Etiology
Jone PN,
Ivy DD,
Hauck A,
Karamlou T,
Truong U,
Coleman RD,
Sandoval JP,
Del Cerro Marín MJ,
Eghtesady P,
Tillman K,
Krishnan US
Circ Heart Fail
2023 Jul;16(7):e00080.
Epub 2023 Jun 26
doi: 10.1161/HHF.0000000000000080.
PMID: 37357777
Rosenkranz S,
Pausch C,
Coghlan JG,
Huscher D,
Pittrow D,
Grünig E,
Staehler G,
Vizza CD,
Gall H,
Distler O,
Delcroix M,
Ghofrani HA,
Ewert R,
Kabitz HJ,
Skowasch D,
Behr J,
Milger K,
Halank M,
Wilkens H,
Seyfarth HJ,
Held M,
Scelsi L,
Neurohr C,
Vonk-Noordegraaf A,
Ulrich S,
Klose H,
Claussen M,
Eisenmann S,
Schmidt KH,
Remppis BA,
Skride A,
Jureviciene E,
Gumbiene L,
Miliauskas S,
Löffler-Ragg J,
Lange TJ,
Olsson KM,
Hoeper MM,
Opitz C
J Heart Lung Transplant
2023 Jan;42(1):102-114.
Epub 2022 Oct 13
doi: 10.1016/j.healun.2022.10.003.
PMID: 36333206
Toshner M,
Church C,
Harbaum L,
Rhodes C,
Villar Moreschi SS,
Liley J,
Jones R,
Arora A,
Batai K,
Desai AA,
Coghlan JG,
Gibbs JSR,
Gor D,
Gräf S,
Harlow L,
Hernandez-Sanchez J,
Howard LS,
Humbert M,
Karnes J,
Kiely DG,
Kittles R,
Knightbridge E,
Lam B,
Lutz KA,
Nichols WC,
Pauciulo MW,
Pepke-Zaba J,
Suntharalingam J,
Soubrier F,
Trembath RC,
Schwantes-An TL,
Wort SJ,
Wilkins MR,
Gaine S,
Morrell NW,
Corris PA;
Uniphy Clinical Trials Network
Eur Respir J
2022 Mar;59(3)
Epub 2022 Mar 10
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PMID: 34588193Free PMC Article
Poch D,
Mandel J
Ann Intern Med
2021 Apr;174(4):ITC49-ITC64.
Epub 2021 Apr 13
doi: 10.7326/AITC202104200.
PMID: 33844574
Pulido T,
Adzerikho I,
Channick RN,
Delcroix M,
Galiè N,
Ghofrani HA,
Jansa P,
Jing ZC,
Le Brun FO,
Mehta S,
Mittelholzer CM,
Perchenet L,
Sastry BK,
Sitbon O,
Souza R,
Torbicki A,
Zeng X,
Rubin LJ,
Simonneau G;
SERAPHIN Investigators
N Engl J Med
2013 Aug 29;369(9):809-18.
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PMID: 23984728
Diagnosis
Jone PN,
Ivy DD,
Hauck A,
Karamlou T,
Truong U,
Coleman RD,
Sandoval JP,
Del Cerro Marín MJ,
Eghtesady P,
Tillman K,
Krishnan US
Circ Heart Fail
2023 Jul;16(7):e00080.
Epub 2023 Jun 26
doi: 10.1161/HHF.0000000000000080.
PMID: 37357777
Rosenkranz S,
Pausch C,
Coghlan JG,
Huscher D,
Pittrow D,
Grünig E,
Staehler G,
Vizza CD,
Gall H,
Distler O,
Delcroix M,
Ghofrani HA,
Ewert R,
Kabitz HJ,
Skowasch D,
Behr J,
Milger K,
Halank M,
Wilkens H,
Seyfarth HJ,
Held M,
Scelsi L,
Neurohr C,
Vonk-Noordegraaf A,
Ulrich S,
Klose H,
Claussen M,
Eisenmann S,
Schmidt KH,
Remppis BA,
Skride A,
Jureviciene E,
Gumbiene L,
Miliauskas S,
Löffler-Ragg J,
Lange TJ,
Olsson KM,
Hoeper MM,
Opitz C
J Heart Lung Transplant
2023 Jan;42(1):102-114.
Epub 2022 Oct 13
doi: 10.1016/j.healun.2022.10.003.
PMID: 36333206
Hoeper MM,
Dwivedi K,
Pausch C,
Lewis RA,
Olsson KM,
Huscher D,
Pittrow D,
Grünig E,
Staehler G,
Vizza CD,
Gall H,
Distler O,
Opitz C,
Gibbs JSR,
Delcroix M,
Park DH,
Ghofrani HA,
Ewert R,
Kaemmerer H,
Kabitz HJ,
Skowasch D,
Behr J,
Milger K,
Lange TJ,
Wilkens H,
Seyfarth HJ,
Held M,
Dumitrescu D,
Tsangaris I,
Vonk-Noordegraaf A,
Ulrich S,
Klose H,
Claussen M,
Eisenmann S,
Schmidt KH,
Swift AJ,
Thompson AAR,
Elliot CA,
Rosenkranz S,
Condliffe R,
Kiely DG,
Halank M
Lancet Respir Med
2022 Oct;10(10):937-948.
Epub 2022 Jun 28
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PMID: 35777416Free PMC Article
Poch D,
Mandel J
Ann Intern Med
2021 Apr;174(4):ITC49-ITC64.
Epub 2021 Apr 13
doi: 10.7326/AITC202104200.
PMID: 33844574
Vonk-Noordegraaf A,
Haddad F,
Chin KM,
Forfia PR,
Kawut SM,
Lumens J,
Naeije R,
Newman J,
Oudiz RJ,
Provencher S,
Torbicki A,
Voelkel NF,
Hassoun PM
J Am Coll Cardiol
2013 Dec 24;62(25 Suppl):D22-33.
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PMID: 24355638
Therapy
Hoeper MM,
Badesch DB,
Ghofrani HA,
Gibbs JSR,
Gomberg-Maitland M,
McLaughlin VV,
Preston IR,
Souza R,
Waxman AB,
Grünig E,
Kopeć G,
Meyer G,
Olsson KM,
Rosenkranz S,
Xu Y,
Miller B,
Fowler M,
Butler J,
Koglin J,
de Oliveira Pena J,
Humbert M;
STELLAR Trial Investigators
N Engl J Med
2023 Apr 20;388(16):1478-1490.
Epub 2023 Mar 6
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PMID: 36877098
Zhang H,
Wei Y,
Zhang C,
Yang Z,
Kan J,
Gu H,
Fan F,
Gu H,
Wang Q,
Xie D,
Zhang G,
Guo X,
Yin Y,
Jin B,
Zhou H,
Yang Z,
Wang Z,
Xin Y,
Zhang C,
Meng L,
Wang X,
Sun J,
Zhao C,
Zhang J,
Yan X,
Chen F,
Yao C,
Stone GW,
Chen SL
JACC Cardiovasc Interv
2022 Dec 12;15(23):2412-2423.
Epub 2022 Sep 18
doi: 10.1016/j.jcin.2022.09.013.
PMID: 36121246
Attard G,
Murphy L,
Clarke NW,
Cross W,
Jones RJ,
Parker CC,
Gillessen S,
Cook A,
Brawley C,
Amos CL,
Atako N,
Pugh C,
Buckner M,
Chowdhury S,
Malik Z,
Russell JM,
Gilson C,
Rush H,
Bowen J,
Lydon A,
Pedley I,
O'Sullivan JM,
Birtle A,
Gale J,
Srihari N,
Thomas C,
Tanguay J,
Wagstaff J,
Das P,
Gray E,
Alzoueb M,
Parikh O,
Robinson A,
Syndikus I,
Wylie J,
Zarkar A,
Thalmann G,
de Bono JS,
Dearnaley DP,
Mason MD,
Gilbert D,
Langley RE,
Millman R,
Matheson D,
Sydes MR,
Brown LC,
Parmar MKB,
James ND;
Systemic Therapy in Advancing or Metastatic Prostate cancer: Evaluation of Drug Efficacy (STAMPEDE) investigators
Lancet
2022 Jan 29;399(10323):447-460.
Epub 2021 Dec 23
doi: 10.1016/S0140-6736(21)02437-5.
PMID: 34953525Free PMC Article
Waxman A,
Restrepo-Jaramillo R,
Thenappan T,
Ravichandran A,
Engel P,
Bajwa A,
Allen R,
Feldman J,
Argula R,
Smith P,
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Tapson V,
Nathan SD
N Engl J Med
2021 Jan 28;384(4):325-334.
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PMID: 33440084
Pulido T,
Adzerikho I,
Channick RN,
Delcroix M,
Galiè N,
Ghofrani HA,
Jansa P,
Jing ZC,
Le Brun FO,
Mehta S,
Mittelholzer CM,
Perchenet L,
Sastry BK,
Sitbon O,
Souza R,
Torbicki A,
Zeng X,
Rubin LJ,
Simonneau G;
SERAPHIN Investigators
N Engl J Med
2013 Aug 29;369(9):809-18.
doi: 10.1056/NEJMoa1213917.
PMID: 23984728
Prognosis
Rosenkranz S,
Pausch C,
Coghlan JG,
Huscher D,
Pittrow D,
Grünig E,
Staehler G,
Vizza CD,
Gall H,
Distler O,
Delcroix M,
Ghofrani HA,
Ewert R,
Kabitz HJ,
Skowasch D,
Behr J,
Milger K,
Halank M,
Wilkens H,
Seyfarth HJ,
Held M,
Scelsi L,
Neurohr C,
Vonk-Noordegraaf A,
Ulrich S,
Klose H,
Claussen M,
Eisenmann S,
Schmidt KH,
Remppis BA,
Skride A,
Jureviciene E,
Gumbiene L,
Miliauskas S,
Löffler-Ragg J,
Lange TJ,
Olsson KM,
Hoeper MM,
Opitz C
J Heart Lung Transplant
2023 Jan;42(1):102-114.
Epub 2022 Oct 13
doi: 10.1016/j.healun.2022.10.003.
PMID: 36333206
Condon DF,
Agarwal S,
Chakraborty A,
Auer N,
Vazquez R,
Patel H,
Zamanian RT,
de Jesus Perez VA
Chest
2022 Apr;161(4):1060-1072.
Epub 2021 Oct 13
doi: 10.1016/j.chest.2021.10.010.
PMID: 34655569Free PMC Article
Blay JY,
Serrano C,
Heinrich MC,
Zalcberg J,
Bauer S,
Gelderblom H,
Schöffski P,
Jones RL,
Attia S,
D'Amato G,
Chi P,
Reichardt P,
Meade J,
Shi K,
Ruiz-Soto R,
George S,
von Mehren M
Lancet Oncol
2020 Jul;21(7):923-934.
Epub 2020 Jun 5
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PMID: 32511981Free PMC Article
Vonk-Noordegraaf A,
Haddad F,
Chin KM,
Forfia PR,
Kawut SM,
Lumens J,
Naeije R,
Newman J,
Oudiz RJ,
Provencher S,
Torbicki A,
Voelkel NF,
Hassoun PM
J Am Coll Cardiol
2013 Dec 24;62(25 Suppl):D22-33.
doi: 10.1016/j.jacc.2013.10.027.
PMID: 24355638
Sharifi M,
Bay C,
Skrocki L,
Rahimi F,
Mehdipour M;
“MOPETT” Investigators
Am J Cardiol
2013 Jan 15;111(2):273-7.
Epub 2012 Oct 24
doi: 10.1016/j.amjcard.2012.09.027.
PMID: 23102885
Clinical prediction guides
Rosenkranz S,
Pausch C,
Coghlan JG,
Huscher D,
Pittrow D,
Grünig E,
Staehler G,
Vizza CD,
Gall H,
Distler O,
Delcroix M,
Ghofrani HA,
Ewert R,
Kabitz HJ,
Skowasch D,
Behr J,
Milger K,
Halank M,
Wilkens H,
Seyfarth HJ,
Held M,
Scelsi L,
Neurohr C,
Vonk-Noordegraaf A,
Ulrich S,
Klose H,
Claussen M,
Eisenmann S,
Schmidt KH,
Remppis BA,
Skride A,
Jureviciene E,
Gumbiene L,
Miliauskas S,
Löffler-Ragg J,
Lange TJ,
Olsson KM,
Hoeper MM,
Opitz C
J Heart Lung Transplant
2023 Jan;42(1):102-114.
Epub 2022 Oct 13
doi: 10.1016/j.healun.2022.10.003.
PMID: 36333206
Ogo T,
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Sakao S,
Abe K,
Matoba S,
Motoki H,
Takama N,
Ako J,
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Joho S,
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Saeki T,
Sugano T,
Tsujino I,
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Yamamoto C,
Tanabe N,
Tatsumi K;
Study Group
Eur Respir J
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PMID: 34824052Free PMC Article
Toshner M,
Church C,
Harbaum L,
Rhodes C,
Villar Moreschi SS,
Liley J,
Jones R,
Arora A,
Batai K,
Desai AA,
Coghlan JG,
Gibbs JSR,
Gor D,
Gräf S,
Harlow L,
Hernandez-Sanchez J,
Howard LS,
Humbert M,
Karnes J,
Kiely DG,
Kittles R,
Knightbridge E,
Lam B,
Lutz KA,
Nichols WC,
Pauciulo MW,
Pepke-Zaba J,
Suntharalingam J,
Soubrier F,
Trembath RC,
Schwantes-An TL,
Wort SJ,
Wilkins MR,
Gaine S,
Morrell NW,
Corris PA;
Uniphy Clinical Trials Network
Eur Respir J
2022 Mar;59(3)
Epub 2022 Mar 10
doi: 10.1183/13993003.02463-2020.
PMID: 34588193Free PMC Article
Zhang J,
Gajjala S,
Agrawal P,
Tison GH,
Hallock LA,
Beussink-Nelson L,
Lassen MH,
Fan E,
Aras MA,
Jordan C,
Fleischmann KE,
Melisko M,
Qasim A,
Shah SJ,
Bajcsy R,
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Circulation
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PMID: 30354459Free PMC Article
Pulido T,
Adzerikho I,
Channick RN,
Delcroix M,
Galiè N,
Ghofrani HA,
Jansa P,
Jing ZC,
Le Brun FO,
Mehta S,
Mittelholzer CM,
Perchenet L,
Sastry BK,
Sitbon O,
Souza R,
Torbicki A,
Zeng X,
Rubin LJ,
Simonneau G;
SERAPHIN Investigators
N Engl J Med
2013 Aug 29;369(9):809-18.
doi: 10.1056/NEJMoa1213917.
PMID: 23984728