thyroid, with or without cervical lymphadenopathy. Hoarseness and dyspnea may occur, while constitutional symptoms are rare. Prognosis is favorable for patients with localized tumors. [from ORDO]

Professional guidelines

PubMed

Klubo-Gwiezdzinska J, Wartofsky L
Pol Arch Intern Med 2022 Mar 30;132(3) Epub 2022 Mar 3 doi: 10.20452/pamw.16222. PMID: 35243857Free PMC Article
Pynnonen MA, Gillespie MB, Roman B, Rosenfeld RM, Tunkel DE, Bontempo L, Brook I, Chick DA, Colandrea M, Finestone SA, Fowler JC, Griffith CC, Henson Z, Levine C, Mehta V, Salama A, Scharpf J, Shatzkes DR, Stern WB, Youngerman JS, Corrigan MD
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Johnson CA, King HS, Dent D, Jacobs P
S Afr Med J 1991 Aug 3;80(3):161-2. PMID: 1862455

Recent clinical studies

Etiology

Klubo-Gwiezdzinska J, Wartofsky L
Pol Arch Intern Med 2022 Mar 30;132(3) Epub 2022 Mar 3 doi: 10.20452/pamw.16222. PMID: 35243857Free PMC Article
Canberk S, Thodou E, Bongiovanni M
Acta Cytol 2022;66(4):307-318. Epub 2022 Jan 11 doi: 10.1159/000520876. PMID: 35016187
Walsh S, Lowery AJ, Evoy D, McDermott EW, Prichard RS
Oncologist 2013;18(9):994-1003. Epub 2013 Jul 23 doi: 10.1634/theoncologist.2013-0036. PMID: 23881987Free PMC Article
Widder S, Pasieka JL
Curr Treat Options Oncol 2004 Aug;5(4):307-13. doi: 10.1007/s11864-004-0021-7. PMID: 15233907
Honing ML, Seldenrijk CA, de Maat CE
Neth J Med 1998 Feb;52(2):75-8. doi: 10.1016/s0300-2977(97)00085-5. PMID: 9557530

Diagnosis

Rovira A, Carroll P, Simo R
Curr Opin Otolaryngol Head Neck Surg 2023 Apr 1;31(2):83-88. doi: 10.1097/MOO.0000000000000875. PMID: 36912220
Bhattacharya S, Kantroo V, Atreja A, Kalra S
J Pak Med Assoc 2022 Oct;72(10):2117-2118. doi: 10.47391/JPMA.22-102. PMID: 36661012
Klubo-Gwiezdzinska J, Wartofsky L
Pol Arch Intern Med 2022 Mar 30;132(3) Epub 2022 Mar 3 doi: 10.20452/pamw.16222. PMID: 35243857Free PMC Article
Czopnik P, Aporowicz M, Niepokój-Czopnik A, Wojtczak B, Domosławski P, Bolanowski M
Pol Arch Intern Med 2017 May 31;127(5):361-364. doi: 10.20452/pamw.4037. PMID: 28581452
Ito Y, Amino N, Miyauchi A
World J Surg 2010 Jun;34(6):1171-80. doi: 10.1007/s00268-009-0211-3. PMID: 19823911

Therapy

Klubo-Gwiezdzinska J, Wartofsky L
Pol Arch Intern Med 2022 Mar 30;132(3) Epub 2022 Mar 3 doi: 10.20452/pamw.16222. PMID: 35243857Free PMC Article
Spielman DB, Badhey A, Kadakia S, Inman JC, Ducic Y
Clin Oncol (R Coll Radiol) 2017 May;29(5):298-306. Epub 2017 Feb 24 doi: 10.1016/j.clon.2017.01.041. PMID: 28242165
Widder S, Pasieka JL
Curr Treat Options Oncol 2004 Aug;5(4):307-13. doi: 10.1007/s11864-004-0021-7. PMID: 15233907
Ansell SM, Grant CS, Habermann TM
Semin Oncol 1999 Jun;26(3):316-23. PMID: 10375088
Honing ML, Seldenrijk CA, de Maat CE
Neth J Med 1998 Feb;52(2):75-8. doi: 10.1016/s0300-2977(97)00085-5. PMID: 9557530

Prognosis

Rovira A, Carroll P, Simo R
Curr Opin Otolaryngol Head Neck Surg 2023 Apr 1;31(2):83-88. doi: 10.1097/MOO.0000000000000875. PMID: 36912220
Rezkallah E, Hanna RS, Elsaify WM
Am Surg 2023 Nov;89(11):4811-4816. Epub 2022 Jun 27 doi: 10.1177/00031348221111512. PMID: 35759750
Bai Z, Li L, Guan T, Wang J, Zhao J, Su L
Medicine (Baltimore) 2021 Feb 12;100(6):e24598. doi: 10.1097/MD.0000000000024598. PMID: 33578562Free PMC Article
Widder S, Pasieka JL
Curr Treat Options Oncol 2004 Aug;5(4):307-13. doi: 10.1007/s11864-004-0021-7. PMID: 15233907
Honing ML, Seldenrijk CA, de Maat CE
Neth J Med 1998 Feb;52(2):75-8. doi: 10.1016/s0300-2977(97)00085-5. PMID: 9557530

Clinical prediction guides

Vander Poorten V, Goedseels N, Triantafyllou A, Sanabria A, Clement PM, Cohen O, Golusinski P, Guntinas-Lichius O, Piazza C, Randolph GW, Rinaldo A, Ronen O, Cabanillas ME, Shaha AR, Teng Y, Tufano RP, Williams MD, Zafereo M, Ferlito A
Front Endocrinol (Lausanne) 2022;13:971249. Epub 2022 Sep 20 doi: 10.3389/fendo.2022.971249. PMID: 36204100Free PMC Article
Bai Z, Li L, Guan T, Wang J, Zhao J, Su L
Medicine (Baltimore) 2021 Feb 12;100(6):e24598. doi: 10.1097/MD.0000000000024598. PMID: 33578562Free PMC Article
Hirokawa M, Suzuki A, Hashimoto Y, Satoh S, Canberk S, Jhuang JY, Jung CK, Tangnuntachai N, Kovacevic B, Zhu Y, Agarwal S, Kakudo K
Endocr J 2020 Nov 28;67(11):1085-1091. Epub 2020 Jul 9 doi: 10.1507/endocrj.EJ20-0202. PMID: 32641619
Travaglino A, Pace M, Varricchio S, Insabato L, Picardi M, Severino A, Pane F, Staibano S, Mascolo M
Pathol Res Pract 2020 Mar;216(3):152819. Epub 2020 Jan 10 doi: 10.1016/j.prp.2020.152819. PMID: 31974002
Li P, Zhang H
Ultrasound Q 2019 Sep;35(3):246-252. doi: 10.1097/RUQ.0000000000000414. PMID: 30601440

Recent systematic reviews

Vander Poorten V, Goedseels N, Triantafyllou A, Sanabria A, Clement PM, Cohen O, Golusinski P, Guntinas-Lichius O, Piazza C, Randolph GW, Rinaldo A, Ronen O, Cabanillas ME, Shaha AR, Teng Y, Tufano RP, Williams MD, Zafereo M, Ferlito A
Front Endocrinol (Lausanne) 2022;13:971249. Epub 2022 Sep 20 doi: 10.3389/fendo.2022.971249. PMID: 36204100Free PMC Article
Travaglino A, Pace M, Varricchio S, Insabato L, Picardi M, Severino A, Pane F, Staibano S, Mascolo M
Pathol Res Pract 2020 Mar;216(3):152819. Epub 2020 Jan 10 doi: 10.1016/j.prp.2020.152819. PMID: 31974002

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