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Congenital coronary artery aneurysm

MedGen UID:
573848
•Concept ID:
C0340627
•
Congenital Abnormality
Synonyms: Congenital coronary aneurysm; congenital coronary aneurysm; congenital coronary artery aneurysm
SNOMED CT: Congenital coronary aneurysm (204378009)
 
Monarch Initiative: MONDO:0019825
Orphanet: ORPHA95491

Definition

Congenital coronary artery aneurysm is a rare congenital coronary artery malformation defined as a more than 1.5 fold the normal size dilatation of a coronary artery segment with no identified underlying inflammatory or connective tissue disease. It may be asymptomatic or may present with angina pectoris, myocardial infarction, sudden cardiac death, fistula formation, pericardial tamponade, compression of surrounding structures, or congestive heart failure. [from ORDO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVCongenital coronary artery aneurysm

Professional guidelines

PubMed

Etiology, clinical presentation, and management of left main coronary artery aneurysms.
Negro F, Gentile F, Rizza A, Giannoni A, Bianchi G, Clemente A, Emdin M, Palmieri C
J Card Surg 2022 Nov;37(11):3675-3686. Epub 2022 Aug 21 doi: 10.1111/jocs.16870. PMID: 35989523
European consensus on the diagnosis and management of fibromuscular dysplasia.
Persu A, Giavarini A, Touzé E, Januszewicz A, Sapoval M, Azizi M, Barral X, Jeunemaitre X, Morganti A, Plouin PF, de Leeuw P; ESH Working Group Hypertension and the Kidney
J Hypertens 2014 Jul;32(7):1367-78. doi: 10.1097/HJH.0000000000000213. PMID: 24842696
Coronary artery aneurysms: a review of the natural history, pathophysiology, and management.
Cohen P, O'Gara PT
Cardiol Rev 2008 Nov-Dec;16(6):301-4. doi: 10.1097/CRD.0b013e3181852659. PMID: 18923233

Recent clinical studies

Diagnosis

MRI of congenital coronary artery aneurysm.
Meinert D, Mohammed Z
Br J Radiol 2000 Mar;73(867):322-4. doi: 10.1259/bjr.73.867.10817051. PMID: 10817051
Repair of an aneurysm of the left main coronary artery.
Lepojärvi M, Salmela E, Huikuri H, Kärkölä P
Ann Thorac Surg 1996 Apr;61(4):1247-9. doi: 10.1016/0003-4975(95)01037-8. PMID: 8607696
Asymptomatic congenital coronary artery aneurysm in adulthood.
Wong CK, Cheng CH, Lau CP, Leung WH
Eur Heart J 1989 Oct;10(10):947-9. doi: 10.1093/oxfordjournals.eurheartj.a059407. PMID: 2598952

Therapy

Giant congenital coronary artery aneurysm in pulmonary atresia with intact septum.
Park RE, Occleshaw CJ, Finucane AK, Hornung TS
Heart Lung Circ 2009 Aug;18(4):310-2. Epub 2008 Apr 8 doi: 10.1016/j.hlc.2008.01.002. PMID: 18396460

Prognosis

Giant congenital coronary artery aneurysm in pulmonary atresia with intact septum.
Park RE, Occleshaw CJ, Finucane AK, Hornung TS
Heart Lung Circ 2009 Aug;18(4):310-2. Epub 2008 Apr 8 doi: 10.1016/j.hlc.2008.01.002. PMID: 18396460

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