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Celiac artery stenosis from compression by median arcuate ligament of diaphragm

MedGen UID:
349361
•Concept ID:
C1861783
•
Disease or Syndrome
Synonym: Celiac artery compression
SNOMED CT: CACS - Celiac axis compression syndrome (9250002); Celiac axis compression syndrome (9250002); Celiac artery compression syndrome (9250002); Celiac axis syndrome (9250002); Marable's syndrome (9250002); Median arcuate ligament syndrome (9250002)
 
HPO: HP:0012327
Monarch Initiative: MONDO:0004914
OMIM®: 116870

Definition

Compression of the celiac artery. [from HPO]

Clinical features

From HPO
Abdominal pain
MedGen UID:
7803
•Concept ID:
C0000737
•
Sign or Symptom
An unpleasant sensation characterized by physical discomfort (such as pricking, throbbing, or aching) and perceived to originate in the abdomen.
See: Feature record | Search on this feature
Celiac artery stenosis from compression by median arcuate ligament of diaphragm
MedGen UID:
349361
•Concept ID:
C1861783
•
Disease or Syndrome
Compression of the celiac artery.
See: Feature record | Search on this feature
Show allHide all

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVCeliac artery stenosis from compression by median arcuate ligament of diaphragm

Conditions with this feature

Celiac artery stenosis from compression by median arcuate ligament of diaphragm
MedGen UID:
349361
•Concept ID:
C1861783
•
Disease or Syndrome
Compression of the celiac artery.
See: Condition Record
Celiac artery stenosis from compression by median arcuate ligament of diaphragm

Professional guidelines

PubMed

ACR Appropriateness Criteria® Radiologic Management of Mesenteric Ischemia: 2022 Update.
Expert Panel on Interventional Radiology, Lam A, Kim YJ, Fidelman N, Higgins M, Cash BD, Charalel RA, Guimaraes MS, Kwan SW, Patel PJ, Plett S, Scali ST, Stadtlander KS, Stoner M, Tong R, Kapoor BS
J Am Coll Radiol 2022 Nov;19(11S):S433-S444. doi: 10.1016/j.jacr.2022.09.006. PMID: 36436968
Clinical management of chronic mesenteric ischemia.
van Dijk LJ, van Noord D, de Vries AC, Kolkman JJ, Geelkerken RH, Verhagen HJ, Moelker A, Bruno MJ
United European Gastroenterol J 2019 Mar;7(2):179-188. Epub 2018 Dec 4 doi: 10.1177/2050640618817698. PMID: 31080602Free PMC Article
ACR Appropriateness Criteria(®) Radiologic Management of Mesenteric Ischemia.
Expert Panel on Interventional Radiology:, Fidelman N, AbuRahma AF, Cash BD, Kapoor BS, Knuttinen MG, Minocha J, Rochon PJ, Shaw CM, Ray CE Jr, Lorenz JM
J Am Coll Radiol 2017 May;14(5S):S266-S271. doi: 10.1016/j.jacr.2017.02.014. PMID: 28473083

Recent clinical studies

Etiology

Prediction of common hepatic artery catheter insertion based on celiac trunk morphology.
Saiga A, Yokota H, Akutsu A, Ooka Y, Kubota Y, Wada T, Koizumi J, Uno T
Diagn Interv Radiol 2023 Jan 31;29(1):161-166. Epub 2022 Dec 5 doi: 10.5152/dir.2022.21010. PMID: 36960583Free PMC Article
Prevalence of celiac artery compression by median arcuate ligament in patients with splanchnic artery aneurysms/pseudoaneurysms submitted to endovascular embolization.
Borges AP, Antunes C, Donato P
Abdom Radiol (NY) 2023 Apr;48(4):1415-1428. Epub 2023 Feb 18 doi: 10.1007/s00261-023-03844-x. PMID: 36801957Free PMC Article
Median arcuate ligament syndrome.
Goodall R, Langridge B, Onida S, Ellis M, Lane T, Davies AH
J Vasc Surg 2020 Jun;71(6):2170-2176. Epub 2019 Dec 25 doi: 10.1016/j.jvs.2019.11.012. PMID: 31882314
Nonatherosclerotic Abdominal Vasculopathies.
Skeik N, Hyde JR, Olson SL, Thaler CM, Abuatiyeh W, Ahmed AK, Lyon DR, Witt DR, Garberich R, Sullivan T
Ann Vasc Surg 2019 Oct;60:128-146. Epub 2019 Jun 12 doi: 10.1016/j.avsg.2019.04.004. PMID: 31200053
Vascular compression syndromes.
Czihal M, Banafsche R, Hoffmann U, Koeppel T
Vasa 2015 Nov;44(6):419-34. doi: 10.1024/0301-1526/a000465. PMID: 26515219

Diagnosis

Median arcuate ligament syndrome.
Goodall R, Langridge B, Onida S, Ellis M, Lane T, Davies AH
J Vasc Surg 2020 Jun;71(6):2170-2176. Epub 2019 Dec 25 doi: 10.1016/j.jvs.2019.11.012. PMID: 31882314
Nonatherosclerotic Abdominal Vasculopathies.
Skeik N, Hyde JR, Olson SL, Thaler CM, Abuatiyeh W, Ahmed AK, Lyon DR, Witt DR, Garberich R, Sullivan T
Ann Vasc Surg 2019 Oct;60:128-146. Epub 2019 Jun 12 doi: 10.1016/j.avsg.2019.04.004. PMID: 31200053
Median Arcuate Ligament Syndrome-Review of This Rare Disease.
Kim EN, Lamb K, Relles D, Moudgill N, DiMuzio PJ, Eisenberg JA
JAMA Surg 2016 May 1;151(5):471-7. doi: 10.1001/jamasurg.2016.0002. PMID: 26934394
Vascular compression syndromes.
Czihal M, Banafsche R, Hoffmann U, Koeppel T
Vasa 2015 Nov;44(6):419-34. doi: 10.1024/0301-1526/a000465. PMID: 26515219
Mesenteric ischemia.
Bobadilla JL
Surg Clin North Am 2013 Aug;93(4):925-40, ix. Epub 2013 May 16 doi: 10.1016/j.suc.2013.04.002. PMID: 23885938

Therapy

Factors associated with successful median arcuate ligament release in an international, multi-institutional cohort.
DeCarlo C, Woo K, van Petersen AS, Geelkerken RH, Chen AJ, Yeh SL, Kim GY, Henke PK, Tracci MC, Schneck MB, Grotemeyer D, Meyer B, DeMartino RR, Wilkins PB, Iranmanesh S, Rastogi V, Aulivola B, Korepta LM, Shutze WP, Jett KG, Sorber R, Abularrage CJ, Long GW, Bove PG, Davies MG, Miserlis D, Shih M, Yi J, Gupta R, Loa J, Robinson DA, Gombert A, Doukas P, de Caridi G, Benedetto F, Wittgen CM, Smeds MR, Sumpio BE, Harris S, Szeberin Z, Pomozi E, Stilo F, Montelione N, Mouawad NJ, Lawrence P, Dua A
J Vasc Surg 2023 Feb;77(2):567-577.e2. Epub 2022 Oct 26 doi: 10.1016/j.jvs.2022.10.022. PMID: 36306935
Median arcuate ligament syndrome.
Goodall R, Langridge B, Onida S, Ellis M, Lane T, Davies AH
J Vasc Surg 2020 Jun;71(6):2170-2176. Epub 2019 Dec 25 doi: 10.1016/j.jvs.2019.11.012. PMID: 31882314
Nonatherosclerotic Abdominal Vasculopathies.
Skeik N, Hyde JR, Olson SL, Thaler CM, Abuatiyeh W, Ahmed AK, Lyon DR, Witt DR, Garberich R, Sullivan T
Ann Vasc Surg 2019 Oct;60:128-146. Epub 2019 Jun 12 doi: 10.1016/j.avsg.2019.04.004. PMID: 31200053
Median arcuate ligament compression of the mesenteric vasculature.
Tracci MC
Tech Vasc Interv Radiol 2015 Mar;18(1):43-50. Epub 2014 Dec 29 doi: 10.1053/j.tvir.2014.12.007. PMID: 25814203
Open and laparoscopic treatment of median arcuate ligament syndrome.
Jimenez JC, Harlander-Locke M, Dutson EP
J Vasc Surg 2012 Sep;56(3):869-73. Epub 2012 Jun 27 doi: 10.1016/j.jvs.2012.04.057. PMID: 22743019

Prognosis

Prediction of common hepatic artery catheter insertion based on celiac trunk morphology.
Saiga A, Yokota H, Akutsu A, Ooka Y, Kubota Y, Wada T, Koizumi J, Uno T
Diagn Interv Radiol 2023 Jan 31;29(1):161-166. Epub 2022 Dec 5 doi: 10.5152/dir.2022.21010. PMID: 36960583Free PMC Article
Outcomes of Median Arcuate Ligament Release: A Single Institution Retrospective Review.
Chen AJ, Yeh S, Dhindsa Y, Lawrence PF, Woo K
Ann Vasc Surg 2023 Aug;94:296-300. Epub 2023 Mar 15 doi: 10.1016/j.avsg.2023.02.030. PMID: 36924990
Factors associated with successful median arcuate ligament release in an international, multi-institutional cohort.
DeCarlo C, Woo K, van Petersen AS, Geelkerken RH, Chen AJ, Yeh SL, Kim GY, Henke PK, Tracci MC, Schneck MB, Grotemeyer D, Meyer B, DeMartino RR, Wilkins PB, Iranmanesh S, Rastogi V, Aulivola B, Korepta LM, Shutze WP, Jett KG, Sorber R, Abularrage CJ, Long GW, Bove PG, Davies MG, Miserlis D, Shih M, Yi J, Gupta R, Loa J, Robinson DA, Gombert A, Doukas P, de Caridi G, Benedetto F, Wittgen CM, Smeds MR, Sumpio BE, Harris S, Szeberin Z, Pomozi E, Stilo F, Montelione N, Mouawad NJ, Lawrence P, Dua A
J Vasc Surg 2023 Feb;77(2):567-577.e2. Epub 2022 Oct 26 doi: 10.1016/j.jvs.2022.10.022. PMID: 36306935
Nonatherosclerotic Abdominal Vasculopathies.
Skeik N, Hyde JR, Olson SL, Thaler CM, Abuatiyeh W, Ahmed AK, Lyon DR, Witt DR, Garberich R, Sullivan T
Ann Vasc Surg 2019 Oct;60:128-146. Epub 2019 Jun 12 doi: 10.1016/j.avsg.2019.04.004. PMID: 31200053
Vascular compression syndromes.
Czihal M, Banafsche R, Hoffmann U, Koeppel T
Vasa 2015 Nov;44(6):419-34. doi: 10.1024/0301-1526/a000465. PMID: 26515219

Clinical prediction guides

Prediction of common hepatic artery catheter insertion based on celiac trunk morphology.
Saiga A, Yokota H, Akutsu A, Ooka Y, Kubota Y, Wada T, Koizumi J, Uno T
Diagn Interv Radiol 2023 Jan 31;29(1):161-166. Epub 2022 Dec 5 doi: 10.5152/dir.2022.21010. PMID: 36960583Free PMC Article
Outcomes of Median Arcuate Ligament Release: A Single Institution Retrospective Review.
Chen AJ, Yeh S, Dhindsa Y, Lawrence PF, Woo K
Ann Vasc Surg 2023 Aug;94:296-300. Epub 2023 Mar 15 doi: 10.1016/j.avsg.2023.02.030. PMID: 36924990
Surgical therapy of celiac axis and superior mesenteric artery syndrome.
Jonas JP, Rössler F, Ghafoor S, Kobe A, Pfammatter T, Schlag C, Gutschow CA, Petrowsky H, Müller PC, Oberkofler CE
Langenbecks Arch Surg 2023 Jan 24;408(1):59. doi: 10.1007/s00423-023-02803-w. PMID: 36690823Free PMC Article
Factors associated with successful median arcuate ligament release in an international, multi-institutional cohort.
DeCarlo C, Woo K, van Petersen AS, Geelkerken RH, Chen AJ, Yeh SL, Kim GY, Henke PK, Tracci MC, Schneck MB, Grotemeyer D, Meyer B, DeMartino RR, Wilkins PB, Iranmanesh S, Rastogi V, Aulivola B, Korepta LM, Shutze WP, Jett KG, Sorber R, Abularrage CJ, Long GW, Bove PG, Davies MG, Miserlis D, Shih M, Yi J, Gupta R, Loa J, Robinson DA, Gombert A, Doukas P, de Caridi G, Benedetto F, Wittgen CM, Smeds MR, Sumpio BE, Harris S, Szeberin Z, Pomozi E, Stilo F, Montelione N, Mouawad NJ, Lawrence P, Dua A
J Vasc Surg 2023 Feb;77(2):567-577.e2. Epub 2022 Oct 26 doi: 10.1016/j.jvs.2022.10.022. PMID: 36306935
Vascular compression syndromes.
Czihal M, Banafsche R, Hoffmann U, Koeppel T
Vasa 2015 Nov;44(6):419-34. doi: 10.1024/0301-1526/a000465. PMID: 26515219

Recent systematic reviews

Surgical therapy of celiac axis and superior mesenteric artery syndrome.
Jonas JP, Rössler F, Ghafoor S, Kobe A, Pfammatter T, Schlag C, Gutschow CA, Petrowsky H, Müller PC, Oberkofler CE
Langenbecks Arch Surg 2023 Jan 24;408(1):59. doi: 10.1007/s00423-023-02803-w. PMID: 36690823Free PMC Article
Laparoscopic treatment of median arcuate ligament syndrome: a systematic review.
San Norberto EM, Romero A, Fidalgo-Domingos LA, García-Saiz I, Taylor J, Vaquero C
Int Angiol 2019 Dec;38(6):474-483. Epub 2019 Sep 30 doi: 10.23736/S0392-9590.19.04161-0. PMID: 31580040

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