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Dextro-Transposition of the Great Vessels with Intact Ventricular Septum

MedGen UID:
768659
•Concept ID:
C3640019
•
Disease or Syndrome

Definition

A congenital heart defect in which there is an abnormal arrangement of any of the primary blood vessels of the heart in conjunction with the notable absence of any pathologic opening between the cardiac ventricles. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVDextro-Transposition of the Great Vessels with Intact Ventricular Septum

Professional guidelines

PubMed

Transposition of the great arteries. Results of treatment with early palliation and late intracardiac repair.
Gutgesell HP, McNamara DG
Circulation 1975 Jan;51(1):32-8. doi: 10.1161/01.cir.51.1.32. PMID: 1109320

Recent clinical studies

Etiology

Growth of the Neo-Aortic Root and Prognosis of Transposition of the Great Arteries.
Sengupta A, Carreon CK, Gauvreau K, Lee JM, Sanders SP, Colan SD, Del Nido PJ, Mayer JE Jr, Nathan M
J Am Coll Cardiol 2024 Jan 30;83(4):516-527. Epub 2023 Nov 6 doi: 10.1016/j.jacc.2023.10.023. PMID: 37939977
D-Transposition of the great arteries with restrictive foramen ovale in the fetus: the dilemma of predicting the need for postnatal urgent balloon atrial septostomy.
Gottschalk I, Walter A, Menzel T, Weber EC, Wendt S, Sreeram N, Gembruch U, Berg C, Abel JS
Arch Gynecol Obstet 2024 Apr;309(4):1353-1367. Epub 2023 Mar 27 doi: 10.1007/s00404-023-06997-8. PMID: 36971845Free PMC Article
Reliability of Fetal Echocardiography in Predicting Postnatal Critical Hypoxia in Patients with Transposition of Great Arteries and Intact Ventricular Septum.
Masci M, Pasquini L, Alsaied T, Di Chiara L, Formigari R, Galletti L, Campanale CM, Romiti A, Bonito M, Bagolan P, Toscano A
Pediatr Cardiol 2021 Oct;42(7):1575-1584. Epub 2021 May 29 doi: 10.1007/s00246-021-02642-w. PMID: 34052858
Late presenters with dextro-transposition of great arteries and intact ventricular septum: to train or not to train the left ventricle for arterial switch operation?
Parker NM, Zuhdi M, Kouatli A, Baslaim G
Congenit Heart Dis 2009 Nov-Dec;4(6):424-32. doi: 10.1111/j.1747-0803.2009.00352.x. PMID: 19925535
Transposition of the great arteries. Results of treatment with early palliation and late intracardiac repair.
Gutgesell HP, McNamara DG
Circulation 1975 Jan;51(1):32-8. doi: 10.1161/01.cir.51.1.32. PMID: 1109320

Diagnosis

D-Transposition of the great arteries with restrictive foramen ovale in the fetus: the dilemma of predicting the need for postnatal urgent balloon atrial septostomy.
Gottschalk I, Walter A, Menzel T, Weber EC, Wendt S, Sreeram N, Gembruch U, Berg C, Abel JS
Arch Gynecol Obstet 2024 Apr;309(4):1353-1367. Epub 2023 Mar 27 doi: 10.1007/s00404-023-06997-8. PMID: 36971845Free PMC Article
Tubular Pouch Technique Using Aortic Tissues for Single Coronary Artery Transfer.
Arai Y, Asai H, Ebuoka N, Oba J, Tachibana T
Ann Thorac Surg 2023 Apr;115(4):e97-e99. Epub 2022 Apr 2 doi: 10.1016/j.athoracsur.2022.03.046. PMID: 35378088
Preoperative Care of Neonates With Congenital Heart Disease.
Tran NN, Tran M, Lemus RE, Woon J, Lopez J, Dang R, Votava-Smith JK
Neonatal Netw 2022 Jul 1;41(4):200-210. doi: 10.1891/NN-2021-0028. PMID: 35840337Free PMC Article
Reliability of Fetal Echocardiography in Predicting Postnatal Critical Hypoxia in Patients with Transposition of Great Arteries and Intact Ventricular Septum.
Masci M, Pasquini L, Alsaied T, Di Chiara L, Formigari R, Galletti L, Campanale CM, Romiti A, Bonito M, Bagolan P, Toscano A
Pediatr Cardiol 2021 Oct;42(7):1575-1584. Epub 2021 May 29 doi: 10.1007/s00246-021-02642-w. PMID: 34052858
Successful Management of a COVID-19 Positive Infant With Transposition of the Great Arteries.
Nabialek TJ, Puppala NK, Riordan A, Ramaraj R, Duong P, Guerrero R
World J Pediatr Congenit Heart Surg 2021 Jul;12(4):554-556. Epub 2021 Mar 18 doi: 10.1177/21501351211000687. PMID: 33736537

Therapy

Severe Pulmonary Vascular Obstructive Disease After Neonatal Arterial Switch Operation for Simple Transposition of the Great Arteries.
Kimura D, Briceno-Medina M, Kumar TK, Knott-Craig CJ
World J Pediatr Congenit Heart Surg 2017 Jan;8(1):114-116. Epub 2016 Jun 23 doi: 10.1177/2150135115623288. PMID: 27098605
The role of aortopulmonary collaterals after an arterial switch operation: a word of caution.
Veshti A, Vida VL, Padalino MA, Stellin G
Pediatr Cardiol 2009 Apr;30(3):347-8. Epub 2008 Oct 4 doi: 10.1007/s00246-008-9310-4. PMID: 18836756

Prognosis

Growth of the Neo-Aortic Root and Prognosis of Transposition of the Great Arteries.
Sengupta A, Carreon CK, Gauvreau K, Lee JM, Sanders SP, Colan SD, Del Nido PJ, Mayer JE Jr, Nathan M
J Am Coll Cardiol 2024 Jan 30;83(4):516-527. Epub 2023 Nov 6 doi: 10.1016/j.jacc.2023.10.023. PMID: 37939977
D-Transposition of the great arteries with restrictive foramen ovale in the fetus: the dilemma of predicting the need for postnatal urgent balloon atrial septostomy.
Gottschalk I, Walter A, Menzel T, Weber EC, Wendt S, Sreeram N, Gembruch U, Berg C, Abel JS
Arch Gynecol Obstet 2024 Apr;309(4):1353-1367. Epub 2023 Mar 27 doi: 10.1007/s00404-023-06997-8. PMID: 36971845Free PMC Article
Tubular Pouch Technique Using Aortic Tissues for Single Coronary Artery Transfer.
Arai Y, Asai H, Ebuoka N, Oba J, Tachibana T
Ann Thorac Surg 2023 Apr;115(4):e97-e99. Epub 2022 Apr 2 doi: 10.1016/j.athoracsur.2022.03.046. PMID: 35378088
Reliability of Fetal Echocardiography in Predicting Postnatal Critical Hypoxia in Patients with Transposition of Great Arteries and Intact Ventricular Septum.
Masci M, Pasquini L, Alsaied T, Di Chiara L, Formigari R, Galletti L, Campanale CM, Romiti A, Bonito M, Bagolan P, Toscano A
Pediatr Cardiol 2021 Oct;42(7):1575-1584. Epub 2021 May 29 doi: 10.1007/s00246-021-02642-w. PMID: 34052858
Transposition of the great arteries. Results of treatment with early palliation and late intracardiac repair.
Gutgesell HP, McNamara DG
Circulation 1975 Jan;51(1):32-8. doi: 10.1161/01.cir.51.1.32. PMID: 1109320

Clinical prediction guides

Growth of the Neo-Aortic Root and Prognosis of Transposition of the Great Arteries.
Sengupta A, Carreon CK, Gauvreau K, Lee JM, Sanders SP, Colan SD, Del Nido PJ, Mayer JE Jr, Nathan M
J Am Coll Cardiol 2024 Jan 30;83(4):516-527. Epub 2023 Nov 6 doi: 10.1016/j.jacc.2023.10.023. PMID: 37939977
D-Transposition of the great arteries with restrictive foramen ovale in the fetus: the dilemma of predicting the need for postnatal urgent balloon atrial septostomy.
Gottschalk I, Walter A, Menzel T, Weber EC, Wendt S, Sreeram N, Gembruch U, Berg C, Abel JS
Arch Gynecol Obstet 2024 Apr;309(4):1353-1367. Epub 2023 Mar 27 doi: 10.1007/s00404-023-06997-8. PMID: 36971845Free PMC Article
Reliability of Fetal Echocardiography in Predicting Postnatal Critical Hypoxia in Patients with Transposition of Great Arteries and Intact Ventricular Septum.
Masci M, Pasquini L, Alsaied T, Di Chiara L, Formigari R, Galletti L, Campanale CM, Romiti A, Bonito M, Bagolan P, Toscano A
Pediatr Cardiol 2021 Oct;42(7):1575-1584. Epub 2021 May 29 doi: 10.1007/s00246-021-02642-w. PMID: 34052858

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