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Anaplastic large cell lymphoma

MedGen UID:
61533
Concept ID:
C0206180
Neoplastic Process
Synonyms: Anaplastic Large Cell Lymphoma; Anaplastic Large-Cell Lymphoma; Anaplastic Large-Cell Lymphomas; CD30 Positive Anaplastic Large Cell Lymphoma; CD30+ Anaplastic Large Cell Lymphoma; CD30+ Anaplastic Large-Cell Lymphoma; CD30-Positive Anaplastic Large-Cell Lymphoma; Ki 1 Lymphoma; Ki-1 Lymphoma; Ki-1 Lymphomas; Large-Cell Lymphoma, Anaplastic; Large-Cell Lymphomas, Anaplastic; Lymphoma, Anaplastic Large-Cell; Lymphoma, Ki-1; Lymphoma, Large-Cell, Anaplastic; Lymphoma, Large-Cell, Ki-1; Lymphomas, Anaplastic Large-Cell; Lymphomas, Ki-1; Systemic Anaplastic Large Cell Lymphoma; Systemic Anaplastic Large-Cell Lymphoma
SNOMED CT: Anaplastic large cell lymphoma, CD30+ (53237008); Anaplastic large cell lymphoma, T cell and Null cell type (53237008); Large cell anaplastic lymphoma T cell and Null cell type (702785000); Large cell (Ki-1 positive) lymphoma (702785000); Large cell (Ki-1 positive) lymphoma (53237008); Anaplastic large cell lymphoma CD30 positive (53237008); Anaplastic large cell lymphoma CD30 positive (702785000); Anaplastic large cell lymphoma (ALCL) CD30+ (53237008)
 
HPO: HP:0012193
Monarch Initiative: MONDO:0020325

Definition

A type of T-cell lymphoma that is characterized by so-called hallmark cells with a pleomorphic appearance that express the CD30 antigen, are lobulated, and have indented nuclei. [from HPO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVAnaplastic large cell lymphoma

Professional guidelines

PubMed

Horwitz SM, Ansell S, Ai WZ, Barnes J, Barta SK, Brammer J, Clemens MW, Dogan A, Foss F, Ghione P, Goodman AM, Guitart J, Halwani A, Haverkos BM, Hoppe RT, Jacobsen E, Jagadeesh D, Jones A, Kallam A, Kim YH, Kumar K, Mehta-Shah N, Olsen EA, Rajguru SA, Rozati S, Said J, Shaver A, Shea L, Shinohara MM, Sokol L, Torres-Cabala C, Wilcox R, Wu P, Zain J, Dwyer M, Sundar H
J Natl Compr Canc Netw 2022 Mar;20(3):285-308. doi: 10.6004/jnccn.2022.0015. PMID: 35276674
Zhang P, Zhang M
Clin Epigenetics 2020 Nov 7;12(1):169. doi: 10.1186/s13148-020-00962-x. PMID: 33160401Free PMC Article
Shustov A, Soma L
Cancer Treat Res 2019;176:127-144. doi: 10.1007/978-3-319-99716-2_6. PMID: 30596216

Recent clinical studies

Etiology

Horwitz SM, Ansell S, Ai WZ, Barnes J, Barta SK, Brammer J, Clemens MW, Dogan A, Foss F, Ghione P, Goodman AM, Guitart J, Halwani A, Haverkos BM, Hoppe RT, Jacobsen E, Jagadeesh D, Jones A, Kallam A, Kim YH, Kumar K, Mehta-Shah N, Olsen EA, Rajguru SA, Rozati S, Said J, Shaver A, Shea L, Shinohara MM, Sokol L, Torres-Cabala C, Wilcox R, Wu P, Zain J, Dwyer M, Sundar H
J Natl Compr Canc Netw 2022 Mar;20(3):285-308. doi: 10.6004/jnccn.2022.0015. PMID: 35276674
Ganapathi KA, Brown LE, Prakash S, Bhargava P
Pathology 2021 Apr;53(3):349-366. Epub 2021 Mar 5 doi: 10.1016/j.pathol.2021.01.002. PMID: 33685720
Marra A, Viale G, Pileri SA, Pravettoni G, Viale G, De Lorenzi F, Nolè F, Veronesi P, Curigliano G
Cancer Treat Rev 2020 Mar;84:101963. Epub 2020 Jan 13 doi: 10.1016/j.ctrv.2020.101963. PMID: 31958739
Shustov A, Soma L
Cancer Treat Res 2019;176:127-144. doi: 10.1007/978-3-319-99716-2_6. PMID: 30596216
Pulitzer M
Clin Lab Med 2017 Sep;37(3):527-546. doi: 10.1016/j.cll.2017.06.006. PMID: 28802499Free PMC Article

Diagnosis

Amador C, Feldman AL
Am J Clin Pathol 2021 Mar 15;155(4):479-497. doi: 10.1093/ajcp/aqab012. PMID: 33686426
Marra A, Viale G, Pileri SA, Pravettoni G, Viale G, De Lorenzi F, Nolè F, Veronesi P, Curigliano G
Cancer Treat Rev 2020 Mar;84:101963. Epub 2020 Jan 13 doi: 10.1016/j.ctrv.2020.101963. PMID: 31958739
Shustov A, Soma L
Cancer Treat Res 2019;176:127-144. doi: 10.1007/978-3-319-99716-2_6. PMID: 30596216
Pierce JM, Mehta A
Expert Rev Hematol 2017 Jan;10(1):29-37. Epub 2016 Dec 21 doi: 10.1080/17474086.2017.1270202. PMID: 27927047
Sandlund JT, Martin MG
Hematology Am Soc Hematol Educ Program 2016 Dec 2;2016(1):589-597. doi: 10.1182/asheducation-2016.1.589. PMID: 27913533Free PMC Article

Therapy

Horwitz S, O'Connor OA, Pro B, Trümper L, Iyer S, Advani R, Bartlett NL, Christensen JH, Morschhauser F, Domingo-Domenech E, Rossi G, Kim WS, Feldman T, Menne T, Belada D, Illés Á, Tobinai K, Tsukasaki K, Yeh SP, Shustov A, Hüttmann A, Savage KJ, Yuen S, Zinzani PL, Miao H, Bunn V, Fenton K, Fanale M, Puhlmann M, Illidge T
Ann Oncol 2022 Mar;33(3):288-298. Epub 2021 Dec 16 doi: 10.1016/j.annonc.2021.12.002. PMID: 34921960Free PMC Article
Shustov A, Soma L
Cancer Treat Res 2019;176:127-144. doi: 10.1007/978-3-319-99716-2_6. PMID: 30596216
Van Der Weyden C, Dickinson M, Whisstock J, Prince HM
Expert Rev Hematol 2019 Jan;12(1):5-19. Epub 2018 Dec 18 doi: 10.1080/17474086.2019.1558399. PMID: 30526166
Horwitz S, O'Connor OA, Pro B, Illidge T, Fanale M, Advani R, Bartlett NL, Christensen JH, Morschhauser F, Domingo-Domenech E, Rossi G, Kim WS, Feldman T, Lennard A, Belada D, Illés Á, Tobinai K, Tsukasaki K, Yeh SP, Shustov A, Hüttmann A, Savage KJ, Yuen S, Iyer S, Zinzani PL, Hua Z, Little M, Rao S, Woolery J, Manley T, Trümper L; ECHELON-2 Study Group
Lancet 2019 Jan 19;393(10168):229-240. Epub 2018 Dec 4 doi: 10.1016/S0140-6736(18)32984-2. PMID: 30522922Free PMC Article
Pierce JM, Mehta A
Expert Rev Hematol 2017 Jan;10(1):29-37. Epub 2016 Dec 21 doi: 10.1080/17474086.2017.1270202. PMID: 27927047

Prognosis

Alotaibi S, Hamadani M, Al-Mansour M, Aljurf M
Clin Lymphoma Myeloma Leuk 2021 Mar;21(3):e272-e276. Epub 2020 Dec 13 doi: 10.1016/j.clml.2020.12.005. PMID: 33384263
Fukano R, Mori T, Sekimizu M, Choi I, Kada A, Saito AM, Asada R, Takeuchi K, Terauchi T, Tateishi U, Horibe K, Nagai H
Cancer Sci 2020 Dec;111(12):4540-4547. Epub 2020 Oct 28 doi: 10.1111/cas.14671. PMID: 33010107Free PMC Article
Marra A, Viale G, Pileri SA, Pravettoni G, Viale G, De Lorenzi F, Nolè F, Veronesi P, Curigliano G
Cancer Treat Rev 2020 Mar;84:101963. Epub 2020 Jan 13 doi: 10.1016/j.ctrv.2020.101963. PMID: 31958739
Leventaki V, Bhattacharyya S, Lim MS
Semin Diagn Pathol 2020 Jan;37(1):57-71. Epub 2019 Dec 18 doi: 10.1053/j.semdp.2019.12.002. PMID: 31882178
Kempf W, Pfaltz K, Vermeer MH, Cozzio A, Ortiz-Romero PL, Bagot M, Olsen E, Kim YH, Dummer R, Pimpinelli N, Whittaker S, Hodak E, Cerroni L, Berti E, Horwitz S, Prince HM, Guitart J, Estrach T, Sanches JA, Duvic M, Ranki A, Dreno B, Ostheeren-Michaelis S, Knobler R, Wood G, Willemze R
Blood 2011 Oct 13;118(15):4024-35. Epub 2011 Aug 12 doi: 10.1182/blood-2011-05-351346. PMID: 21841159Free PMC Article

Clinical prediction guides

Pu Q, Qiao J, Liu Y, Cao X, Tan R, Yan D, Wang X, Li J, Yue B
Front Immunol 2022;13:1008695. Epub 2022 Nov 18 doi: 10.3389/fimmu.2022.1008695. PMID: 36466894Free PMC Article
Stuver R, Epstein-Peterson ZD, Johnson WT, Khan N, Lewis N, Moskowitz AJ, Sauter CS, Horwitz S
Oncology (Williston Park) 2022 May 9;36(5):293-305. doi: 10.46883/2022.25920960. PMID: 35576176
Shustov A, Soma L
Cancer Treat Res 2019;176:127-144. doi: 10.1007/978-3-319-99716-2_6. PMID: 30596216
Martin JM, Wu H, Barta SK
Chin Clin Oncol 2019 Feb;8(1):4. Epub 2018 Oct 11 doi: 10.21037/cco.2018.09.06. PMID: 30525751
Sandlund JT, Martin MG
Hematology Am Soc Hematol Educ Program 2016 Dec 2;2016(1):589-597. doi: 10.1182/asheducation-2016.1.589. PMID: 27913533Free PMC Article

Recent systematic reviews

Padhi S, Panigrahi MK, Mohapatra S, Mishra P, Patra S, Sable MN, Thakur B, Nayak M, Panigrahi A
J Cancer Res Ther 2021 Oct-Dec;17(6):1297-1306. doi: 10.4103/jcrt.JCRT_1089_19. PMID: 34916357
Leberfinger AN, Behar BJ, Williams NC, Rakszawski KL, Potochny JD, Mackay DR, Ravnic DJ
JAMA Surg 2017 Dec 1;152(12):1161-1168. doi: 10.1001/jamasurg.2017.4026. PMID: 29049466
Gidengil CA, Predmore Z, Mattke S, van Busum K, Kim B
Plast Reconstr Surg 2015 Mar;135(3):713-720. doi: 10.1097/PRS.0000000000001037. PMID: 25490539
Kempf W, Pfaltz K, Vermeer MH, Cozzio A, Ortiz-Romero PL, Bagot M, Olsen E, Kim YH, Dummer R, Pimpinelli N, Whittaker S, Hodak E, Cerroni L, Berti E, Horwitz S, Prince HM, Guitart J, Estrach T, Sanches JA, Duvic M, Ranki A, Dreno B, Ostheeren-Michaelis S, Knobler R, Wood G, Willemze R
Blood 2011 Oct 13;118(15):4024-35. Epub 2011 Aug 12 doi: 10.1182/blood-2011-05-351346. PMID: 21841159Free PMC Article
Kim B, Roth C, Chung KC, Young VL, van Busum K, Schnyer C, Mattke S
Plast Reconstr Surg 2011 Jun;127(6):2141-2150. doi: 10.1097/PRS.0b013e3182172418. PMID: 21358562

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