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Colorectal Small Cell Neuroendocrine Carcinoma

MedGen UID:
313041
Concept ID:
C1707441
Neoplastic Process
Synonyms: Colorectal Small Cell Carcinoma; Large Intestinal Small Cell Neuroendocrine Carcinoma

Definition

An aggressive, high-grade, and poorly differentiated carcinoma with neuroendocrine differentiation that arises from the colon or rectum. It is characterized by the presence of malignant small cells. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVColorectal Small Cell Neuroendocrine Carcinoma

Professional guidelines

PubMed

Garcia J, Hurwitz HI, Sandler AB, Miles D, Coleman RL, Deurloo R, Chinot OL
Cancer Treat Rev 2020 Jun;86:102017. Epub 2020 Mar 26 doi: 10.1016/j.ctrv.2020.102017. PMID: 32335505
Gaya A, Tse V
Cancer Treat Rev 2012 Aug;38(5):484-93. Epub 2012 Jan 20 doi: 10.1016/j.ctrv.2011.12.008. PMID: 22264850
Goddard AF, James MW, McIntyre AS, Scott BB; British Society of Gastroenterology
Gut 2011 Oct;60(10):1309-16. Epub 2011 May 11 doi: 10.1136/gut.2010.228874. PMID: 21561874

Recent clinical studies

Etiology

You D, Wang D, Wu Y, Chen X, Shao F, Wei Y, Zhang R, Lange T, Ma H, Xu H, Hu Z, Christiani DC, Shen H, Chen F, Zhao Y
BMC Med 2022 Jun 6;20(1):203. doi: 10.1186/s12916-022-02400-6. PMID: 35658861Free PMC Article
Pimentel-Nunes P, Libânio D, Bastiaansen BAJ, Bhandari P, Bisschops R, Bourke MJ, Esposito G, Lemmers A, Maselli R, Messmann H, Pech O, Pioche M, Vieth M, Weusten BLAM, van Hooft JE, Deprez PH, Dinis-Ribeiro M
Endoscopy 2022 Jun;54(6):591-622. Epub 2022 May 6 doi: 10.1055/a-1811-7025. PMID: 35523224
Gould MK, Huang BZ, Tammemagi MC, Kinar Y, Shiff R
Am J Respir Crit Care Med 2021 Aug 15;204(4):445-453. doi: 10.1164/rccm.202007-2791OC. PMID: 33823116
Van de Moortele M, De Hertogh G, Sagaert X, Van Cutsem E
Acta Gastroenterol Belg 2020 Jul-Sep;83(3):441-448. PMID: 33094592
Jonna S, Feldman RA, Swensen J, Gatalica Z, Korn WM, Borghaei H, Ma PC, Nieva JJ, Spira AI, Vanderwalde AM, Wozniak AJ, Kim ES, Liu SV
Clin Cancer Res 2019 Aug 15;25(16):4966-4972. Epub 2019 Apr 15 doi: 10.1158/1078-0432.CCR-19-0160. PMID: 30988082Free PMC Article

Diagnosis

Pimentel-Nunes P, Libânio D, Bastiaansen BAJ, Bhandari P, Bisschops R, Bourke MJ, Esposito G, Lemmers A, Maselli R, Messmann H, Pech O, Pioche M, Vieth M, Weusten BLAM, van Hooft JE, Deprez PH, Dinis-Ribeiro M
Endoscopy 2022 Jun;54(6):591-622. Epub 2022 May 6 doi: 10.1055/a-1811-7025. PMID: 35523224
Gould MK, Huang BZ, Tammemagi MC, Kinar Y, Shiff R
Am J Respir Crit Care Med 2021 Aug 15;204(4):445-453. doi: 10.1164/rccm.202007-2791OC. PMID: 33823116
Van de Moortele M, De Hertogh G, Sagaert X, Van Cutsem E
Acta Gastroenterol Belg 2020 Jul-Sep;83(3):441-448. PMID: 33094592
Zhu G, Cheng Z, Huang Y, Zheng W, Yang S, Lin C, Ye J
Int J Mol Med 2020 Jan;45(1):131-140. Epub 2019 Oct 31 doi: 10.3892/ijmm.2019.4390. PMID: 31746347Free PMC Article
Dijkstra KK, Cattaneo CM, Weeber F, Chalabi M, van de Haar J, Fanchi LF, Slagter M, van der Velden DL, Kaing S, Kelderman S, van Rooij N, van Leerdam ME, Depla A, Smit EF, Hartemink KJ, de Groot R, Wolkers MC, Sachs N, Snaebjornsson P, Monkhorst K, Haanen J, Clevers H, Schumacher TN, Voest EE
Cell 2018 Sep 6;174(6):1586-1598.e12. Epub 2018 Aug 9 doi: 10.1016/j.cell.2018.07.009. PMID: 30100188Free PMC Article

Therapy

Markham A
Drugs 2021 Sep;81(14):1665-1670. doi: 10.1007/s40265-021-01584-0. PMID: 34455538
Van de Moortele M, De Hertogh G, Sagaert X, Van Cutsem E
Acta Gastroenterol Belg 2020 Jul-Sep;83(3):441-448. PMID: 33094592
Garcia J, Hurwitz HI, Sandler AB, Miles D, Coleman RL, Deurloo R, Chinot OL
Cancer Treat Rev 2020 Jun;86:102017. Epub 2020 Mar 26 doi: 10.1016/j.ctrv.2020.102017. PMID: 32335505
Li AY, McCusker MG, Russo A, Scilla KA, Gittens A, Arensmeyer K, Mehra R, Adamo V, Rolfo C
Cancer Treat Rev 2019 Dec;81:101911. Epub 2019 Oct 30 doi: 10.1016/j.ctrv.2019.101911. PMID: 31715421
Topalian SL, Hodi FS, Brahmer JR, Gettinger SN, Smith DC, McDermott DF, Powderly JD, Carvajal RD, Sosman JA, Atkins MB, Leming PD, Spigel DR, Antonia SJ, Horn L, Drake CG, Pardoll DM, Chen L, Sharfman WH, Anders RA, Taube JM, McMiller TL, Xu H, Korman AJ, Jure-Kunkel M, Agrawal S, McDonald D, Kollia GD, Gupta A, Wigginton JM, Sznol M
N Engl J Med 2012 Jun 28;366(26):2443-54. Epub 2012 Jun 2 doi: 10.1056/NEJMoa1200690. PMID: 22658127Free PMC Article

Prognosis

Zhao W, Jin L, Chen P, Li D, Gao W, Dong G
Cancer Lett 2022 Oct 1;545:215816. Epub 2022 Jul 8 doi: 10.1016/j.canlet.2022.215816. PMID: 35810989
Van de Moortele M, De Hertogh G, Sagaert X, Van Cutsem E
Acta Gastroenterol Belg 2020 Jul-Sep;83(3):441-448. PMID: 33094592
Zhu G, Cheng Z, Huang Y, Zheng W, Yang S, Lin C, Ye J
Int J Mol Med 2020 Jan;45(1):131-140. Epub 2019 Oct 31 doi: 10.3892/ijmm.2019.4390. PMID: 31746347Free PMC Article
Dankner M, Rose AAN, Rajkumar S, Siegel PM, Watson IR
Oncogene 2018 Jun;37(24):3183-3199. Epub 2018 Mar 15 doi: 10.1038/s41388-018-0171-x. PMID: 29540830
Mazzarella L, Guida A, Curigliano G
Expert Opin Biol Ther 2018 Apr;18(4):483-493. doi: 10.1080/14712598.2018.1452906. PMID: 29534625

Clinical prediction guides

Zhao W, Jin L, Chen P, Li D, Gao W, Dong G
Cancer Lett 2022 Oct 1;545:215816. Epub 2022 Jul 8 doi: 10.1016/j.canlet.2022.215816. PMID: 35810989
Dankner M, Rose AAN, Rajkumar S, Siegel PM, Watson IR
Oncogene 2018 Jun;37(24):3183-3199. Epub 2018 Mar 15 doi: 10.1038/s41388-018-0171-x. PMID: 29540830
Mazzarella L, Guida A, Curigliano G
Expert Opin Biol Ther 2018 Apr;18(4):483-493. doi: 10.1080/14712598.2018.1452906. PMID: 29534625
Brahmer JR, Tykodi SS, Chow LQ, Hwu WJ, Topalian SL, Hwu P, Drake CG, Camacho LH, Kauh J, Odunsi K, Pitot HC, Hamid O, Bhatia S, Martins R, Eaton K, Chen S, Salay TM, Alaparthy S, Grosso JF, Korman AJ, Parker SM, Agrawal S, Goldberg SM, Pardoll DM, Gupta A, Wigginton JM
N Engl J Med 2012 Jun 28;366(26):2455-65. Epub 2012 Jun 2 doi: 10.1056/NEJMoa1200694. PMID: 22658128Free PMC Article
Topalian SL, Hodi FS, Brahmer JR, Gettinger SN, Smith DC, McDermott DF, Powderly JD, Carvajal RD, Sosman JA, Atkins MB, Leming PD, Spigel DR, Antonia SJ, Horn L, Drake CG, Pardoll DM, Chen L, Sharfman WH, Anders RA, Taube JM, McMiller TL, Xu H, Korman AJ, Jure-Kunkel M, Agrawal S, McDonald D, Kollia GD, Gupta A, Wigginton JM, Sznol M
N Engl J Med 2012 Jun 28;366(26):2443-54. Epub 2012 Jun 2 doi: 10.1056/NEJMoa1200690. PMID: 22658127Free PMC Article

Recent systematic reviews

Ou SL, Luo J, Wei H, Qin XL, Du SY, Wang S, Jiang Q
Front Immunol 2022;13:953761. Epub 2022 Jul 13 doi: 10.3389/fimmu.2022.953761. PMID: 35911744Free PMC Article
van Gestel T, Groen LCB, Puik JR, van Rooijen SJ, van der Zaag-Loonen HJ, Schoonmade LJ, Danjoux G, Daams F, Schreurs WH, Bruns ERJ
Eur J Surg Oncol 2022 Jun;48(6):1189-1197. Epub 2022 Feb 9 doi: 10.1016/j.ejso.2022.02.010. PMID: 35183411Free PMC Article
Pedersen TB, Kildsig J, Serup-Hansen E, Gocht-Jensen P, Klein MF
Int J Colorectal Dis 2020 Sep;35(9):1663-1671. Epub 2020 Jul 15 doi: 10.1007/s00384-020-03687-8. PMID: 32671458
Xiao B, Huang Z, Zhou R, Zhang J, Yu B
Med Sci Monit 2018 Aug 6;24:5462-5472. doi: 10.12659/MSM.911687. PMID: 30080819Free PMC Article
Wang HH, Zhang CZ, Zhang BL, Chen J, Zeng XL, Deng L, Meng MB
Oncotarget 2017 Jan 24;8(4):6033-6042. doi: 10.18632/oncotarget.14010. PMID: 28002808Free PMC Article

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