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Small Intestinal T-Cell Non-Hodgkin Lymphoma

MedGen UID:
474154
•Concept ID:
C3272521
•
Neoplastic Process

Definition

A T-cell non-Hodgkin lymphoma that arises from the small intestine. It includes the enteropathy-associated T-cell lymphoma and the monomorphic CD56 positive intestinal T-cell lymphoma. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVSmall Intestinal T-Cell Non-Hodgkin Lymphoma

Professional guidelines

PubMed

Review of lymphoma in the duodenum: An update of diagnosis and management.
Iwamuro M, Tanaka T, Okada H
World J Gastroenterol 2023 Mar 28;29(12):1852-1862. doi: 10.3748/wjg.v29.i12.1852. PMID: 37032723Free PMC Article
AGA Clinical Practice Update on Management of Refractory Celiac Disease: Expert Review.
Green PHR, Paski S, Ko CW, Rubio-Tapia A
Gastroenterology 2022 Nov;163(5):1461-1469. Epub 2022 Sep 19 doi: 10.1053/j.gastro.2022.07.086. PMID: 36137844
Management of celiac disease in daily clinical practice.
Elli L, Ferretti F, Orlando S, Vecchi M, Monguzzi E, Roncoroni L, Schuppan D
Eur J Intern Med 2019 Mar;61:15-24. Epub 2018 Dec 5 doi: 10.1016/j.ejim.2018.11.012. PMID: 30528262

Recent clinical studies

Etiology

Celiac Disease Is a Risk Factor for Mature T and NK Cell Lymphoma: A Mendelian Randomization Study.
Martín-Masot R, Herrador-López M, Navas-López VM, Carmona FD, Nestares T, Bossini-Castillo L
Int J Mol Sci 2023 Apr 13;24(8) doi: 10.3390/ijms24087216. PMID: 37108375Free PMC Article
Gastrointestinal non-Hodgkin lymphomas.
Olszewska-Szopa M, Wróbel T
Adv Clin Exp Med 2019 Aug;28(8):1119-1124. doi: 10.17219/acem/94068. PMID: 31414733
Refractory Celiac Disease.
Malamut G, Cellier C
Gastroenterol Clin North Am 2019 Mar;48(1):137-144. Epub 2018 Dec 13 doi: 10.1016/j.gtc.2018.09.010. PMID: 30711206
Rare T-Cell Subtypes.
van der Weyden C, McCormack C, Lade S, Johnstone RW, Prince HM
Cancer Treat Res 2019;176:195-224. doi: 10.1007/978-3-319-99716-2_10. PMID: 30596220
Gamma-delta t-cell lymphomas.
Foppoli M, Ferreri AJ
Eur J Haematol 2015 Mar;94(3):206-18. Epub 2014 Oct 1 doi: 10.1111/ejh.12439. PMID: 25154298

Diagnosis

AGA Clinical Practice Update on Management of Refractory Celiac Disease: Expert Review.
Green PHR, Paski S, Ko CW, Rubio-Tapia A
Gastroenterology 2022 Nov;163(5):1461-1469. Epub 2022 Sep 19 doi: 10.1053/j.gastro.2022.07.086. PMID: 36137844
Gastrointestinal non-Hodgkin lymphomas.
Olszewska-Szopa M, Wróbel T
Adv Clin Exp Med 2019 Aug;28(8):1119-1124. doi: 10.17219/acem/94068. PMID: 31414733
Refractory Celiac Disease.
Malamut G, Cellier C
Gastroenterol Clin North Am 2019 Mar;48(1):137-144. Epub 2018 Dec 13 doi: 10.1016/j.gtc.2018.09.010. PMID: 30711206
Enteropathy-associated T-cell lymphoma.
Ferreri AJ, Zinzani PL, Govi S, Pileri SA
Crit Rev Oncol Hematol 2011 Jul;79(1):84-90. Epub 2010 Jul 23 doi: 10.1016/j.critrevonc.2010.06.006. PMID: 20655757
Celiac disease.
Green PH, Cellier C
N Engl J Med 2007 Oct 25;357(17):1731-43. doi: 10.1056/NEJMra071600. PMID: 17960014

Therapy

Celiac Disease Is a Risk Factor for Mature T and NK Cell Lymphoma: A Mendelian Randomization Study.
Martín-Masot R, Herrador-López M, Navas-López VM, Carmona FD, Nestares T, Bossini-Castillo L
Int J Mol Sci 2023 Apr 13;24(8) doi: 10.3390/ijms24087216. PMID: 37108375Free PMC Article
Refractory Celiac Disease.
Malamut G, Cellier C
Gastroenterol Clin North Am 2019 Mar;48(1):137-144. Epub 2018 Dec 13 doi: 10.1016/j.gtc.2018.09.010. PMID: 30711206
Refractory celiac disease.
Rishi AR, Rubio-Tapia A, Murray JA
Expert Rev Gastroenterol Hepatol 2016;10(4):537-46. Epub 2015 Dec 16 doi: 10.1586/17474124.2016.1124759. PMID: 26603931
Gamma-delta t-cell lymphomas.
Foppoli M, Ferreri AJ
Eur J Haematol 2015 Mar;94(3):206-18. Epub 2014 Oct 1 doi: 10.1111/ejh.12439. PMID: 25154298
Celiac disease.
Green PH, Cellier C
N Engl J Med 2007 Oct 25;357(17):1731-43. doi: 10.1056/NEJMra071600. PMID: 17960014

Prognosis

AGA Clinical Practice Update on Management of Refractory Celiac Disease: Expert Review.
Green PHR, Paski S, Ko CW, Rubio-Tapia A
Gastroenterology 2022 Nov;163(5):1461-1469. Epub 2022 Sep 19 doi: 10.1053/j.gastro.2022.07.086. PMID: 36137844
Refractory Celiac Disease.
Malamut G, Cellier C
Gastroenterol Clin North Am 2019 Mar;48(1):137-144. Epub 2018 Dec 13 doi: 10.1016/j.gtc.2018.09.010. PMID: 30711206
Refractory celiac disease.
Rishi AR, Rubio-Tapia A, Murray JA
Expert Rev Gastroenterol Hepatol 2016;10(4):537-46. Epub 2015 Dec 16 doi: 10.1586/17474124.2016.1124759. PMID: 26603931
Refractory celiac disease.
Malamut G, Murray JA, Cellier C
Gastrointest Endosc Clin N Am 2012 Oct;22(4):759-72. Epub 2012 Aug 24 doi: 10.1016/j.giec.2012.07.007. PMID: 23083992
Enteropathy-associated T-cell lymphoma.
Ferreri AJ, Zinzani PL, Govi S, Pileri SA
Crit Rev Oncol Hematol 2011 Jul;79(1):84-90. Epub 2010 Jul 23 doi: 10.1016/j.critrevonc.2010.06.006. PMID: 20655757

Clinical prediction guides

Celiac Disease Is a Risk Factor for Mature T and NK Cell Lymphoma: A Mendelian Randomization Study.
Martín-Masot R, Herrador-López M, Navas-López VM, Carmona FD, Nestares T, Bossini-Castillo L
Int J Mol Sci 2023 Apr 13;24(8) doi: 10.3390/ijms24087216. PMID: 37108375Free PMC Article
Single-Cell Analysis of Refractory Celiac Disease Demonstrates Inter- and Intra-Patient Aberrant Cell Heterogeneity.
Dieckman T, Schreurs M, Mahfouz A, Kooy-Winkelaar Y, Neefjes-Borst A, Bouma G, Koning F
Cell Mol Gastroenterol Hepatol 2022;14(1):173-192. Epub 2022 Mar 23 doi: 10.1016/j.jcmgh.2022.03.005. PMID: 35338007Free PMC Article
T-cell repertoires in refractory coeliac disease.
Ritter J, Zimmermann K, Jöhrens K, Mende S, Seegebarth A, Siegmund B, Hennig S, Todorova K, Rosenwald A, Daum S, Hummel M, Schumann M
Gut 2018 Apr;67(4):644-653. Epub 2017 Feb 10 doi: 10.1136/gutjnl-2016-311816. PMID: 28188172Free PMC Article
Refractory celiac disease.
Rishi AR, Rubio-Tapia A, Murray JA
Expert Rev Gastroenterol Hepatol 2016;10(4):537-46. Epub 2015 Dec 16 doi: 10.1586/17474124.2016.1124759. PMID: 26603931
Small bowel imaging in celiac disease.
Van Weyenberg SJB, Mulder CJJ, Van Waesberghe JHTM
Dig Dis 2015;33(2):252-259. Epub 2015 Apr 22 doi: 10.1159/000369516. PMID: 25925931

Recent systematic reviews

Pancreatic Cancer in Celiac Disease Patients-A Systematic Review and Meta-Analysis.
Gromny I, Neubauer K
Int J Environ Res Public Health 2023 Jan 14;20(2) doi: 10.3390/ijerph20021565. PMID: 36674320Free PMC Article
Composite EBV negative peripheral T-cell lymphoma and diffuse large B-cell lymphoma involving the ileum: a case report and a systematic review of the literature.
Abou-Elella AA, Nifong TP
Leuk Lymphoma 2006 Oct;47(10):2208-17. doi: 10.1080/10428190600763348. PMID: 17071497

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