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Cor triatriatum sinister

MedGen UID:
576445
Concept ID:
C0344712
Congenital Abnormality
Synonyms: cor triatriatum sinister; Cor triatriatum sinistrum; cor triatriatum sinistrum; Divided left atrium; divided left atrium
SNOMED CT: Cor triatriatum sinister (253353007); Divided left atrium (253353007)
 
Monarch Initiative: MONDO:0020430
Orphanet: ORPHA99099

Definition

A rare, congenital, non-syndromic, heart malformation characterized by the presence of a thin, fibromuscular membrane subdividing the left atrium into an upper and lower chamber. The upper chamber receives blood from the pulmonary veins and the lower chamber is attached to the left atrial appendage. Therefore, the membrane blocks the orifice of the mitral valve and leads to obstruction of the left ventricular inflow. It may be asymptomatic or present in infancy with tachypnea, dyspnea, hemoptysis, chest pain, syncope, pulmonary edema, pulmonary hypertension, or heart failure, depending on the degree of obstruction. The anomaly may be isolated or associated with other congenital heart anomalies. [from ORDO]

Term Hierarchy

Professional guidelines

PubMed

Matsubara Y, Inamura N, Takada N, Fujita T
Ultrasound Obstet Gynecol 2023 Jan;61(1):124-126. doi: 10.1002/uog.26099. PMID: 36273403
Al Kindi HN, Shehata M, Ibrahim AM, Roshdy M, Simry W, Aguib Y, Yacoub MH
Ann Thorac Surg 2020 Oct;110(4):1380-1386. Epub 2020 Feb 28 doi: 10.1016/j.athoracsur.2020.01.025. PMID: 32114046

Recent clinical studies

Therapy

Zaidi SJ, Adhikari RR, El-Zein C, Siddiqui S
Ann Thorac Surg 2017 Nov;104(5):e385-e387. doi: 10.1016/j.athoracsur.2017.06.029. PMID: 29054235
Ridjab DA, Wittchen F, Tschishow W, Buddecke J, Lamp B, Manegold J, Schäbitz WR, Israel CW
Herz 2015 May;40(3):447-8. Epub 2013 Aug 17 doi: 10.1007/s00059-013-3934-8. PMID: 23949551
Kadner A, Meszaros K, Mueller C, Schoenhoff F, Hutter D, Carrel T
Multimed Man Cardiothorac Surg 2014;2014 Epub 2014 May 30 doi: 10.1093/mmcts/mmu005. PMID: 24878580

Prognosis

Qasim A, Doan TT, Furtun BY, Binsalamah Z, Adachi I, Morris SA
Prenat Diagn 2024 Jun;44(6-7):758-772. Epub 2024 Mar 6 doi: 10.1002/pd.6539. PMID: 38447986
Mashadi AH, Narasimhan SL, Said SM
J Card Surg 2022 Dec;37(12):4526-4533. Epub 2022 Nov 2 doi: 10.1111/jocs.17032. PMID: 36321701
Alaloola AA, Alghamdi R, Arafat AA
J Card Surg 2022 Dec;37(12):4534-4535. Epub 2022 Oct 13 doi: 10.1111/jocs.17031. PMID: 36229961
Goel A, Viswamitra S, Reddy BN, Gaduputi J
Br J Radiol 2021 Mar 1;94(1119):20201252. Epub 2021 Jan 5 doi: 10.1259/bjr.20201252. PMID: 33400560Free PMC Article
Saxena P, Burkhart HM, Schaff HV, Daly R, Joyce LD, Dearani JA
Ann Thorac Surg 2014 May;97(5):1659-63. Epub 2014 Mar 12 doi: 10.1016/j.athoracsur.2013.12.046. PMID: 24630764

Clinical prediction guides

Xu H, Wang Z, Sa S, Yang Y, Zhang X, Li D
Gene 2024 Dec 15;929:148827. Epub 2024 Aug 8 doi: 10.1016/j.gene.2024.148827. PMID: 39122231
Patel MB, Samuel BP, Berjaoui WK, Girgis RE, Vettukattil JJ
Can J Cardiol 2015 Jun;31(6):819.e3-4. Epub 2015 Feb 4 doi: 10.1016/j.cjca.2015.01.036. PMID: 26022992
Howe MJ, Thomas MP, Agarwal PP, Bach DS, Rubenfire M
Can J Cardiol 2015 Apr;31(4):548.e1-3. Epub 2014 Nov 13 doi: 10.1016/j.cjca.2014.11.009. PMID: 25745881
Guvenc TS, Bilgin S, Kantarci UH, Sevingil T, Ercakmak B, Ilhan E, Ozen K, Karabag Y, Balci B
Folia Morphol (Warsz) 2012 Nov;71(4):275-9. PMID: 23197149
Kelmendi M, Bejiqi R, Bajraktari G, Beqiraj R
Med Arh 2009;63(5):300-2. PMID: 20380136

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