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Pulmonary vein stenosis

MedGen UID:
473065
Concept ID:
C0340756
Disease or Syndrome
Synonyms: Pulmonary Vein Stenoses; Pulmonary Vein Stenosis; Stenoses, Pulmonary Vein; Stenosis, Pulmonary Vein; Vein Stenoses, Pulmonary; Vein Stenosis, Pulmonary
SNOMED CT: Pulmonary vein stenosis (234062003)

Definition

Obstruction of the pulmonary vein in one or multiple sites. The obstruction is the result of wall thickening and narrowing of the lumen of the vein. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVPulmonary vein stenosis

Professional guidelines

PubMed

Simard T, Sarma D, Miranda WR, Jain CC, Anderson JH, Collins JD, El Sabbagh A, Jhand A, Peikert T, Reeder GS, Munger TM, Packer DL, Holmes DR
J Am Coll Cardiol 2023 Jun 20;81(24):2361-2373. doi: 10.1016/j.jacc.2023.04.016. PMID: 37316116
Vanderlaan RD, Rome J, Hirsch R, Ivy D, Caldarone CA
J Thorac Cardiovasc Surg 2021 Jun;161(6):2169-2176. Epub 2020 Jun 27 doi: 10.1016/j.jtcvs.2020.05.117. PMID: 32763037
Suntharos P, Prieto LR
Curr Cardiol Rep 2020 Oct 3;22(11):153. doi: 10.1007/s11886-020-01395-x. PMID: 33009955

Recent clinical studies

Etiology

Almakadma AH, Sarma D, Hassett L, Miranda W, Alkhouli M, Reeder GS, Munger TM, Packer DL, Simard T, Holmes DR Jr
JACC Clin Electrophysiol 2022 Oct;8(10):1323-1333. Epub 2022 Sep 16 doi: 10.1016/j.jacep.2022.08.008. PMID: 36117046
Patel JD, Briones M, Mandhani M, Jones S, Suthar D, Gray R, Pettus J, McCracken C, Thomas A, Petit CJ
J Am Coll Cardiol 2021 Jun 8;77(22):2807-2818. doi: 10.1016/j.jacc.2021.04.013. PMID: 34082911
Suntharos P, Prieto LR
Curr Cardiol Rep 2020 Oct 3;22(11):153. doi: 10.1007/s11886-020-01395-x. PMID: 33009955
Reddy VY, Grimaldi M, De Potter T, Vijgen JM, Bulava A, Duytschaever MF, Martinek M, Natale A, Knecht S, Neuzil P, Pürerfellner H
JACC Clin Electrophysiol 2019 Jul;5(7):778-786. Epub 2019 May 8 doi: 10.1016/j.jacep.2019.04.009. PMID: 31320006
Nasr VG, Callahan R, Wichner Z, Odegard KC, DiNardo JA
Anesth Analg 2019 Jul;129(1):27-40. doi: 10.1213/ANE.0000000000003924. PMID: 30451723

Diagnosis

Simard T, Sarma D, Miranda WR, Jain CC, Anderson JH, Collins JD, El Sabbagh A, Jhand A, Peikert T, Reeder GS, Munger TM, Packer DL, Holmes DR
J Am Coll Cardiol 2023 Jun 20;81(24):2361-2373. doi: 10.1016/j.jacc.2023.04.016. PMID: 37316116
Duytschaever M, De Potter T, Grimaldi M, Anic A, Vijgen J, Neuzil P, Van Herendael H, Verma A, Skanes A, Scherr D, Pürerfellner H, Rackauskas G, Jaïs P, Reddy VY; inspIRE Trial Investigators
Circ Arrhythm Electrophysiol 2023 Mar;16(3):e011780. Epub 2023 Feb 3 doi: 10.1161/CIRCEP.122.011780. PMID: 36735937Free PMC Article
Patel JD, Briones M, Mandhani M, Jones S, Suthar D, Gray R, Pettus J, McCracken C, Thomas A, Petit CJ
J Am Coll Cardiol 2021 Jun 8;77(22):2807-2818. doi: 10.1016/j.jacc.2021.04.013. PMID: 34082911
Vanderlaan RD, Rome J, Hirsch R, Ivy D, Caldarone CA
J Thorac Cardiovasc Surg 2021 Jun;161(6):2169-2176. Epub 2020 Jun 27 doi: 10.1016/j.jtcvs.2020.05.117. PMID: 32763037
Nasr VG, Callahan R, Wichner Z, Odegard KC, DiNardo JA
Anesth Analg 2019 Jul;129(1):27-40. doi: 10.1213/ANE.0000000000003924. PMID: 30451723

Therapy

Duytschaever M, De Potter T, Grimaldi M, Anic A, Vijgen J, Neuzil P, Van Herendael H, Verma A, Skanes A, Scherr D, Pürerfellner H, Rackauskas G, Jaïs P, Reddy VY; inspIRE Trial Investigators
Circ Arrhythm Electrophysiol 2023 Mar;16(3):e011780. Epub 2023 Feb 3 doi: 10.1161/CIRCEP.122.011780. PMID: 36735937Free PMC Article
Almakadma AH, Sarma D, Hassett L, Miranda W, Alkhouli M, Reeder GS, Munger TM, Packer DL, Simard T, Holmes DR Jr
JACC Clin Electrophysiol 2022 Oct;8(10):1323-1333. Epub 2022 Sep 16 doi: 10.1016/j.jacep.2022.08.008. PMID: 36117046
Patel JD, Briones M, Mandhani M, Jones S, Suthar D, Gray R, Pettus J, McCracken C, Thomas A, Petit CJ
J Am Coll Cardiol 2021 Jun 8;77(22):2807-2818. doi: 10.1016/j.jacc.2021.04.013. PMID: 34082911
Reddy VY, Grimaldi M, De Potter T, Vijgen JM, Bulava A, Duytschaever MF, Martinek M, Natale A, Knecht S, Neuzil P, Pürerfellner H
JACC Clin Electrophysiol 2019 Jul;5(7):778-786. Epub 2019 May 8 doi: 10.1016/j.jacep.2019.04.009. PMID: 31320006
Fender EA, Widmer RJ, Knavel Koepsel EM, Welby JP, Kern R, Peikert T, Bjarnason H, Holmes DR Jr
Catheter Cardiovasc Interv 2019 Nov 15;94(6):878-885. Epub 2019 Feb 21 doi: 10.1002/ccd.28152. PMID: 30790443

Prognosis

Feng Z, Mao F, Ma K, He F, Yang Y, Yuan J, Zhang S, Zhang B, He Q, Li S
Ann Thorac Surg 2022 Apr;113(4):1239-1247. Epub 2021 Mar 18 doi: 10.1016/j.athoracsur.2021.03.015. PMID: 33745903
Suntharos P, Prieto LR
Curr Cardiol Rep 2020 Oct 3;22(11):153. doi: 10.1007/s11886-020-01395-x. PMID: 33009955
Fender EA, Widmer RJ, Mahowald MK, Hodge DO, Packer DL, Holmes DR Jr
Catheter Cardiovasc Interv 2020 Apr 1;95(5):954-958. Epub 2019 Dec 19 doi: 10.1002/ccd.28645. PMID: 31854110
Nasr VG, Callahan R, Wichner Z, Odegard KC, DiNardo JA
Anesth Analg 2019 Jul;129(1):27-40. doi: 10.1213/ANE.0000000000003924. PMID: 30451723
Edriss H, Denega T, Test V, Nugent K
Respir Med 2016 Aug;117:215-22. Epub 2016 Jun 15 doi: 10.1016/j.rmed.2016.06.014. PMID: 27492534

Clinical prediction guides

Lin Y, Amin EK, Keller RL, Teitel DF, Nawaytou HM
J Am Soc Echocardiogr 2022 Apr;35(4):435-442. Epub 2022 Jan 2 doi: 10.1016/j.echo.2021.12.015. PMID: 34986343
Feng Z, Mao F, Ma K, He F, Yang Y, Yuan J, Zhang S, Zhang B, He Q, Li S
Ann Thorac Surg 2022 Apr;113(4):1239-1247. Epub 2021 Mar 18 doi: 10.1016/j.athoracsur.2021.03.015. PMID: 33745903
Suntharos P, Prieto LR
Curr Cardiol Rep 2020 Oct 3;22(11):153. doi: 10.1007/s11886-020-01395-x. PMID: 33009955
Nasr VG, Callahan R, Wichner Z, Odegard KC, DiNardo JA
Anesth Analg 2019 Jul;129(1):27-40. doi: 10.1213/ANE.0000000000003924. PMID: 30451723
Sun CC, Doyle T, Ringel RE
Hum Pathol 1995 Aug;26(8):880-6. doi: 10.1016/0046-8177(95)90011-x. PMID: 7635450

Recent systematic reviews

Almakadma AH, Sarma D, Hassett L, Miranda W, Alkhouli M, Reeder GS, Munger TM, Packer DL, Simard T, Holmes DR Jr
JACC Clin Electrophysiol 2022 Oct;8(10):1323-1333. Epub 2022 Sep 16 doi: 10.1016/j.jacep.2022.08.008. PMID: 36117046
Wang P, He W, Li C, Xiang T, Yang Q, Chen Q
Ann Palliat Med 2021 Oct;10(10):10542-10555. doi: 10.21037/apm-21-2313. PMID: 34763501
Kumar N, Essandoh M, Bhatt A, Whitson BA, Sawyer TR, Flores A, Awad H, Dimitrova G, Gorelik L, Bhandary S, Perez WJ, Iyer MH, Stein E, Fiorini K, Turner K, Saklayen S, Hussain N
J Heart Lung Transplant 2019 May;38(5):530-544. Epub 2019 Jan 7 doi: 10.1016/j.healun.2019.01.005. PMID: 30718043
Backes CH, Nealon E, Armstrong AK, Cua CL, Mitchell C, Krishnan U, Vanderlaan RD, Song MK, Viola N, Smith CV, McConnell PI, Rivera BK, Bridge J
J Pediatr 2018 Jul;198:36-45.e3. Epub 2018 Apr 9 doi: 10.1016/j.jpeds.2018.02.030. PMID: 29650415
Stavrakis S, Madden GW, Stoner JA, Sivaram CA
Echocardiography 2010 Oct;27(9):1141-6. doi: 10.1111/j.1540-8175.2010.01250.x. PMID: 20678129

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