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Carcinoma of liver and intrahepatic biliary tract

MedGen UID:
78921
Concept ID:
C0279000
Neoplastic Process
Synonyms: Cancer of Liver; Cancer of Liver and Intrahepatic Biliary Tract; Cancer of the Liver; Cancer of the Liver and Intrahepatic Biliary Tract; Carcinoma of liver and IBT; carcinoma of liver and IBT; carcinoma of liver and intrahepatic biliary tract; hepatocellular carcinoma plus intrahepatic cholangiocarcinoma; Liver and Intrahepatic Bile Duct Cancer; Liver and Intrahepatic Bile Duct Carcinoma; liver and intrahepatic bile duct carcinoma; Liver and Intrahepatic Biliary Tract Cancer; liver and intrahepatic biliary tract cancer; Liver and Intrahepatic Biliary Tract Carcinoma; liver and intrahepatic biliary tract carcinoma; Liver Cancer; Liver Carcinoma; Primary Liver Carcinoma; primary liver carcinoma
 
Monarch Initiative: MONDO:0018531
Orphanet: ORPHA424936

Definition

A carcinoma that arises from the hepatocytes or intrahepatic bile ducts. The main subtypes are hepatocellular carcinoma (hepatoma) and cholangiocarcinoma. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVCarcinoma of liver and intrahepatic biliary tract

Professional guidelines

PubMed

Elvevi A, Laffusa A, Scaravaglio M, Rossi RE, Longarini R, Stagno AM, Cristoferi L, Ciaccio A, Cortinovis DL, Invernizzi P, Massironi S
Ann Hepatol 2022 Sep-Oct;27(5):100737. Epub 2022 Jul 7 doi: 10.1016/j.aohep.2022.100737. PMID: 35809836
Marrero JA, Ahn J, Rajender Reddy K; Americal College of Gastroenterology
Am J Gastroenterol 2014 Sep;109(9):1328-47; quiz 1348. Epub 2014 Aug 19 doi: 10.1038/ajg.2014.213. PMID: 25135008
Rizvi S, Gores GJ
Gastroenterology 2013 Dec;145(6):1215-29. Epub 2013 Oct 15 doi: 10.1053/j.gastro.2013.10.013. PMID: 24140396Free PMC Article

Recent clinical studies

Etiology

Lapitz A, Azkargorta M, Milkiewicz P, Olaizola P, Zhuravleva E, Grimsrud MM, Schramm C, Arbelaiz A, O'Rourke CJ, La Casta A, Milkiewicz M, Pastor T, Vesterhus M, Jimenez-Agüero R, Dill MT, Lamarca A, Valle JW, Macias RIR, Izquierdo-Sanchez L, Pérez Castaño Y, Caballero-Camino FJ, Riaño I, Krawczyk M, Ibarra C, Bustamante J, Nova-Camacho LM, Falcon-Perez JM, Elortza F, Perugorria MJ, Andersen JB, Bujanda L, Karlsen TH, Folseraas T, Rodrigues PM, Banales JM
J Hepatol 2023 Jul;79(1):93-108. Epub 2023 Mar 1 doi: 10.1016/j.jhep.2023.02.027. PMID: 36868481Free PMC Article
Ma J, Li J, Jin C, Yang J, Zheng C, Chen K, Xie Y, Yang Y, Bo Z, Wang J, Su Q, Wang J, Chen G, Wang Y
Liver Int 2023 Jan;43(1):221-233. Epub 2022 Nov 8 doi: 10.1111/liv.15466. PMID: 36300678
Elvevi A, Laffusa A, Scaravaglio M, Rossi RE, Longarini R, Stagno AM, Cristoferi L, Ciaccio A, Cortinovis DL, Invernizzi P, Massironi S
Ann Hepatol 2022 Sep-Oct;27(5):100737. Epub 2022 Jul 7 doi: 10.1016/j.aohep.2022.100737. PMID: 35809836
Sarcognato S, Sacchi D, Fassan M, Fabris L, Cadamuro M, Zanus G, Cataldo I, Capelli P, Baciorri F, Cacciatore M, Guido M
Pathologica 2021 Jun;113(3):158-169. doi: 10.32074/1591-951X-252. PMID: 34294934Free PMC Article
Sia D, Villanueva A, Friedman SL, Llovet JM
Gastroenterology 2017 Mar;152(4):745-761. Epub 2016 Dec 30 doi: 10.1053/j.gastro.2016.11.048. PMID: 28043904

Diagnosis

Lapitz A, Azkargorta M, Milkiewicz P, Olaizola P, Zhuravleva E, Grimsrud MM, Schramm C, Arbelaiz A, O'Rourke CJ, La Casta A, Milkiewicz M, Pastor T, Vesterhus M, Jimenez-Agüero R, Dill MT, Lamarca A, Valle JW, Macias RIR, Izquierdo-Sanchez L, Pérez Castaño Y, Caballero-Camino FJ, Riaño I, Krawczyk M, Ibarra C, Bustamante J, Nova-Camacho LM, Falcon-Perez JM, Elortza F, Perugorria MJ, Andersen JB, Bujanda L, Karlsen TH, Folseraas T, Rodrigues PM, Banales JM
J Hepatol 2023 Jul;79(1):93-108. Epub 2023 Mar 1 doi: 10.1016/j.jhep.2023.02.027. PMID: 36868481Free PMC Article
Elvevi A, Laffusa A, Scaravaglio M, Rossi RE, Longarini R, Stagno AM, Cristoferi L, Ciaccio A, Cortinovis DL, Invernizzi P, Massironi S
Ann Hepatol 2022 Sep-Oct;27(5):100737. Epub 2022 Jul 7 doi: 10.1016/j.aohep.2022.100737. PMID: 35809836
Weber M, Lam M, Chiesa C, Konijnenberg M, Cremonesi M, Flamen P, Gnesin S, Bodei L, Kracmerova T, Luster M, Garin E, Herrmann K
Eur J Nucl Med Mol Imaging 2022 Apr;49(5):1682-1699. Epub 2022 Feb 11 doi: 10.1007/s00259-021-05600-z. PMID: 35146577Free PMC Article
Sarcognato S, Sacchi D, Fassan M, Fabris L, Cadamuro M, Zanus G, Cataldo I, Capelli P, Baciorri F, Cacciatore M, Guido M
Pathologica 2021 Jun;113(3):158-169. doi: 10.32074/1591-951X-252. PMID: 34294934Free PMC Article
Marrero JA, Ahn J, Rajender Reddy K; Americal College of Gastroenterology
Am J Gastroenterol 2014 Sep;109(9):1328-47; quiz 1348. Epub 2014 Aug 19 doi: 10.1038/ajg.2014.213. PMID: 25135008

Therapy

Pinter M, Scheiner B, Pinato DJ
Lancet Gastroenterol Hepatol 2023 Aug;8(8):760-770. Epub 2023 Jun 14 doi: 10.1016/S2468-1253(23)00147-4. PMID: 37327807
Ma J, Li J, Jin C, Yang J, Zheng C, Chen K, Xie Y, Yang Y, Bo Z, Wang J, Su Q, Wang J, Chen G, Wang Y
Liver Int 2023 Jan;43(1):221-233. Epub 2022 Nov 8 doi: 10.1111/liv.15466. PMID: 36300678
Vogel A, Segatto O, Stenzinger A, Saborowski A
Annu Rev Med 2023 Jan 27;74:293-306. Epub 2022 Sep 28 doi: 10.1146/annurev-med-042921-024707. PMID: 36170665
Weber M, Lam M, Chiesa C, Konijnenberg M, Cremonesi M, Flamen P, Gnesin S, Bodei L, Kracmerova T, Luster M, Garin E, Herrmann K
Eur J Nucl Med Mol Imaging 2022 Apr;49(5):1682-1699. Epub 2022 Feb 11 doi: 10.1007/s00259-021-05600-z. PMID: 35146577Free PMC Article
Ma L, Hernandez MO, Zhao Y, Mehta M, Tran B, Kelly M, Rae Z, Hernandez JM, Davis JL, Martin SP, Kleiner DE, Hewitt SM, Ylaya K, Wood BJ, Greten TF, Wang XW
Cancer Cell 2019 Oct 14;36(4):418-430.e6. Epub 2019 Oct 3 doi: 10.1016/j.ccell.2019.08.007. PMID: 31588021Free PMC Article

Prognosis

Cheng K, Cai N, Zhu J, Yang X, Liang H, Zhang W
Cancer Commun (Lond) 2022 Nov;42(11):1112-1140. Epub 2022 Sep 7 doi: 10.1002/cac2.12345. PMID: 36069342Free PMC Article
Elvevi A, Laffusa A, Scaravaglio M, Rossi RE, Longarini R, Stagno AM, Cristoferi L, Ciaccio A, Cortinovis DL, Invernizzi P, Massironi S
Ann Hepatol 2022 Sep-Oct;27(5):100737. Epub 2022 Jul 7 doi: 10.1016/j.aohep.2022.100737. PMID: 35809836
Ma L, Hernandez MO, Zhao Y, Mehta M, Tran B, Kelly M, Rae Z, Hernandez JM, Davis JL, Martin SP, Kleiner DE, Hewitt SM, Ylaya K, Wood BJ, Greten TF, Wang XW
Cancer Cell 2019 Oct 14;36(4):418-430.e6. Epub 2019 Oct 3 doi: 10.1016/j.ccell.2019.08.007. PMID: 31588021Free PMC Article
Sia D, Villanueva A, Friedman SL, Llovet JM
Gastroenterology 2017 Mar;152(4):745-761. Epub 2016 Dec 30 doi: 10.1053/j.gastro.2016.11.048. PMID: 28043904
Rizvi S, Gores GJ
Gastroenterology 2013 Dec;145(6):1215-29. Epub 2013 Oct 15 doi: 10.1053/j.gastro.2013.10.013. PMID: 24140396Free PMC Article

Clinical prediction guides

Yang X, Wang J, Wang H
Eur J Clin Invest 2023 Aug;53(8):e14002. Epub 2023 Apr 17 doi: 10.1111/eci.14002. PMID: 37029746
Lapitz A, Azkargorta M, Milkiewicz P, Olaizola P, Zhuravleva E, Grimsrud MM, Schramm C, Arbelaiz A, O'Rourke CJ, La Casta A, Milkiewicz M, Pastor T, Vesterhus M, Jimenez-Agüero R, Dill MT, Lamarca A, Valle JW, Macias RIR, Izquierdo-Sanchez L, Pérez Castaño Y, Caballero-Camino FJ, Riaño I, Krawczyk M, Ibarra C, Bustamante J, Nova-Camacho LM, Falcon-Perez JM, Elortza F, Perugorria MJ, Andersen JB, Bujanda L, Karlsen TH, Folseraas T, Rodrigues PM, Banales JM
J Hepatol 2023 Jul;79(1):93-108. Epub 2023 Mar 1 doi: 10.1016/j.jhep.2023.02.027. PMID: 36868481Free PMC Article
Ma J, Li J, Jin C, Yang J, Zheng C, Chen K, Xie Y, Yang Y, Bo Z, Wang J, Su Q, Wang J, Chen G, Wang Y
Liver Int 2023 Jan;43(1):221-233. Epub 2022 Nov 8 doi: 10.1111/liv.15466. PMID: 36300678
Weber M, Lam M, Chiesa C, Konijnenberg M, Cremonesi M, Flamen P, Gnesin S, Bodei L, Kracmerova T, Luster M, Garin E, Herrmann K
Eur J Nucl Med Mol Imaging 2022 Apr;49(5):1682-1699. Epub 2022 Feb 11 doi: 10.1007/s00259-021-05600-z. PMID: 35146577Free PMC Article
Zhou YW, Li QF, Chen YY, Wang K, Pu D, Chen XR, Li CH, Jiang L, Wang Y, Li Q, Yang Y, Gou HF, Bi F, Liu JY, Chen Y, Qiu M
Eur J Surg Oncol 2022 Jul;48(7):1559-1566. Epub 2022 Jan 31 doi: 10.1016/j.ejso.2022.01.023. PMID: 35115213

Recent systematic reviews

Miyazaki Y, Kokudo T, Amikura K, Kageyama Y, Takahashi A, Ohkohchi N, Sakamoto H
Jpn J Clin Oncol 2017 Mar 1;47(3):206-212. doi: 10.1093/jjco/hyw182. PMID: 27940488
Amini N, Ejaz A, Spolverato G, Maithel SK, Kim Y, Pawlik TM
J Gastrointest Surg 2014 Dec;18(12):2136-48. Epub 2014 Oct 10 doi: 10.1007/s11605-014-2667-1. PMID: 25300798
Ravaioli M, Ercolani G, Neri F, Cescon M, Stacchini G, Del Gaudio M, Cucchetti A, Pinna AD
World J Gastroenterol 2014 May 14;20(18):5345-52. doi: 10.3748/wjg.v20.i18.5345. PMID: 24833864Free PMC Article
Zhimin G, Noor H, Jian-Bo Z, Lin W, Jha RK
Med Sci Monit 2013 Aug 7;19:648-56. doi: 10.12659/MSM.889379. PMID: 23921971Free PMC Article
Lau SH, Lau WY
Hepatobiliary Pancreat Dis Int 2012 Feb;11(1):12-7. doi: 10.1016/s1499-3872(11)60119-7. PMID: 22251465

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