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Non-Metastatic Paraganglioma

MedGen UID:
473084
Concept ID:
C0346416
Neoplastic Process
Synonyms: Benign neuroendocrine tumor; Benign Paraganglioma; Benign Paraganglionic Neoplasm; Paraganglioma and glomus tumor; Paraganglioma, benign
SNOMED CT: Paraganglioma and glomus tumor (107694002); Paraganglioma, benign (107694002); Benign neuroendocrine tumor (255047001)

Definition

A paraganglioma that is confined to the site of origin. [from NCI]

Professional guidelines

PubMed

Feral CC, Tissot FS, Tosello L, Fakhry N, Sebag F, Pacak K, Taïeb D
Eur J Nucl Med Mol Imaging 2017 May;44(5):812-821. Epub 2016 Nov 29 doi: 10.1007/s00259-016-3586-z. PMID: 27900521Free PMC Article

Recent clinical studies

Etiology

Kimura N, Motoyama T, Saito J, Nishikawa T
Front Endocrinol (Lausanne) 2022;13:1026918. Epub 2022 Sep 16 doi: 10.3389/fendo.2022.1026918. PMID: 36187098Free PMC Article
Wang Y, Chen D, Pang Y, Xu X, Guan X, Liu L
Front Endocrinol (Lausanne) 2022;13:882906. Epub 2022 Apr 28 doi: 10.3389/fendo.2022.882906. PMID: 35574028Free PMC Article
Ghosal S, Das S, Pang Y, Gonzales MK, Huynh TT, Yang Y, Taieb D, Crona J, Shankavaram UT, Pacak K
Int J Cancer 2020 Apr 15;146(8):2326-2335. Epub 2019 Oct 11 doi: 10.1002/ijc.32654. PMID: 31469413Free PMC Article
Koh JM, Ahn SH, Kim H, Kim BJ, Sung TY, Kim YH, Hong SJ, Song DE, Lee SH
PLoS One 2017;12(11):e0187398. Epub 2017 Nov 8 doi: 10.1371/journal.pone.0187398. PMID: 29117221Free PMC Article
Kimura N, Takayanagi R, Takizawa N, Itagaki E, Katabami T, Kakoi N, Rakugi H, Ikeda Y, Tanabe A, Nigawara T, Ito S, Kimura I, Naruse M; Phaeochromocytoma Study Group in Japan
Endocr Relat Cancer 2014 Jun;21(3):405-14. Epub 2014 May 6 doi: 10.1530/ERC-13-0494. PMID: 24521857

Diagnosis

Kimura N, Motoyama T, Saito J, Nishikawa T
Front Endocrinol (Lausanne) 2022;13:1026918. Epub 2022 Sep 16 doi: 10.3389/fendo.2022.1026918. PMID: 36187098Free PMC Article
Wang Y, Chen D, Pang Y, Xu X, Guan X, Liu L
Front Endocrinol (Lausanne) 2022;13:882906. Epub 2022 Apr 28 doi: 10.3389/fendo.2022.882906. PMID: 35574028Free PMC Article
Li H, Hardin H, Zaeem M, Huang W, Hu R, Lloyd RV
Ann Diagn Pathol 2021 Dec;55:151801. Epub 2021 Jul 31 doi: 10.1016/j.anndiagpath.2021.151801. PMID: 34461576
Koh JM, Ahn SH, Kim H, Kim BJ, Sung TY, Kim YH, Hong SJ, Song DE, Lee SH
PLoS One 2017;12(11):e0187398. Epub 2017 Nov 8 doi: 10.1371/journal.pone.0187398. PMID: 29117221Free PMC Article
Kimura N, Takayanagi R, Takizawa N, Itagaki E, Katabami T, Kakoi N, Rakugi H, Ikeda Y, Tanabe A, Nigawara T, Ito S, Kimura I, Naruse M; Phaeochromocytoma Study Group in Japan
Endocr Relat Cancer 2014 Jun;21(3):405-14. Epub 2014 May 6 doi: 10.1530/ERC-13-0494. PMID: 24521857

Therapy

Capitanio U, Rosiello G, Erdem S, Rowe I, Kara O, Roussel E, Campi R, Klatte T, Kriegmair MC, Sibona M, Bertolo R, Ouzaid I, Mir MC, Marra G, Larcher A, Montorsi F, Salonia A; Kidney Cancer Working Group of the Young Academic Urologists (YAU) Working Party of the European Association of Urology (EAU)
World J Urol 2021 Aug;39(8):2969-2975. Epub 2021 Jan 8 doi: 10.1007/s00345-020-03574-5. PMID: 33416974
Amar L, Lussey-Lepoutre C, Lenders JW, Djadi-Prat J, Plouin PF, Steichen O
Eur J Endocrinol 2016 Oct;175(4):R135-45. Epub 2016 Apr 14 doi: 10.1530/EJE-16-0189. PMID: 27080352
Thosani S, Ayala-Ramirez M, Román-González A, Zhou S, Thosani N, Bisanz A, Jimenez C
Eur J Endocrinol 2015 Sep;173(3):377-87. Epub 2015 Jun 9 doi: 10.1530/EJE-15-0456. PMID: 26060051
Timmers HJ, Eisenhofer G, Carrasquillo JA, Chen CC, Whatley M, Ling A, Adams KT, Pacak K
Clin Endocrinol (Oxf) 2009 Jul;71(1):11-7. Epub 2008 Dec 5 doi: 10.1111/j.1365-2265.2008.03496.x. PMID: 19138315Free PMC Article

Prognosis

Ghosal S, Vanova KH, Uher O, Das S, Patel M, Meuter L, Huynh TT, Jha A, Talvacchio S, Knue M, Prodanov T, Zeiger MA, Nilubol N, Taieb D, Crona J, Shankavaram UT, Pacak K
Endocrine 2023 Jan;79(1):171-179. Epub 2022 Nov 12 doi: 10.1007/s12020-022-03218-1. PMID: 36370152
Kimura N, Motoyama T, Saito J, Nishikawa T
Front Endocrinol (Lausanne) 2022;13:1026918. Epub 2022 Sep 16 doi: 10.3389/fendo.2022.1026918. PMID: 36187098Free PMC Article
Li H, Hardin H, Zaeem M, Huang W, Hu R, Lloyd RV
Ann Diagn Pathol 2021 Dec;55:151801. Epub 2021 Jul 31 doi: 10.1016/j.anndiagpath.2021.151801. PMID: 34461576
Kim JH, Moon H, Noh J, Lee J, Kim SG
Endocrinol Metab (Seoul) 2020 Mar;35(1):157-164. doi: 10.3803/EnM.2020.35.1.157. PMID: 32207276Free PMC Article
Kimura N, Takayanagi R, Takizawa N, Itagaki E, Katabami T, Kakoi N, Rakugi H, Ikeda Y, Tanabe A, Nigawara T, Ito S, Kimura I, Naruse M; Phaeochromocytoma Study Group in Japan
Endocr Relat Cancer 2014 Jun;21(3):405-14. Epub 2014 May 6 doi: 10.1530/ERC-13-0494. PMID: 24521857

Clinical prediction guides

Li H, Hardin H, Zaeem M, Huang W, Hu R, Lloyd RV
Ann Diagn Pathol 2021 Dec;55:151801. Epub 2021 Jul 31 doi: 10.1016/j.anndiagpath.2021.151801. PMID: 34461576
Tomić TT, Olausson J, Rehammar A, Deland L, Muth A, Ejeskär K, Nilsson S, Kristiansson E, Wassén ON, Abel F
PLoS Genet 2020 Jun;16(6):e1008803. Epub 2020 Jun 8 doi: 10.1371/journal.pgen.1008803. PMID: 32511227Free PMC Article
Konosu-Fukaya S, Omata K, Tezuka Y, Ono Y, Aoyama Y, Satoh F, Fujishima F, Sasano H, Nakamura Y
Endocr Pathol 2018 Dec;29(4):302-309. doi: 10.1007/s12022-018-9544-5. PMID: 30155766
Koh JM, Ahn SH, Kim H, Kim BJ, Sung TY, Kim YH, Hong SJ, Song DE, Lee SH
PLoS One 2017;12(11):e0187398. Epub 2017 Nov 8 doi: 10.1371/journal.pone.0187398. PMID: 29117221Free PMC Article
Kimura N, Takayanagi R, Takizawa N, Itagaki E, Katabami T, Kakoi N, Rakugi H, Ikeda Y, Tanabe A, Nigawara T, Ito S, Kimura I, Naruse M; Phaeochromocytoma Study Group in Japan
Endocr Relat Cancer 2014 Jun;21(3):405-14. Epub 2014 May 6 doi: 10.1530/ERC-13-0494. PMID: 24521857

Recent systematic reviews

Amar L, Lussey-Lepoutre C, Lenders JW, Djadi-Prat J, Plouin PF, Steichen O
Eur J Endocrinol 2016 Oct;175(4):R135-45. Epub 2016 Apr 14 doi: 10.1530/EJE-16-0189. PMID: 27080352

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