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Rheumatic chorea

MedGen UID:
57506
Concept ID:
C0152113
Disease or Syndrome
Synonyms: Chorea, Rheumatic; Chorea, Sydenham; Chorea, Sydenham's; Choreas, Rheumatic; Choreas, Sydenham; Rheumatic Chorea; Rheumatic Choreas; St. Vitus Dance; St. Vitus's Dance; St. Vitus's Dances; St. Vituss Dance; Sydenham Chorea; Sydenham Choreas; Sydenham's Chorea; Sydenhams Chorea
SNOMED CT: Rheumatic chorea (46826000); Sydenham's chorea (46826000)

Definition

A neurologic disorder characterized by smooth involuntary, uncoordinated movements affecting especially the hands, feet, and face. (ACC-AHA) [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVRheumatic chorea

Professional guidelines

PubMed

Araujo AP, Padua PA, Maia Filho HS
Arq Neuropsiquiatr 2002 Jun;60(2-A):231-3. PMID: 12068350
Harel L, Zecharia A, Straussberg R, Volovitz B, Amir J
Pediatr Neurol 2000 Aug;23(2):147-51. doi: 10.1016/s0887-8994(00)00177-6. PMID: 11020640
EL-GHOLMI A, ABOUL-DAHAB YW
Arch Pediatr (N Y) 1961 Dec;78:478-82. PMID: 13891166

Recent clinical studies

Etiology

Teixeira AL, Vasconcelos LP, Nunes MDCP, Singer H
Expert Rev Neurother 2021 Aug;21(8):913-922. Epub 2021 Aug 18 doi: 10.1080/14737175.2021.1965883. PMID: 34353207
Walker AR, Tani LY, Thompson JA, Firth SD, Veasy LG, Bale JF Jr
J Pediatr 2007 Dec;151(6):679-83. Epub 2007 Aug 24 doi: 10.1016/j.jpeds.2007.04.059. PMID: 18035153
Harel L, Zecharia A, Straussberg R, Volovitz B, Amir J
Pediatr Neurol 2000 Aug;23(2):147-51. doi: 10.1016/s0887-8994(00)00177-6. PMID: 11020640
Carapetis JR, Currie BJ
Arch Dis Child 1999 Apr;80(4):353-8. doi: 10.1136/adc.80.4.353. PMID: 10086943Free PMC Article
Abbas S, Khanna S, Taly AB
Psychopathology 1996;29(3):193-7. doi: 10.1159/000284991. PMID: 8817740

Diagnosis

Santos-Silva R, Corujeira S, Almeida AF, Granja S, Moura C, Azevedo I, Leão M, Maia A
Sao Paulo Med J 2011;129(4):267-70. doi: 10.1590/s1516-31802011000400011. PMID: 21971903
de Oliveira SK
J Pediatr (Rio J) 2007 May-Jun;83(3):201-8. Epub 2007 May 4 doi: 10.2223/JPED.1615. PMID: 17486197
World Health Organ Tech Rep Ser 2004;923:1-122, back cover. PMID: 15382606
Carapetis JR, Currie BJ
Arch Dis Child 1999 Apr;80(4):353-8. doi: 10.1136/adc.80.4.353. PMID: 10086943Free PMC Article
Kandil MR, Tohamy SA, Fattah MA, Ahmed HN, Farwiez HM
Neuroepidemiology 1994;13(5):202-10. doi: 10.1159/000110380. PMID: 7969703

Therapy

Walker AR, Tani LY, Thompson JA, Firth SD, Veasy LG, Bale JF Jr
J Pediatr 2007 Dec;151(6):679-83. Epub 2007 Aug 24 doi: 10.1016/j.jpeds.2007.04.059. PMID: 18035153
World Health Organ Tech Rep Ser 2004;923:1-122, back cover. PMID: 15382606
Araujo AP, Padua PA, Maia Filho HS
Arq Neuropsiquiatr 2002 Jun;60(2-A):231-3. PMID: 12068350
Harel L, Zecharia A, Straussberg R, Volovitz B, Amir J
Pediatr Neurol 2000 Aug;23(2):147-51. doi: 10.1016/s0887-8994(00)00177-6. PMID: 11020640
Sudhindra BK
Indian Pediatr 1996 Jan;33(1):47-9. PMID: 8772953

Prognosis

Santos-Silva R, Corujeira S, Almeida AF, Granja S, Moura C, Azevedo I, Leão M, Maia A
Sao Paulo Med J 2011;129(4):267-70. doi: 10.1590/s1516-31802011000400011. PMID: 21971903
Walker AR, Tani LY, Thompson JA, Firth SD, Veasy LG, Bale JF Jr
J Pediatr 2007 Dec;151(6):679-83. Epub 2007 Aug 24 doi: 10.1016/j.jpeds.2007.04.059. PMID: 18035153
Harel L, Zecharia A, Straussberg R, Volovitz B, Amir J
Pediatr Neurol 2000 Aug;23(2):147-51. doi: 10.1016/s0887-8994(00)00177-6. PMID: 11020640
Sudhindra BK
Indian Pediatr 1996 Jan;33(1):47-9. PMID: 8772953
Kandil MR, Tohamy SA, Fattah MA, Ahmed HN, Farwiez HM
Neuroepidemiology 1994;13(5):202-10. doi: 10.1159/000110380. PMID: 7969703

Clinical prediction guides

Lardhi AA
Neurosciences (Riyadh) 2014 Jul;19(3):236-7. PMID: 24983288Free PMC Article
Araujo AP, Padua PA, Maia Filho HS
Arq Neuropsiquiatr 2002 Jun;60(2-A):231-3. PMID: 12068350
Harel L, Zecharia A, Straussberg R, Volovitz B, Amir J
Pediatr Neurol 2000 Aug;23(2):147-51. doi: 10.1016/s0887-8994(00)00177-6. PMID: 11020640
Agarwal PK, Misra M, Sarkari NB, Gupta AK, Agarwal P
J Assoc Physicians India 1998 Nov;46(11):937-8. PMID: 11229218
Abbas S, Khanna S, Taly AB
Psychopathology 1996;29(3):193-7. doi: 10.1159/000284991. PMID: 8817740

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