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Myxosarcoma

MedGen UID:
6508
Concept ID:
C0027155
Neoplastic Process
Synonym: Myxosarcomas
SNOMED CT: Myxosarcoma (28351005)
 
Monarch Initiative: MONDO:0006863

Definition

An infiltrating malignant soft tissue neoplasm characterized by the presence of immature undifferentiated cells and abundant myxoid stroma formation. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVMyxosarcoma

Professional guidelines

PubMed

Duffy GP, Wood MB, Rock MG, Sim FH
J Bone Joint Surg Am 2000 Apr;82(4):544-54. doi: 10.2106/00004623-200004000-00009. PMID: 10761944

Recent clinical studies

Etiology

Mustafa S, VandenBussche CJ, Ali SZ, Siddiqui MT, Wakely PE Jr
J Am Soc Cytopathol 2020 May-Jun;9(3):191-201. Epub 2020 Feb 22 doi: 10.1016/j.jasc.2020.01.006. PMID: 32197967
Boughzala-Bennadji R, Stoeckle E, Le Péchoux C, Méeus P, Honoré C, Attal J, Duffaud F, De Pinieux G, Bompas E, Thariat J, Leroux A, Bertucci F, Isambert N, Delcambre C, Blay JY, Sunyach MP, Coindre JM, Sargos P, Penel N, Bonvalot S
Int J Radiat Oncol Biol Phys 2018 Oct 1;102(2):399-406. Epub 2018 Jun 2 doi: 10.1016/j.ijrobp.2018.05.055. PMID: 30191871
Maitra RN, McHaffie DJ, Wakefield JS, Delahunt B
Anticancer Res 2003 Jul-Aug;23(4):3549-53. PMID: 12926105
Liu S, Wang Z, Chen AQ, Zhou GH, Jiang ZB, Xiao MD
Asian Cardiovasc Thorac Ann 2002 Mar;10(1):8-11. doi: 10.1177/021849230201000103. PMID: 12079962
Oliva E, Clement PB, Young RH
Adv Anat Pathol 2000 Sep;7(5):257-81. doi: 10.1097/00125480-200007050-00001. PMID: 10976906

Diagnosis

Costigan D, Dal Cin P, Fletcher CDM, Nucci MR, Parra-Herran C, Chapel DB
Am J Surg Pathol 2022 Sep 1;46(9):1196-1206. Epub 2022 Apr 13 doi: 10.1097/PAS.0000000000001906. PMID: 35617488
Lucas DR
Arch Pathol Lab Med 2017 Nov;141(11):1503-1507. doi: 10.5858/arpa.2017-0219-RA. PMID: 29072951
Ieremia E, Thway K
Arch Pathol Lab Med 2014 Oct;138(10):1406-11. doi: 10.5858/arpa.2013-0549-RS. PMID: 25268202
Clarke LE
Dermatol Clin 2012 Oct;30(4):643-56, vi. Epub 2012 Aug 11 doi: 10.1016/j.det.2012.06.005. PMID: 23021051
MORGAN J, WELLS GC
Proc R Soc Med 1963 Oct;56(10):903. PMID: 14072145Free PMC Article

Therapy

Martin-Carreras T, Li H, Cooper K, Fan Y, Sebro R
BMC Med Imaging 2019 Aug 15;19(1):67. doi: 10.1186/s12880-019-0366-9. PMID: 31416421Free PMC Article
Clarke LE
Dermatol Clin 2012 Oct;30(4):643-56, vi. Epub 2012 Aug 11 doi: 10.1016/j.det.2012.06.005. PMID: 23021051
Neragi-Miandoab S, Kim J, Vlahakes GJ
Clin Oncol (R Coll Radiol) 2007 Dec;19(10):748-56. Epub 2007 Aug 10 doi: 10.1016/j.clon.2007.06.009. PMID: 17693068
Liu S, Wang Z, Chen AQ, Zhou GH, Jiang ZB, Xiao MD
Asian Cardiovasc Thorac Ann 2002 Mar;10(1):8-11. doi: 10.1177/021849230201000103. PMID: 12079962
Blodi FC
Am J Ophthalmol 1969 Sep;68(3):407-12. doi: 10.1016/0002-9394(69)90703-x. PMID: 5257914

Prognosis

Lucas DR
Arch Pathol Lab Med 2017 Nov;141(11):1503-1507. doi: 10.5858/arpa.2017-0219-RA. PMID: 29072951
Ieremia E, Thway K
Arch Pathol Lab Med 2014 Oct;138(10):1406-11. doi: 10.5858/arpa.2013-0549-RS. PMID: 25268202
Clarke LE
Dermatol Clin 2012 Oct;30(4):643-56, vi. Epub 2012 Aug 11 doi: 10.1016/j.det.2012.06.005. PMID: 23021051
Lee TH, Huang SC, Su TM, Yang KY, Rau CS
Chang Gung Med J 2011 May-Jun;34(3):315-9. PMID: 21733362
Liu S, Wang Z, Chen AQ, Zhou GH, Jiang ZB, Xiao MD
Asian Cardiovasc Thorac Ann 2002 Mar;10(1):8-11. doi: 10.1177/021849230201000103. PMID: 12079962

Clinical prediction guides

Odei B, Rwigema JC, Eilber FR, Eilber FC, Selch M, Singh A, Chmielowski B, Nelson SD, Wang PC, Steinberg M, Kamrava M
Am J Clin Oncol 2018 Sep;41(9):827-831. doi: 10.1097/COC.0000000000000382. PMID: 28640064
Dell'Aversana Orabona G, Iaconetta G, Abbate V, Piombino P, Romano A, Maglitto F, Salzano G, Califano L
J Med Case Rep 2014 Dec 29;8:468. doi: 10.1186/1752-1947-8-468. PMID: 25547541Free PMC Article
Vander Salm TJ
Semin Thorac Cardiovasc Surg 2000 Apr;12(2):89-100. doi: 10.1053/ct.2000.5080. PMID: 10807431
Burke AP, Cowan D, Virmani R
Cancer 1992 Jan 15;69(2):387-95. doi: 10.1002/1097-0142(19920115)69:2<387::aid-cncr2820690219>3.0.co;2-n. PMID: 1728367
Attum AA, Johnson GS, Masri Z, Girardet R, Lansing AM
Ann Thorac Surg 1987 Aug;44(2):217-22. doi: 10.1016/s0003-4975(10)62052-8. PMID: 3304181

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