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Neoplasm of mediastinum

MedGen UID:
44322
Concept ID:
C0025063
Neoplastic Process
Synonyms: Mediastinal Neoplasm; Mediastinal Neoplasms; Mediastinum Neoplasm; Mediastinum Neoplasms; Neoplasm, Mediastinal; Neoplasm, Mediastinum; Neoplasms, Mediastinal; Neoplasms, Mediastinum
SNOMED CT: Neoplasm of mediastinum (126725000); Tumor of mediastinum (126725000)
 
Monarch Initiative: MONDO:0021386

Definition

A benign or malignant neoplasm that affects the structures of the mediastinum. Representative examples include mediastinal lipoma, mediastinal schwannoma, thymoma, mediastinal germ cell tumor, and mediastinal lymphoma. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVNeoplasm of mediastinum

Professional guidelines

PubMed

Moleti ML, Testi AM, Foà R
Br J Haematol 2020 Jun;189(5):826-843. Epub 2020 Mar 6 doi: 10.1111/bjh.16461. PMID: 32141616
Paydary K, Seraj SM, Zadeh MZ, Emamzadehfard S, Shamchi SP, Gholami S, Werner TJ, Alavi A
Mol Imaging Biol 2019 Feb;21(1):1-10. doi: 10.1007/s11307-018-1181-3. PMID: 29516387
Collins LG, Haines C, Perkel R, Enck RE
Am Fam Physician 2007 Jan 1;75(1):56-63. PMID: 17225705

Recent clinical studies

Etiology

Jiang Y, Lin Y, Yang C, He P, Liu Z, Wang H, Zhong R, Huang L, Li Z, Xu F, Lin X, Liu J, Xu X, Li S, Cui F, Wang W, Liang W, Zhao L, Hu J, Li B, Chen D, Tang W, Chen C, Fu J, Leng X, Pang D, He J, Liang H
Lung Cancer 2024 May;191:107558. Epub 2024 Mar 30 doi: 10.1016/j.lungcan.2024.107558. PMID: 38569278
Gerber TS, Porubsky S
Histopathology 2024 Jan;84(1):183-195. Epub 2023 Nov 21 doi: 10.1111/his.15088. PMID: 37988262
Tang R, Liang H, Guo Y, Li Z, Liu Z, Lin X, Yan Z, Liu J, Xu X, Shao W, Li S, Liang W, Wang W, Cui F, He H, Yang C, Jiang L, Wang H, Chen H, Guo C, Zhang H, Gao Z, He Y, Chen X, Zhao L, Yu H, Hu J, Zhao J, Li B, Yin C, Mao W, Lin W, Xie Y, Liu J, Li X, Wu D, Hou Q, Chen Y, Chen D, Xue Y, Liang Y, Tang W, Wang Q, Li E, Liu H, Wang G, Yu P, Chen C, Zheng B, Chen H, Zhang Z, Wang L, Wang A, Li Z, Fu J, Zhang G, Zhang J, Liu B, Zhao J, Deng B, Han Y, Leng X, Li Z, Zhang M, Liu C, Wang T, Luo Z, Yang C, Guo X, Ma K, Wang L, Jiang W, Han X, Wang Q, Qiao K, Xia Z, Zheng S, Xu C, Peng J, Wu S, Zhang Z, Huang H, Pang D, Liu Q, Li J, Ding X, Liu X, Zhong L, Lu Y, Xu F, Dai Q, He J
Lancet Digit Health 2023 Sep;5(9):e560-e570. doi: 10.1016/S2589-7500(23)00106-1. PMID: 37625894
Carter BW, Benveniste MF, Madan R, Godoy MC, de Groot PM, Truong MT, Rosado-de-Christenson ML, Marom EM
Radiographics 2017 Mar-Apr;37(2):413-436. Epub 2017 Jan 27 doi: 10.1148/rg.2017160095. PMID: 28129068
Brown LR, Reiman HM, Rosenow EC 3rd, Gloviczki PM, Divertie MB
Mayo Clin Proc 1986 Nov;61(11):882-92. doi: 10.1016/s0025-6196(12)62609-3. PMID: 3762227

Diagnosis

Tang R, Liang H, Guo Y, Li Z, Liu Z, Lin X, Yan Z, Liu J, Xu X, Shao W, Li S, Liang W, Wang W, Cui F, He H, Yang C, Jiang L, Wang H, Chen H, Guo C, Zhang H, Gao Z, He Y, Chen X, Zhao L, Yu H, Hu J, Zhao J, Li B, Yin C, Mao W, Lin W, Xie Y, Liu J, Li X, Wu D, Hou Q, Chen Y, Chen D, Xue Y, Liang Y, Tang W, Wang Q, Li E, Liu H, Wang G, Yu P, Chen C, Zheng B, Chen H, Zhang Z, Wang L, Wang A, Li Z, Fu J, Zhang G, Zhang J, Liu B, Zhao J, Deng B, Han Y, Leng X, Li Z, Zhang M, Liu C, Wang T, Luo Z, Yang C, Guo X, Ma K, Wang L, Jiang W, Han X, Wang Q, Qiao K, Xia Z, Zheng S, Xu C, Peng J, Wu S, Zhang Z, Huang H, Pang D, Liu Q, Li J, Ding X, Liu X, Zhong L, Lu Y, Xu F, Dai Q, He J
Lancet Digit Health 2023 Sep;5(9):e560-e570. doi: 10.1016/S2589-7500(23)00106-1. PMID: 37625894
Sohn A, Moran CA
Semin Diagn Pathol 2023 Jan;40(1):37-46. Epub 2022 Jun 11 doi: 10.1053/j.semdp.2022.06.010. PMID: 35717316
Garrana SH, Rosado-de-Christenson ML
Radiol Clin North Am 2021 Mar;59(2):155-168. Epub 2021 Jan 11 doi: 10.1016/j.rcl.2020.10.003. PMID: 33551078
Carter BW, Marom EM, Detterbeck FC
J Thorac Oncol 2014 Sep;9(9 Suppl 2):S102-9. doi: 10.1097/JTO.0000000000000294. PMID: 25396306
Duwe BV, Sterman DH, Musani AI
Chest 2005 Oct;128(4):2893-909. doi: 10.1378/chest.128.4.2893. PMID: 16236967

Therapy

Martelli M, Ceriani L, Ciccone G, Ricardi U, Kriachok I, Botto B, Balzarotti M, Tucci A, Usai SV, Zilioli VR, Pennese E, Arcaini L, Dabrowska-Iwanicka A, Ferreri AJM, Merli F, Zhao W, Rigacci L, Cellini C, Hodgson D, Ionescu C, Minoia C, Lucchini E, Spina M, Fosså A, Janikova A, Cwynarski K, Mikhaeel G, Jerkeman M, Di Rocco A, Stepanishyna Y, Vitolo U, Santoro A, Re A, Puccini B, Olivieri J, Petrucci L, Barrington SF, Malkowski B, Metser U, Versari A, Chauvie S, Walewski J, Trneny M, Cavalli F, Gospodarowicz M, Johnson PWM, Davies A, Zucca E; International Extranodal Lymphoma Study Group (IELSG)
J Clin Oncol 2024 Dec;42(34):4071-4083. Epub 2024 Aug 19 doi: 10.1200/JCO-24-01373. PMID: 39159403
Soueidy C, Kourie HR
Clin Lymphoma Myeloma Leuk 2023 Dec;23(12):866-873. Epub 2023 Aug 21 doi: 10.1016/j.clml.2023.08.014. PMID: 37722943
Savage KJ
Blood 2022 Sep 1;140(9):955-970. doi: 10.1182/blood.2020008376. PMID: 34496020
Yu Y, Dong X, Tu M, Wang H
Thorac Cancer 2021 Nov;12(21):2831-2837. Epub 2021 Sep 29 doi: 10.1111/1759-7714.14155. PMID: 34590432Free PMC Article
Armand P, Rodig S, Melnichenko V, Thieblemont C, Bouabdallah K, Tumyan G, Özcan M, Portino S, Fogliatto L, Caballero MD, Walewski J, Gulbas Z, Ribrag V, Christian B, Perini GF, Salles G, Svoboda J, Zain J, Patel S, Chen PH, Ligon AH, Ouyang J, Neuberg D, Redd R, Chatterjee A, Balakumaran A, Orlowski R, Shipp M, Zinzani PL
J Clin Oncol 2019 Dec 1;37(34):3291-3299. Epub 2019 Oct 14 doi: 10.1200/JCO.19.01389. PMID: 31609651Free PMC Article

Prognosis

Jiang Y, Lin Y, Yang C, He P, Liu Z, Wang H, Zhong R, Huang L, Li Z, Xu F, Lin X, Liu J, Xu X, Li S, Cui F, Wang W, Liang W, Zhao L, Hu J, Li B, Chen D, Tang W, Chen C, Fu J, Leng X, Pang D, He J, Liang H
Lung Cancer 2024 May;191:107558. Epub 2024 Mar 30 doi: 10.1016/j.lungcan.2024.107558. PMID: 38569278
Domínguez Malagón H, Pérez Montiel D
Semin Diagn Pathol 2005 Aug;22(3):230-40. doi: 10.1053/j.semdp.2006.02.009. PMID: 16711404
Duwe BV, Sterman DH, Musani AI
Chest 2005 Oct;128(4):2893-909. doi: 10.1378/chest.128.4.2893. PMID: 16236967
Saenz NC, Schnitzer JJ, Eraklis AE, Hendren WH, Grier HE, Macklis RM, Shamberger RC
J Pediatr Surg 1993 Feb;28(2):172-6. doi: 10.1016/s0022-3468(05)80268-4. PMID: 8437074
Aygun C, Slawson RG, Bajaj K, Salazar OM
Urology 1984 Feb;23(2):109-17. PMID: 6364524

Clinical prediction guides

Martelli M, Ceriani L, Ciccone G, Ricardi U, Kriachok I, Botto B, Balzarotti M, Tucci A, Usai SV, Zilioli VR, Pennese E, Arcaini L, Dabrowska-Iwanicka A, Ferreri AJM, Merli F, Zhao W, Rigacci L, Cellini C, Hodgson D, Ionescu C, Minoia C, Lucchini E, Spina M, Fosså A, Janikova A, Cwynarski K, Mikhaeel G, Jerkeman M, Di Rocco A, Stepanishyna Y, Vitolo U, Santoro A, Re A, Puccini B, Olivieri J, Petrucci L, Barrington SF, Malkowski B, Metser U, Versari A, Chauvie S, Walewski J, Trneny M, Cavalli F, Gospodarowicz M, Johnson PWM, Davies A, Zucca E; International Extranodal Lymphoma Study Group (IELSG)
J Clin Oncol 2024 Dec;42(34):4071-4083. Epub 2024 Aug 19 doi: 10.1200/JCO-24-01373. PMID: 39159403
Jiang Y, Lin Y, Yang C, He P, Liu Z, Wang H, Zhong R, Huang L, Li Z, Xu F, Lin X, Liu J, Xu X, Li S, Cui F, Wang W, Liang W, Zhao L, Hu J, Li B, Chen D, Tang W, Chen C, Fu J, Leng X, Pang D, He J, Liang H
Lung Cancer 2024 May;191:107558. Epub 2024 Mar 30 doi: 10.1016/j.lungcan.2024.107558. PMID: 38569278
Tang R, Liang H, Guo Y, Li Z, Liu Z, Lin X, Yan Z, Liu J, Xu X, Shao W, Li S, Liang W, Wang W, Cui F, He H, Yang C, Jiang L, Wang H, Chen H, Guo C, Zhang H, Gao Z, He Y, Chen X, Zhao L, Yu H, Hu J, Zhao J, Li B, Yin C, Mao W, Lin W, Xie Y, Liu J, Li X, Wu D, Hou Q, Chen Y, Chen D, Xue Y, Liang Y, Tang W, Wang Q, Li E, Liu H, Wang G, Yu P, Chen C, Zheng B, Chen H, Zhang Z, Wang L, Wang A, Li Z, Fu J, Zhang G, Zhang J, Liu B, Zhao J, Deng B, Han Y, Leng X, Li Z, Zhang M, Liu C, Wang T, Luo Z, Yang C, Guo X, Ma K, Wang L, Jiang W, Han X, Wang Q, Qiao K, Xia Z, Zheng S, Xu C, Peng J, Wu S, Zhang Z, Huang H, Pang D, Liu Q, Li J, Ding X, Liu X, Zhong L, Lu Y, Xu F, Dai Q, He J
Lancet Digit Health 2023 Sep;5(9):e560-e570. doi: 10.1016/S2589-7500(23)00106-1. PMID: 37625894
De Leyn P, Dooms C, Kuzdzal J, Lardinois D, Passlick B, Rami-Porta R, Turna A, Van Schil P, Venuta F, Waller D, Weder W, Zielinski M
Eur J Cardiothorac Surg 2014 May;45(5):787-98. Epub 2014 Feb 26 doi: 10.1093/ejcts/ezu028. PMID: 24578407
Thomas CR Jr, Bonomi PD
Curr Opin Oncol 1991 Apr;3(2):335-43. doi: 10.1097/00001622-199104000-00015. PMID: 1648973

Recent systematic reviews

Masuda Y, Leong EKF, So JBY, Shabbir A, Lam Jia Wei T, Chia DKA, Kim G
Surg Oncol 2024 Apr;53:102042. Epub 2024 Feb 1 doi: 10.1016/j.suronc.2024.102042. PMID: 38330804
Botana-Rial M, Lojo-Rodríguez I, Leiro-Fernández V, Ramos-Hernández C, González-Montaos A, Pazos-Area L, Núñez-Delgado M, Fernández-Villar A
Respir Med 2023 Nov;218:107389. Epub 2023 Aug 12 doi: 10.1016/j.rmed.2023.107389. PMID: 37579981
Fernández-Villar A, Mouronte-Roibás C, Botana-Rial M, Ruano-Raviña A
Arch Bronconeumol 2016 Feb;52(2):96-102. Epub 2015 Nov 10 doi: 10.1016/j.arbres.2015.08.007. PMID: 26565072
Wahidi MM, Herth F, Yasufuku K, Shepherd RW, Yarmus L, Chawla M, Lamb C, Casey KR, Patel S, Silvestri GA, Feller-Kopman DJ
Chest 2016 Mar;149(3):816-35. Epub 2016 Jan 12 doi: 10.1378/chest.15-1216. PMID: 26402427
Wang T, Liu L, Luo J, Liu T, Wei A
Urol J 2015 Apr 29;12(2):2057-64. PMID: 25923148

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