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Epithelial predominant Wilms tumor

MedGen UID:
76000
•Concept ID:
C0279608
•
Neoplastic Process
Synonym: Epithelial predominant Wilms' tumor
 
Monarch Initiative: MONDO:0003322

Definition

Wilms tumor of the kidney characterized by the predominance of the epithelial component. The epithelial cells may form papillary and tubular patterns and pseudorosettes. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVEpithelial predominant Wilms tumor

Professional guidelines

PubMed

Metanephric adenoma: the utility of immunohistochemical and cytogenetic analyses in differential diagnosis, including solid variant papillary renal cell carcinoma and epithelial-predominant nephroblastoma.
Kinney SN, Eble JN, Hes O, Williamson SR, Grignon DJ, Wang M, Zhang S, Baldrige LA, Martignoni G, Brunelli M, Wang L, Comperat E, Fan R, Montironi R, MacLennan GT, Cheng L
Mod Pathol 2015 Sep;28(9):1236-48. Epub 2015 Aug 7 doi: 10.1038/modpathol.2015.81. PMID: 26248896
Alpha-methylacyl-CoA racemase as a marker in the differential diagnosis of metanephric adenoma.
Olgac S, Hutchinson B, Tickoo SK, Reuter VE
Mod Pathol 2006 Feb;19(2):218-24. doi: 10.1038/modpathol.3800520. PMID: 16424894

Recent clinical studies

Etiology

The spectrum of metanephric adenofibroma and related lesions: clinicopathologic study of 25 cases from the National Wilms Tumor Study Group Pathology Center.
Arroyo MR, Green DM, Perlman EJ, Beckwith JB, Argani P
Am J Surg Pathol 2001 Apr;25(4):433-44. doi: 10.1097/00000478-200104000-00002. PMID: 11257617

Diagnosis

Cadherin 17 is a sensitive and specific marker for metanephric adenoma.
Yakirevich E, Magi-Galluzzi C, Grada Z, Lu S, Resnick MB, Mangray S
Am J Surg Pathol 2015 Apr;39(4):479-86. doi: 10.1097/PAS.0000000000000401. PMID: 25768256Free PMC Article
The spectrum of metanephric adenofibroma and related lesions: clinicopathologic study of 25 cases from the National Wilms Tumor Study Group Pathology Center.
Arroyo MR, Green DM, Perlman EJ, Beckwith JB, Argani P
Am J Surg Pathol 2001 Apr;25(4):433-44. doi: 10.1097/00000478-200104000-00002. PMID: 11257617

Prognosis

Cadherin 17 is a sensitive and specific marker for metanephric adenoma.
Yakirevich E, Magi-Galluzzi C, Grada Z, Lu S, Resnick MB, Mangray S
Am J Surg Pathol 2015 Apr;39(4):479-86. doi: 10.1097/PAS.0000000000000401. PMID: 25768256Free PMC Article

Clinical prediction guides

Cadherin 17 is a sensitive and specific marker for metanephric adenoma.
Yakirevich E, Magi-Galluzzi C, Grada Z, Lu S, Resnick MB, Mangray S
Am J Surg Pathol 2015 Apr;39(4):479-86. doi: 10.1097/PAS.0000000000000401. PMID: 25768256Free PMC Article

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