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Congenital Vena Cava Abnormality

MedGen UID:
476118
Concept ID:
C3274485
Disease or Syndrome
Synonym: Congenital Abnormality of Vena Cava

Definition

An abnormality of the superior or inferior vena cava that is present at birth. Representative examples include persistent left superior vena cava, absence of infrarenal inferior vena cava, or absence of the entire inferior vena cava. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVCongenital Vena Cava Abnormality

Professional guidelines

PubMed

Durand I, Hazelzet T, Gillibert A, Parrod C, David N, El Youssef F, Brehin AC, Barre E
Arch Cardiovasc Dis 2022 Jun-Jul;115(6-7):335-347. Epub 2022 May 14 doi: 10.1016/j.acvd.2022.03.005. PMID: 35660361
Fick TA, Scott DA, Lupo PJ, Weigand J, Morris SA
Cardiol Young 2022 Apr;32(4):550-557. Epub 2021 Jul 2 doi: 10.1017/S1047951121002535. PMID: 34210367Free PMC Article
Keleş A, Yılmaz O, Dağdeviren G, Çelik ÖY, Yücel A, Şahin D
Fetal Pediatr Pathol 2022 Aug;41(4):592-602. Epub 2021 Jun 9 doi: 10.1080/15513815.2021.1933662. PMID: 34106033

Recent clinical studies

Etiology

Lopes KRM, Bartsota M, Doughty V, Carvalho JS
Ultrasound Obstet Gynecol 2022 Nov;60(5):640-645. doi: 10.1002/uog.24966. PMID: 35656845Free PMC Article
Chen SJ, Wu MH, Wang JK
J Formos Med Assoc 2022 Oct;121(10):1938-1944. Epub 2022 Feb 5 doi: 10.1016/j.jfma.2022.01.021. PMID: 35135704
Nigro B, Ayarragaray JEF
Ann Vasc Surg 2022 Feb;79:372-379. Epub 2021 Oct 10 doi: 10.1016/j.avsg.2021.07.029. PMID: 34644626
Shafi I, Hassan AAI, Akers KG, Bashir R, Alkhouli M, Weinberger JJ, Abidov A
Int J Cardiol 2020 Sep 15;315:29-35. Epub 2020 May 8 doi: 10.1016/j.ijcard.2020.05.017. PMID: 32434672
Syngelaki A, Hammami A, Bower S, Zidere V, Akolekar R, Nicolaides KH
Ultrasound Obstet Gynecol 2019 Oct;54(4):468-476. doi: 10.1002/uog.20844. PMID: 31408229

Diagnosis

Durand I, Hazelzet T, Gillibert A, Parrod C, David N, El Youssef F, Brehin AC, Barre E
Arch Cardiovasc Dis 2022 Jun-Jul;115(6-7):335-347. Epub 2022 May 14 doi: 10.1016/j.acvd.2022.03.005. PMID: 35660361
Lopes KRM, Bartsota M, Doughty V, Carvalho JS
Ultrasound Obstet Gynecol 2022 Nov;60(5):640-645. doi: 10.1002/uog.24966. PMID: 35656845Free PMC Article
Keleş A, Yılmaz O, Dağdeviren G, Çelik ÖY, Yücel A, Şahin D
Fetal Pediatr Pathol 2022 Aug;41(4):592-602. Epub 2021 Jun 9 doi: 10.1080/15513815.2021.1933662. PMID: 34106033
Kim SS, Shin HC, Hwang JA, Jou SS, Lee WH, Choi SY, Park CH
Abdom Radiol (NY) 2018 Aug;43(8):2130-2149. doi: 10.1007/s00261-017-1430-y. PMID: 29264715
Onbaş O, Kantarci M, Koplay M, Olgun H, Alper F, Aydinli B, Zirek H, Ceviz N
Diagn Interv Radiol 2008 Sep;14(3):163-71. PMID: 18814140

Therapy

Li WR, Feng H, Jin L, Chen XM, Zhang ZW
J Int Med Res 2022 May;50(5):3000605221100771. doi: 10.1177/03000605221100771. PMID: 35607249Free PMC Article
Kiblawi R, Zoeller C, Pirr S, Hofmann AD, Ure B, Dingemann J
Eur J Pediatr Surg 2022 Feb;32(1):91-97. Epub 2021 Dec 10 doi: 10.1055/s-0041-1740462. PMID: 34891190
Nigro B, Ayarragaray JEF
Ann Vasc Surg 2022 Feb;79:372-379. Epub 2021 Oct 10 doi: 10.1016/j.avsg.2021.07.029. PMID: 34644626
Alkhouli M, Morad M, Narins CR, Raza F, Bashir R
JACC Cardiovasc Interv 2016 Apr 11;9(7):629-43. Epub 2016 Mar 4 doi: 10.1016/j.jcin.2015.12.268. PMID: 26952909
Hallbergson A, Mascio CE, Rome JJ
Catheter Cardiovasc Interv 2015 Nov;86(5):849-54. Epub 2015 May 6 doi: 10.1002/ccd.25963. PMID: 25945427

Prognosis

Nigro B, Ayarragaray JEF
Ann Vasc Surg 2022 Feb;79:372-379. Epub 2021 Oct 10 doi: 10.1016/j.avsg.2021.07.029. PMID: 34644626
Chowdhury UK, Anderson RH, Sankhyan LK, George N, Pandey NN, Chauhan AS, Arora Y, Goja S
J Card Surg 2021 Oct;36(10):3770-3795. Epub 2021 Aug 16 doi: 10.1111/jocs.15857. PMID: 34396590
Minnella GP, Crupano FM, Syngelaki A, Zidere V, Akolekar R, Nicolaides KH
Ultrasound Obstet Gynecol 2020 May;55(5):637-644. doi: 10.1002/uog.21956. PMID: 31875326
Batouty NM, Sobh DM, Gadelhak B, Sobh HM, Mahmoud W, Tawfik AM
Radiol Med 2020 Mar;125(3):237-246. Epub 2019 Dec 10 doi: 10.1007/s11547-019-01114-9. PMID: 31823296
Midyat L, Demir E, Aşkin M, Gülen F, Ulger Z, Tanaç R, Bayraktaroğlu S
Eur J Pediatr 2010 Oct;169(10):1171-7. Epub 2010 Mar 12 doi: 10.1007/s00431-010-1152-4. PMID: 20225123

Clinical prediction guides

Kim H, Labropoulos N, Blake AM, Desai K
Eur J Vasc Endovasc Surg 2022 Oct;64(4):388-394. Epub 2022 Jun 6 doi: 10.1016/j.ejvs.2022.05.045. PMID: 35671937
Esin D, Aslan Çetin B, Şenol G, Selçuki NFT, Gedik Özköse Z, Acar Z, Yüksel MA
J Gynecol Obstet Hum Reprod 2022 Apr;51(4):102332. Epub 2022 Feb 2 doi: 10.1016/j.jogoh.2022.102332. PMID: 35123124
Nigro B, Ayarragaray JEF
Ann Vasc Surg 2022 Feb;79:372-379. Epub 2021 Oct 10 doi: 10.1016/j.avsg.2021.07.029. PMID: 34644626
Minnella GP, Crupano FM, Syngelaki A, Zidere V, Akolekar R, Nicolaides KH
Ultrasound Obstet Gynecol 2020 May;55(5):637-644. doi: 10.1002/uog.21956. PMID: 31875326
Nossair F, Schoettler P, Starr J, Chan AKC, Kirov I, Paes B, Mahajerin A
Pediatr Blood Cancer 2018 Sep;65(9):e27225. Epub 2018 May 21 doi: 10.1002/pbc.27225. PMID: 29781569

Recent systematic reviews

Al-Sinan A, Chan KH, Young GD, Martin A, Sepahpour A, Sy RW
J Cardiovasc Electrophysiol 2022 Jun;33(6):1300-1311. Epub 2022 Apr 30 doi: 10.1111/jce.15505. PMID: 35441755Free PMC Article
Shafi I, Hassan AAI, Akers KG, Bashir R, Alkhouli M, Weinberger JJ, Abidov A
Int J Cardiol 2020 Sep 15;315:29-35. Epub 2020 May 8 doi: 10.1016/j.ijcard.2020.05.017. PMID: 32434672
Hostiuc S, Minoiu C, Negoi I, Rusu MC, Hostiuc M
J Vasc Surg Venous Lymphat Disord 2019 Sep;7(5):742-755. Epub 2019 May 5 doi: 10.1016/j.jvsv.2019.01.063. PMID: 31068277
Nossair F, Schoettler P, Starr J, Chan AKC, Kirov I, Paes B, Mahajerin A
Pediatr Blood Cancer 2018 Sep;65(9):e27225. Epub 2018 May 21 doi: 10.1002/pbc.27225. PMID: 29781569
Gustapane S, Leombroni M, Khalil A, Giacci F, Marrone L, Bascietto F, Rizzo G, Acharya G, Liberati M, D'Antonio F
Ultrasound Obstet Gynecol 2016 Dec;48(6):701-708. Epub 2016 Nov 1 doi: 10.1002/uog.15914. PMID: 26970258

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