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Renal vasculitis

MedGen UID:
508849
Concept ID:
C0152002
Disease or Syndrome
SNOMED CT: Renal vasculitis (95578000)
 
HPO: HP:6000076

Definition

Vasculitis (inflammation of blood vessels) in the kidney. Renal vasculitis can be observed with numerous disorders and presents clinically as rapidly progressive glomerulonephritis (RPGN) which is characterized by acute kidney injury (AKI), haematuria and proteinuria. Histological examination of the kidney reveals severe inflammation in the form of crescent formation, glomerular necrosis and vasculitis of small and medium sized vessels within the kidney. [from HPO]

Professional guidelines

PubMed

Turkmen K, Ozer H, Tesar V
Int Urol Nephrol 2023 Nov;55(11):2817-2827. Epub 2023 Apr 3 doi: 10.1007/s11255-023-03565-6. PMID: 37010734
Dhaun N, Bellamy CO, Cattran DC, Kluth DC
Kidney Int 2014 May;85(5):1039-48. Epub 2014 Jan 8 doi: 10.1038/ki.2013.512. PMID: 24402095
Altieri P, Sau G, Cao R, Barracca A, Menneas A, Micchittu B, Cabiddu G, Esposito P, Pani A
Nephrol Dial Transplant 2002;17 Suppl 8:2-9. doi: 10.1093/ndt/17.suppl_8.2. PMID: 12147770

Recent clinical studies

Etiology

Geetha D, Dua A, Yue H, Springer J, Salvarani C, Jayne D, Merkel P; ADVOCATE Study Group
Ann Rheum Dis 2024 Jan 11;83(2):223-232. doi: 10.1136/ard-2023-224816. PMID: 37979959Free PMC Article
Hatemi G, Esatoglu SN, Yazici Y
Curr Opin Rheumatol 2018 Jan;30(1):30-35. doi: 10.1097/BOR.0000000000000447. PMID: 28937415
Jones RB, Furuta S, Tervaert JW, Hauser T, Luqmani R, Morgan MD, Peh CA, Savage CO, Segelmark M, Tesar V, van Paassen P, Walsh M, Westman K, Jayne DR; European Vasculitis Society (EUVAS)
Ann Rheum Dis 2015 Jun;74(6):1178-82. Epub 2015 Mar 4 doi: 10.1136/annrheumdis-2014-206404. PMID: 25739829
Jones RB, Tervaert JW, Hauser T, Luqmani R, Morgan MD, Peh CA, Savage CO, Segelmark M, Tesar V, van Paassen P, Walsh D, Walsh M, Westman K, Jayne DR; European Vasculitis Study Group
N Engl J Med 2010 Jul 15;363(3):211-20. doi: 10.1056/NEJMoa0909169. PMID: 20647198
Jayne DR, Gaskin G, Rasmussen N, Abramowicz D, Ferrario F, Guillevin L, Mirapeix E, Savage CO, Sinico RA, Stegeman CA, Westman KW, van der Woude FJ, de Lind van Wijngaarden RA, Pusey CD; European Vasculitis Study Group
J Am Soc Nephrol 2007 Jul;18(7):2180-8. Epub 2007 Jun 20 doi: 10.1681/ASN.2007010090. PMID: 17582159

Diagnosis

Geetha D, Dua A, Yue H, Springer J, Salvarani C, Jayne D, Merkel P; ADVOCATE Study Group
Ann Rheum Dis 2024 Jan 11;83(2):223-232. doi: 10.1136/ard-2023-224816. PMID: 37979959Free PMC Article
Turkmen K, Ozer H, Tesar V
Int Urol Nephrol 2023 Nov;55(11):2817-2827. Epub 2023 Apr 3 doi: 10.1007/s11255-023-03565-6. PMID: 37010734
Jones RB, Furuta S, Tervaert JW, Hauser T, Luqmani R, Morgan MD, Peh CA, Savage CO, Segelmark M, Tesar V, van Paassen P, Walsh M, Westman K, Jayne DR; European Vasculitis Society (EUVAS)
Ann Rheum Dis 2015 Jun;74(6):1178-82. Epub 2015 Mar 4 doi: 10.1136/annrheumdis-2014-206404. PMID: 25739829
Jones RB, Tervaert JW, Hauser T, Luqmani R, Morgan MD, Peh CA, Savage CO, Segelmark M, Tesar V, van Paassen P, Walsh D, Walsh M, Westman K, Jayne DR; European Vasculitis Study Group
N Engl J Med 2010 Jul 15;363(3):211-20. doi: 10.1056/NEJMoa0909169. PMID: 20647198
Jayne DR, Gaskin G, Rasmussen N, Abramowicz D, Ferrario F, Guillevin L, Mirapeix E, Savage CO, Sinico RA, Stegeman CA, Westman KW, van der Woude FJ, de Lind van Wijngaarden RA, Pusey CD; European Vasculitis Study Group
J Am Soc Nephrol 2007 Jul;18(7):2180-8. Epub 2007 Jun 20 doi: 10.1681/ASN.2007010090. PMID: 17582159

Therapy

Turkmen K, Ozer H, Tesar V
Int Urol Nephrol 2023 Nov;55(11):2817-2827. Epub 2023 Apr 3 doi: 10.1007/s11255-023-03565-6. PMID: 37010734
Hatemi G, Esatoglu SN, Yazici Y
Curr Opin Rheumatol 2018 Jan;30(1):30-35. doi: 10.1097/BOR.0000000000000447. PMID: 28937415
Jones RB, Furuta S, Tervaert JW, Hauser T, Luqmani R, Morgan MD, Peh CA, Savage CO, Segelmark M, Tesar V, van Paassen P, Walsh M, Westman K, Jayne DR; European Vasculitis Society (EUVAS)
Ann Rheum Dis 2015 Jun;74(6):1178-82. Epub 2015 Mar 4 doi: 10.1136/annrheumdis-2014-206404. PMID: 25739829
Jones RB, Tervaert JW, Hauser T, Luqmani R, Morgan MD, Peh CA, Savage CO, Segelmark M, Tesar V, van Paassen P, Walsh D, Walsh M, Westman K, Jayne DR; European Vasculitis Study Group
N Engl J Med 2010 Jul 15;363(3):211-20. doi: 10.1056/NEJMoa0909169. PMID: 20647198
Jayne DR, Gaskin G, Rasmussen N, Abramowicz D, Ferrario F, Guillevin L, Mirapeix E, Savage CO, Sinico RA, Stegeman CA, Westman KW, van der Woude FJ, de Lind van Wijngaarden RA, Pusey CD; European Vasculitis Study Group
J Am Soc Nephrol 2007 Jul;18(7):2180-8. Epub 2007 Jun 20 doi: 10.1681/ASN.2007010090. PMID: 17582159

Prognosis

Turkmen K, Ozer H, Tesar V
Int Urol Nephrol 2023 Nov;55(11):2817-2827. Epub 2023 Apr 3 doi: 10.1007/s11255-023-03565-6. PMID: 37010734
Grewal MK, Adams MD, Valentini RP
Pediatr Clin North Am 2022 Dec;69(6):1199-1217. Epub 2022 Oct 29 doi: 10.1016/j.pcl.2022.07.009. PMID: 36880930
Corthier A, Jachiet M, Bertin D, Servais A, Barbet C, Bigot A, Doutre MS, Bessis D, Bouffandeau A, Moranne O, Jarrot PA, Bardin N, Terrier B, Burtey S, Puéchal X, Daniel L, Jourde-Chiche N
BMC Nephrol 2022 Feb 16;23(1):67. doi: 10.1186/s12882-022-02689-8. PMID: 35172758Free PMC Article
Hatemi G, Esatoglu SN, Yazici Y
Curr Opin Rheumatol 2018 Jan;30(1):30-35. doi: 10.1097/BOR.0000000000000447. PMID: 28937415
Jones RB, Tervaert JW, Hauser T, Luqmani R, Morgan MD, Peh CA, Savage CO, Segelmark M, Tesar V, van Paassen P, Walsh D, Walsh M, Westman K, Jayne DR; European Vasculitis Study Group
N Engl J Med 2010 Jul 15;363(3):211-20. doi: 10.1056/NEJMoa0909169. PMID: 20647198

Clinical prediction guides

Corthier A, Jachiet M, Bertin D, Servais A, Barbet C, Bigot A, Doutre MS, Bessis D, Bouffandeau A, Moranne O, Jarrot PA, Bardin N, Terrier B, Burtey S, Puéchal X, Daniel L, Jourde-Chiche N
BMC Nephrol 2022 Feb 16;23(1):67. doi: 10.1186/s12882-022-02689-8. PMID: 35172758Free PMC Article
Aiyegbusi O, Frleta-Gilchrist M, Traynor JP, Mackinnon B, Bell S, Hunter RW, Dhaun N, Kidder D, Stewart G, Joss N, Kelly M, Shah S, Dey V, Buck K, Stevens KI, Geddes CC, McQuarrie EP; Scottish Renal Biopsy Registry
RMD Open 2021 Apr;7(2) doi: 10.1136/rmdopen-2020-001555. PMID: 33875562Free PMC Article
Hatemi G, Esatoglu SN, Yazici Y
Curr Opin Rheumatol 2018 Jan;30(1):30-35. doi: 10.1097/BOR.0000000000000447. PMID: 28937415
Brogan P, Eleftheriou D
Pediatr Nephrol 2018 Feb;33(2):187-198. Epub 2017 Aug 7 doi: 10.1007/s00467-017-3597-4. PMID: 28785984Free PMC Article
Mejía-Vilet JM, Córdova-Sánchez BM, Uribe-Uribe NO, Correa-Rotter R, Morales-Buenrostro LE
Lupus 2017 Sep;26(10):1042-1050. Epub 2017 Feb 8 doi: 10.1177/0961203317692419. PMID: 28178879

Recent systematic reviews

Corthier A, Jachiet M, Bertin D, Servais A, Barbet C, Bigot A, Doutre MS, Bessis D, Bouffandeau A, Moranne O, Jarrot PA, Bardin N, Terrier B, Burtey S, Puéchal X, Daniel L, Jourde-Chiche N
BMC Nephrol 2022 Feb 16;23(1):67. doi: 10.1186/s12882-022-02689-8. PMID: 35172758Free PMC Article
Walters G
Pediatr Nephrol 2016 Feb;31(2):217-25. Epub 2015 May 19 doi: 10.1007/s00467-014-3038-6. PMID: 25986911
Walters G, Willis NS, Craig JC
Cochrane Database Syst Rev 2015 Sep 24;(9):CD003232. doi: 10.1002/14651858.CD003232.pub3. PMID: 26400765
Walsh M, Catapano F, Szpirt W, Thorlund K, Bruchfeld A, Guillevin L, Haubitz M, Merkel PA, Peh CA, Pusey C, Jayne D
Am J Kidney Dis 2011 Apr;57(4):566-74. Epub 2010 Dec 30 doi: 10.1053/j.ajkd.2010.10.049. PMID: 21194817Free PMC Article
Walters GD, Willis NS, Craig JC
BMC Nephrol 2010 Jun 24;11:12. doi: 10.1186/1471-2369-11-12. PMID: 20573267Free PMC Article

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