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Esophageal Malignant Peripheral Nerve Sheath Tumor

MedGen UID:
457127
•Concept ID:
C2984901
•
Neoplastic Process
Synonym: Malignant Esophageal Peripheral Nerve Sheath Tumor

Definition

A malignant peripheral nerve sheath tumor that affects the esophageal wall. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVEsophageal Malignant Peripheral Nerve Sheath Tumor

Recent clinical studies

Etiology

Impact of Transcript (p16/p14ARF) Alteration on Cancer Risk in CDKN2A Germline Pathogenic Variant Carriers.
Sargen MR, Helgadottir H, Yang XR, Harland M, Hatton JN, Jones K, Hicks BD, Hutchinson A, Curry M, Tucker MA, Goldstein AM, Pfeiffer RM
JNCI Cancer Spectr 2022 Nov 1;6(6) doi: 10.1093/jncics/pkac074. PMID: 36269225Free PMC Article
A clinicopathologic study of malignancy in VCP-associated multisystem proteinopathy.
Shmara A, Perez-Rosendahl M, Murphy K, Kwon A, Smith C, Kimonis V
Orphanet J Rare Dis 2022 Jul 15;17(1):272. doi: 10.1186/s13023-022-02403-9. PMID: 35841038Free PMC Article
Videothoracoscopic excision of mediastinal tumors and cysts using the harmonic scalpel.
Lang-Lazdunski L, Pilling J
Thorac Cardiovasc Surg 2008 Aug;56(5):278-82. doi: 10.1055/s-2008-1038630. PMID: 18615374

Diagnosis

Malignant peripheral nerve sheath tumor of the esophagus.
Manger T, Pross M, Haeckel C, Lippert H
Dig Surg 2000;17(6):627-631. doi: 10.1159/000051973. PMID: 11155010

Therapy

Videothoracoscopic excision of mediastinal tumors and cysts using the harmonic scalpel.
Lang-Lazdunski L, Pilling J
Thorac Cardiovasc Surg 2008 Aug;56(5):278-82. doi: 10.1055/s-2008-1038630. PMID: 18615374

Prognosis

Cell-type- and tumour-type-related patterns of bcl-2 reactivity in mesenchymal cells and soft tissue tumours.
Miettinen M, Sarlomo-Rikala M, Kovatich AJ
Virchows Arch 1998 Sep;433(3):255-60. doi: 10.1007/s004280050244. PMID: 9769129

Clinical prediction guides

Impact of Transcript (p16/p14ARF) Alteration on Cancer Risk in CDKN2A Germline Pathogenic Variant Carriers.
Sargen MR, Helgadottir H, Yang XR, Harland M, Hatton JN, Jones K, Hicks BD, Hutchinson A, Curry M, Tucker MA, Goldstein AM, Pfeiffer RM
JNCI Cancer Spectr 2022 Nov 1;6(6) doi: 10.1093/jncics/pkac074. PMID: 36269225Free PMC Article
Cell-type- and tumour-type-related patterns of bcl-2 reactivity in mesenchymal cells and soft tissue tumours.
Miettinen M, Sarlomo-Rikala M, Kovatich AJ
Virchows Arch 1998 Sep;433(3):255-60. doi: 10.1007/s004280050244. PMID: 9769129

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