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Idiopathic interstitial pneumonia

MedGen UID:
389939
Concept ID:
C2350236
Disease or Syndrome
Synonyms: Idiopathic Interstitial Pneumonia; Idiopathic Interstitial Pneumonias; Interstitial Pneumonia, Idiopathic; Interstitial Pneumonias, Idiopathic; Pneumonia, Idiopathic Interstitial; Pneumonias, Idiopathic Interstitial
SNOMED CT: Idiopathic interstitial pneumonia (700249006)
 
Monarch Initiative: MONDO:0002429
Orphanet: ORPHA98300

Definition

Non-infectious inflammation of the interstitial lung tissue of unknown etiology. This category includes desquamative interstitial pneumonia, usual interstitial pneumonia, lymphocytic interstitial pneumonia, acute interstitial pneumonia, and nonspecific interstitial pneumonia. [from NCI]

Professional guidelines

PubMed

Pugashetti JV, Adegunsoye A, Wu Z, Lee CT, Srikrishnan A, Ghodrati S, Vo V, Renzoni EA, Wells AU, Garcia CK, Chua F, Newton CA, Molyneaux PL, Oldham JM
Am J Respir Crit Care Med 2023 Jan 1;207(1):69-76. doi: 10.1164/rccm.202201-0124OC. PMID: 35943866Free PMC Article
Munchel JK, Shea BS
R I Med J (2013) 2021 Sep 1;104(7):26-29. PMID: 34437662
Garibaldi BT, Danoff SK
Respirology 2016 Nov;21(8):1357-1365. Epub 2015 Oct 9 doi: 10.1111/resp.12649. PMID: 26450007

Recent clinical studies

Etiology

Mankikian J, Caille A, Reynaud-Gaubert M, Agier MS, Bermudez J, Bonniaud P, Borie R, Brillet PY, Cadranel J, Court-Fortune I, Crestani B, Debray MP, Gomez E, Gondouin A, Hirschi-Santelmo S, Israel-Biet D, Jouneau S, Juvin K, Leger J, Kerjouan M, Marquette CH, Naccache JM, Nunes H, Plantier L, Prevot G, Quetant S, Traclet J, Valentin V, Uzunhan Y, Wémeau-Stervinou L, Bejan-Angoulvant T, Cottin V, Marchand-Adam S; EVER-ILD investigators and the OrphaLung network
Eur Respir J 2023 Jun;61(6) Epub 2023 Jun 8 doi: 10.1183/13993003.02071-2022. PMID: 37230499
Pugashetti JV, Adegunsoye A, Wu Z, Lee CT, Srikrishnan A, Ghodrati S, Vo V, Renzoni EA, Wells AU, Garcia CK, Chua F, Newton CA, Molyneaux PL, Oldham JM
Am J Respir Crit Care Med 2023 Jan 1;207(1):69-76. doi: 10.1164/rccm.202201-0124OC. PMID: 35943866Free PMC Article
Kishaba T
Medicina (Kaunas) 2019 Mar 16;55(3) doi: 10.3390/medicina55030070. PMID: 30884853Free PMC Article
Cottin V, Hirani NA, Hotchkin DL, Nambiar AM, Ogura T, Otaola M, Skowasch D, Park JS, Poonyagariyagorn HK, Wuyts W, Wells AU
Eur Respir Rev 2018 Dec 31;27(150) Epub 2018 Dec 21 doi: 10.1183/16000617.0076-2018. PMID: 30578335Free PMC Article
Meyer KC
Expert Rev Respir Med 2017 May;11(5):343-359. Epub 2017 Apr 10 doi: 10.1080/17476348.2017.1312346. PMID: 28345383

Diagnosis

Munchel JK, Shea BS
R I Med J (2013) 2021 Sep 1;104(7):26-29. PMID: 34437662
Kishaba T
Medicina (Kaunas) 2019 Mar 16;55(3) doi: 10.3390/medicina55030070. PMID: 30884853Free PMC Article
Cottin V, Hirani NA, Hotchkin DL, Nambiar AM, Ogura T, Otaola M, Skowasch D, Park JS, Poonyagariyagorn HK, Wuyts W, Wells AU
Eur Respir Rev 2018 Dec 31;27(150) Epub 2018 Dec 21 doi: 10.1183/16000617.0076-2018. PMID: 30578335Free PMC Article
Meyer KC
Expert Rev Respir Med 2017 May;11(5):343-359. Epub 2017 Apr 10 doi: 10.1080/17476348.2017.1312346. PMID: 28345383
Belloli EA, Beckford R, Hadley R, Flaherty KR
Respirology 2016 Feb;21(2):259-68. Epub 2015 Nov 13 doi: 10.1111/resp.12674. PMID: 26564810

Therapy

Mankikian J, Caille A, Reynaud-Gaubert M, Agier MS, Bermudez J, Bonniaud P, Borie R, Brillet PY, Cadranel J, Court-Fortune I, Crestani B, Debray MP, Gomez E, Gondouin A, Hirschi-Santelmo S, Israel-Biet D, Jouneau S, Juvin K, Leger J, Kerjouan M, Marquette CH, Naccache JM, Nunes H, Plantier L, Prevot G, Quetant S, Traclet J, Valentin V, Uzunhan Y, Wémeau-Stervinou L, Bejan-Angoulvant T, Cottin V, Marchand-Adam S; EVER-ILD investigators and the OrphaLung network
Eur Respir J 2023 Jun;61(6) Epub 2023 Jun 8 doi: 10.1183/13993003.02071-2022. PMID: 37230499
Phan THG, Paliogiannis P, Nasrallah GK, Giordo R, Eid AH, Fois AG, Zinellu A, Mangoni AA, Pintus G
Cell Mol Life Sci 2021 Mar;78(5):2031-2057. Epub 2020 Nov 17 doi: 10.1007/s00018-020-03693-7. PMID: 33201251Free PMC Article
Rao LZ, Wang Y, Zhang L, Wu G, Zhang L, Wang FX, Chen LM, Sun F, Jia S, Zhang S, Yu Q, Wei JH, Lei HR, Yuan T, Li J, Huang X, Cheng B, Zhao J, Xu Y, Mo BW, Wang CY, Zhang H
Cell Death Differ 2021 Apr;28(4):1270-1283. Epub 2020 Nov 3 doi: 10.1038/s41418-020-00650-6. PMID: 33144678Free PMC Article
Wells AU, Flaherty KR, Brown KK, Inoue Y, Devaraj A, Richeldi L, Moua T, Crestani B, Wuyts WA, Stowasser S, Quaresma M, Goeldner RG, Schlenker-Herceg R, Kolb M; INBUILD trial investigators
Lancet Respir Med 2020 May;8(5):453-460. Epub 2020 Mar 5 doi: 10.1016/S2213-2600(20)30036-9. PMID: 32145830
Kishaba T
Medicina (Kaunas) 2019 Mar 16;55(3) doi: 10.3390/medicina55030070. PMID: 30884853Free PMC Article

Prognosis

Mankikian J, Caille A, Reynaud-Gaubert M, Agier MS, Bermudez J, Bonniaud P, Borie R, Brillet PY, Cadranel J, Court-Fortune I, Crestani B, Debray MP, Gomez E, Gondouin A, Hirschi-Santelmo S, Israel-Biet D, Jouneau S, Juvin K, Leger J, Kerjouan M, Marquette CH, Naccache JM, Nunes H, Plantier L, Prevot G, Quetant S, Traclet J, Valentin V, Uzunhan Y, Wémeau-Stervinou L, Bejan-Angoulvant T, Cottin V, Marchand-Adam S; EVER-ILD investigators and the OrphaLung network
Eur Respir J 2023 Jun;61(6) Epub 2023 Jun 8 doi: 10.1183/13993003.02071-2022. PMID: 37230499
Arenas-Jiménez JJ, García-Garrigós E, Ureña Vacas A, Sirera Matilla M, Feliu Rey E
Radiologia (Engl Ed) 2022 Dec;64 Suppl 3:240-249. doi: 10.1016/j.rxeng.2022.08.002. PMID: 36737163
Cottin V, Hirani NA, Hotchkin DL, Nambiar AM, Ogura T, Otaola M, Skowasch D, Park JS, Poonyagariyagorn HK, Wuyts W, Wells AU
Eur Respir Rev 2018 Dec 31;27(150) Epub 2018 Dec 21 doi: 10.1183/16000617.0076-2018. PMID: 30578335Free PMC Article
Meyer KC
Expert Rev Respir Med 2017 May;11(5):343-359. Epub 2017 Apr 10 doi: 10.1080/17476348.2017.1312346. PMID: 28345383
Belloli EA, Beckford R, Hadley R, Flaherty KR
Respirology 2016 Feb;21(2):259-68. Epub 2015 Nov 13 doi: 10.1111/resp.12674. PMID: 26564810

Clinical prediction guides

Lee KS, Han J, Wada N, Hata A, Lee HY, Yi C, Hino T, Doyle TJ, Franquet T, Hatabu H
AJR Am J Roentgenol 2024 Feb;222(2):e2329119. Epub 2023 Apr 12 doi: 10.2214/AJR.23.29119. PMID: 37095673
Mankikian J, Caille A, Reynaud-Gaubert M, Agier MS, Bermudez J, Bonniaud P, Borie R, Brillet PY, Cadranel J, Court-Fortune I, Crestani B, Debray MP, Gomez E, Gondouin A, Hirschi-Santelmo S, Israel-Biet D, Jouneau S, Juvin K, Leger J, Kerjouan M, Marquette CH, Naccache JM, Nunes H, Plantier L, Prevot G, Quetant S, Traclet J, Valentin V, Uzunhan Y, Wémeau-Stervinou L, Bejan-Angoulvant T, Cottin V, Marchand-Adam S; EVER-ILD investigators and the OrphaLung network
Eur Respir J 2023 Jun;61(6) Epub 2023 Jun 8 doi: 10.1183/13993003.02071-2022. PMID: 37230499
Pugashetti JV, Adegunsoye A, Wu Z, Lee CT, Srikrishnan A, Ghodrati S, Vo V, Renzoni EA, Wells AU, Garcia CK, Chua F, Newton CA, Molyneaux PL, Oldham JM
Am J Respir Crit Care Med 2023 Jan 1;207(1):69-76. doi: 10.1164/rccm.202201-0124OC. PMID: 35943866Free PMC Article
Wells AU, Flaherty KR, Brown KK, Inoue Y, Devaraj A, Richeldi L, Moua T, Crestani B, Wuyts WA, Stowasser S, Quaresma M, Goeldner RG, Schlenker-Herceg R, Kolb M; INBUILD trial investigators
Lancet Respir Med 2020 May;8(5):453-460. Epub 2020 Mar 5 doi: 10.1016/S2213-2600(20)30036-9. PMID: 32145830
Cottin V, Hirani NA, Hotchkin DL, Nambiar AM, Ogura T, Otaola M, Skowasch D, Park JS, Poonyagariyagorn HK, Wuyts W, Wells AU
Eur Respir Rev 2018 Dec 31;27(150) Epub 2018 Dec 21 doi: 10.1183/16000617.0076-2018. PMID: 30578335Free PMC Article

Recent systematic reviews

Hellemons ME, Moor CC, von der Thüsen J, Rossius M, Odink A, Thorgersen LH, Verschakelen J, Wuyts W, Wijsenbeek MS, Bendstrup E
Eur Respir Rev 2020 Jun 30;29(156) Epub 2020 Jun 23 doi: 10.1183/16000617.0181-2019. PMID: 32581140Free PMC Article
Kamiya H, Panlaqui OM
BMJ Open 2019 Dec 11;9(12):e031444. doi: 10.1136/bmjopen-2019-031444. PMID: 31831537Free PMC Article
Dhooria S, Sehgal IS, Aggarwal AN, Behera D, Agarwal R
Respir Care 2016 May;61(5):700-12. Epub 2016 Mar 1 doi: 10.4187/respcare.04488. PMID: 26932382
Suzuki M, Yokoyama Y, Yamazaki H
Acupunct Med 2009 Jun;27(2):54-60. doi: 10.1136/aim.2009.000471. PMID: 19502460
Polosa R, Simidchiev A, Walters EH
Cochrane Database Syst Rev 2002;2002(3):CD002872. doi: 10.1002/14651858.CD002872. PMID: 12137662Free PMC Article

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