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Subarterial ventricular septal defect

MedGen UID:
757534
Concept ID:
C3165130
Congenital Abnormality
Synonym: Infundibular ventricular septal defect
SNOMED CT: Subarterial ventricular septal defect (448876006)
 
HPO: HP:0011681

Definition

A ventricular septal defect that lies beneath the semilunar valve(s) in the conal or outlet septum. [from HPO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVSubarterial ventricular septal defect

Professional guidelines

PubMed

Griffin ML, Sullivan ID, Anderson RH, Macartney FJ
Br Heart J 1988 Apr;59(4):474-9. doi: 10.1136/hrt.59.4.474. PMID: 3370182Free PMC Article

Recent clinical studies

Etiology

Wang G, Liu R, Ma K, Zhang B, Pang K, Qi L, Hua Z, Li S
Cardiol Young 2021 May;31(5):799-803. Epub 2021 Jan 28 doi: 10.1017/S1047951120004643. PMID: 33504385
Wang L, Xie L, Ruan W, Li T, Gan C, Lin K
BMC Surg 2020 Sep 18;20(1):208. doi: 10.1186/s12893-020-00854-0. PMID: 32948172Free PMC Article
Chen Z, Chen W, Chen H, Liao Z, Chen Q, Chen L
Cardiol Young 2020 May;30(5):599-606. Epub 2020 Apr 20 doi: 10.1017/S1047951120000530. PMID: 32308178
Cao H, Chen Q, Zhang GC, Chen LW, Qiu ZH, Xu F
J Card Surg 2016 Jun;31(6):398-402. Epub 2016 May 2 doi: 10.1111/jocs.12754. PMID: 27132625
Byard RW, Bourne AJ, Adams PS
Am J Cardiovasc Pathol 1990;3(4):333-6. PMID: 2151785

Diagnosis

Chen Z, Chen W, Chen H, Liao Z, Chen Q, Chen L
Cardiol Young 2020 May;30(5):599-606. Epub 2020 Apr 20 doi: 10.1017/S1047951120000530. PMID: 32308178
Jivanji SG, Derrick G, Khambadkone S
Catheter Cardiovasc Interv 2016 Aug;88(2):244-7. Epub 2016 Jan 17 doi: 10.1002/ccd.26412. PMID: 26775289
Hu G, Zhu X, Li G, Jiang F, Li J
Echocardiography 2015 Sep;32(9):1438-40. Epub 2015 Mar 1 doi: 10.1111/echo.12923. PMID: 25728324
Kenny D, Hares D, Uzun O
Heart 2007 May;93(5):647. doi: 10.1136/hrt.2006.090480. PMID: 17435076Free PMC Article
Griffin ML, Sullivan ID, Anderson RH, Macartney FJ
Br Heart J 1988 Apr;59(4):474-9. doi: 10.1136/hrt.59.4.474. PMID: 3370182Free PMC Article

Therapy

Amaral V, So EK, Chow PC, Cheung YF
Pediatr Cardiol 2021 Jun;42(5):1216-1223. Epub 2021 Apr 19 doi: 10.1007/s00246-021-02603-3. PMID: 33871684
Chen Z, Chen W, Chen H, Liao Z, Chen Q, Chen L
Cardiol Young 2020 May;30(5):599-606. Epub 2020 Apr 20 doi: 10.1017/S1047951120000530. PMID: 32308178
Huang JS, Sun KP, Huang ST, Chen Q, Chen LW, Kuo YR
J Cardiothorac Surg 2020 Jan 28;15(1):28. doi: 10.1186/s13019-020-1062-0. PMID: 31992348Free PMC Article
Jivanji SG, Derrick G, Khambadkone S
Catheter Cardiovasc Interv 2016 Aug;88(2):244-7. Epub 2016 Jan 17 doi: 10.1002/ccd.26412. PMID: 26775289
Chang YH, Sung SC, Lee HD, Ban JE, Choo KS, Lee YS
Eur J Cardiothorac Surg 2007 Jul;32(1):149-55. Epub 2007 Apr 20 doi: 10.1016/j.ejcts.2007.03.027. PMID: 17449263

Prognosis

Amaral V, So EK, Chow PC, Cheung YF
Pediatr Cardiol 2021 Jun;42(5):1216-1223. Epub 2021 Apr 19 doi: 10.1007/s00246-021-02603-3. PMID: 33871684
Wang G, Liu R, Ma K, Zhang B, Pang K, Qi L, Hua Z, Li S
Cardiol Young 2021 May;31(5):799-803. Epub 2021 Jan 28 doi: 10.1017/S1047951120004643. PMID: 33504385
Wang L, Xie L, Ruan W, Li T, Gan C, Lin K
BMC Surg 2020 Sep 18;20(1):208. doi: 10.1186/s12893-020-00854-0. PMID: 32948172Free PMC Article
Cao H, Chen Q, Zhang GC, Chen LW, Qiu ZH, Xu F
J Card Surg 2016 Jun;31(6):398-402. Epub 2016 May 2 doi: 10.1111/jocs.12754. PMID: 27132625
Chang YH, Sung SC, Lee HD, Ban JE, Choo KS, Lee YS
Eur J Cardiothorac Surg 2007 Jul;32(1):149-55. Epub 2007 Apr 20 doi: 10.1016/j.ejcts.2007.03.027. PMID: 17449263

Clinical prediction guides

Amaral V, So EK, Chow PC, Cheung YF
Pediatr Cardiol 2021 Jun;42(5):1216-1223. Epub 2021 Apr 19 doi: 10.1007/s00246-021-02603-3. PMID: 33871684
Liao Z, Chen H, Lin L, Chen Q, Chen L, Chen Z
Eur J Cardiothorac Surg 2020 May 1;57(5):929-936. doi: 10.1093/ejcts/ezaa020. PMID: 32163571
Cao H, Chen Q, Zhang GC, Chen LW, Qiu ZH, Xu F
J Card Surg 2016 Jun;31(6):398-402. Epub 2016 May 2 doi: 10.1111/jocs.12754. PMID: 27132625
Jivanji SG, Derrick G, Khambadkone S
Catheter Cardiovasc Interv 2016 Aug;88(2):244-7. Epub 2016 Jan 17 doi: 10.1002/ccd.26412. PMID: 26775289
Komai H, Naito Y, Fujiwara K, Noguchi Y, Nishimura Y, Uemura S
Ann Thorac Surg 1997 Oct;64(4):1146-9. doi: 10.1016/s0003-4975(97)00718-2. PMID: 9354542

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