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Dextro-Transposition of the Great Vessels with Intact Ventricular Septum

MedGen UID:
768659
Concept ID:
C3640019
Disease or Syndrome

Definition

A congenital heart defect in which there is an abnormal arrangement of any of the primary blood vessels of the heart in conjunction with the notable absence of any pathologic opening between the cardiac ventricles. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVDextro-Transposition of the Great Vessels with Intact Ventricular Septum

Professional guidelines

PubMed

Gutgesell HP, McNamara DG
Circulation 1975 Jan;51(1):32-8. doi: 10.1161/01.cir.51.1.32. PMID: 1109320

Recent clinical studies

Etiology

Masci M, Pasquini L, Alsaied T, Di Chiara L, Formigari R, Galletti L, Campanale CM, Romiti A, Bonito M, Bagolan P, Toscano A
Pediatr Cardiol 2021 Oct;42(7):1575-1584. Epub 2021 May 29 doi: 10.1007/s00246-021-02642-w. PMID: 34052858
Parker NM, Zuhdi M, Kouatli A, Baslaim G
Congenit Heart Dis 2009 Nov-Dec;4(6):424-32. doi: 10.1111/j.1747-0803.2009.00352.x. PMID: 19925535
Fortune RL, Paquet M, Collins-Nakai RL, Duncan NF
J Thorac Cardiovasc Surg 1983 Mar;85(3):371-4. PMID: 6827844
Arciniegas E, Farooki ZQ, Hakimi M, Perry BL, Green EW
J Thorac Cardiovasc Surg 1981 Apr;81(4):580-7. PMID: 7206766
Gutgesell HP, McNamara DG
Circulation 1975 Jan;51(1):32-8. doi: 10.1161/01.cir.51.1.32. PMID: 1109320

Diagnosis

Arai Y, Asai H, Ebuoka N, Oba J, Tachibana T
Ann Thorac Surg 2023 Apr;115(4):e97-e99. Epub 2022 Apr 2 doi: 10.1016/j.athoracsur.2022.03.046. PMID: 35378088
Tran NN, Tran M, Lemus RE, Woon J, Lopez J, Dang R, Votava-Smith JK
Neonatal Netw 2022 Jul 1;41(4):200-210. doi: 10.1891/NN-2021-0028. PMID: 35840337Free PMC Article
Masci M, Pasquini L, Alsaied T, Di Chiara L, Formigari R, Galletti L, Campanale CM, Romiti A, Bonito M, Bagolan P, Toscano A
Pediatr Cardiol 2021 Oct;42(7):1575-1584. Epub 2021 May 29 doi: 10.1007/s00246-021-02642-w. PMID: 34052858
Nabialek TJ, Puppala NK, Riordan A, Ramaraj R, Duong P, Guerrero R
World J Pediatr Congenit Heart Surg 2021 Jul;12(4):554-556. Epub 2021 Mar 18 doi: 10.1177/21501351211000687. PMID: 33736537
Veshti A, Vida VL, Padalino MA, Stellin G
Pediatr Cardiol 2009 Apr;30(3):347-8. Epub 2008 Oct 4 doi: 10.1007/s00246-008-9310-4. PMID: 18836756

Therapy

Kimura D, Briceno-Medina M, Kumar TK, Knott-Craig CJ
World J Pediatr Congenit Heart Surg 2017 Jan;8(1):114-116. Epub 2016 Jun 23 doi: 10.1177/2150135115623288. PMID: 27098605
Veshti A, Vida VL, Padalino MA, Stellin G
Pediatr Cardiol 2009 Apr;30(3):347-8. Epub 2008 Oct 4 doi: 10.1007/s00246-008-9310-4. PMID: 18836756

Prognosis

Arai Y, Asai H, Ebuoka N, Oba J, Tachibana T
Ann Thorac Surg 2023 Apr;115(4):e97-e99. Epub 2022 Apr 2 doi: 10.1016/j.athoracsur.2022.03.046. PMID: 35378088
Masci M, Pasquini L, Alsaied T, Di Chiara L, Formigari R, Galletti L, Campanale CM, Romiti A, Bonito M, Bagolan P, Toscano A
Pediatr Cardiol 2021 Oct;42(7):1575-1584. Epub 2021 May 29 doi: 10.1007/s00246-021-02642-w. PMID: 34052858
Kimura D, Briceno-Medina M, Kumar TK, Knott-Craig CJ
World J Pediatr Congenit Heart Surg 2017 Jan;8(1):114-116. Epub 2016 Jun 23 doi: 10.1177/2150135115623288. PMID: 27098605
Fortune RL, Paquet M, Collins-Nakai RL, Duncan NF
J Thorac Cardiovasc Surg 1983 Mar;85(3):371-4. PMID: 6827844
Gutgesell HP, McNamara DG
Circulation 1975 Jan;51(1):32-8. doi: 10.1161/01.cir.51.1.32. PMID: 1109320

Clinical prediction guides

Masci M, Pasquini L, Alsaied T, Di Chiara L, Formigari R, Galletti L, Campanale CM, Romiti A, Bonito M, Bagolan P, Toscano A
Pediatr Cardiol 2021 Oct;42(7):1575-1584. Epub 2021 May 29 doi: 10.1007/s00246-021-02642-w. PMID: 34052858

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