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Cranial nodular fasciitis

MedGen UID:
272511
Concept ID:
C1333162
Neoplastic Process
Synonyms: Cranial Nodular Fasciitis; cranial nodular fasciitis; Cranial Pseudosarcomatous Fasciitis; cranial pseudosarcomatous fasciitis
 
Monarch Initiative: MONDO:0004186

Definition

A rare, self-limiting, rapidly growing, non-encapsulated benign osteolytic neoplasm that arises from the cranium. It is characterized by the presence of plump spindle-shaped fibroblasts, multinucleated osteoclast-like giant cells, chronic inflammatory infiltrate, red blood cell extravasation, and high mitotic activity. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVCranial nodular fasciitis

Recent clinical studies

Etiology

Baranov E, Hornick JL
Head Neck Pathol 2020 Mar;14(1):43-58. Epub 2020 Jan 16 doi: 10.1007/s12105-019-01104-3. PMID: 31950474Free PMC Article
Kaçar A, Paker I, Orhan D, Poyraz A, Okçu Heper A, Arda N, Boduroğlu E
Turk Patoloji Derg 2012;28(1):24-30. doi: 10.5146/tjpath.2012.01093. PMID: 22207428
Kim ST, Kim HJ, Park SW, Baek CH, Byun HS, Kim YM
AJNR Am J Neuroradiol 2005 Nov-Dec;26(10):2617-23. PMID: 16286411Free PMC Article
Kang SK, Kim HH, Ahn SJ, Choi JH, Sung KJ, Moon KC, Koh JK
J Dermatol 2002 May;29(5):310-4. doi: 10.1111/j.1346-8138.2002.tb00269.x. PMID: 12081164
Sarangarajan R, Dehner LP
Hum Pathol 1999 Jan;30(1):87-92. doi: 10.1016/s0046-8177(99)90306-4. PMID: 9923933

Diagnosis

Paulson VA, Stojanov IA, Wasman JK, Restrepo T, Cano S, Plunkitt J, Duraisamy S, Harris MH, Chute DJ, Al-Ibraheemi A, Church AJ
Mod Pathol 2020 May;33(5):775-780. Epub 2019 Dec 11 doi: 10.1038/s41379-019-0422-6. PMID: 31827231
Flaman AN, Wasserman JK, Gravel DH, Purgina BM
Head Neck Pathol 2018 Sep;12(3):392-406. Epub 2018 Aug 1 doi: 10.1007/s12105-018-0891-9. PMID: 30069839Free PMC Article
Kim ST, Kim HJ, Park SW, Baek CH, Byun HS, Kim YM
AJNR Am J Neuroradiol 2005 Nov-Dec;26(10):2617-23. PMID: 16286411Free PMC Article
Sarangarajan R, Dehner LP
Hum Pathol 1999 Jan;30(1):87-92. doi: 10.1016/s0046-8177(99)90306-4. PMID: 9923933
Patterson JW, Moran SL, Konerding H
Arch Dermatol 1989 May;125(5):674-8. PMID: 2653227

Therapy

Chow SP, Nastri A, Hardy T
Clin Exp Ophthalmol 2010 Oct;38(7):727-30. Epub 2010 Jul 9 doi: 10.1111/j.1442-9071.2010.02329.x. PMID: 20497435
Daroca PJ Jr, Pulitzer DR, LoCicero J 3rd
Arch Pathol Lab Med 1982 Dec;106(13):682-5. PMID: 6814399

Prognosis

Paulson VA, Stojanov IA, Wasman JK, Restrepo T, Cano S, Plunkitt J, Duraisamy S, Harris MH, Chute DJ, Al-Ibraheemi A, Church AJ
Mod Pathol 2020 May;33(5):775-780. Epub 2019 Dec 11 doi: 10.1038/s41379-019-0422-6. PMID: 31827231
Summers LE, Florez L, Berberian ZJ, Bhattacharjee M, Walsh JW
J Neurosurg 2007 Jun;106(6):1080-5. doi: 10.3171/jns.2007.106.6.1080. PMID: 17564183
Kang SK, Kim HH, Ahn SJ, Choi JH, Sung KJ, Moon KC, Koh JK
J Dermatol 2002 May;29(5):310-4. doi: 10.1111/j.1346-8138.2002.tb00269.x. PMID: 12081164
Patterson JW, Moran SL, Konerding H
Arch Dermatol 1989 May;125(5):674-8. PMID: 2653227
Lauer DH, Enzinger FM
Cancer 1980 Jan 15;45(2):401-6. doi: 10.1002/1097-0142(19800115)45:2<401::aid-cncr2820450236>3.0.co;2-c. PMID: 7351023

Clinical prediction guides

Eida S, Hotokezaka Y, Sasaki M, Hotokezaka H, Fujita S, Katayama I, Takagi Y, Sumi M
Oral Radiol 2022 Jan;38(1):175-181. Epub 2021 Jun 18 doi: 10.1007/s11282-021-00544-4. PMID: 34143356Free PMC Article
Malik F, Wang L, Yu Z, Edelman MC, Miles L, Clay MR, Hedges D, Brennan RC, Nichols KE, Beth McCarville M, Bahrami A
Histopathology 2020 Nov;77(5):760-768. Epub 2020 Sep 12 doi: 10.1111/his.14182. PMID: 32583473
Jebastin Thangaiah J, Vickery J, Selwanes W, Al-Haddad E, Perry KD, Palanisamy N, Poulik JM, Williamson SR, Chitale DA, Shehata BM
Int J Surg Pathol 2020 Sep;28(6):678-682. Epub 2020 Mar 19 doi: 10.1177/1066896920912485. PMID: 32192385
Paulson VA, Stojanov IA, Wasman JK, Restrepo T, Cano S, Plunkitt J, Duraisamy S, Harris MH, Chute DJ, Al-Ibraheemi A, Church AJ
Mod Pathol 2020 May;33(5):775-780. Epub 2019 Dec 11 doi: 10.1038/s41379-019-0422-6. PMID: 31827231
Patterson JW, Moran SL, Konerding H
Arch Dermatol 1989 May;125(5):674-8. PMID: 2653227

Recent systematic reviews

Alshareef M, Klapthor G, Alshareef A, Almadidy Z, Wright Z, Infinger L, Eskandari R
World Neurosurg 2019 May;125:e829-e842. Epub 2019 Feb 8 doi: 10.1016/j.wneu.2019.01.193. PMID: 30743035

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