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Sarcomatoid Hepatocellular Carcinoma

MedGen UID:
690058
Concept ID:
C1266019
Neoplastic Process
Synonyms: Hepatocellular carcinoma, sarcomatoid; Hepatocellular carcinoma, spindle cell variant; Sarcomatous Hepatocellular Carcinoma
SNOMED CT: Hepatocellular carcinoma, sarcomatoid (128648009); Hepatocellular carcinoma, spindle cell variant (128648009)

Definition

A morphologic variant of hepatocellular carcinoma characterized by the presence of malignant spindle cells or atypical giant cells. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVSarcomatoid Hepatocellular Carcinoma

Professional guidelines

PubMed

Wu L, Tsilimigras DI, Farooq A, Hyer JM, Merath K, Paredes AZ, Mehta R, Sahara K, Shen F, Pawlik TM
Cancer 2019 Nov 1;125(21):3767-3775. Epub 2019 Jul 12 doi: 10.1002/cncr.32396. PMID: 31299092
Kan A, Guo RP
Int J Surg 2018 Jul;55:145-151. Epub 2018 May 31 doi: 10.1016/j.ijsu.2018.05.736. PMID: 29860126

Recent clinical studies

Etiology

He G, Huang W, Zhou Z, Wu H, Tian Q, Tan L, Li X
Abdom Radiol (NY) 2023 Oct;48(10):3091-3100. Epub 2023 Jul 10 doi: 10.1007/s00261-023-03983-1. PMID: 37428205Free PMC Article
Kimura M, Matsuoka R, Nishikawa K, Imamura J, Kimura K
Am J Case Rep 2023 May 17;24:e939126. doi: 10.12659/AJCR.939126. PMID: 37194213Free PMC Article
Kelley RK, Rimassa L, Cheng AL, Kaseb A, Qin S, Zhu AX, Chan SL, Melkadze T, Sukeepaisarnjaroen W, Breder V, Verset G, Gane E, Borbath I, Rangel JDG, Ryoo BY, Makharadze T, Merle P, Benzaghou F, Banerjee K, Hazra S, Fawcett J, Yau T
Lancet Oncol 2022 Aug;23(8):995-1008. Epub 2022 Jul 4 doi: 10.1016/S1470-2045(22)00326-6. PMID: 35798016
Zhang C, Feng S, Tu Z, Sun J, Rui T, Zhang X, Huang H, Ling Q, Zheng S
Cancer Med 2021 Sep;10(18):6227-6238. Epub 2021 Jul 31 doi: 10.1002/cam4.4162. PMID: 34331411Free PMC Article
Wang JP, Yao ZG, Sun YW, Liu XH, Sun FK, Lin CH, Ren FX, Lv BB, Zhang SJ, Wang Y, Meng FY, Zheng SZ, Gong W, Liu J
World J Gastroenterol 2020 Aug 7;26(29):4327-4342. doi: 10.3748/wjg.v26.i29.4327. PMID: 32848337Free PMC Article

Diagnosis

He G, Huang W, Zhou Z, Wu H, Tian Q, Tan L, Li X
Abdom Radiol (NY) 2023 Oct;48(10):3091-3100. Epub 2023 Jul 10 doi: 10.1007/s00261-023-03983-1. PMID: 37428205Free PMC Article
Kimura M, Matsuoka R, Nishikawa K, Imamura J, Kimura K
Am J Case Rep 2023 May 17;24:e939126. doi: 10.12659/AJCR.939126. PMID: 37194213Free PMC Article
Wege H, Schulze K, von Felden J, Calderaro J, Reig M; rare liver tumors working group of the European Reference Network on Hepatological Diseases (ERN RARE-LIVER)
Eur J Med Genet 2021 Nov;64(11):104313. Epub 2021 Aug 18 doi: 10.1016/j.ejmg.2021.104313. PMID: 34418585
Zhang C, Feng S, Tu Z, Sun J, Rui T, Zhang X, Huang H, Ling Q, Zheng S
Cancer Med 2021 Sep;10(18):6227-6238. Epub 2021 Jul 31 doi: 10.1002/cam4.4162. PMID: 34331411Free PMC Article
Wang JP, Yao ZG, Sun YW, Liu XH, Sun FK, Lin CH, Ren FX, Lv BB, Zhang SJ, Wang Y, Meng FY, Zheng SZ, Gong W, Liu J
World J Gastroenterol 2020 Aug 7;26(29):4327-4342. doi: 10.3748/wjg.v26.i29.4327. PMID: 32848337Free PMC Article

Therapy

Pinter M, Scheiner B, Pinato DJ
Lancet Gastroenterol Hepatol 2023 Aug;8(8):760-770. Epub 2023 Jun 14 doi: 10.1016/S2468-1253(23)00147-4. PMID: 37327807
Kelley RK, Rimassa L, Cheng AL, Kaseb A, Qin S, Zhu AX, Chan SL, Melkadze T, Sukeepaisarnjaroen W, Breder V, Verset G, Gane E, Borbath I, Rangel JDG, Ryoo BY, Makharadze T, Merle P, Benzaghou F, Banerjee K, Hazra S, Fawcett J, Yau T
Lancet Oncol 2022 Aug;23(8):995-1008. Epub 2022 Jul 4 doi: 10.1016/S1470-2045(22)00326-6. PMID: 35798016
Zhang C, Feng S, Tu Z, Sun J, Rui T, Zhang X, Huang H, Ling Q, Zheng S
Cancer Med 2021 Sep;10(18):6227-6238. Epub 2021 Jul 31 doi: 10.1002/cam4.4162. PMID: 34331411Free PMC Article
Morisue R, Kojima M, Suzuki T, Nakatsura T, Ojima H, Watanabe R, Sugimoto M, Kobayashi S, Takahashi S, Konishi M, Ishii G, Gotohda N, Fujiwara T, Ochiai A
Int J Cancer 2021 Aug 1;149(3):546-560. Epub 2021 Mar 13 doi: 10.1002/ijc.33545. PMID: 33662146
Wang JP, Yao ZG, Sun YW, Liu XH, Sun FK, Lin CH, Ren FX, Lv BB, Zhang SJ, Wang Y, Meng FY, Zheng SZ, Gong W, Liu J
World J Gastroenterol 2020 Aug 7;26(29):4327-4342. doi: 10.3748/wjg.v26.i29.4327. PMID: 32848337Free PMC Article

Prognosis

Kimura M, Matsuoka R, Nishikawa K, Imamura J, Kimura K
Am J Case Rep 2023 May 17;24:e939126. doi: 10.12659/AJCR.939126. PMID: 37194213Free PMC Article
Lv TR, Hu HJ, Regmi P, Liu F, Li FY
J Cancer Res Clin Oncol 2022 Jul;148(7):1685-1696. Epub 2022 Feb 24 doi: 10.1007/s00432-022-03949-8. PMID: 35201426
Zhang C, Feng S, Tu Z, Sun J, Rui T, Zhang X, Huang H, Ling Q, Zheng S
Cancer Med 2021 Sep;10(18):6227-6238. Epub 2021 Jul 31 doi: 10.1002/cam4.4162. PMID: 34331411Free PMC Article
Luo C, Xin H, Yin D, Zhao T, Hu Z, Zhou Z, Sun R, Yao N, Sun Q, Fan J, Huang X, Zhou J, Zhou S
Aging (Albany NY) 2021 Jun 3;13(11):15126-15138. doi: 10.18632/aging.203076. PMID: 34081621Free PMC Article
Wang JP, Yao ZG, Sun YW, Liu XH, Sun FK, Lin CH, Ren FX, Lv BB, Zhang SJ, Wang Y, Meng FY, Zheng SZ, Gong W, Liu J
World J Gastroenterol 2020 Aug 7;26(29):4327-4342. doi: 10.3748/wjg.v26.i29.4327. PMID: 32848337Free PMC Article

Clinical prediction guides

He G, Huang W, Zhou Z, Wu H, Tian Q, Tan L, Li X
Abdom Radiol (NY) 2023 Oct;48(10):3091-3100. Epub 2023 Jul 10 doi: 10.1007/s00261-023-03983-1. PMID: 37428205Free PMC Article
Zhang C, Feng S, Tu Z, Sun J, Rui T, Zhang X, Huang H, Ling Q, Zheng S
Cancer Med 2021 Sep;10(18):6227-6238. Epub 2021 Jul 31 doi: 10.1002/cam4.4162. PMID: 34331411Free PMC Article
Luo C, Xin H, Yin D, Zhao T, Hu Z, Zhou Z, Sun R, Yao N, Sun Q, Fan J, Huang X, Zhou J, Zhou S
Aging (Albany NY) 2021 Jun 3;13(11):15126-15138. doi: 10.18632/aging.203076. PMID: 34081621Free PMC Article
Wang JP, Yao ZG, Sun YW, Liu XH, Sun FK, Lin CH, Ren FX, Lv BB, Zhang SJ, Wang Y, Meng FY, Zheng SZ, Gong W, Liu J
World J Gastroenterol 2020 Aug 7;26(29):4327-4342. doi: 10.3748/wjg.v26.i29.4327. PMID: 32848337Free PMC Article
Liao SH, Su TH, Jeng YM, Liang PC, Chen DS, Chen CH, Kao JH
Hepatology 2019 Jan;69(1):209-221. doi: 10.1002/hep.30162. PMID: 30014620

Recent systematic reviews

Lv TR, Hu HJ, Regmi P, Liu F, Li FY
J Cancer Res Clin Oncol 2022 Jul;148(7):1685-1696. Epub 2022 Feb 24 doi: 10.1007/s00432-022-03949-8. PMID: 35201426

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