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Restrictive ventricular septal defect

MedGen UID:
488872
Concept ID:
C0344924
Congenital Abnormality
SNOMED CT: Restrictive ventricular septal defect (253551005)
 
HPO: HP:0011683

Definition

Any ventricular septal defect (VSD) that is small enough to restrict flow across it such that a pressure gradient exists between the two sides of the VSD. [from HPO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVRestrictive ventricular septal defect

Professional guidelines

PubMed

Däbritz S, Engelhardt W, von Bernuth G, Messmer BJ
Eur J Cardiothorac Surg 1997 Jan;11(1):112-6. doi: 10.1016/s1010-7940(96)01065-2. PMID: 9030798
van den Heuvel F, Timmers T, Hess J
Br Heart J 1995 Jan;73(1):49-52. doi: 10.1136/hrt.73.1.49. PMID: 7888261Free PMC Article
Rothman A, Lang P, Lock JE, Jonas RA, Mayer JE, Castaneda AR
J Am Coll Cardiol 1987 Aug;10(2):421-6. doi: 10.1016/s0735-1097(87)80027-x. PMID: 3598012

Recent clinical studies

Etiology

Xu LP, Lin SH, Zhang QL, Zheng Y, Lin G
Heart Surg Forum 2022 Oct 31;25(5):E745-E749. doi: 10.1532/hsf.5009. PMID: 36317897
Zhang QL, Xu N, Huang ST, Lin ZW, Cao H, Chen Q
Psychol Health Med 2022 Apr;27(4):948-955. Epub 2021 Oct 15 doi: 10.1080/13548506.2021.1990360. PMID: 34651528
Chen Q, Wu WX, Huang JS, Chen LW, Fang GH
J Invest Surg 2021 Apr;34(4):467-472. Epub 2019 Aug 1 doi: 10.1080/08941939.2019.1645247. PMID: 31366250
Huang ST, Xu N, Sun KP, Chen LW, Cao H, Chen Q
Pediatr Cardiol 2020 Oct;41(7):1334-1339. Epub 2020 May 28 doi: 10.1007/s00246-020-02387-y. PMID: 32468125
Backer CL, Winters RC, Zales VR, Takami H, Muster AJ, Benson DW Jr, Mavroudis C
Ann Thorac Surg 1993 Nov;56(5):1014-8; discussion 1018-9. doi: 10.1016/0003-4975(95)90006-3. PMID: 8239793

Diagnosis

Savaş G, Yazıcı S, Kılıç Ö, Terzi S
Turk Kardiyol Dern Ars 2022 Jan;50(1):70-78. doi: 10.5543/tkda.2022.21093. PMID: 35197236
El-Asmar JM, Degheili JA, Al-Halabi E, Sklansky M
Pediatr Cardiol 2019 Jan;40(1):234-236. Epub 2018 Dec 19 doi: 10.1007/s00246-018-2048-8. PMID: 30569250
Reshmi LJ, Gadhinglajkar S, Mathew T, Venkateshwaran S, Sreedhar R, Dharan B
Asian Cardiovasc Thorac Ann 2016 Feb;24(2):190-4. Epub 2014 Oct 6 doi: 10.1177/0218492314553995. PMID: 25293418
Le Gloan L, Leduc L, O'Meara E, Khairy P, Dore A
Congenit Heart Dis 2011 Nov-Dec;6(6):638-40. Epub 2011 May 5 doi: 10.1111/j.1747-0803.2011.00519.x. PMID: 21545467
van den Heuvel F, Timmers T, Hess J
Br Heart J 1995 Jan;73(1):49-52. doi: 10.1136/hrt.73.1.49. PMID: 7888261Free PMC Article

Therapy

Xu LP, Lin SH, Zhang QL, Zheng Y, Lin G
Heart Surg Forum 2022 Oct 31;25(5):E745-E749. doi: 10.1532/hsf.5009. PMID: 36317897
Zhang QL, Xu N, Huang ST, Lin ZW, Cao H, Chen Q
Psychol Health Med 2022 Apr;27(4):948-955. Epub 2021 Oct 15 doi: 10.1080/13548506.2021.1990360. PMID: 34651528
Chen Q, Wu WX, Huang JS, Chen LW, Fang GH
J Invest Surg 2021 Apr;34(4):467-472. Epub 2019 Aug 1 doi: 10.1080/08941939.2019.1645247. PMID: 31366250
Patel R, Thingnam SKS, Mishra AK, Rohit MK, Upadhyay V, Halder V, Bansal V
J Card Surg 2020 Dec;35(12):3302-3309. Epub 2020 Sep 16 doi: 10.1111/jocs.15030. PMID: 32939849
Huang ST, Xu N, Sun KP, Chen LW, Cao H, Chen Q
Pediatr Cardiol 2020 Oct;41(7):1334-1339. Epub 2020 May 28 doi: 10.1007/s00246-020-02387-y. PMID: 32468125

Prognosis

Zhang QL, Xu N, Huang ST, Chen Q, Cao H
Heart Surg Forum 2020 Dec 2;23(6):E897-E901. doi: 10.1532/hsf.3323. PMID: 33399530
Le Gloan L, Leduc L, O'Meara E, Khairy P, Dore A
Congenit Heart Dis 2011 Nov-Dec;6(6):638-40. Epub 2011 May 5 doi: 10.1111/j.1747-0803.2011.00519.x. PMID: 21545467
Anderson RH, Ho SY
Ann Thorac Surg 1998 Aug;66(2):644-8. doi: 10.1016/s0003-4975(98)00576-1. PMID: 9725445
Metras D, Kreitmann B, Riberi A, Yao JG, el-Khoury E, Wernert F, Pannetier-Mille A
J Thorac Cardiovasc Surg 1997 Nov;114(5):746-53; discussion 753-4. doi: 10.1016/S0022-5223(97)70078-3. PMID: 9375604
van den Heuvel F, Timmers T, Hess J
Br Heart J 1995 Jan;73(1):49-52. doi: 10.1136/hrt.73.1.49. PMID: 7888261Free PMC Article

Clinical prediction guides

Xu LP, Lin SH, Zhang QL, Zheng Y, Lin G
Heart Surg Forum 2022 Oct 31;25(5):E745-E749. doi: 10.1532/hsf.5009. PMID: 36317897
Mumtaz ZA, Sagar P, Rajendran M, Sivakumar K
Pediatr Cardiol 2022 Oct;43(7):1494-1501. Epub 2022 Apr 5 doi: 10.1007/s00246-022-02873-5. PMID: 35380217
Zhang QL, Xu N, Huang ST, Lin ZW, Cao H, Chen Q
Psychol Health Med 2022 Apr;27(4):948-955. Epub 2021 Oct 15 doi: 10.1080/13548506.2021.1990360. PMID: 34651528
Zhang QL, Xu N, Huang ST, Chen Q, Cao H
Heart Surg Forum 2020 Dec 2;23(6):E897-E901. doi: 10.1532/hsf.3323. PMID: 33399530
van den Heuvel F, Timmers T, Hess J
Br Heart J 1995 Jan;73(1):49-52. doi: 10.1136/hrt.73.1.49. PMID: 7888261Free PMC Article

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