Interrupted aortic arch type C

MedGen UID:: 488876
•Concept ID:: C0345094
•: Congenital Abnormality

Synonyms:	Interrupted aortic arch between left common carotid and brachiocephalic artery; Type C interrupted aortic arch
SNOMED CT:	Interrupted aortic arch between left common carotid and brachiocephalic artery (253683008); Type C interrupted aortic arch (253683008)

HPO:	HP:0011614

Definition

Non-continuity of the aortic arch with an atretic point or absent segment between the innominate and left carotid arteries. [from HPO]

Term Hierarchy

GTR
MeSH

CClinical test, RResearch test, OOMIM, GGeneReviews, VClinVar

CROGVInterrupted aortic arch type C

Abnormal vascular morphology
- Abnormal blood vessel morphology
  - Abnormal morphology of the great vessels
    - Abnormal aortic morphology
      - Abnormal aortic arch morphology
        Aortic arch interruption
        Interrupted aortic arch type C

Professional guidelines

PubMed

The interrupted aortic arch: an overview after 20 years of surgical treatment.

Schreiber C, Mazzitelli D, Haehnel JC, Lorenz HP, Meisner H
Eur J Cardiothorac Surg 1997 Sep;12(3):466-9; discussion 469-70. doi: 10.1016/s1010-7940(97)00194-2. PMID: 9332928

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Recent clinical studies

Etiology

Biventricular Repair in Interrupted Aortic Arch Type C With Aortic Atresia.

Malankar DP, Glatz AC, Weinberg PM, Gaynor JW
World J Pediatr Congenit Heart Surg 2019 Mar;10(2):228-230. Epub 2017 Jul 26 doi: 10.1177/2150135117715211. PMID: 28743203

A rare form of interrupted aortic arch.

Agnoletti G, Borghi A, Annecchino F
Ital Heart J 2001 Mar;2(3):228-30. PMID: 11305535

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