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Nonanaplastic kidney Wilms tumor

MedGen UID:
277434
Concept ID:
C1335062
Neoplastic Process
Synonyms: Nonanaplastic Kidney Wilms Tumor; nonanaplastic kidney Wilms tumor; Nonanaplastic Renal Wilm's Tumor; nonanaplastic renal Wilm's tumor; Nonanaplastic Renal Wilms Tumor; nonanaplastic renal Wilms tumor; Nonanaplastic Renal Wilms' Tumor; nonanaplastic renal Wilms' tumor
 
Monarch Initiative: MONDO:0003316

Definition

Wilms tumor of the kidney characterized by the absence of nuclear anaplasia. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVNonanaplastic kidney Wilms tumor

Professional guidelines

PubMed

Abdelhafeez AH, Reljic T, Kumar A, Banu T, Cox S, Davidoff AM, Elgendy A, Ghandour K, Gerstle JT, Karpelowsky J, Kaste SC, Kechiche N, Esiashvili N, Nasir A, Ngongola A, Marollano J, Moreno AA, Muzira A, Parkes J, Saldaña LJ, Shalkow J, Vujanić GM, Velasquez T, Lakhoo K, Mukkada S, Abib S
Pediatr Blood Cancer 2022 Dec;69(12):e29906. Epub 2022 Aug 5 doi: 10.1002/pbc.29906. PMID: 35929184
Pritchard-Jones K, Moroz V, Vujanić G, Powis M, Walker J, Messahel B, Hobson R, Levitt G, Kelsey A, Mitchell C
Ann Oncol 2012 Sep;23(9):2457-2463. Epub 2012 Mar 13 doi: 10.1093/annonc/mds025. PMID: 22415585

Recent clinical studies

Etiology

Abdelhafeez AH, Reljic T, Kumar A, Banu T, Cox S, Davidoff AM, Elgendy A, Ghandour K, Gerstle JT, Karpelowsky J, Kaste SC, Kechiche N, Esiashvili N, Nasir A, Ngongola A, Marollano J, Moreno AA, Muzira A, Parkes J, Saldaña LJ, Shalkow J, Vujanić GM, Velasquez T, Lakhoo K, Mukkada S, Abib S
Pediatr Blood Cancer 2022 Dec;69(12):e29906. Epub 2022 Aug 5 doi: 10.1002/pbc.29906. PMID: 35929184
Vujanić GM, Mifsud W, Chowdhury T, Al-Saadi R, Pritchard-Jones K; Renal Tumour Special Interest Group of the Children's Cancer and Leukaemia Group
Cancer 2022 Apr 15;128(8):1666-1675. Epub 2022 Feb 4 doi: 10.1002/cncr.34107. PMID: 35119702
Vujanić GM, Schiavo Lena M, Sebire NJ
Virchows Arch 2019 Feb;474(2):227-234. Epub 2018 Dec 4 doi: 10.1007/s00428-018-2500-4. PMID: 30515564
Vujanić GM, D'Hooghe E, Popov SD, Sebire NJ, Kelsey A
Pediatr Blood Cancer 2019 Mar;66(3):e27549. Epub 2018 Nov 8 doi: 10.1002/pbc.27549. PMID: 30408319
Spreafico F, Biasoni D, Lo Vullo S, Gandola L, D'Angelo P, Terenziani M, Bianchi M, Provenzi M, Indolfi P, Pession A, Nantron M, Di Cataldo A, Morosi C, Perotti D, Catania S, Bellani FF, Collini P; AIEOP Wilms Tumor Working Group
J Urol 2017 Nov;198(5):1138-1145. Epub 2017 Jun 24 doi: 10.1016/j.juro.2017.06.081. PMID: 28655531

Diagnosis

Abdelhafeez AH, Reljic T, Kumar A, Banu T, Cox S, Davidoff AM, Elgendy A, Ghandour K, Gerstle JT, Karpelowsky J, Kaste SC, Kechiche N, Esiashvili N, Nasir A, Ngongola A, Marollano J, Moreno AA, Muzira A, Parkes J, Saldaña LJ, Shalkow J, Vujanić GM, Velasquez T, Lakhoo K, Mukkada S, Abib S
Pediatr Blood Cancer 2022 Dec;69(12):e29906. Epub 2022 Aug 5 doi: 10.1002/pbc.29906. PMID: 35929184
Vujanić GM, Mifsud W, Chowdhury T, Al-Saadi R, Pritchard-Jones K; Renal Tumour Special Interest Group of the Children's Cancer and Leukaemia Group
Cancer 2022 Apr 15;128(8):1666-1675. Epub 2022 Feb 4 doi: 10.1002/cncr.34107. PMID: 35119702
Vujanić GM, Schiavo Lena M, Sebire NJ
Virchows Arch 2019 Feb;474(2):227-234. Epub 2018 Dec 4 doi: 10.1007/s00428-018-2500-4. PMID: 30515564
Spreafico F, Biasoni D, Lo Vullo S, Gandola L, D'Angelo P, Terenziani M, Bianchi M, Provenzi M, Indolfi P, Pession A, Nantron M, Di Cataldo A, Morosi C, Perotti D, Catania S, Bellani FF, Collini P; AIEOP Wilms Tumor Working Group
J Urol 2017 Nov;198(5):1138-1145. Epub 2017 Jun 24 doi: 10.1016/j.juro.2017.06.081. PMID: 28655531
Bonadio JF, Storer B, Norkool P, Farewell VT, Beckwith JB, D'Angio GJ
J Clin Oncol 1985 Apr;3(4):513-20. doi: 10.1200/JCO.1985.3.4.513. PMID: 2984344

Therapy

Vujanić GM, D'Hooghe E, Popov SD, Sebire NJ, Kelsey A
Pediatr Blood Cancer 2019 Mar;66(3):e27549. Epub 2018 Nov 8 doi: 10.1002/pbc.27549. PMID: 30408319
Graf N, van Tinteren H, Bergeron C, Pein F, van den Heuvel-Eibrink MM, Sandstedt B, Schenk JP, Godzinski J, Oldenburger F, Furtwängler R, de Kraker J
Eur J Cancer 2012 Nov;48(17):3240-8. Epub 2012 Jul 12 doi: 10.1016/j.ejca.2012.06.007. PMID: 22795263
Boccon-Gibod L, Rey A, Sandstedt B, Delemarre J, Harms D, Vujanic G, De Kraker J, Weirich A, Tournade MF
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Am J Surg Pathol 1996 Aug;20(8):909-20. doi: 10.1097/00000478-199608000-00001. PMID: 8712292
Douglass EC, Look AT, Webber B, Parham D, Wilimas JA, Green AA, Roberson PK
J Clin Oncol 1986 Jun;4(6):975-81. doi: 10.1200/JCO.1986.4.6.975. PMID: 3012007

Prognosis

Vujanić GM, Mifsud W, Chowdhury T, Al-Saadi R, Pritchard-Jones K; Renal Tumour Special Interest Group of the Children's Cancer and Leukaemia Group
Cancer 2022 Apr 15;128(8):1666-1675. Epub 2022 Feb 4 doi: 10.1002/cncr.34107. PMID: 35119702
Woods AD, Berlow NE, Ortiz MV, Dela Cruz F, Siddiquee A, Coutinho DF, Purohit R, Freier KET, Michalek JE, Lathara M, Matlock K, Srivivasa G, Royer-Pokora B, Veselska R, Kung AL, Keller C
Pediatr Blood Cancer 2022 Feb;69(2):e29401. Epub 2021 Oct 24 doi: 10.1002/pbc.29401. PMID: 34693628Free PMC Article
Vujanić GM, Schiavo Lena M, Sebire NJ
Virchows Arch 2019 Feb;474(2):227-234. Epub 2018 Dec 4 doi: 10.1007/s00428-018-2500-4. PMID: 30515564
Spreafico F, Biasoni D, Lo Vullo S, Gandola L, D'Angelo P, Terenziani M, Bianchi M, Provenzi M, Indolfi P, Pession A, Nantron M, Di Cataldo A, Morosi C, Perotti D, Catania S, Bellani FF, Collini P; AIEOP Wilms Tumor Working Group
J Urol 2017 Nov;198(5):1138-1145. Epub 2017 Jun 24 doi: 10.1016/j.juro.2017.06.081. PMID: 28655531
Beckwith JB
Cancer Invest 1997;15(2):153-62. doi: 10.3109/07357909709115768. PMID: 9095211

Clinical prediction guides

Woods AD, Berlow NE, Ortiz MV, Dela Cruz F, Siddiquee A, Coutinho DF, Purohit R, Freier KET, Michalek JE, Lathara M, Matlock K, Srivivasa G, Royer-Pokora B, Veselska R, Kung AL, Keller C
Pediatr Blood Cancer 2022 Feb;69(2):e29401. Epub 2021 Oct 24 doi: 10.1002/pbc.29401. PMID: 34693628Free PMC Article
Natrajan R, Warren W, Messahel B, Reis-Filho JS, Brundler MA, Dome JS, Grundy PE, Vujanic G, Pritchard-Jones K, Jones C
J Clin Pathol 2008 Jan;61(1):95-102. Epub 2007 Mar 16 doi: 10.1136/jcp.2007.047159. PMID: 17369505
Fridman E, Pinthus JH, Kopolovic J, Ramon J, Mor O, Mor Y
J Urol 2006 Oct;176(4 Pt 2):1747-50. doi: 10.1016/j.juro.2006.03.118. PMID: 16945639
Perotti D, Vecchi GD, Lualdi E, Testi MA, Sozzi G, Collini P, Spreafico F, Terenziani M, Fossati-Bellani F, Radice P
J Pediatr Hematol Oncol 2005 Oct;27(10):521-5. doi: 10.1097/01.mph.0000184309.22583.66. PMID: 16217254
Li W, Kessler P, Yeger H, Alami J, Reeve AE, Heathcott R, Skeen J, Williams BR
Cancer Res 2005 Apr 1;65(7):2592-601. doi: 10.1158/0008-5472.CAN-04-1532. PMID: 15805255

Recent systematic reviews

Abdelhafeez AH, Reljic T, Kumar A, Banu T, Cox S, Davidoff AM, Elgendy A, Ghandour K, Gerstle JT, Karpelowsky J, Kaste SC, Kechiche N, Esiashvili N, Nasir A, Ngongola A, Marollano J, Moreno AA, Muzira A, Parkes J, Saldaña LJ, Shalkow J, Vujanić GM, Velasquez T, Lakhoo K, Mukkada S, Abib S
Pediatr Blood Cancer 2022 Dec;69(12):e29906. Epub 2022 Aug 5 doi: 10.1002/pbc.29906. PMID: 35929184

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