U.S. flag

An official website of the United States government

Format

Send to:

Choose Destination

Orbit alveolar rhabdomyosarcoma

MedGen UID:
235408
Concept ID:
C1335126
Neoplastic Process
Synonyms: Alveolar Rhabdomyosarcoma of Orbit; alveolar rhabdomyosarcoma of orbit; Alveolar Rhabdomyosarcoma of the Orbit; alveolar rhabdomyosarcoma of the orbit; Orbit Alveolar Rhabdomyosarcoma; orbit alveolar rhabdomyosarcoma
 
Monarch Initiative: MONDO:0002978

Definition

A malignant mesenchymal neoplasm that arises in the orbit. It is characterized by the presence of round cells with myoblastic differentiation and a fibrovascular stroma. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVOrbit alveolar rhabdomyosarcoma

Professional guidelines

PubMed

Sobel RK, Ford JR, Dong W, Shriver E, Griepentrog GJ, Debnam JM, Esmaeli B
Am J Ophthalmol 2022 Feb;234:28-36. Epub 2021 Jul 17 doi: 10.1016/j.ajo.2021.06.035. PMID: 34280364
Darwish C, Shim T, Sparks AD, Chillakuru Y, Strum D, Benito DA, Monfared A
Int J Pediatr Otorhinolaryngol 2020 Dec;139:110403. Epub 2020 Sep 25 doi: 10.1016/j.ijporl.2020.110403. PMID: 33049553
Grosfeld JL
J Am Coll Surg 1999 Oct;189(4):407-25. doi: 10.1016/s1072-7515(99)00167-2. PMID: 10509467

Recent clinical studies

Etiology

Darwish C, Shim T, Sparks AD, Chillakuru Y, Strum D, Benito DA, Monfared A
Int J Pediatr Otorhinolaryngol 2020 Dec;139:110403. Epub 2020 Sep 25 doi: 10.1016/j.ijporl.2020.110403. PMID: 33049553
Iatrou I, Theologie-Lygidakis N, Schoinohoriti O, Tzermpos F, Vessala AM
J Craniomaxillofac Surg 2017 Jun;45(6):831-838. Epub 2017 Mar 23 doi: 10.1016/j.jcms.2017.03.005. PMID: 28431807
Arnold MA, Anderson JR, Gastier-Foster JM, Barr FG, Skapek SX, Hawkins DS, Raney RB Jr, Parham DM, Teot LA, Rudzinski ER, Walterhouse DO
Pediatr Blood Cancer 2016 Apr;63(4):634-9. Epub 2016 Jan 12 doi: 10.1002/pbc.25862. PMID: 26756883Free PMC Article
Karcioglu ZA, Hadjistilianou D, Rozans M, DeFrancesco S
Cancer Control 2004 Sep-Oct;11(5):328-33. doi: 10.1177/107327480401100507. PMID: 15377992
Grosfeld JL
J Am Coll Surg 1999 Oct;189(4):407-25. doi: 10.1016/s1072-7515(99)00167-2. PMID: 10509467

Diagnosis

Milman T, Ida CM, Zhang PJL, Eagle RC Jr
Am J Ophthalmol 2021 Jan;221:211-225. Epub 2020 Aug 13 doi: 10.1016/j.ajo.2020.08.012. PMID: 32800827
Cortes Barrantes P, Jakobiec FA, Dryja TP
Semin Ophthalmol 2019;34(4):243-251. Epub 2019 May 30 doi: 10.1080/08820538.2019.1620802. PMID: 31146616
Turner JH, Richmon JD
Otolaryngol Head Neck Surg 2011 Dec;145(6):967-73. Epub 2011 Aug 26 doi: 10.1177/0194599811417063. PMID: 21873599
Karcioglu ZA, Hadjistilianou D, Rozans M, DeFrancesco S
Cancer Control 2004 Sep-Oct;11(5):328-33. doi: 10.1177/107327480401100507. PMID: 15377992
Grosfeld JL
J Am Coll Surg 1999 Oct;189(4):407-25. doi: 10.1016/s1072-7515(99)00167-2. PMID: 10509467

Therapy

Afghani T, Mansoor H, Mughal AM, Asif M, Asif M, Hamdani NR
J Coll Physicians Surg Pak 2019 Jun;29(6):553-557. doi: 10.29271/jcpsp.2019.06.553. PMID: 31133156
Casey DL, Wexler LH, Wolden SL
Int J Radiat Oncol Biol Phys 2019 Apr 1;103(5):1151-1157. Epub 2018 Nov 30 doi: 10.1016/j.ijrobp.2018.11.049. PMID: 30508617Free PMC Article
Häußler SM, Stromberger C, Olze H, Seifert G, Knopke S, Böttcher A
J Cancer Res Clin Oncol 2018 Feb;144(2):371-379. Epub 2017 Nov 16 doi: 10.1007/s00432-017-2544-x. PMID: 29143871
Sarkar D, Ray S, Saha M, Chakrabarti P
BMJ Case Rep 2012 Sep 3;2012 doi: 10.1136/bcr-2012-006523. PMID: 22948994Free PMC Article
Karcioglu ZA, Hadjistilianou D, Rozans M, DeFrancesco S
Cancer Control 2004 Sep-Oct;11(5):328-33. doi: 10.1177/107327480401100507. PMID: 15377992

Prognosis

Milman T, Ida CM, Zhang PJL, Eagle RC Jr
Am J Ophthalmol 2021 Jan;221:211-225. Epub 2020 Aug 13 doi: 10.1016/j.ajo.2020.08.012. PMID: 32800827
Cortes Barrantes P, Jakobiec FA, Dryja TP
Semin Ophthalmol 2019;34(4):243-251. Epub 2019 May 30 doi: 10.1080/08820538.2019.1620802. PMID: 31146616
Iatrou I, Theologie-Lygidakis N, Schoinohoriti O, Tzermpos F, Vessala AM
J Craniomaxillofac Surg 2017 Jun;45(6):831-838. Epub 2017 Mar 23 doi: 10.1016/j.jcms.2017.03.005. PMID: 28431807
Company F, Pedram M, Rezaei N
Acta Med Iran 2011;49(4):219-24. PMID: 21713731
Karcioglu ZA, Hadjistilianou D, Rozans M, DeFrancesco S
Cancer Control 2004 Sep-Oct;11(5):328-33. doi: 10.1177/107327480401100507. PMID: 15377992

Clinical prediction guides

Zeng J, Liu L, Li J, Huang Q, Pi L, Jin K
Dentomaxillofac Radiol 2021 Dec 1;50(8):20210030. Epub 2021 Apr 9 doi: 10.1259/dmfr.20210030. PMID: 33835837Free PMC Article
Afghani T, Mansoor H, Mughal AM, Asif M, Asif M, Hamdani NR
J Coll Physicians Surg Pak 2019 Jun;29(6):553-557. doi: 10.29271/jcpsp.2019.06.553. PMID: 31133156
Machleder DJ, Banik R, Rosenberg RB, Parikh SR
Int J Pediatr Otorhinolaryngol 2005 Feb;69(2):249-54. doi: 10.1016/j.ijporl.2004.07.018. PMID: 15656960
Hicks J, Flaitz C
Oral Oncol 2002 Jul;38(5):450-9. doi: 10.1016/s1368-8375(01)00105-1. PMID: 12110339
Grosfeld JL
J Am Coll Surg 1999 Oct;189(4):407-25. doi: 10.1016/s1072-7515(99)00167-2. PMID: 10509467

Supplemental Content

Table of contents

    Clinical resources

    Practice guidelines

    • PubMed
      See practice and clinical guidelines in PubMed. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.
    • Bookshelf
      See practice and clinical guidelines in NCBI Bookshelf. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.

    Consumer resources

    Recent activity

    Your browsing activity is empty.

    Activity recording is turned off.

    Turn recording back on

    See more...