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Bilateral deafness

MedGen UID:
777106
•Concept ID:
C3665473
•
Finding
Synonyms: Bilateral Deafness; Bilateral, Deafness; Bilaterals, Deafness; Deafness Bilateral; Deafness Bilaterals; Deafness, Bilateral
SNOMED CT: Bilateral deafness (162344009)

Definition

Partial or total inability to hear sounds in both ears. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVBilateral deafness

Professional guidelines

PubMed

Fetal anemia in monochorionic twins: a review on diagnosis, management, and outcome.
Tollenaar LSA, Slaghekke F, Middeldorp JM, Lopriore E
Expert Rev Hematol 2023 Jan;16(1):9-16. Epub 2023 Jan 19 doi: 10.1080/17474086.2023.2166921. PMID: 36609186
American Cochlear Implant Alliance Task Force Guidelines for Clinical Assessment and Management of Cochlear Implantation in Children With Single-Sided Deafness.
Park LR, Griffin AM, Sladen DP, Neumann S, Young NM
Ear Hear 2022 Mar/Apr;43(2):255-267. doi: 10.1097/AUD.0000000000001204. PMID: 35213890Free PMC Article
Rapidly progressive bilateral postmeningitic deafness in children: Diagnosis and management.
De Barros A, Roy T, Amstutz Montadert I, Marie JP, Marcolla A, Obstoy MF, Choussy O, Dehesdin D, Lerosey Y
Eur Ann Otorhinolaryngol Head Neck Dis 2014 Apr;131(2):107-12. Epub 2014 Feb 18 doi: 10.1016/j.anorl.2013.04.006. PMID: 24559741

Recent clinical studies

Etiology

Neurodevelopmental impairment at 3 years of age after fetoscopic laser surgery for twin-to-twin transfusion syndrome.
Matsushima S, Ozawa K, Sugibayashi R, Ogawa K, Tsukamoto K, Miyazaki O, Wada S, Ito Y, Sago H
Prenat Diagn 2020 Jul;40(8):1013-1019. Epub 2020 May 13 doi: 10.1002/pd.5726. PMID: 32362029
Acute otitis media associated bilateral sudden hearing loss: case report and literature review.
Smith A, Gutteridge I, Elliott D, Cronin M
J Laryngol Otol 2017 Jul;131(S2):S57-S61. Epub 2017 Apr 17 doi: 10.1017/S0022215117000779. PMID: 28412992
Long-term neurodevelopmental outcome after selective feticide in monochorionic pregnancies.
van Klink J, Koopman HM, Middeldorp JM, Klumper FJ, Rijken M, Oepkes D, Lopriore E
BJOG 2015 Oct;122(11):1517-24. Epub 2015 Jul 6 doi: 10.1111/1471-0528.13490. PMID: 26147116
Sudden-onset bilateral deafness revealing early neurosyphilis.
Cassilde AL, Barnaud G, Baccar S, Mortier E
Eur Ann Otorhinolaryngol Head Neck Dis 2014 Dec;131(6):389-391. Epub 2014 May 29 doi: 10.1016/j.anorl.2014.02.003. PMID: 24880727
An auditory brainstem implant system.
Jackson KB, Mark G, Helms J, Mueller J, Behr R
Am J Audiol 2002 Dec;11(2):128-33. doi: 10.1044/1059-0889(2002/015). PMID: 12691224

Diagnosis

Deafness after COVID-19?
Gerstacker K, Speck I, Riemann S, Aschendorff A, Knopf A, Arndt S
HNO 2021 Aug;69(Suppl 2):92-95. Epub 2021 May 21 doi: 10.1007/s00106-021-01041-0. PMID: 34019138Free PMC Article
Hearing Impairment in Old Age.
Löhler J, Cebulla M, Shehata-Dieler W, Volkenstein S, Völter C, Walther LE
Dtsch Arztebl Int 2019 Apr 26;116(17):301-310. doi: 10.3238/arztebl.2019.0301. PMID: 31196393Free PMC Article
Long-term neurodevelopmental outcome after selective feticide in monochorionic pregnancies.
van Klink J, Koopman HM, Middeldorp JM, Klumper FJ, Rijken M, Oepkes D, Lopriore E
BJOG 2015 Oct;122(11):1517-24. Epub 2015 Jul 6 doi: 10.1111/1471-0528.13490. PMID: 26147116
Sudden-onset bilateral deafness revealing early neurosyphilis.
Cassilde AL, Barnaud G, Baccar S, Mortier E
Eur Ann Otorhinolaryngol Head Neck Dis 2014 Dec;131(6):389-391. Epub 2014 May 29 doi: 10.1016/j.anorl.2014.02.003. PMID: 24880727
The age of identification of childhood deafness--improvements since the 1970s.
Watkin PM
Public Health 1991 Jul;105(4):303-12. doi: 10.1016/s0033-3506(05)80215-x. PMID: 1767003

Therapy

Profound bilateral deafness complicating aortic arch surgery.
Carré F, Mamelle E, Ferrier S, Achouh P
Interact Cardiovasc Thorac Surg 2021 Jan 22;32(2):330-332. doi: 10.1093/icvts/ivaa256. PMID: 33450028Free PMC Article
Bilateral deafness two days following influenza vaccination: a case report.
Kolarov C, Löbermann M, Fritzsche C, Hemmer C, Mlynski R, Reisinger EC
Hum Vaccin Immunother 2019;15(1):107-108. Epub 2018 Sep 5 doi: 10.1080/21645515.2018.1509657. PMID: 30118641Free PMC Article
Bilateral Deafness as a Complication of the Vaccination-A Case Report.
Rikitake M, Sampei S, Komori M, Sakurai Y, Kojima H
Int Tinnitus J 2018 Jun 1;22(1):19-22. doi: 10.5935/0946-5448.20180003. PMID: 29993212
Massive Tension Pneumocephalus Following Cochlear Implant Surgery.
Di Lella F, D'Angelo G, Iaccarino I, Piccinini S, Negri M, Vincenti V
Otol Neurotol 2016 Oct;37(9):1263-6. doi: 10.1097/MAO.0000000000001168. PMID: 27525712
Influenza A (H1N1): a rare cause of deafness in two children.
Alsanosi AA
J Laryngol Otol 2012 Dec;126(12):1274-5. Epub 2012 Oct 1 doi: 10.1017/S0022215112002125. PMID: 23020865

Prognosis

Neurodevelopmental impairment at 3 years of age after fetoscopic laser surgery for twin-to-twin transfusion syndrome.
Matsushima S, Ozawa K, Sugibayashi R, Ogawa K, Tsukamoto K, Miyazaki O, Wada S, Ito Y, Sago H
Prenat Diagn 2020 Jul;40(8):1013-1019. Epub 2020 May 13 doi: 10.1002/pd.5726. PMID: 32362029
Long-term neurodevelopmental outcome after selective feticide in monochorionic pregnancies.
van Klink J, Koopman HM, Middeldorp JM, Klumper FJ, Rijken M, Oepkes D, Lopriore E
BJOG 2015 Oct;122(11):1517-24. Epub 2015 Jul 6 doi: 10.1111/1471-0528.13490. PMID: 26147116
Diffusion tensor imaging of the auditory nerve in patients with long-term single-sided deafness.
Vos SB, Haakma W, Versnel H, Froeling M, Speleman L, Dik P, Viergever MA, Leemans A, Grolman W
Hear Res 2015 May;323:1-8. Epub 2015 Feb 3 doi: 10.1016/j.heares.2015.01.010. PMID: 25655832
Novel mutations of KCNQ1 in Long QT syndrome.
Qureshi SF, Ali A, Ananthapur V, Jayakrishnan MP, Calambur N, Thangaraj K, Nallari P
Indian Heart J 2013 Sep-Oct;65(5):552-60. Epub 2013 Sep 4 doi: 10.1016/j.ihj.2013.08.025. PMID: 24206879Free PMC Article
Pancreatic adenocarcinoma presenting with sudden onset bilateral deafness secondary to metastatic leptomeningeal infiltration.
Blows SJ, Morgan R, Dhariwal U, Petts G, Roncaroli F
Age Ageing 2012 Nov;41(6):818-9. Epub 2012 Jun 27 doi: 10.1093/ageing/afs085. PMID: 22743150

Clinical prediction guides

Temporal Pitch Perception in Cochlear-Implant Users: Channel Independence in Apical Cochlear Regions.
Griessner A, Schatzer R, Steixner V, Rajan GP, Zierhofer C, Távora-Vieira D
Trends Hear 2021 Jan-Dec;25:23312165211020645. doi: 10.1177/23312165211020645. PMID: 34041983Free PMC Article
Neurodevelopmental impairment at 3 years of age after fetoscopic laser surgery for twin-to-twin transfusion syndrome.
Matsushima S, Ozawa K, Sugibayashi R, Ogawa K, Tsukamoto K, Miyazaki O, Wada S, Ito Y, Sago H
Prenat Diagn 2020 Jul;40(8):1013-1019. Epub 2020 May 13 doi: 10.1002/pd.5726. PMID: 32362029
Long-term neurodevelopmental outcome after selective feticide in monochorionic pregnancies.
van Klink J, Koopman HM, Middeldorp JM, Klumper FJ, Rijken M, Oepkes D, Lopriore E
BJOG 2015 Oct;122(11):1517-24. Epub 2015 Jul 6 doi: 10.1111/1471-0528.13490. PMID: 26147116
Diffusion tensor imaging of the auditory nerve in patients with long-term single-sided deafness.
Vos SB, Haakma W, Versnel H, Froeling M, Speleman L, Dik P, Viergever MA, Leemans A, Grolman W
Hear Res 2015 May;323:1-8. Epub 2015 Feb 3 doi: 10.1016/j.heares.2015.01.010. PMID: 25655832
Novel mutations of KCNQ1 in Long QT syndrome.
Qureshi SF, Ali A, Ananthapur V, Jayakrishnan MP, Calambur N, Thangaraj K, Nallari P
Indian Heart J 2013 Sep-Oct;65(5):552-60. Epub 2013 Sep 4 doi: 10.1016/j.ihj.2013.08.025. PMID: 24206879Free PMC Article

Recent systematic reviews

Genedrive kit for detecting single nucleotide polymorphism m.1555A>G in neonates and their mothers: a systematic review and cost-effectiveness analysis.
Shabaninejad H, Kenny RP, Robinson T, Stoniute A, O'Keefe H, Still M, Thornton C, Pearson F, Beyer F, Meader N
Health Technol Assess 2024 Oct;28(75):1-75. doi: 10.3310/TGAC4201. PMID: 39487741
Endocrine disorders in Woodhouse-Sakati syndrome: a systematic review of the literature.
Agopiantz M, Corbonnois P, Sorlin A, Bonnet C, Klein M, Hubert N, Pascal-Vigneron V, Jonveaux P, Cuny T, Leheup B, Weryha G
J Endocrinol Invest 2014 Jan;37(1):1-7. Epub 2014 Jan 8 doi: 10.1007/s40618-013-0001-5. PMID: 24464444
Cochlear implantation versus auditory brainstem implantation in bilateral total deafness after head trauma: personal experience and review of the literature.
Medina M, Di Lella F, Di Trapani G, Prasad SC, Bacciu A, Aristegui M, Russo A, Sanna M
Otol Neurotol 2014 Feb;35(2):260-70. doi: 10.1097/MAO.0000000000000235. PMID: 24448286
Bilateral cochlear implantation in children and the impact of the inter-implant interval.
Lammers MJ, Venekamp RP, Grolman W, van der Heijden GJ
Laryngoscope 2014 Apr;124(4):993-9. Epub 2013 Oct 10 doi: 10.1002/lary.24395. PMID: 24122619
Effectiveness of multi-channel unilateral cochlear implants for profoundly deaf children: a systematic review.
Bond M, Elston J, Mealing S, Anderson R, Weiner G, Taylor RS, Liu Z, Stein K
Clin Otolaryngol 2009 Jun;34(3):199-211. doi: 10.1111/j.1749-4486.2009.01916.x. PMID: 19531168

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