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Extrahepatic bile duct rhabdomyosarcoma

MedGen UID:
473530
•Concept ID:
C2064434
•
Neoplastic Process
Synonyms: bile duct rhabdomyosarcoma; bile duct rhabdomyosarcoma (disease); Extrahepatic Bile Duct Rhabdomyosarcoma; extrahepatic bile duct rhabdomyosarcoma; extrahepatic bile duct rhabdomyosarcoma (disease); rhabdomyosarcoma (disease) of extrahepatic bile duct; Rhabdomyosarcoma of Extrahepatic Bile Duct; rhabdomyosarcoma of extrahepatic bile duct; rhabdomyosarcoma of the bile duct; Rhabdomyosarcoma of the Extrahepatic Bile Duct; rhabdomyosarcoma of the extrahepatic bile duct
 
Monarch Initiative: MONDO:0002577

Definition

A malignant mesenchymal tumor with skeletal muscle differentiation, arising from the extrahepatic bile ducts. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVExtrahepatic bile duct rhabdomyosarcoma

Professional guidelines

PubMed

Management of carcinoma of the extrahepatic bile ducts.
Black K, Hanna SS, Langer B, Jirsch DW, Rider WD
Can J Surg 1978 Nov;21(6):542-5. PMID: 83901

Recent clinical studies

Etiology

A child with unresectable biliary rhabdomyosarcoma: 48-month disease-free survival after liver transplantation.
Paganelli M, Beaunoyer M, Samson Y, Dal Soglio D, Dubois J, Lallier M, Alvarez F
Pediatr Transplant 2014 Aug;18(5):E146-51. Epub 2014 May 12 doi: 10.1111/petr.12279. PMID: 24815678
ERCP with intracholedocal biopsy for the diagnosis of biliary tract rhabdomyosarcoma in children.
Scottoni F, De Angelis P, Dall'Oglio L, Francalanci P, Monti L, de Ville de Goyet J
Pediatr Surg Int 2013 Jun;29(6):659-62. Epub 2013 Feb 17 doi: 10.1007/s00383-013-3282-z. PMID: 23417547
Management of carcinoma of the extrahepatic bile ducts.
Black K, Hanna SS, Langer B, Jirsch DW, Rider WD
Can J Surg 1978 Nov;21(6):542-5. PMID: 83901

Diagnosis

A Rare Association With Obstructive Jaundice.
Borges VP, Alves R, Coimbra J
Gastroenterology 2020 Apr;158(5):e12-e13. Epub 2019 Nov 15 doi: 10.1053/j.gastro.2019.10.043. PMID: 31738922
ERCP with intracholedocal biopsy for the diagnosis of biliary tract rhabdomyosarcoma in children.
Scottoni F, De Angelis P, Dall'Oglio L, Francalanci P, Monti L, de Ville de Goyet J
Pediatr Surg Int 2013 Jun;29(6):659-62. Epub 2013 Feb 17 doi: 10.1007/s00383-013-3282-z. PMID: 23417547
Botryoid rhabdomyosarcoma of the biliary tract in children: a unique case report.
Zampieri N, Camoglio F, Corroppolo M, Cecchetto M, Ornis S, Ottolenghi A
Eur J Cancer Care (Engl) 2006 Dec;15(5):463-6. doi: 10.1111/j.1365-2354.2006.00683.x. PMID: 17177904
Botryoid rhabdomyosarcoma of the biliary tract.
Lack EE, Perez-Atayde AR, Schuster SR
Am J Surg Pathol 1981 Oct;5(7):643-52. doi: 10.1097/00000478-198110000-00006. PMID: 7337157
Rhabdomyosarcoma of the bile ducts.
Nagaraj HS, Kmetz DR, Leitner C
J Pediatr Surg 1977 Dec;12(6):1071-4. doi: 10.1016/0022-3468(77)90621-2. PMID: 592061

Therapy

A child with unresectable biliary rhabdomyosarcoma: 48-month disease-free survival after liver transplantation.
Paganelli M, Beaunoyer M, Samson Y, Dal Soglio D, Dubois J, Lallier M, Alvarez F
Pediatr Transplant 2014 Aug;18(5):E146-51. Epub 2014 May 12 doi: 10.1111/petr.12279. PMID: 24815678
Botryoid rhabdomyosarcoma of the biliary tract in children: a unique case report.
Zampieri N, Camoglio F, Corroppolo M, Cecchetto M, Ornis S, Ottolenghi A
Eur J Cancer Care (Engl) 2006 Dec;15(5):463-6. doi: 10.1111/j.1365-2354.2006.00683.x. PMID: 17177904
Management of carcinoma of the extrahepatic bile ducts.
Black K, Hanna SS, Langer B, Jirsch DW, Rider WD
Can J Surg 1978 Nov;21(6):542-5. PMID: 83901
Sarcoma botryoides (rhabdomyosarcoma) of the bile ducts with survival.
Akers DR, Needham ME
J Pediatr Surg 1971 Aug;6(4):474-9. doi: 10.1016/s0022-3468(71)80011-8. PMID: 5563889

Prognosis

Hepatobiliary rhabdomyosarcoma in children: diagnostic radiology.
Roebuck DJ, Yang WT, Lam WW, Stanley P
Pediatr Radiol 1998 Feb;28(2):101-8. doi: 10.1007/s002470050305. PMID: 9472056
Rhabdomyosarcoma of the biliary tree.
Sanz N, de Mingo L, Flórez F, Rollán V
Pediatr Surg Int 1997 Feb;12(2-3):200-1. PMID: 9156861
Botryoid rhabdomyosarcoma of the biliary tract.
Lack EE, Perez-Atayde AR, Schuster SR
Am J Surg Pathol 1981 Oct;5(7):643-52. doi: 10.1097/00000478-198110000-00006. PMID: 7337157
Management of carcinoma of the extrahepatic bile ducts.
Black K, Hanna SS, Langer B, Jirsch DW, Rider WD
Can J Surg 1978 Nov;21(6):542-5. PMID: 83901
Embryonal rhabdomyosarcoma (sarcoma botryoides) of the common bile duct: a case report.
Majmudar B, Kumar VS
Hum Pathol 1976 Nov;7(6):705-8. doi: 10.1016/s0046-8177(76)80081-0. PMID: 992649

Clinical prediction guides

Three-dimensional magnetic resonance cholangiopancreatography for evaluation of obstructive jaundice.
Ng KK, Wan YL, Lui KW, Wong HF, Hung CF, Kong MS, Chiu CT
J Formos Med Assoc 1997 Aug;96(8):586-92. PMID: 9290267
Rhabdomyosarcoma of the biliary tree.
Sanz N, de Mingo L, Flórez F, Rollán V
Pediatr Surg Int 1997 Feb;12(2-3):200-1. PMID: 9156861
Ultrastructure of botryoid sarcoma of the common bile duct.
Taura S, Taura M, Tanaka N, Ito T, Tsuchiya R
Gastroenterol Jpn 1977;12(4):305-10. doi: 10.1007/BF02776799. PMID: 590703

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