U.S. flag

An official website of the United States government

Format

Send to:

Choose Destination

Ampulla of Vater Neuroendocrine Tumor

MedGen UID:
474110
Concept ID:
C3272477
Neoplastic Process
Synonyms: Ampulla of Vater NET; Neuroendocrine tumor of ampulla of Vater; Neuroendocrine Tumor of the Ampullary Region; Well-differentiated neuroendocrine tumor of ampulla of Vater
SNOMED CT: Neuroendocrine tumor of ampulla of Vater (1290066001); Well-differentiated neuroendocrine tumor of ampulla of Vater (1290066001)

Definition

A well differentiated, low, intermediate, or high grade neoplasm with neuroendocrine differentiation that arises from the ampulla of Vater and periampullary region. [from NCI]

Professional guidelines

PubMed

Komiyama S, Okusaka T, Maruki Y, Ohba A, Nagashio Y, Kondo S, Hijioka S, Morizane C, Ueno H, Sukeda A, Mizui T, Takamoto T, Nara S, Ban D, Esaki M, Hiraoka N, Shimada K
Intern Med 2024 Apr 1;63(7):891-901. Epub 2023 Aug 23 doi: 10.2169/internalmedicine.2016-23. PMID: 37612088Free PMC Article
Zhu J, Xiao W, Li Y
J Laparoendosc Adv Surg Tech A 2022 Jun;32(6):639-645. Epub 2021 Oct 11 doi: 10.1089/lap.2021.0482. PMID: 34637632
Jang SK, Kim JH, Joo I, Jeon JH, Shin KS, Han JK, Choi BI
Eur Radiol 2015 Oct;25(10):2880-8. Epub 2015 Apr 28 doi: 10.1007/s00330-015-3721-4. PMID: 25916385

Recent clinical studies

Etiology

Karam E, Hollenbach M, Abou Ali E, Auriemma F, Anderloni A, Barbier L, Belfiori G, Caillol F, Crippa S, Del Chiaro M, De Ponthaud C, Dahel Y, Falconi M, Giovannini M, Heling D, Inoue Y, Jarnagin WR, Leung G, Lupinacci RM, Mariani A, Masaryk V, Miksch RC, Musquer N, Napoleon B, Oba A, Partelli S, Petrone MC, Prat F, Repici A, Sauvanet A, Salzmann K, Schattner MA, Schulick R, Schwarz L, Soares K, Souche FR, Truant S, Vaillant JC, Wang T, Wedi E, Werner J, Weismüller TJ, Wichmann D, Will U, Zaccari P, Gulla A, Heise C, Regner S, Gaujoux S; Pancreas 2000 Research Group
Neuroendocrinology 2023;113(10):1024-1034. Epub 2023 Jun 27 doi: 10.1159/000531712. PMID: 37369186
Luchini C, Scarpa A
Hum Pathol 2023 Feb;132:176-182. Epub 2022 Jun 14 doi: 10.1016/j.humpath.2022.06.009. PMID: 35714836
Zhu J, Xiao W, Li Y
J Laparoendosc Adv Surg Tech A 2022 Jun;32(6):639-645. Epub 2021 Oct 11 doi: 10.1089/lap.2021.0482. PMID: 34637632
Ardengh JC, Ardengh AO, Almeida AF, Machado MA
Arq Gastroenterol 2021 Jul-Sep;58(3):411-412. doi: 10.1590/S0004-2803.202100000-71. PMID: 34705982
Fukatsu H, Kawamoto H, Fujii M, Tsutsumi K, Kato H, Hirao K, Kurihara N, Okamoto Y, Ogawa T, Ishida E, Okada H, Sakaguchi K
Endoscopy 2007 Feb;39 Suppl 1:E49-50. Epub 2007 Feb 7 doi: 10.1055/s-2006-945068. PMID: 17285506

Diagnosis

Trindade AJ, Benias PC, Goldenberg S
Clin Gastroenterol Hepatol 2021 Mar;19(3):e24-e25. Epub 2020 Jan 15 doi: 10.1016/j.cgh.2020.01.010. PMID: 31954200
Ardengh JC, Lemos de Bonotto M, Surjan R, Pereira Lima J, Machado MA
Endoscopy 2015;47 Suppl 1 UCTN:E127-8. Epub 2015 Mar 11 doi: 10.1055/s-0034-1391339. PMID: 25857473
Gilani N, Ramirez FC
World J Gastroenterol 2007 Feb 28;13(8):1268-70. doi: 10.3748/wjg.v13.i8.1268. PMID: 17451212Free PMC Article
Fukatsu H, Kawamoto H, Fujii M, Tsutsumi K, Kato H, Hirao K, Kurihara N, Okamoto Y, Ogawa T, Ishida E, Okada H, Sakaguchi K
Endoscopy 2007 Feb;39 Suppl 1:E49-50. Epub 2007 Feb 7 doi: 10.1055/s-2006-945068. PMID: 17285506
Chang KJ
Endoscopy 2006 Jun;38 Suppl 1:S56-60. doi: 10.1055/s-2006-946654. PMID: 16802226

Therapy

Wen LJ, Chen JH, Xu HJ, Yu Q, Deng Y, Liu K
Medicine (Baltimore) 2020 Dec 11;99(50):e23271. doi: 10.1097/MD.0000000000023271. PMID: 33327249Free PMC Article
Odufalu FD, Zubairu J, Silverman W
BMJ Case Rep 2018 Sep 4;2018 doi: 10.1136/bcr-2017-221895. PMID: 30181397Free PMC Article
Fukasawa H, Tounou S, Nabetani M, Michida T
Intern Med 2017;56(5):499-503. Epub 2017 Mar 1 doi: 10.2169/internalmedicine.56.7520. PMID: 28250294Free PMC Article
Ardengh JC, Lemos de Bonotto M, Surjan R, Pereira Lima J, Machado MA
Endoscopy 2015;47 Suppl 1 UCTN:E127-8. Epub 2015 Mar 11 doi: 10.1055/s-0034-1391339. PMID: 25857473
Snady H
Hematol Oncol Clin North Am 2002 Feb;16(1):53-79. doi: 10.1016/s0889-8588(01)00010-7. PMID: 12063829

Prognosis

Karam E, Hollenbach M, Abou Ali E, Auriemma F, Anderloni A, Barbier L, Belfiori G, Caillol F, Crippa S, Del Chiaro M, De Ponthaud C, Dahel Y, Falconi M, Giovannini M, Heling D, Inoue Y, Jarnagin WR, Leung G, Lupinacci RM, Mariani A, Masaryk V, Miksch RC, Musquer N, Napoleon B, Oba A, Partelli S, Petrone MC, Prat F, Repici A, Sauvanet A, Salzmann K, Schattner MA, Schulick R, Schwarz L, Soares K, Souche FR, Truant S, Vaillant JC, Wang T, Wedi E, Werner J, Weismüller TJ, Wichmann D, Will U, Zaccari P, Gulla A, Heise C, Regner S, Gaujoux S; Pancreas 2000 Research Group
Neuroendocrinology 2023;113(10):1024-1034. Epub 2023 Jun 27 doi: 10.1159/000531712. PMID: 37369186
Zhu J, Xiao W, Li Y
J Laparoendosc Adv Surg Tech A 2022 Jun;32(6):639-645. Epub 2021 Oct 11 doi: 10.1089/lap.2021.0482. PMID: 34637632
Saito Y, Muramatsu T, Kanai Y, Ojima H, Sukeda A, Hiraoka N, Arai E, Sugiyama Y, Matsuzaki J, Uchida R, Yoshikawa N, Furukawa R, Saito H
Cell Rep 2019 Apr 23;27(4):1265-1276.e4. doi: 10.1016/j.celrep.2019.03.088. PMID: 31018139
Uiterwaal MT, Mooi WJ, Van Weyenberg SJ
Dig Liver Dis 2011 Apr;43(4):e8. Epub 2010 Nov 9 doi: 10.1016/j.dld.2010.10.003. PMID: 21067982
Fukatsu H, Kawamoto H, Fujii M, Tsutsumi K, Kato H, Hirao K, Kurihara N, Okamoto Y, Ogawa T, Ishida E, Okada H, Sakaguchi K
Endoscopy 2007 Feb;39 Suppl 1:E49-50. Epub 2007 Feb 7 doi: 10.1055/s-2006-945068. PMID: 17285506

Clinical prediction guides

Komiyama S, Okusaka T, Maruki Y, Ohba A, Nagashio Y, Kondo S, Hijioka S, Morizane C, Ueno H, Sukeda A, Mizui T, Takamoto T, Nara S, Ban D, Esaki M, Hiraoka N, Shimada K
Intern Med 2024 Apr 1;63(7):891-901. Epub 2023 Aug 23 doi: 10.2169/internalmedicine.2016-23. PMID: 37612088Free PMC Article
Karam E, Hollenbach M, Abou Ali E, Auriemma F, Anderloni A, Barbier L, Belfiori G, Caillol F, Crippa S, Del Chiaro M, De Ponthaud C, Dahel Y, Falconi M, Giovannini M, Heling D, Inoue Y, Jarnagin WR, Leung G, Lupinacci RM, Mariani A, Masaryk V, Miksch RC, Musquer N, Napoleon B, Oba A, Partelli S, Petrone MC, Prat F, Repici A, Sauvanet A, Salzmann K, Schattner MA, Schulick R, Schwarz L, Soares K, Souche FR, Truant S, Vaillant JC, Wang T, Wedi E, Werner J, Weismüller TJ, Wichmann D, Will U, Zaccari P, Gulla A, Heise C, Regner S, Gaujoux S; Pancreas 2000 Research Group
Neuroendocrinology 2023;113(10):1024-1034. Epub 2023 Jun 27 doi: 10.1159/000531712. PMID: 37369186
Luchini C, Scarpa A
Hum Pathol 2023 Feb;132:176-182. Epub 2022 Jun 14 doi: 10.1016/j.humpath.2022.06.009. PMID: 35714836
Zheng BH, Zhang C, Wan WZ, Sun WT, Cheng X, Ni XJ, Ni XL, Suo T, Liu H, Shen S, Liu HB
BMC Surg 2022 Jun 29;22(1):253. doi: 10.1186/s12893-022-01689-7. PMID: 35768809Free PMC Article
Lee YH, Hsu MT, Tsai TJ
Gastroenterology 2012 Jan;142(1):e28-9. Epub 2011 Nov 19 doi: 10.1053/j.gastro.2011.01.067. PMID: 22107712

Recent systematic reviews

Saito K, Matsuo Y, Denda Y, Nonoyama K, Murase H, Kato T, Hayashi Y, Imafuji H, Morimoto M, Ogawa R, Takahashi H, Takiguchi S
J Med Case Rep 2023 Mar 28;17(1):127. doi: 10.1186/s13256-023-03828-x. PMID: 36973791Free PMC Article
Ziogas IA, Rallis KS, Tasoudis PT, Moris D, Schulick RD, Del Chiaro M
Eur J Surg Oncol 2023 Apr;49(4):682-687. Epub 2023 Jan 9 doi: 10.1016/j.ejso.2023.01.005. PMID: 36646615
Giannakodimos I, Giannakodimos A, Ziogou A, Frountzas M, Kritikos N, Vlachos K, Toutouzas KG, Schizas D
J Gastrointestin Liver Dis 2022 Dec 17;31(4):459-466. doi: 10.15403/jgld-4383. PMID: 36535044
Wen LJ, Chen JH, Xu HJ, Yu Q, Deng Y, Liu K
Medicine (Baltimore) 2020 Dec 11;99(50):e23271. doi: 10.1097/MD.0000000000023271. PMID: 33327249Free PMC Article

Supplemental Content

Table of contents

    Practice guidelines

    • PubMed
      See practice and clinical guidelines in PubMed. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.
    • Bookshelf
      See practice and clinical guidelines in NCBI Bookshelf. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.

    Recent activity

    Your browsing activity is empty.

    Activity recording is turned off.

    Turn recording back on

    See more...