U.S. flag

An official website of the United States government

Format

Send to:

Choose Destination

Congenital Ventricular Tachycardia

MedGen UID:
768669
Concept ID:
C3640029
Finding
Synonyms: Congenital VT; Congenital VTach

Definition

An electrocardiographic finding of a tachycardia that originates in the ventricles that is present at birth. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVCongenital Ventricular Tachycardia

Professional guidelines

PubMed

Wilde AAM, Amin AS, Postema PG
Heart 2022 Mar;108(5):332-338. Epub 2021 May 26 doi: 10.1136/heartjnl-2020-318259. PMID: 34039680Free PMC Article
Al-Khatib SM, Stevenson WG, Ackerman MJ, Bryant WJ, Callans DJ, Curtis AB, Deal BJ, Dickfeld T, Field ME, Fonarow GC, Gillis AM, Granger CB, Hammill SC, Hlatky MA, Joglar JA, Kay GN, Matlock DD, Myerburg RJ, Page RL
J Am Coll Cardiol 2018 Oct 2;72(14):e91-e220. Epub 2018 Aug 16 doi: 10.1016/j.jacc.2017.10.054. PMID: 29097296
Al-Khatib SM, Stevenson WG, Ackerman MJ, Bryant WJ, Callans DJ, Curtis AB, Deal BJ, Dickfeld T, Field ME, Fonarow GC, Gillis AM, Granger CB, Hammill SC, Hlatky MA, Joglar JA, Kay GN, Matlock DD, Myerburg RJ, Page RL
Circulation 2018 Sep 25;138(13):e272-e391. doi: 10.1161/CIR.0000000000000549. PMID: 29084731

Recent clinical studies

Etiology

Bessière F, Waldmann V, Combes N, Metton O, Dib N, Mondésert B, O'Leary E, De Witt E, Carreon CK, Sanders SP, Moore JP, Triedman J, Khairy P
J Am Coll Cardiol 2023 Sep 12;82(11):1121-1130. doi: 10.1016/j.jacc.2023.06.036. PMID: 37673513
Bokma JP, Geva T, Sleeper LA, Lee JH, Lu M, Sompolinsky T, Babu-Narayan SV, Wald RM, Mulder BJM, Valente AM
J Am Coll Cardiol 2023 May 30;81(21):2075-2085. doi: 10.1016/j.jacc.2023.02.052. PMID: 37225360
Al-Khatib SM, Stevenson WG, Ackerman MJ, Bryant WJ, Callans DJ, Curtis AB, Deal BJ, Dickfeld T, Field ME, Fonarow GC, Gillis AM, Granger CB, Hammill SC, Hlatky MA, Joglar JA, Kay GN, Matlock DD, Myerburg RJ, Page RL
Circulation 2018 Sep 25;138(13):e210-e271. doi: 10.1161/CIR.0000000000000548. PMID: 29084733
Al-Khatib SM, Stevenson WG, Ackerman MJ, Bryant WJ, Callans DJ, Curtis AB, Deal BJ, Dickfeld T, Field ME, Fonarow GC, Gillis AM, Granger CB, Hammill SC, Hlatky MA, Joglar JA, Kay GN, Matlock DD, Myerburg RJ, Page RL
Circulation 2018 Sep 25;138(13):e272-e391. doi: 10.1161/CIR.0000000000000549. PMID: 29084731
Wren C
Eur Heart J 1998 May;19 Suppl E:E32-6, E54-9. PMID: 9717022

Diagnosis

Writing Committee Members, Shah MJ, Silka MJ, Silva JNA, Balaji S, Beach CM, Benjamin MN, Berul CI, Cannon B, Cecchin F, Cohen MI, Dalal AS, Dechert BE, Foster A, Gebauer R, Gonzalez Corcia MC, Kannankeril PJ, Karpawich PP, Kim JJ, Krishna MR, Kubuš P, LaPage MJ, Mah DY, Malloy-Walton L, Miyazaki A, Motonaga KS, Niu MC, Olen M, Paul T, Rosenthal E, Saarel EV, Silvetti MS, Stephenson EA, Tan RB, Triedman J, Bergen NHV, Wackel PL
Heart Rhythm 2021 Nov;18(11):1888-1924. Epub 2021 Jul 29 doi: 10.1016/j.hrthm.2021.07.038. PMID: 34363988
Bennett S, Thamman R, Griffiths T, Oxley C, Khan JN, Phan T, Patwala A, Heatlie G, Kwok CS
Echocardiography 2019 Aug;36(8):1549-1558. Epub 2019 Aug 5 doi: 10.1111/echo.14437. PMID: 31385360
Al-Khatib SM, Stevenson WG, Ackerman MJ, Bryant WJ, Callans DJ, Curtis AB, Deal BJ, Dickfeld T, Field ME, Fonarow GC, Gillis AM, Granger CB, Hammill SC, Hlatky MA, Joglar JA, Kay GN, Matlock DD, Myerburg RJ, Page RL
J Am Coll Cardiol 2018 Oct 2;72(14):e91-e220. Epub 2018 Aug 16 doi: 10.1016/j.jacc.2017.10.054. PMID: 29097296
Al-Khatib SM, Stevenson WG, Ackerman MJ, Bryant WJ, Callans DJ, Curtis AB, Deal BJ, Dickfeld T, Field ME, Fonarow GC, Gillis AM, Granger CB, Hammill SC, Hlatky MA, Joglar JA, Kay GN, Matlock DD, Myerburg RJ, Page RL
Circulation 2018 Sep 25;138(13):e210-e271. doi: 10.1161/CIR.0000000000000548. PMID: 29084733
Al-Khatib SM, Stevenson WG, Ackerman MJ, Bryant WJ, Callans DJ, Curtis AB, Deal BJ, Dickfeld T, Field ME, Fonarow GC, Gillis AM, Granger CB, Hammill SC, Hlatky MA, Joglar JA, Kay GN, Matlock DD, Myerburg RJ, Page RL
Circulation 2018 Sep 25;138(13):e272-e391. doi: 10.1161/CIR.0000000000000549. PMID: 29084731

Therapy

Wallet J, Kimura Y, Zeppenfeld K
Card Electrophysiol Clin 2022 Dec;14(4):709-727. Epub 2022 Oct 28 doi: 10.1016/j.ccep.2022.06.008. PMID: 36396188
Al-Khatib SM, Stevenson WG, Ackerman MJ, Bryant WJ, Callans DJ, Curtis AB, Deal BJ, Dickfeld T, Field ME, Fonarow GC, Gillis AM, Granger CB, Hammill SC, Hlatky MA, Joglar JA, Kay GN, Matlock DD, Myerburg RJ, Page RL
J Am Coll Cardiol 2018 Oct 2;72(14):e91-e220. Epub 2018 Aug 16 doi: 10.1016/j.jacc.2017.10.054. PMID: 29097296
Saw J, Humphries K, Aymong E, Sedlak T, Prakash R, Starovoytov A, Mancini GBJ
J Am Coll Cardiol 2017 Aug 29;70(9):1148-1158. doi: 10.1016/j.jacc.2017.06.053. PMID: 28838364
Priori SG, Blomström-Lundqvist C, Mazzanti A, Blom N, Borggrefe M, Camm J, Elliott PM, Fitzsimons D, Hatala R, Hindricks G, Kirchhof P, Kjeldsen K, Kuck KH, Hernandez-Madrid A, Nikolaou N, Norekvål TM, Spaulding C, Van Veldhuisen DJ; ESC Scientific Document Group
Eur Heart J 2015 Nov 1;36(41):2793-2867. Epub 2015 Aug 29 doi: 10.1093/eurheartj/ehv316. PMID: 26320108
Wren C
Eur Heart J 1998 May;19 Suppl E:E32-6, E54-9. PMID: 9717022

Prognosis

Bessière F, Waldmann V, Combes N, Metton O, Dib N, Mondésert B, O'Leary E, De Witt E, Carreon CK, Sanders SP, Moore JP, Triedman J, Khairy P
J Am Coll Cardiol 2023 Sep 12;82(11):1121-1130. doi: 10.1016/j.jacc.2023.06.036. PMID: 37673513
Bennett S, Thamman R, Griffiths T, Oxley C, Khan JN, Phan T, Patwala A, Heatlie G, Kwok CS
Echocardiography 2019 Aug;36(8):1549-1558. Epub 2019 Aug 5 doi: 10.1111/echo.14437. PMID: 31385360
Saw J, Humphries K, Aymong E, Sedlak T, Prakash R, Starovoytov A, Mancini GBJ
J Am Coll Cardiol 2017 Aug 29;70(9):1148-1158. doi: 10.1016/j.jacc.2017.06.053. PMID: 28838364
Zeppenfeld K
Herzschrittmacherther Elektrophysiol 2016 Jun;27(2):131-6. Epub 2016 May 19 doi: 10.1007/s00399-016-0428-4. PMID: 27193903Free PMC Article
Schmidt M, Burrell A, Roberts L, Bailey M, Sheldrake J, Rycus PT, Hodgson C, Scheinkestel C, Cooper DJ, Thiagarajan RR, Brodie D, Pellegrino V, Pilcher D
Eur Heart J 2015 Sep 1;36(33):2246-56. Epub 2015 Jun 1 doi: 10.1093/eurheartj/ehv194. PMID: 26033984

Clinical prediction guides

Crotti L, Spazzolini C, Nyegaard M, Overgaard MT, Kotta MC, Dagradi F, Sala L, Aiba T, Ayers MD, Baban A, Barc J, Beach CM, Behr ER, Bos JM, Cerrone M, Covi P, Cuneo B, Denjoy I, Donner B, Elbert A, Eliasson H, Etheridge SP, Fukuyama M, Girolami F, Hamilton R, Horie M, Iascone M, Jiménez-Jaimez J, Jensen HK, Kannankeril PJ, Kaski JP, Makita N, Muñoz-Esparza C, Odland HH, Ohno S, Papagiannis J, Porretta AP, Prandstetter C, Probst V, Robyns T, Rosenthal E, Rosés-Noguer F, Sekarski N, Singh A, Spentzou G, Stute F, Tfelt-Hansen J, Till J, Tobert KE, Vinocur JM, Webster G, Wilde AAM, Wolf CM, Ackerman MJ, Schwartz PJ
Eur Heart J 2023 Sep 14;44(35):3357-3370. doi: 10.1093/eurheartj/ehad418. PMID: 37528649Free PMC Article
Bokma JP, Geva T, Sleeper LA, Lee JH, Lu M, Sompolinsky T, Babu-Narayan SV, Wald RM, Mulder BJM, Valente AM
J Am Coll Cardiol 2023 May 30;81(21):2075-2085. doi: 10.1016/j.jacc.2023.02.052. PMID: 37225360
Bennett S, Thamman R, Griffiths T, Oxley C, Khan JN, Phan T, Patwala A, Heatlie G, Kwok CS
Echocardiography 2019 Aug;36(8):1549-1558. Epub 2019 Aug 5 doi: 10.1111/echo.14437. PMID: 31385360
Saw J, Humphries K, Aymong E, Sedlak T, Prakash R, Starovoytov A, Mancini GBJ
J Am Coll Cardiol 2017 Aug 29;70(9):1148-1158. doi: 10.1016/j.jacc.2017.06.053. PMID: 28838364
Itoh H, Crotti L, Aiba T, Spazzolini C, Denjoy I, Fressart V, Hayashi K, Nakajima T, Ohno S, Makiyama T, Wu J, Hasegawa K, Mastantuono E, Dagradi F, Pedrazzini M, Yamagishi M, Berthet M, Murakami Y, Shimizu W, Guicheney P, Schwartz PJ, Horie M
Eur Heart J 2016 May 7;37(18):1456-64. Epub 2015 Dec 28 doi: 10.1093/eurheartj/ehv695. PMID: 26715165Free PMC Article

Recent systematic reviews

Araújo CS, Silva CLB, da Silva Menezes Júnior A, Barbosa VA, de Almeida Laranjeira T, Fernandes JF, Gonçalves LC, Silva AMC
Curr Cardiol Rev 2022;18(3):e081221198647. doi: 10.2174/1573403X17666211208100151. PMID: 34879809Free PMC Article
Bennett S, Thamman R, Griffiths T, Oxley C, Khan JN, Phan T, Patwala A, Heatlie G, Kwok CS
Echocardiography 2019 Aug;36(8):1549-1558. Epub 2019 Aug 5 doi: 10.1111/echo.14437. PMID: 31385360
Kayvanpour E, Sedaghat-Hamedani F, Gi WT, Tugrul OF, Amr A, Haas J, Zhu F, Ehlermann P, Uhlmann L, Katus HA, Meder B
Clin Res Cardiol 2019 Nov;108(11):1297-1308. Epub 2019 Apr 12 doi: 10.1007/s00392-019-01465-3. PMID: 30980206
Olde Nordkamp LR, Postema PG, Knops RE, van Dijk N, Limpens J, Wilde AA, de Groot JR
Heart Rhythm 2016 Feb;13(2):443-54. Epub 2015 Sep 15 doi: 10.1016/j.hrthm.2015.09.010. PMID: 26385533
Loomba RS, Willes RJ, Kovach JR, Anderson RH
Congenit Heart Dis 2016 Jan-Feb;11(1):7-18. Epub 2015 Jul 29 doi: 10.1111/chd.12288. PMID: 26219620

Supplemental Content

Table of contents

    Practice guidelines

    • PubMed
      See practice and clinical guidelines in PubMed. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.
    • Bookshelf
      See practice and clinical guidelines in NCBI Bookshelf. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.

    Recent activity

    Your browsing activity is empty.

    Activity recording is turned off.

    Turn recording back on

    See more...