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Rectum rhabdomyosarcoma

MedGen UID:
235532
•Concept ID:
C1335687
•
Neoplastic Process
Synonyms: Rectal Rhabdomyosarcoma; rectal rhabdomyosarcoma; rectum rhabdomyosarcoma; rectum rhabdomyosarcoma (disease); rhabdomyosarcoma (disease) of rectum; Rhabdomyosarcoma of Rectum; rhabdomyosarcoma of rectum; Rhabdomyosarcoma of the Rectum; rhabdomyosarcoma of the rectum
 
Monarch Initiative: MONDO:0002853

Definition

A malignant mesenchymal tumor with skeletal muscle differentiation affecting the rectum. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVRectum rhabdomyosarcoma

Professional guidelines

PubMed

Management of stage I cervical sarcoma botryoides in childhood and adolescence.
Gruessner SE, Omwandho CO, Dreyer T, Blütters-Sawatzki R, Reiter A, Tinneberg HR, Bohle RM
Eur J Pediatr 2004 Aug;163(8):452-6. Epub 2004 Jun 2 doi: 10.1007/s00431-004-1469-y. PMID: 15173941

Recent clinical studies

Etiology

Pediatric presacral tumors with intraspinal extension: a rare entity with diagnostic challenges.
A E, Prakash A, Ashta A, Garg A, Verma A, Padaliya P
Acta Radiol 2023 Dec;64(12):3056-3073. Epub 2023 Sep 27 doi: 10.1177/02841851231202688. PMID: 37753549
Primitive neuroectodermal tumor in a child with Currarino syndrome.
Çebi MN, Yılmaz G, Çelikdemir G, Özcan R, Ocak S, Celkan TT, Çomunoğlu N
Turk J Pediatr 2022;64(2):385-388. doi: 10.24953/turkjped.2021.264. PMID: 35611429
Use of an intravaginal spacer in young girls treated with brachytherapy for bladder neck rhabdomyosarcoma: Dosimetric impact for organs at risk sparing and acute tolerance.
Limkin EJ, Guérin F, Espenel S, Terlizzi M, Martelli H, Haie-Meder C, Minard V, Chargari C
Cancer Radiother 2022 May;26(3):486-490. Epub 2021 Oct 26 doi: 10.1016/j.canrad.2021.09.010. PMID: 34711484
Perianal and perineal rhabdomyosarcomas: a retrospective multicenter study of 35 cases.
Guo Y, Hu B, Huang D, Wang X, Li J, Zhang D, Li X, Chen G, Ren D
BMC Surg 2021 Jan 30;21(1):66. doi: 10.1186/s12893-021-01073-x. PMID: 33516222Free PMC Article
Pelvic neoplasms in children.
Groff DB
J Surg Oncol 2001 May;77(1):65-71. doi: 10.1002/jso.1068. PMID: 11344486

Diagnosis

Pediatric presacral tumors with intraspinal extension: a rare entity with diagnostic challenges.
A E, Prakash A, Ashta A, Garg A, Verma A, Padaliya P
Acta Radiol 2023 Dec;64(12):3056-3073. Epub 2023 Sep 27 doi: 10.1177/02841851231202688. PMID: 37753549
Primitive neuroectodermal tumor in a child with Currarino syndrome.
Çebi MN, Yılmaz G, Çelikdemir G, Özcan R, Ocak S, Celkan TT, Çomunoğlu N
Turk J Pediatr 2022;64(2):385-388. doi: 10.24953/turkjped.2021.264. PMID: 35611429
Perianal and perineal rhabdomyosarcomas: a retrospective multicenter study of 35 cases.
Guo Y, Hu B, Huang D, Wang X, Li J, Zhang D, Li X, Chen G, Ren D
BMC Surg 2021 Jan 30;21(1):66. doi: 10.1186/s12893-021-01073-x. PMID: 33516222Free PMC Article
Impact of bowel and rectum air on target dose with robustly optimized intensity-modulated proton therapy plans.
Yao W, Schweitzer N, Biswal N, Polf J, Farr J, Vujaskovic Z
Acta Oncol 2020 Oct;59(10):1186-1192. Epub 2020 Jun 5 doi: 10.1080/0284186X.2020.1769859. PMID: 32500780
Pelvic neoplasms in children.
Groff DB
J Surg Oncol 2001 May;77(1):65-71. doi: 10.1002/jso.1068. PMID: 11344486

Therapy

Use of an intravaginal spacer in young girls treated with brachytherapy for bladder neck rhabdomyosarcoma: Dosimetric impact for organs at risk sparing and acute tolerance.
Limkin EJ, Guérin F, Espenel S, Terlizzi M, Martelli H, Haie-Meder C, Minard V, Chargari C
Cancer Radiother 2022 May;26(3):486-490. Epub 2021 Oct 26 doi: 10.1016/j.canrad.2021.09.010. PMID: 34711484
Analysis of Radiation Dose/Volume Effect Relationship for Anorectal Morbidity in Children Treated for Pelvic Malignancies.
Romano E, Simon R, Minard-Colin V, Martin V, Bockel S, Espenel S, Fresneau B, Metayer L, Levy A, Guerin F, Martelli H, Dumas I, Bolle S, Deutsch E, Haie-Meder C, Chargari C
Int J Radiat Oncol Biol Phys 2021 Jan 1;109(1):231-241. Epub 2020 Aug 14 doi: 10.1016/j.ijrobp.2020.08.033. PMID: 32805302
Pulsed-dose rate brachytherapy for pediatric bladder prostate rhabdomyosarcoma: Compliance and early clinical results.
Chargari C, Martelli H, Guérin F, Bacorro W, de Lambert G, Escande A, Minard-Colin V, Dumas I, Deutsch E, Haie-Meder C
Radiother Oncol 2017 Aug;124(2):285-290. Epub 2017 Jul 28 doi: 10.1016/j.radonc.2017.07.010. PMID: 28760484
Second cancers in children treated with modern radiotherapy techniques.
Schneider U, Lomax A, Timmermann B
Radiother Oncol 2008 Nov;89(2):135-40. Epub 2008 Aug 15 doi: 10.1016/j.radonc.2008.07.017. PMID: 18707783
Management of stage I cervical sarcoma botryoides in childhood and adolescence.
Gruessner SE, Omwandho CO, Dreyer T, Blütters-Sawatzki R, Reiter A, Tinneberg HR, Bohle RM
Eur J Pediatr 2004 Aug;163(8):452-6. Epub 2004 Jun 2 doi: 10.1007/s00431-004-1469-y. PMID: 15173941

Prognosis

Perianal and perineal rhabdomyosarcomas: a retrospective multicenter study of 35 cases.
Guo Y, Hu B, Huang D, Wang X, Li J, Zhang D, Li X, Chen G, Ren D
BMC Surg 2021 Jan 30;21(1):66. doi: 10.1186/s12893-021-01073-x. PMID: 33516222Free PMC Article
Impact of bowel and rectum air on target dose with robustly optimized intensity-modulated proton therapy plans.
Yao W, Schweitzer N, Biswal N, Polf J, Farr J, Vujaskovic Z
Acta Oncol 2020 Oct;59(10):1186-1192. Epub 2020 Jun 5 doi: 10.1080/0284186X.2020.1769859. PMID: 32500780
Colon pouch (Mainz III) for continent urinary diversion.
Stolzenburg JU, Schwalenberg T, Liatsikos EN, Sakelaropoulos G, Rödder K, Hohenfellner R, Fisch M
BJU Int 2007 Jun;99(6):1473-7. Epub 2007 Mar 6 doi: 10.1111/j.1464-410X.2007.06767.x. PMID: 17346278
The posterior midsagittal approach for the surgical excision of intrapelvic malignant tumours.
Keramidas DC, Soutis M, Koulopoulos K, Moschovi M
Eur J Pediatr Surg 2003 Aug;13(4):245-8. doi: 10.1055/s-2003-42241. PMID: 13680493
Perineal and perirectal sarcomas: report of two cases.
Kessler KJ, Kerlakian GM, Welling RE
Dis Colon Rectum 1996 Apr;39(4):468-72. doi: 10.1007/BF02054066. PMID: 8878511

Clinical prediction guides

Pediatric presacral tumors with intraspinal extension: a rare entity with diagnostic challenges.
A E, Prakash A, Ashta A, Garg A, Verma A, Padaliya P
Acta Radiol 2023 Dec;64(12):3056-3073. Epub 2023 Sep 27 doi: 10.1177/02841851231202688. PMID: 37753549
Analysis of Radiation Dose/Volume Effect Relationship for Anorectal Morbidity in Children Treated for Pelvic Malignancies.
Romano E, Simon R, Minard-Colin V, Martin V, Bockel S, Espenel S, Fresneau B, Metayer L, Levy A, Guerin F, Martelli H, Dumas I, Bolle S, Deutsch E, Haie-Meder C, Chargari C
Int J Radiat Oncol Biol Phys 2021 Jan 1;109(1):231-241. Epub 2020 Aug 14 doi: 10.1016/j.ijrobp.2020.08.033. PMID: 32805302
Posterior sagittal approach with perirectal dissection for reconstructive surgery of severe urogenital anomalies.
Pinter A, Hock A, Vastyan AM, Farkas A, Oberritter Z
Pediatr Surg Int 2007 Jan;23(1):57-60. Epub 2006 Oct 28 doi: 10.1007/s00383-006-1809-2. PMID: 17072623
Management of stage I cervical sarcoma botryoides in childhood and adolescence.
Gruessner SE, Omwandho CO, Dreyer T, Blütters-Sawatzki R, Reiter A, Tinneberg HR, Bohle RM
Eur J Pediatr 2004 Aug;163(8):452-6. Epub 2004 Jun 2 doi: 10.1007/s00431-004-1469-y. PMID: 15173941

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