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Pleural Epithelioid Hemangioendothelioma

MedGen UID:
318030
•Concept ID:
C1709573
•
Neoplastic Process

Definition

A low-grade malignant blood vessel neoplasm arising from the pleura. It is characterized by the presence of epithelioid endothelial cells. The neoplastic cells are arranged in cords and nests, which are embedded in a myxoid to hyalinized stroma. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVPleural Epithelioid Hemangioendothelioma

Recent clinical studies

Etiology

Primary pleural epithelioid hemangioendothelioma compressing the myocardium.
Yu L, Gu T, Xiu Z, Shi E, Zhao X
J Card Surg 2013 May;28(3):266-8. Epub 2013 Apr 1 doi: 10.1111/jocs.12094. PMID: 23551388

Diagnosis

Thoracic Epithelioid Hemangioendothelioma: clinical demonstration and therapeutic procedures.
Graça LL, Almeida Cunha S, Lopes RS, Carvalho L, Prieto D
Port J Card Thorac Vasc Surg 2022 Jul 3;29(2):39-44. doi: 10.48729/pjctvs.276. PMID: 35780414
Primary pleural epithelioid hemangioendothelioma: case report and review of the literature.
Lavacchi D, Voltolini L, Comin CE, Mazzoni F, Baldi GG, Briganti V, Luvarà S, Bongiolatti S, Antonuzzo L
Anticancer Drugs 2021 Nov 1;32(10):1131-1137. doi: 10.1097/CAD.0000000000001122. PMID: 34232937Free PMC Article
Pleural Epithelioid Hemangioendothelioma: A Case Report and Literature Review.
Fan Y, Wang F, Li S, Ye C, Ying Y, Mao H
J Natl Med Assoc 2016 May;108(2):124-9. doi: 10.1016/j.jnma.2016.05.001. PMID: 27372473
Pleural epithelioid hemangioendothelioma.
Bansal A, Chawla M, Cohen PJ, Kwon JS
Lung 2012 Aug;190(4):469-70. Epub 2012 Mar 6 doi: 10.1007/s00408-012-9377-9. PMID: 22392541
Pleural epithelioid hemangioendothelioma.
Lee YJ, Chung MJ, Jeong KC, Hahn CH, Hong KP, Kim YJ, Kim YT
Yonsei Med J 2008 Dec 31;49(6):1036-40. doi: 10.3349/ymj.2008.49.6.1036. PMID: 19108030Free PMC Article

Therapy

Primary pleural epithelioid hemangioendothelioma compressing the myocardium.
Yu L, Gu T, Xiu Z, Shi E, Zhao X
J Card Surg 2013 May;28(3):266-8. Epub 2013 Apr 1 doi: 10.1111/jocs.12094. PMID: 23551388
Pleural epithelioid hemangioendothelioma.
Bansal A, Chawla M, Cohen PJ, Kwon JS
Lung 2012 Aug;190(4):469-70. Epub 2012 Mar 6 doi: 10.1007/s00408-012-9377-9. PMID: 22392541
Primary pleural epithelioid hemangioendothelioma (EHE)--two cases and review of the literature.
Lazarus A, Fuhrer G, Malekiani C, McKay S, Thurber J
Clin Respir J 2011 Jan;5(1):e1-5. Epub 2010 Aug 16 doi: 10.1111/j.1752-699X.2010.00221.x. PMID: 21159132
Pleural epithelioid hemangioendothelioma.
Lee YJ, Chung MJ, Jeong KC, Hahn CH, Hong KP, Kim YJ, Kim YT
Yonsei Med J 2008 Dec 31;49(6):1036-40. doi: 10.3349/ymj.2008.49.6.1036. PMID: 19108030Free PMC Article

Prognosis

Pleural Epithelioid Hemangioendothelioma: A Case Report and Literature Review.
Fan Y, Wang F, Li S, Ye C, Ying Y, Mao H
J Natl Med Assoc 2016 May;108(2):124-9. doi: 10.1016/j.jnma.2016.05.001. PMID: 27372473
Pleural epithelioid hemangioendothelioma harboring CAMTA1 rearrangement.
Ha SY, Choi IH, Han J, Choi YL, Cho JH, Lee KJ, Sun JM
Lung Cancer 2014 Mar;83(3):411-5. Epub 2014 Jan 7 doi: 10.1016/j.lungcan.2013.12.015. PMID: 24461304
Pleural epithelioid hemangioendothelioma.
Bansal A, Chawla M, Cohen PJ, Kwon JS
Lung 2012 Aug;190(4):469-70. Epub 2012 Mar 6 doi: 10.1007/s00408-012-9377-9. PMID: 22392541
Primary pleural epithelioid hemangioendothelioma (EHE)--two cases and review of the literature.
Lazarus A, Fuhrer G, Malekiani C, McKay S, Thurber J
Clin Respir J 2011 Jan;5(1):e1-5. Epub 2010 Aug 16 doi: 10.1111/j.1752-699X.2010.00221.x. PMID: 21159132
Pleural epithelioid hemangioendothelioma.
Lee YJ, Chung MJ, Jeong KC, Hahn CH, Hong KP, Kim YJ, Kim YT
Yonsei Med J 2008 Dec 31;49(6):1036-40. doi: 10.3349/ymj.2008.49.6.1036. PMID: 19108030Free PMC Article

Clinical prediction guides

Malignant epithelioid vascular tumors of the pleura: report of a series and literature review.
Zhang PJ, Livolsi VA, Brooks JJ
Hum Pathol 2000 Jan;31(1):29-34. doi: 10.1016/s0046-8177(00)80194-x. PMID: 10665909

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