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Bilateral basilar pulmonary fibrosis

MedGen UID:
573414
•Concept ID:
C0339904
•
Disease or Syndrome
Synonyms: Lung disease with systemic sclerosis; lung disease with systemic sclerosis; lung involvement in systemic sclerosis; pulmonary systemic sclerosis; Scleroderma lung disease; scleroderma lung disease; Scleroderma of lung; scleroderma of lung; Systemic Sclerosis with Lung Involvement
SNOMED CT: Scleroderma lung disease (196133001); Scleroderma of lung (196133001); Lung disease with systemic sclerosis (196133001)
 
HPO: HP:0550005
Monarch Initiative: MONDO:0002047

Definition

It is a bilateral reticular pattern of linear or lineonodular densities that are most pronounced in basilar portions of the lungs on standard chest x-ray. It is the third minor criterion for scleroderma diagnosis. [from HPO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVBilateral basilar pulmonary fibrosis

Recent clinical studies

Etiology

Lung fibrosis and exposure to wood dusts: Two case reports and review of the literature.
Riccò M
Med Pr 2015;66(5):739-47. doi: 10.13075/mp.5893.00140. PMID: 26647991
Idiopathic pulmonary fibrosis, clinical features in Thai patients.
Palwatwichai A, Tiyanon W, Chaoprasong C, Vattanathum A, Tantamacharik D
J Med Assoc Thai 2000 Oct;83(10):1248-52. PMID: 11143492
Preliminary criteria for the classification of systemic sclerosis (scleroderma). Subcommittee for scleroderma criteria of the American Rheumatism Association Diagnostic and Therapeutic Criteria Committee.
Arthritis Rheum 1980 May;23(5):581-90. doi: 10.1002/art.1780230510. PMID: 7378088

Diagnosis

A case report of acute fibrinous and organizing pneumonia.
Wang K, Du X, Wu Q, Cheng D
Medicine (Baltimore) 2019 Dec;98(49):e18140. doi: 10.1097/MD.0000000000018140. PMID: 31804325Free PMC Article
Lung fibrosis and exposure to wood dusts: Two case reports and review of the literature.
Riccò M
Med Pr 2015;66(5):739-47. doi: 10.13075/mp.5893.00140. PMID: 26647991
Acute fibrinous and organizing pneumonia masquerading as a lower respiratory tract infection: a case report and review of the literature.
Akhtar A, Ul Abideen Z
BMC Res Notes 2015 Feb 10;8:38. doi: 10.1186/s13104-015-0984-4. PMID: 25890084Free PMC Article
Idiopathic pulmonary fibrosis, clinical features in Thai patients.
Palwatwichai A, Tiyanon W, Chaoprasong C, Vattanathum A, Tantamacharik D
J Med Assoc Thai 2000 Oct;83(10):1248-52. PMID: 11143492
Preliminary criteria for the classification of systemic sclerosis (scleroderma). Subcommittee for scleroderma criteria of the American Rheumatism Association Diagnostic and Therapeutic Criteria Committee.
Arthritis Rheum 1980 May;23(5):581-90. doi: 10.1002/art.1780230510. PMID: 7378088

Therapy

A case report of acute fibrinous and organizing pneumonia.
Wang K, Du X, Wu Q, Cheng D
Medicine (Baltimore) 2019 Dec;98(49):e18140. doi: 10.1097/MD.0000000000018140. PMID: 31804325Free PMC Article
Lung fibrosis and exposure to wood dusts: Two case reports and review of the literature.
Riccò M
Med Pr 2015;66(5):739-47. doi: 10.13075/mp.5893.00140. PMID: 26647991
Acute fibrinous and organizing pneumonia masquerading as a lower respiratory tract infection: a case report and review of the literature.
Akhtar A, Ul Abideen Z
BMC Res Notes 2015 Feb 10;8:38. doi: 10.1186/s13104-015-0984-4. PMID: 25890084Free PMC Article

Prognosis

A case report of acute fibrinous and organizing pneumonia.
Wang K, Du X, Wu Q, Cheng D
Medicine (Baltimore) 2019 Dec;98(49):e18140. doi: 10.1097/MD.0000000000018140. PMID: 31804325Free PMC Article
Lung fibrosis and exposure to wood dusts: Two case reports and review of the literature.
Riccò M
Med Pr 2015;66(5):739-47. doi: 10.13075/mp.5893.00140. PMID: 26647991
Idiopathic pulmonary fibrosis, clinical features in Thai patients.
Palwatwichai A, Tiyanon W, Chaoprasong C, Vattanathum A, Tantamacharik D
J Med Assoc Thai 2000 Oct;83(10):1248-52. PMID: 11143492
Preliminary criteria for the classification of systemic sclerosis (scleroderma). Subcommittee for scleroderma criteria of the American Rheumatism Association Diagnostic and Therapeutic Criteria Committee.
Arthritis Rheum 1980 May;23(5):581-90. doi: 10.1002/art.1780230510. PMID: 7378088

Clinical prediction guides

Lung fibrosis and exposure to wood dusts: Two case reports and review of the literature.
Riccò M
Med Pr 2015;66(5):739-47. doi: 10.13075/mp.5893.00140. PMID: 26647991

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