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Refractory Primary Cutaneous T-Cell Non-Hodgkin Lymphoma

MedGen UID:
311212
Concept ID:
C1709881
Neoplastic Process
Synonym: Refractory Cutaneous T-Cell Non-Hodgkin's Lymphoma

Definition

A T-cell non-Hodgkin lymphoma that arises from the skin and does not respond to treatment. [from NCI]

Professional guidelines

PubMed

Ta VA, Battistella M, Zhao LP, Dobos G, Ram-Wolff C, Madelaine I, Bories JC, Tournilhac O, Rouanet J, Veyrat-Masson R, Bouaziz JD, Marie-Cardine A, Bagot M, Bensussan A, Moins-Teisserenc H, De Masson A
J Invest Dermatol 2023 Jul;143(7):1329-1332.e3. Epub 2023 Jan 28 doi: 10.1016/j.jid.2023.01.009. PMID: 36716922
Al-Toma A, Volta U, Auricchio R, Castillejo G, Sanders DS, Cellier C, Mulder CJ, Lundin KEA
United European Gastroenterol J 2019 Jun;7(5):583-613. Epub 2019 Apr 13 doi: 10.1177/2050640619844125. PMID: 31210940Free PMC Article
del Alcázar-Viladomiu E, Tuneu-Valls A, López-Pestaña A, Vidal-Manceñido MJ
Actas Dermosifiliogr 2015 Sep;106(7):e33-9. Epub 2015 May 7 doi: 10.1016/j.ad.2015.02.008. PMID: 25960287

Recent clinical studies

Etiology

Karsten H, Matrisch L, Cichutek S, Fiedler W, Alsdorf W, Block A
Front Immunol 2023;14:1285406. Epub 2023 Nov 27 doi: 10.3389/fimmu.2023.1285406. PMID: 38090582Free PMC Article
de Masson A, Beylot-Barry M, Ram-Wolff C, Mear JB, Dalle S, d'Incan M, Ingen-Housz-Oro S, Orvain C, Abraham J, Dereure O, Charbonnier A, Cornillon J, Longvert C, Barete S, Boulinguez S, Wierzbicka-Hainaut E, Aubin F, Rubio MT, Bernard M, Schmidt-Tanguy A, Houot R, Pham-Ledard A, Michonneau D, Brice P, Labussière-Wallet H, Bouaziz JD, Grange F, Moins-Teisserenc H, Jondeau K, Michel L, Mourah S, Battistella M, Daguindau E, Loschi M, Picard A, Franck N, Maillard N, Huynh A, Nguyen S, Marçais A, Chaby G, Ceballos P, Le Corre Y, Maury S, Bay JO, Adamski H, Bachy E, Forcade E, Socié G, Bagot M, Chevret S, Peffault de Latour R; CUTALLO Investigators; Groupe Français d'Etude des Lymphomes Cutanés; Société Française de Greffe de Moëlle et Thérapie Cellulaire
Lancet 2023 Jun 10;401(10392):1941-1950. Epub 2023 Apr 24 doi: 10.1016/S0140-6736(23)00329-X. PMID: 37105210
Prince HM, Hutchings M, Domingo-Domenech E, Eichenauer DA, Advani R
Ann Hematol 2023 Jan;102(1):13-29. Epub 2022 Dec 13 doi: 10.1007/s00277-022-05054-9. PMID: 36512081Free PMC Article
Al-Toma A, Volta U, Auricchio R, Castillejo G, Sanders DS, Cellier C, Mulder CJ, Lundin KEA
United European Gastroenterol J 2019 Jun;7(5):583-613. Epub 2019 Apr 13 doi: 10.1177/2050640619844125. PMID: 31210940Free PMC Article
Kim YH, Bagot M, Pinter-Brown L, Rook AH, Porcu P, Horwitz SM, Whittaker S, Tokura Y, Vermeer M, Zinzani PL, Sokol L, Morris S, Kim EJ, Ortiz-Romero PL, Eradat H, Scarisbrick J, Tsianakas A, Elmets C, Dalle S, Fisher DC, Halwani A, Poligone B, Greer J, Fierro MT, Khot A, Moskowitz AJ, Musiek A, Shustov A, Pro B, Geskin LJ, Dwyer K, Moriya J, Leoni M, Humphrey JS, Hudgens S, Grebennik DO, Tobinai K, Duvic M; MAVORIC Investigators
Lancet Oncol 2018 Sep;19(9):1192-1204. Epub 2018 Aug 9 doi: 10.1016/S1470-2045(18)30379-6. PMID: 30100375

Diagnosis

Watson LR, Lew TE, Fox LC, Khot A, van der Weyden C
Leuk Lymphoma 2022 Dec;63(13):3217-3221. Epub 2022 Sep 7 doi: 10.1080/10428194.2022.2118537. PMID: 36070587
Kamijo H, Miyagaki T
Curr Treat Options Oncol 2021 Jan 7;22(2):10. doi: 10.1007/s11864-020-00809-w. PMID: 33415447
Sibaud V, Beylot-Barry M, Protin C, Vigarios E, Recher C, Ysebaert L
Am J Clin Dermatol 2020 Dec;21(6):799-812. doi: 10.1007/s40257-020-00535-x. PMID: 32613545
Al-Toma A, Volta U, Auricchio R, Castillejo G, Sanders DS, Cellier C, Mulder CJ, Lundin KEA
United European Gastroenterol J 2019 Jun;7(5):583-613. Epub 2019 Apr 13 doi: 10.1177/2050640619844125. PMID: 31210940Free PMC Article
Ladizinski B, Alavi A, Jambrosic J, Mistry N, Sibbald RG
Adv Skin Wound Care 2014 Jul;27(7):301-9. doi: 10.1097/01.ASW.0000446864.26807.43. PMID: 24932950

Therapy

Zinzani PL, Salles G, Moskowitz AJ, Santoro A, Mehta A, Barr PM, Mehta-Shah N, Collins GP, Ansell SM, Brody JD, Domingo-Domenech E, Johnson NA, Cunningham D, Ferrari S, Lisano J, Krajewski J, Wen R, Akyol A, Crowe R, Savage KJ
Blood Adv 2024 May 28;8(10):2400-2404. doi: 10.1182/bloodadvances.2023011030. PMID: 38531062Free PMC Article
Kamijo H, Miyagaki T
Curr Treat Options Oncol 2021 Jan 7;22(2):10. doi: 10.1007/s11864-020-00809-w. PMID: 33415447
Sibaud V, Beylot-Barry M, Protin C, Vigarios E, Recher C, Ysebaert L
Am J Clin Dermatol 2020 Dec;21(6):799-812. doi: 10.1007/s40257-020-00535-x. PMID: 32613545
Kim YH, Bagot M, Pinter-Brown L, Rook AH, Porcu P, Horwitz SM, Whittaker S, Tokura Y, Vermeer M, Zinzani PL, Sokol L, Morris S, Kim EJ, Ortiz-Romero PL, Eradat H, Scarisbrick J, Tsianakas A, Elmets C, Dalle S, Fisher DC, Halwani A, Poligone B, Greer J, Fierro MT, Khot A, Moskowitz AJ, Musiek A, Shustov A, Pro B, Geskin LJ, Dwyer K, Moriya J, Leoni M, Humphrey JS, Hudgens S, Grebennik DO, Tobinai K, Duvic M; MAVORIC Investigators
Lancet Oncol 2018 Sep;19(9):1192-1204. Epub 2018 Aug 9 doi: 10.1016/S1470-2045(18)30379-6. PMID: 30100375
Yoshie O, Matsushima K
Int Immunol 2015 Jan;27(1):11-20. Epub 2014 Aug 2 doi: 10.1093/intimm/dxu079. PMID: 25087232

Prognosis

Karsten H, Matrisch L, Cichutek S, Fiedler W, Alsdorf W, Block A
Front Immunol 2023;14:1285406. Epub 2023 Nov 27 doi: 10.3389/fimmu.2023.1285406. PMID: 38090582Free PMC Article
de Masson A, Beylot-Barry M, Ram-Wolff C, Mear JB, Dalle S, d'Incan M, Ingen-Housz-Oro S, Orvain C, Abraham J, Dereure O, Charbonnier A, Cornillon J, Longvert C, Barete S, Boulinguez S, Wierzbicka-Hainaut E, Aubin F, Rubio MT, Bernard M, Schmidt-Tanguy A, Houot R, Pham-Ledard A, Michonneau D, Brice P, Labussière-Wallet H, Bouaziz JD, Grange F, Moins-Teisserenc H, Jondeau K, Michel L, Mourah S, Battistella M, Daguindau E, Loschi M, Picard A, Franck N, Maillard N, Huynh A, Nguyen S, Marçais A, Chaby G, Ceballos P, Le Corre Y, Maury S, Bay JO, Adamski H, Bachy E, Forcade E, Socié G, Bagot M, Chevret S, Peffault de Latour R; CUTALLO Investigators; Groupe Français d'Etude des Lymphomes Cutanés; Société Française de Greffe de Moëlle et Thérapie Cellulaire
Lancet 2023 Jun 10;401(10392):1941-1950. Epub 2023 Apr 24 doi: 10.1016/S0140-6736(23)00329-X. PMID: 37105210
Benjamin R, Jain N, Maus MV, Boissel N, Graham C, Jozwik A, Yallop D, Konopleva M, Frigault MJ, Teshima T, Kato K, Boucaud F, Balandraud S, Gianella-Borradori A, Binlich F, Marchiq I, Dupouy S, Almena-Carrasco M, Pannaux M, Fouliard S, Brissot E, Mohty M; CALM Study Group
Lancet Haematol 2022 Nov;9(11):e833-e843. Epub 2022 Oct 10 doi: 10.1016/S2352-3026(22)00245-9. PMID: 36228643Free PMC Article
Kamijo H, Miyagaki T
Curr Treat Options Oncol 2021 Jan 7;22(2):10. doi: 10.1007/s11864-020-00809-w. PMID: 33415447
Sibaud V, Beylot-Barry M, Protin C, Vigarios E, Recher C, Ysebaert L
Am J Clin Dermatol 2020 Dec;21(6):799-812. doi: 10.1007/s40257-020-00535-x. PMID: 32613545

Clinical prediction guides

Bachy E, Savage KJ, Huang H, Kwong YL, Gritti G, Zhang Q, Liberati AM, Cao J, Yang H, Hao S, Hu J, Zhou K, Petrini M, Russo F, Zhang H, Sang W, Ji J, Ferreri AJM, Damaj GL, Liu H, Zhang W, Ke X, Ghiggi C, Huang S, Li X, Yao H, Paik J, Novotny W, Zhou W, Zhu H, Zinzani PL
Blood Adv 2023 Aug 22;7(16):4435-4447. doi: 10.1182/bloodadvances.2022009575. PMID: 37276067Free PMC Article
Nicolay JP, Melchers S, Albrecht JD, Assaf C, Dippel E, Stadler R, Wehkamp U, Wobser M, Zhao J, Burghaus I, Schneider S, Gülow K, Goerdt S, Schürch CM, Utikal JS, Krammer PH
Blood 2023 Aug 31;142(9):794-805. doi: 10.1182/blood.2022018669. PMID: 37217183Free PMC Article
de Masson A, Beylot-Barry M, Ram-Wolff C, Mear JB, Dalle S, d'Incan M, Ingen-Housz-Oro S, Orvain C, Abraham J, Dereure O, Charbonnier A, Cornillon J, Longvert C, Barete S, Boulinguez S, Wierzbicka-Hainaut E, Aubin F, Rubio MT, Bernard M, Schmidt-Tanguy A, Houot R, Pham-Ledard A, Michonneau D, Brice P, Labussière-Wallet H, Bouaziz JD, Grange F, Moins-Teisserenc H, Jondeau K, Michel L, Mourah S, Battistella M, Daguindau E, Loschi M, Picard A, Franck N, Maillard N, Huynh A, Nguyen S, Marçais A, Chaby G, Ceballos P, Le Corre Y, Maury S, Bay JO, Adamski H, Bachy E, Forcade E, Socié G, Bagot M, Chevret S, Peffault de Latour R; CUTALLO Investigators; Groupe Français d'Etude des Lymphomes Cutanés; Société Française de Greffe de Moëlle et Thérapie Cellulaire
Lancet 2023 Jun 10;401(10392):1941-1950. Epub 2023 Apr 24 doi: 10.1016/S0140-6736(23)00329-X. PMID: 37105210
Kim YH, Bagot M, Pinter-Brown L, Rook AH, Porcu P, Horwitz SM, Whittaker S, Tokura Y, Vermeer M, Zinzani PL, Sokol L, Morris S, Kim EJ, Ortiz-Romero PL, Eradat H, Scarisbrick J, Tsianakas A, Elmets C, Dalle S, Fisher DC, Halwani A, Poligone B, Greer J, Fierro MT, Khot A, Moskowitz AJ, Musiek A, Shustov A, Pro B, Geskin LJ, Dwyer K, Moriya J, Leoni M, Humphrey JS, Hudgens S, Grebennik DO, Tobinai K, Duvic M; MAVORIC Investigators
Lancet Oncol 2018 Sep;19(9):1192-1204. Epub 2018 Aug 9 doi: 10.1016/S1470-2045(18)30379-6. PMID: 30100375
Lewis DJ, Duvic M
Expert Opin Investig Drugs 2017 Jun;26(6):771-775. Epub 2017 May 5 doi: 10.1080/13543784.2017.1324569. PMID: 28447489

Recent systematic reviews

Dalal M, Mitchell S, McCloskey C, Zagadailov E, Gautam A
Expert Rev Hematol 2020 Apr;13(4):405-419. Epub 2020 Jan 31 doi: 10.1080/17474086.2020.1717945. PMID: 31958235
Stewart JR, Desai N, Rizvi S, Zhu H, Goff HW
Eur J Dermatol 2018 Dec 1;28(6):764-774. doi: 10.1684/ejd.2018.3444. PMID: 30591425
Stranzenbach R, Dippel E, Schlaak M, Stadler R
Br J Dermatol 2017 Dec;177(6):1503-1509. Epub 2017 Nov 22 doi: 10.1111/bjd.15801. PMID: 28703284
Xue J, Liu C, Liu Y
Photodiagnosis Photodyn Ther 2017 Mar;17:87-91. Epub 2016 Nov 23 doi: 10.1016/j.pdpdt.2016.11.010. PMID: 27888162

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