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Juvenile Systemic Sclerosis

MedGen UID:
419841
Concept ID:
C2931591
Disease or Syndrome
Synonym: Juvenile systemic scleroderma

Definition

Systemic sclerosis that is diagnosed in children. Juvenile systemic sclerosis is more likely to be of the overlap variant and presents with musculoskeletal involvement. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVJuvenile Systemic Sclerosis

Professional guidelines

PubMed

Foeldvari I, Culpo R, Sperotto F, Anton J, Avcin T, Baildam E, Boros C, Chaitow J, Constantin T, Kasapcopur O, Knupp Feitosa de Oliveira S, Pilkington C, Toplak N, van Royen A, Saad Magalhaes C, Vastert SJ, Wulffraat N, Zulian F
Rheumatology (Oxford) 2021 Apr 6;60(4):1651-1658. doi: 10.1093/rheumatology/keaa584. PMID: 33147624
Zulian F, Tirelli F
Curr Rheumatol Rep 2020 Jun 26;22(8):45. doi: 10.1007/s11926-020-00910-x. PMID: 32591919
Zulian F, Balzarin M, Birolo C
Expert Rev Clin Immunol 2017 Apr;13(4):361-369. Epub 2016 Oct 11 doi: 10.1080/1744666X.2017.1243467. PMID: 27690679

Recent clinical studies

Etiology

Thomas KN, Aggarwal A
Clin Rheumatol 2023 Oct;42(10):2703-2715. Epub 2023 May 9 doi: 10.1007/s10067-023-06621-9. PMID: 37160484Free PMC Article
Zulian F, Lanzoni G, Castaldi B, Meneghel A, Tirelli F, Zanatta E, Martini G
Rheumatology (Oxford) 2022 May 30;61(6):2555-2562. doi: 10.1093/rheumatology/keab738. PMID: 34605913Free PMC Article
Coit P, Schollaert KL, Mirizio EM, Torok KS, Sawalha AH
Clin Immunol 2021 Jul;228:108756. Epub 2021 May 13 doi: 10.1016/j.clim.2021.108756. PMID: 33992755Free PMC Article
Zulian F, Tirelli F
Curr Rheumatol Rep 2020 Jun 26;22(8):45. doi: 10.1007/s11926-020-00910-x. PMID: 32591919
Li SC
Pediatr Clin North Am 2018 Aug;65(4):757-781. doi: 10.1016/j.pcl.2018.04.002. PMID: 30031497

Diagnosis

Thomas KN, Aggarwal A
Clin Rheumatol 2023 Oct;42(10):2703-2715. Epub 2023 May 9 doi: 10.1007/s10067-023-06621-9. PMID: 37160484Free PMC Article
Zulian F, Lanzoni G, Castaldi B, Meneghel A, Tirelli F, Zanatta E, Martini G
Rheumatology (Oxford) 2022 May 30;61(6):2555-2562. doi: 10.1093/rheumatology/keab738. PMID: 34605913Free PMC Article
Li SC
Pediatr Clin North Am 2018 Aug;65(4):757-781. doi: 10.1016/j.pcl.2018.04.002. PMID: 30031497
Zulian F
Best Pract Res Clin Rheumatol 2017 Aug;31(4):576-595. Epub 2018 Mar 27 doi: 10.1016/j.berh.2018.02.004. PMID: 29773274
Foeldvari I
Curr Rheumatol Rep 2015 Mar;17(3):18. doi: 10.1007/s11926-014-0491-y. PMID: 25761925

Therapy

Adrovic A, Yildiz M, Haslak F, Koker O, Aliyeva A, Sahin S, Barut K, Kasapcopur O
Rheumatol Int 2021 Jan;41(1):121-128. Epub 2020 Oct 27 doi: 10.1007/s00296-020-04732-z. PMID: 33108799
Zulian F, Tirelli F
Curr Rheumatol Rep 2020 Jun 26;22(8):45. doi: 10.1007/s11926-020-00910-x. PMID: 32591919
Li SC
Pediatr Clin North Am 2018 Aug;65(4):757-781. doi: 10.1016/j.pcl.2018.04.002. PMID: 30031497
Adrovic A, Sahin S, Barut K, Kasapcopur O
Curr Rheumatol Rev 2018;14(3):219-225. doi: 10.2174/1573397114666180423105056. PMID: 29692255
Zulian F
Best Pract Res Clin Rheumatol 2017 Aug;31(4):576-595. Epub 2018 Mar 27 doi: 10.1016/j.berh.2018.02.004. PMID: 29773274

Prognosis

Zulian F, Lanzoni G, Castaldi B, Meneghel A, Tirelli F, Zanatta E, Martini G
Rheumatology (Oxford) 2022 May 30;61(6):2555-2562. doi: 10.1093/rheumatology/keab738. PMID: 34605913Free PMC Article
Zulian F, Dal Pozzolo R, Meneghel A, Castaldi B, Marcolongo R, Caforio ALP, Martini G
Rheumatology (Oxford) 2020 Dec 1;59(12):3793-3797. doi: 10.1093/rheumatology/keaa193. PMID: 32442284
Li SC
Pediatr Clin North Am 2018 Aug;65(4):757-781. doi: 10.1016/j.pcl.2018.04.002. PMID: 30031497
Adrovic A, Sahin S, Barut K, Kasapcopur O
Curr Rheumatol Rev 2018;14(3):219-225. doi: 10.2174/1573397114666180423105056. PMID: 29692255
Zulian F, Martini G
Curr Opin Rheumatol 2007 Nov;19(6):592-7. doi: 10.1097/BOR.0b013e3282f01625. PMID: 17917540

Clinical prediction guides

Zulian F, Tirelli F
Curr Rheumatol Rep 2020 Jun 26;22(8):45. doi: 10.1007/s11926-020-00910-x. PMID: 32591919
Zulian F, Dal Pozzolo R, Meneghel A, Castaldi B, Marcolongo R, Caforio ALP, Martini G
Rheumatology (Oxford) 2020 Dec 1;59(12):3793-3797. doi: 10.1093/rheumatology/keaa193. PMID: 32442284
Zulian F
Best Pract Res Clin Rheumatol 2017 Aug;31(4):576-595. Epub 2018 Mar 27 doi: 10.1016/j.berh.2018.02.004. PMID: 29773274
Foeldvari I
Curr Rheumatol Rep 2015 Mar;17(3):18. doi: 10.1007/s11926-014-0491-y. PMID: 25761925
Zulian F, Cuffaro G, Sperotto F
Curr Opin Rheumatol 2013 Sep;25(5):643-50. doi: 10.1097/BOR.0b013e3283641f61. PMID: 23912318

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