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Constriction ring syndrome

MedGen UID:
265
Concept ID:
C0002636
Disease or Syndrome
Synonyms: Amniotic Band Syndrome; Streeter Syndrome; Syndrome, Amniotic Band; Syndrome, Streeter
SNOMED CT: Congenital constriction band (765206003); Constriction ring syndrome (765206003); Amniotic band syndrome (765206003); Deformity due to amniotic band (765206003)

Definition

Disorder with an extremely variable clinical presentation characterised by the presence of partial to complete, congenital, fibrous, circumferential, constriction bands/rings on any part of the body, although a particular predilection for the upper or lower extremities is seen. Phenotypes range from only a mild skin indentation to complete amputation of parts of the fetus (for example digits, distal limb). Compression from the rings may lead to oedema, skeletal anomalies (for example fractures, foot deformities) and infrequently neural compromise. [from SNOMEDCT_US]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVConstriction ring syndrome

Professional guidelines

PubMed

Weber SU, Kranke P
Curr Opin Anaesthesiol 2019 Jun;32(3):291-297. doi: 10.1097/ACO.0000000000000718. PMID: 31045636
Mathis J, Raio L, Baud D
Prenat Diagn 2015 Jul;35(7):623-36. Epub 2015 Apr 5 doi: 10.1002/pd.4587. PMID: 25736523
Barzilay E, Harel Y, Haas J, Berkenstadt M, Katorza E, Achiron R, Gilboa Y
J Matern Fetal Neonatal Med 2015 Feb;28(3):281-3. Epub 2014 May 22 doi: 10.3109/14767058.2014.915935. PMID: 24735486

Recent clinical studies

Etiology

Furukawa H, Nakamura T, Wada A, Takamura K, Yanagida H, Yamaguchi T
J Hand Surg Asian Pac Vol 2023 Jun;28(3):315-320. Epub 2023 May 5 doi: 10.1142/S2424835523500327. PMID: 37173140
Garagnani L, Gibson M, Smith PJ, Smith GD
J Hand Surg Am 2012 Apr;37(4):764-74. Epub 2012 Feb 3 doi: 10.1016/j.jhsa.2011.12.010. PMID: 22305432
Ekblom AG, Laurell T, Arner M
J Hand Surg Am 2010 Nov;35(11):1742-54. Epub 2010 Oct 20 doi: 10.1016/j.jhsa.2010.07.007. PMID: 20961708
Cavallo AV, Smith PJ, Morley S, Morsi AW
J Hand Surg Br 2003 Dec;28(6):520-7. doi: 10.1016/s0266-7681(03)00084-6. PMID: 14599822
Van Holder C, Giele H, Gilbert A
J Hand Surg Br 1999 Aug;24(4):471-5. doi: 10.1054/jhsb.1999.0162. PMID: 10473161

Diagnosis

Furukawa H, Nakamura T, Wada A, Takamura K, Yanagida H, Yamaguchi T
J Hand Surg Asian Pac Vol 2023 Jun;28(3):315-320. Epub 2023 May 5 doi: 10.1142/S2424835523500327. PMID: 37173140
Garagnani L, Gibson M, Smith PJ, Smith GD
J Hand Surg Am 2012 Apr;37(4):764-74. Epub 2012 Feb 3 doi: 10.1016/j.jhsa.2011.12.010. PMID: 22305432
Bates SJ, Hansen SL, Jones NF
Plast Reconstr Surg 2009 Jul;124(1 Suppl):128e-143e. doi: 10.1097/PRS.0b013e3181a80777. PMID: 19568146
Bernal E, Oeltjen JC
J Craniofac Surg 2009 Jul;20(4):1018-20. doi: 10.1097/SCS.0b013e3181abb156. PMID: 19553861
Smith AM, Peckett W, Davies M
Foot Ankle Int 2003 Aug;24(8):640-1. doi: 10.1177/107110070302400812. PMID: 12956571

Therapy

Pahwa HS, Kumar A, Srivastava R, Kumar S, Goel A, Ahmad A
Urology 2013 Mar;81(3):653-4. Epub 2013 Jan 3 doi: 10.1016/j.urology.2012.11.012. PMID: 23290150
Smith AM, Peckett W, Davies M
Foot Ankle Int 2003 Aug;24(8):640-1. doi: 10.1177/107110070302400812. PMID: 12956571

Prognosis

Garagnani L, Gibson M, Smith PJ, Smith GD
J Hand Surg Am 2012 Apr;37(4):764-74. Epub 2012 Feb 3 doi: 10.1016/j.jhsa.2011.12.010. PMID: 22305432
Ekblom AG, Laurell T, Arner M
J Hand Surg Am 2010 Nov;35(11):1742-54. Epub 2010 Oct 20 doi: 10.1016/j.jhsa.2010.07.007. PMID: 20961708
O'Quinn JC, Friedman RL, Wilms KL
J Am Podiatr Med Assoc 2006 May-Jun;96(3):253-5. doi: 10.7547/0960253. PMID: 16707638
Cavallo AV, Smith PJ, Morley S, Morsi AW
J Hand Surg Br 2003 Dec;28(6):520-7. doi: 10.1016/s0266-7681(03)00084-6. PMID: 14599822
Smith AM, Peckett W, Davies M
Foot Ankle Int 2003 Aug;24(8):640-1. doi: 10.1177/107110070302400812. PMID: 12956571

Clinical prediction guides

Furukawa H, Nakamura T, Wada A, Takamura K, Yanagida H, Yamaguchi T
J Hand Surg Asian Pac Vol 2023 Jun;28(3):315-320. Epub 2023 May 5 doi: 10.1142/S2424835523500327. PMID: 37173140
Ogino T
Clin Orthop Relat Res 1996 Feb;(323):12-21. doi: 10.1097/00003086-199602000-00003. PMID: 8625568

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