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Criss-cross heart

MedGen UID:
8181
Concept ID:
C0010334
Congenital Abnormality
Synonyms: Criss cross Heart; Criss-cross Heart; Criss-cross Hearts; Crisscross Heart; Crisscross Hearts; Heart, Criss-cross; Heart, Crisscross; Hearts, Criss-cross; Hearts, Crisscross
SNOMED CT: Crisscross heart (253269002); Criss-cross heart (253269002); Twisted atrioventricular connections (253269002)
Modes of inheritance:
Unknown inheritance
MedGen UID:
989040
Concept ID:
CN307042
Finding
Source: Orphanet
Hereditary clinical entity whose mode of inheritance is unknown.
 
Monarch Initiative: MONDO:0015449
Orphanet: ORPHA1461

Definition

Criss cross heart (CCH) is a cardiac malformation where the inflow streams of the two ventricles cross due to twisting of the heart about its major axis. The clinical features depend on the particular cardiac defects associated, like simple or corrected transposition of the great arteries and ventricular septal defects. [from ORDO]

Term Hierarchy

Professional guidelines

PubMed

Vorisek CN, Kurkevych A, Kuhn V, Stessig R, Ritgen J, Degenhardt J, Enzensberger C, Wolter A, Götte M, Khalil M, Akintürk H, Axt-Fliedner R
Ultraschall Med 2022 Dec;43(6):e90-e97. Epub 2020 Jul 16 doi: 10.1055/a-1205-0289. PMID: 32674186
Ravi P, Fruitman D, Mills L, Colen T, Hornberger LK
Am J Cardiol 2017 Mar 15;119(6):916-922. Epub 2016 Dec 18 doi: 10.1016/j.amjcard.2016.11.046. PMID: 28215417
Li S, Luo G, Norwitz ER, Wang C, Ouyang S, Yao Y, Wen H, Chen C, Fu Q, Xia X, Bi J, Zhu J
J Perinatol 2013 Feb;33(2):98-102. Epub 2012 May 3 doi: 10.1038/jp.2012.56. PMID: 22555779

Recent clinical studies

Etiology

Valverde I, Gomez G, Byrne N, Anwar S, Silva Cerpa MA, Martin Talavera M, Pushparajah K, Velasco Forte MN
Anat Sci Educ 2022 Jul;15(4):719-730. Epub 2021 Oct 25 doi: 10.1002/ase.2105. PMID: 34008341
Vorisek CN, Kurkevych A, Kuhn V, Stessig R, Ritgen J, Degenhardt J, Enzensberger C, Wolter A, Götte M, Khalil M, Akintürk H, Axt-Fliedner R
Ultraschall Med 2022 Dec;43(6):e90-e97. Epub 2020 Jul 16 doi: 10.1055/a-1205-0289. PMID: 32674186
Manuel D, Ghosh G, Joseph G, Lahiri A, George PV
Indian Heart J 2018 Jan-Feb;70(1):71-74. Epub 2017 Mar 23 doi: 10.1016/j.ihj.2017.03.008. PMID: 29455791Free PMC Article
Li S, Luo G, Norwitz ER, Wang C, Ouyang S, Yao Y, Wen H, Chen C, Fu Q, Xia X, Bi J, Zhu J
J Perinatol 2013 Feb;33(2):98-102. Epub 2012 May 3 doi: 10.1038/jp.2012.56. PMID: 22555779
Ming Z, Yumin Z
Pediatr Cardiol 2008 Mar;29(2):359-65. Epub 2007 Oct 5 doi: 10.1007/s00246-007-9069-z. PMID: 17917768

Diagnosis

Sheikh AM, Kanwal A, Sattar H
J Pak Med Assoc 2022 Jul;72(7):1429-1431. doi: 10.47391/JPMA.3162. PMID: 36156574
Vorisek CN, Kurkevych A, Kuhn V, Stessig R, Ritgen J, Degenhardt J, Enzensberger C, Wolter A, Götte M, Khalil M, Akintürk H, Axt-Fliedner R
Ultraschall Med 2022 Dec;43(6):e90-e97. Epub 2020 Jul 16 doi: 10.1055/a-1205-0289. PMID: 32674186
Manuel D, Ghosh G, Joseph G, Lahiri A, George PV
Indian Heart J 2018 Jan-Feb;70(1):71-74. Epub 2017 Mar 23 doi: 10.1016/j.ihj.2017.03.008. PMID: 29455791Free PMC Article
Ravi P, Fruitman D, Mills L, Colen T, Hornberger LK
Am J Cardiol 2017 Mar 15;119(6):916-922. Epub 2016 Dec 18 doi: 10.1016/j.amjcard.2016.11.046. PMID: 28215417
Li S, Luo G, Norwitz ER, Wang C, Ouyang S, Yao Y, Wen H, Chen C, Fu Q, Xia X, Bi J, Zhu J
J Perinatol 2013 Feb;33(2):98-102. Epub 2012 May 3 doi: 10.1038/jp.2012.56. PMID: 22555779

Therapy

Valverde I, Gomez G, Byrne N, Anwar S, Silva Cerpa MA, Martin Talavera M, Pushparajah K, Velasco Forte MN
Anat Sci Educ 2022 Jul;15(4):719-730. Epub 2021 Oct 25 doi: 10.1002/ase.2105. PMID: 34008341
Seckeler MD, White SC, Klewer SE, Ott P
JACC Clin Electrophysiol 2019 Aug;5(8):998-999. Epub 2019 Aug 19 doi: 10.1016/j.jacep.2019.05.009. PMID: 31439306
Bonanomi C, Gherbesi E, Colli AM, Malanchini G, Lombardi F
Echocardiography 2019 Jan;36(1):204-205. Epub 2018 Nov 29 doi: 10.1111/echo.14204. PMID: 30488490

Prognosis

Vorisek CN, Kurkevych A, Kuhn V, Stessig R, Ritgen J, Degenhardt J, Enzensberger C, Wolter A, Götte M, Khalil M, Akintürk H, Axt-Fliedner R
Ultraschall Med 2022 Dec;43(6):e90-e97. Epub 2020 Jul 16 doi: 10.1055/a-1205-0289. PMID: 32674186
Ravi P, Fruitman D, Mills L, Colen T, Hornberger LK
Am J Cardiol 2017 Mar 15;119(6):916-922. Epub 2016 Dec 18 doi: 10.1016/j.amjcard.2016.11.046. PMID: 28215417
Ming Z, Yumin Z
Pediatr Cardiol 2008 Mar;29(2):359-65. Epub 2007 Oct 5 doi: 10.1007/s00246-007-9069-z. PMID: 17917768
Duncan WJ, Wong KK, Freedom RM
Pediatr Cardiol 2006 Sep-Oct;27(5):604-7. Epub 2006 Aug 1 doi: 10.1007/s00246-006-1153-2. PMID: 16897313
Sato K, Ohara S, Tsukaguchi I, Yasui K, Nakada T, Tamai M, Kobayashi Y, Kozuka T
Circulation 1978 Feb;57(2):396-400. doi: 10.1161/01.cir.57.2.396. PMID: 618633

Clinical prediction guides

Valverde I, Gomez G, Byrne N, Anwar S, Silva Cerpa MA, Martin Talavera M, Pushparajah K, Velasco Forte MN
Anat Sci Educ 2022 Jul;15(4):719-730. Epub 2021 Oct 25 doi: 10.1002/ase.2105. PMID: 34008341
Vorisek CN, Kurkevych A, Kuhn V, Stessig R, Ritgen J, Degenhardt J, Enzensberger C, Wolter A, Götte M, Khalil M, Akintürk H, Axt-Fliedner R
Ultraschall Med 2022 Dec;43(6):e90-e97. Epub 2020 Jul 16 doi: 10.1055/a-1205-0289. PMID: 32674186
Manuel D, Ghosh G, Joseph G, Lahiri A, George PV
Indian Heart J 2018 Jan-Feb;70(1):71-74. Epub 2017 Mar 23 doi: 10.1016/j.ihj.2017.03.008. PMID: 29455791Free PMC Article
Ravi P, Fruitman D, Mills L, Colen T, Hornberger LK
Am J Cardiol 2017 Mar 15;119(6):916-922. Epub 2016 Dec 18 doi: 10.1016/j.amjcard.2016.11.046. PMID: 28215417
Yang YL, Wang XF, Cheng TO, Xie MX, Lü Q, He L, Lu XF, Wang J, Li L, Anderson RH
Int J Cardiol 2010 Apr 15;140(2):133-7. Epub 2009 Sep 16 doi: 10.1016/j.ijcard.2009.08.039. PMID: 19762095

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